title: Rosette-forming glioneuronal tumor outside the fourth ventricle: a case-based update.
abstract: BACKGROUND
  Rosette-forming glioneuronal tumors (RGNTs) that do not involve the fourth ventricle are rare. RGNTs were originally thought to be exclusively localized into the fourth ventricle but were found in various anatomical localizations.
  
  
  METHODS
  We review the literature and found 32 cases of this particular RGNT. The outcome was excellent with no mortality reported after surgical treatment. Only two patients had received adjuvant therapy for progression. We added one case of a RGNT located in the cerebellar hemisphere.
  She underwent a subtotal removal with no evidence of progression after. This WHO grade I tumor with a specific biphasic histopathology is of a good oncological outcome after surgical treatment. A long follow-up is needed as recurrence or metastatic progressions exist.
authors.affiliation: Department of Pediatric Neurosurgery, Necker-Enfants Malades Hospital, 149 Rue de Sèvres, 75015, Paris, France. pierre-aurelien.beuriat@neurochirurgie.fr.|Department of Pediatric Neurosurgery, Neurological and Neurosurgical Hospital Pierre Wertheimer, 59 Boulevard Pinel, 69677, Lyon Cedex, France. pierre-aurelien.beuriat@neurochirurgie.fr.
authors.forename: Pierre-Aurelien
authors.initials: PA
authors.lastname: Beuriat
authors.affiliation: Department of Neuropathology, Sainte-Anne Hospital, 75674, Paris, Cedex 14, France.
authors.forename: Arnault
authors.initials: A
authors.lastname: Tauziede-Espariat
authors.affiliation: Department of Neuropathology, Sainte-Anne Hospital, 75674, Paris, Cedex 14, France.|Paris Descartes University, 12 Rue de l'École de Médecine, 75006, Paris, France.
authors.forename: Melanie
authors.initials: M
authors.lastname: Pages
authors.affiliation: Department of Neuropathology, Sainte-Anne Hospital, 75674, Paris, Cedex 14, France.|Paris Descartes University, 12 Rue de l'École de Médecine, 75006, Paris, France.
authors.forename: Pascalae
authors.initials: P
authors.lastname: Varlet
authors.affiliation: Department of Pediatric Neurosurgery, Necker-Enfants Malades Hospital, 149 Rue de Sèvres, 75015, Paris, France.|Department of Pediatric Neurosurgery, Neurological and Neurosurgical Hospital Pierre Wertheimer, 59 Boulevard Pinel, 69677, Lyon Cedex, France.
authors.forename: Federico
authors.initials: F
authors.lastname: Di Rocco
mesh_terms: D002551:Cerebral Ventricle Neoplasms / Q000175:diagnosis / Q000628:therapy; D019468:Disease Management; D005260:Female; D018303:Ganglioglioma / Q000175:diagnosis / Q000628:therapy; D006801:Humans; D008279:Magnetic Resonance Imaging; D008297:Male; D012397:Rosette Formation; D055815:Young Adult
keywords: Cerebellum; Pediatric; Posterior fossa; Rosette-forming glioneuronal tumor