title: Prenatal Sonographic Features of a Double Aortic Arch: Literature Review and Perinatal Management.
abstract: A double aortic arch is a relatively uncommon anomaly occasionally associated with congenital heart disease or the chromosome 22q11 deletion. We report a case of prenatal diagnosis of a double aortic arch in which the sonographic features in the 3-vessel and trachea view are highlighted. A PubMed-based search was made to retrieve all cases of prenatal diagnosis of double aortic arch. A total of 13 articles and 35 cases were found. The average gestational age at diagnosis was 29 weeks. Six cases had associated cardiac anomalies. Only 1 case had the 22q11 deletion, showing extracardiac anomalies without cardiac defect. The postnatal evolution was characterized by symptoms of tracheoesophageal compression in 72.4% of the cases. Detection of a double aortic arch should be followed by a thorough fetal scan and echocardiography, and a chromosomal study should be considered when the sonographic findings are consistent with the 22q11 deletion.
authors.affiliation: Departments of Obstetrics and Gynecology (D.T., R.P., F.G., J.D.L.-L.) and Pediatric Cardiology (T.A.), Hospital General Gregorio Marañón, Universidad Complutense de Madrid, Madrid, Spain; and Department of Obstetrics and Gynecology, Hospital Central de la Defensa Gómez Ulla, Universidad de Alcalá de Henares, Madrid, Spain (C.B.).
authors.forename: Duna
authors.initials: D
authors.lastname: Trobo
authors.affiliation: Departments of Obstetrics and Gynecology (D.T., R.P., F.G., J.D.L.-L.) and Pediatric Cardiology (T.A.), Hospital General Gregorio Marañón, Universidad Complutense de Madrid, Madrid, Spain; and Department of Obstetrics and Gynecology, Hospital Central de la Defensa Gómez Ulla, Universidad de Alcalá de Henares, Madrid, Spain (C.B.).
authors.forename: Coral
authors.initials: C
authors.lastname: Bravo
authors.affiliation: Departments of Obstetrics and Gynecology (D.T., R.P., F.G., J.D.L.-L.) and Pediatric Cardiology (T.A.), Hospital General Gregorio Marañón, Universidad Complutense de Madrid, Madrid, Spain; and Department of Obstetrics and Gynecology, Hospital Central de la Defensa Gómez Ulla, Universidad de Alcalá de Henares, Madrid, Spain (C.B.).
authors.forename: Teresa
authors.initials: T
authors.lastname: Alvarez
authors.affiliation: Departments of Obstetrics and Gynecology (D.T., R.P., F.G., J.D.L.-L.) and Pediatric Cardiology (T.A.), Hospital General Gregorio Marañón, Universidad Complutense de Madrid, Madrid, Spain; and Department of Obstetrics and Gynecology, Hospital Central de la Defensa Gómez Ulla, Universidad de Alcalá de Henares, Madrid, Spain (C.B.).
authors.forename: Ricardo
authors.initials: R
authors.lastname: Pérez
authors.affiliation: Departments of Obstetrics and Gynecology (D.T., R.P., F.G., J.D.L.-L.) and Pediatric Cardiology (T.A.), Hospital General Gregorio Marañón, Universidad Complutense de Madrid, Madrid, Spain; and Department of Obstetrics and Gynecology, Hospital Central de la Defensa Gómez Ulla, Universidad de Alcalá de Henares, Madrid, Spain (C.B.).
authors.forename: Francisco
authors.initials: F
authors.lastname: Gámez
authors.affiliation: Departments of Obstetrics and Gynecology (D.T., R.P., F.G., J.D.L.-L.) and Pediatric Cardiology (T.A.), Hospital General Gregorio Marañón, Universidad Complutense de Madrid, Madrid, Spain; and Department of Obstetrics and Gynecology, Hospital Central de la Defensa Gómez Ulla, Universidad de Alcalá de Henares, Madrid, Spain (C.B.). jdeleonluis@yahoo.es.
authors.forename: Juan
authors.initials: J
authors.lastname: De León-Luis
mesh_terms: D000328:Adult; D001013:Aorta, Thoracic / Q000002:abnormalities* / Q000000981:diagnostic imaging* / Q000196:embryology; D005260:Female; D006330:Heart Defects, Congenital / Q000000981:diagnostic imaging* / Q000628:therapy; D006801:Humans; D008297:Male; D018743:Perinatal Care; D011247:Pregnancy; D016896:Treatment Outcome; D016216:Ultrasonography, Prenatal / Q000379:methods*
keywords: aortic arch anomalies; fetal double aortic arch; fetal echocardiography; prenatal diagnosis; vascular ring