title: Moyamoya Disease Associated with Recurrent Right Thalamic Haemorrhage and Hydrocephalus: A Case Report.
abstract: Moyamoya disease, a rare chronic, progressive cerebrovascular disease leads to occlusion of intracranial internal carotid arteries and its proximal branches. We report a case of a 51-year-old female who presented with recurrent thalamic bleed and intraventricular haemorrhage nine years apart in the same territory. The first bleed was managed conservatively and second bleed led to development of hydrocephalus. The acute phase of the hydrocephalus was managed by external ventricular drainage and the final CSF diversion was managed by ventriculoperitoneal shunt. The definitive treatment could not be done to denial of consent from the patient. We present the case to highlight the role CSF diversion as a means of palliative treatment for the Moyamoya disease.
authors.affiliation: Sikkim Manipal Institute of Medical Sciences, Central Referral Hospital, Department of Neurosurgery, Gangtok, Sikkim, India.
authors.forename: Rohan
authors.initials: R
authors.lastname: Sinha
authors.forename: Amit Kumar
authors.initials: AK
authors.lastname: Jain
authors.forename: Nitin
authors.initials: N
authors.lastname: Jagdhane
authors.forename: Parvati
authors.initials: P
authors.lastname: Nandy
authors.forename: Satish Kumar
authors.initials: SK
authors.lastname: Khanna
mesh_terms: D002543:Cerebral Hemorrhage / Q000209:etiology*; D005260:Female; D006801:Humans; D006849:Hydrocephalus / Q000209:etiology* / Q000601:surgery; D008875:Middle Aged; D009072:Moyamoya Disease / Q000150:complications*; D013788:Thalamus / Q000473:pathology; D017287:Ventriculoperitoneal Shunt