title: Linear acral pseudolymphomatous angiokeratoma of children with associated nail dystrophy.
abstract: Acral pseudolymphomatous angiokeratoma of children (APACHE) is a rare entity that typically occurs on the extremities of young females. Although linear arrangement of cutaneous lesions has been rarely reported, accompanying nail dystrophy has not been linked with this condition to our knowledge. We describe a case of linearly-oriented infiltrative papules and nodules on the index finger of a young female with associated onychodystrophy. Histology demonstrated a heavy lymphocytic infiltrate with plasma cells and proliferation of blood vessels consistent with APACHE. Our case is unique given the linear array of cutaneous lesions and associated nail dystrophy.
authors.affiliation: Baylor Scott & White Health, Texas A&M Health Science Center. cmcfaddin@sw.org.
authors.forename: Courtney
authors.initials: C
authors.lastname: McFaddin
authors.forename: John
authors.initials: J
authors.lastname: Greene
authors.forename: Palak
authors.initials: P
authors.lastname: Parekh
mesh_terms: D000794:Angiokeratoma / Q000150:complications / Q000175:diagnosis / Q000473:pathology*; D001707:Biopsy, Needle; D002648:Child; D005260:Female; D005385:Fingers / Q000473:pathology; D006801:Humans; D007150:Immunohistochemistry; D009260:Nail Diseases / Q000150:complications / Q000175:diagnosis / Q000473:pathology*; D011379:Prognosis; D019310:Pseudolymphoma / Q000150:complications / Q000175:diagnosis / Q000473:pathology*; D035583:Rare Diseases; D012878:Skin Neoplasms / Q000150:complications / Q000175:diagnosis / Q000473:pathology*