title: Congenital Absence of One Pulmonary Valve Cusp With Other Hypoplastic Cusps.
abstract: Congenital absence of a single pulmonary valve cusp is extremely rare. We report a case of a 38-year-old woman with a confirmed congenital absence of a single pulmonary valve cusp associated with dextrocardia. The other 2 leaflets were moderately hypoplastic, and transthoracic echocardiography showed severe pulmonary regurgitation. This combination of lesions has not been reported previously. Pulmonary valve replacement using a composite biologic valved conduit was performed with an excellent outcome.
authors.affiliation: Department of Cardiovascular Surgery, Fukui Cardiovascular Center, Fukui, Japan. Electronic address: rockyyamazaki@yahoo.co.jp.
authors.forename: Sachiko
authors.initials: S
authors.lastname: Yamazaki
authors.affiliation: Department of Cardiovascular Surgery, Fukui Cardiovascular Center, Fukui, Japan; Department of Pediatric Cardiovascular Surgery, Children's Medical Center, Kyoto Prefectural University of Medicine, Kyoto, Japan.
authors.forename: Masaaki
authors.initials: M
authors.lastname: Yamagishi
authors.affiliation: Department of Cardiovascular Surgery, Fukui Cardiovascular Center, Fukui, Japan.
authors.forename: Kouichi
authors.initials: K
authors.lastname: Nishida
authors.affiliation: Department of Cardiovascular Surgery, Fukui Cardiovascular Center, Fukui, Japan.
authors.forename: Satoshi
authors.initials: S
authors.lastname: Tamura
authors.affiliation: Department of Cardiovascular Surgery, Fukui Cardiovascular Center, Fukui, Japan.
authors.forename: Osamu
authors.initials: O
authors.lastname: Monta
authors.affiliation: Department of Cardiovascular Surgery, Fukui Cardiovascular Center, Fukui, Japan.
authors.forename: Satoshi
authors.initials: S
authors.lastname: Numata
authors.affiliation: Department of Cardiovascular Surgery, Fukui Cardiovascular Center, Fukui, Japan.
authors.forename: Yasushi
authors.initials: Y
authors.lastname: Tsutsumi
authors.affiliation: Department of Cardiovascular Surgery, Fukui Cardiovascular Center, Fukui, Japan.
authors.forename: Hirokazu
authors.initials: H
authors.lastname: Ohashi
mesh_terms: D000015:Abnormalities, Multiple / Q000601:surgery; D000328:Adult; D003914:Dextrocardia / Q000150:complications; D005260:Female; D006801:Humans; D011664:Pulmonary Valve / Q000002:abnormalities* / Q000601:surgery; D011665:Pulmonary Valve Insufficiency / Q000150:complications