title: Bilateral Multifocal Renal Angiomyolipoma Associated with Wunderlich's Syndrome in A Tuberous Sclerosis Patient.
abstract: Renal Angiomyolipoma (renal AML) is a benign clonal neoplasm with a incidence of 0.3-3%, occurring as isolated sporadic entity or in association with Tuberous sclerosis (TS) in 80% cases. Multiple, bilateral renal AML are considered diagnostic of Tuberous sclerosis. Wunderlich's syndrome, a urological emergency is a spontaneous nontraumatic bleeding into subcapsular and or peri-renal space and is a life threatening complication of renal AML occurring in 10% cases which has to be timely diagnosed and treated. Here, we present an unusual case of TS with bilateral, multifocal renal AML in a 25-year-old female who presented with Wunderlich's syndrome, which is a rare but life threatening complication that has to be suspected, timely diagnosed and treated. We have discussed the importance of early diagnosis, timely treatment, follow up and education of patient and relatives of the possible complications associated.
authors.affiliation: Assistant Professor, Department of Pathology, Sri Devaraj Urs Medical College , SDUAHER, Tamaka, Kolar, India .
authors.forename: Sushma
authors.initials: S
authors.lastname: Shankar
authors.affiliation: Post Graduate Student, Department of Surgery, Sri Devaraj Urs Medical College , SDUAHER, Tamaka, Kolar, India .
authors.forename: Kiran Shankar
authors.initials: KS
authors.lastname: Hulikanthimatt
authors.affiliation: Assistant Professor, Department of Urology, Sri Devaraj Urs Medical College , SDUAHER, Tamaka, Kolar, India .
authors.forename: Shreeharsha Mallappa
authors.initials: SM
authors.lastname: Awatti
authors.affiliation: Professor, Department of Pathology, Sri Devaraj Urs Medical College , SDUAHER, Tamaka, Kolar, India .
authors.forename: Suresh Turuvekere
authors.initials: ST
authors.lastname: Narayanrao
keywords: Bilateral; Female; Life threatening