title: Congenital Erythropoietic Porphyria With Calcific Constrictive Pericarditis: A Case Report and Brief Review of Literature.
abstract: An 18-year-old boy with congenital erythropoietic porphyria and calcific constrictive pericarditis underwent total pericardiectomy. The cause of pericardial calcification could be deposition of porphyrins in the pericardium. Surgical importance of this rare condition is highlighted.
authors.affiliation: Cardiothoracic Sciences Centre, All India Institute of Medical Sciences, New Delhi, India ujjwalchow@rediffmail.com ujjwalchowdhury@gmail.com.
authors.forename: Ujjwal K
authors.initials: UK
authors.lastname: Chowdhury
authors.affiliation: Cardiothoracic Sciences Centre, All India Institute of Medical Sciences, New Delhi, India.
authors.forename: Kartik
authors.initials: K
authors.lastname: Patel
authors.affiliation: Cardiothoracic Sciences Centre, All India Institute of Medical Sciences, New Delhi, India.
authors.forename: Sandeep
authors.initials: S
authors.lastname: Seth
authors.affiliation: Cardiothoracic Sciences Centre, All India Institute of Medical Sciences, New Delhi, India.
authors.forename: Ruma
authors.initials: R
authors.lastname: Ray
authors.affiliation: Cardiothoracic Sciences Centre, All India Institute of Medical Sciences, New Delhi, India.
authors.forename: Priya
authors.initials: P
authors.lastname: Jagia
authors.affiliation: Cardiothoracic Sciences Centre, All India Institute of Medical Sciences, New Delhi, India.
authors.forename: Manoj
authors.initials: M
authors.lastname: Sahu
mesh_terms: D000293:Adolescent; D004452:Echocardiography; D006801:Humans; D008297:Male; D010492:Pericardiectomy / Q000379:methods*; D010494:Pericarditis, Constrictive / Q000209:etiology* / Q000235:genetics / Q000601:surgery; D010496:Pericardium / Q000378:metabolism; D017092:Porphyria, Erythropoietic / Q000150:complications* / Q000175:diagnosis / Q000235:genetics; D011166:Porphyrins / Q000378:metabolism; D014057:Tomography, X-Ray Computed
chemical_list: D011166:Porphyrins
keywords: calcification; pericardium; porphyria