title: Orthotopic Heart Transplantation in an Adult Patient with Heterotaxy Syndrome: Surgical Implications.
abstract: Modified techniques for orthotopic heart transplantation are mandatory when complex congenital anomalies are associated in adult patients. An unusual case of a heterotaxy syndrome and dilated cardiomyopathy following mitral ring annuloplasty is presented in a 62-year-old male. Orthotopic cardiac transplantation was performed by using a modified operative strategy: selective peripheral and central venous cannulation according to the thoraco-abdominal venous challenges, biatrial technique, and preservation of venous drainage via the native coronary sinus. We discuss the anatomical features of heterotaxy in adult patients and surgical approaches when heart transplantation is needed.
authors.affiliation: Department of Congenital Cardiac Surgery, Gregorio Marañón Hospital, Madrid, Spain.
authors.forename: María-Teresa
authors.initials: MT
authors.lastname: González-López
authors.affiliation: Department of Congenital Cardiac Surgery, Gregorio Marañón Hospital, Madrid, Spain.
authors.forename: Ramón
authors.initials: R
authors.lastname: Pérez-Caballero-Martínez
authors.affiliation: Department of Cardiac Surgery Department, Gregorio Marañón Hospital, Madrid, Spain.
authors.forename: Carlos
authors.initials: C
authors.lastname: Amoros-Rivera
authors.affiliation: Cardiovascular Perfusion Team, Gregorio Marañón Hospital, Madrid, Spain.
authors.forename: José
authors.initials: J
authors.lastname: Zamorano-Serrano
authors.affiliation: Department of Congenital Cardiac Surgery, Gregorio Marañón Hospital, Madrid, Spain.
authors.forename: Ana-María
authors.initials: AM
authors.lastname: Pita-Fernández
authors.affiliation: Department of Congenital Cardiac Surgery, Gregorio Marañón Hospital, Madrid, Spain.
authors.forename: Juan-Miguel
authors.initials: JM
authors.lastname: Gil-Jaurena
mesh_terms: D002311:Cardiomyopathy, Dilated / Q000150:complications; D002405:Catheterization, Central Venous / Q000379:methods; D002406:Catheterization, Peripheral / Q000379:methods; D054326:Coronary Sinus; D004322:Drainage; D016027:Heart Transplantation / Q000379:methods*; D059446:Heterotaxy Syndrome / Q000209:etiology / Q000473:pathology / Q000601:surgery*; D006801:Humans; D008297:Male; D008875:Middle Aged; D058386:Mitral Valve Annuloplasty