title: [Atypic hemolytic uremic syndrome taken for Goodpasture's syndrome: A case report].
abstract: We report the case of a patient suffering from atypical hemolytic uremic syndrome with inaugural intra-alveolar hemorrhage. Clinical features and detection of circulating anti-glomerular basal membrane antibodies first raise the possibility of a Goodpasture syndrome. Renal biopsy allows to correct the diagnosis. Partial remission is obtained thanks to specific care and eculizumab infusions.
authors.affiliation: Service de néphrologie, hôpital d'instruction des armées du Val-de-Grâce, 74, boulevard Port-Royal, 75005 Paris, France. Electronic address: marie.garraud@gmail.com.
authors.forename: Marie
authors.initials: M
authors.lastname: Bourgault
authors.affiliation: Service de néphrologie, hôpital d'instruction des armées du Val-de-Grâce, 74, boulevard Port-Royal, 75005 Paris, France.
authors.forename: Damien
authors.initials: D
authors.lastname: Sarret
authors.affiliation: Service de néphrologie, hôpital d'instruction des armées du Val-de-Grâce, 74, boulevard Port-Royal, 75005 Paris, France.
authors.forename: Pierre
authors.initials: P
authors.lastname: Isnard
authors.affiliation: Service d'anatomopathologie, hôpital Necker, 149, rue de Sèvres, 75015 Paris, France.
authors.forename: Marion
authors.initials: M
authors.lastname: Rabant
authors.affiliation: Service de néphrologie, hôpital d'instruction des armées du Val-de-Grâce, 74, boulevard Port-Royal, 75005 Paris, France.
authors.forename: Jacques
authors.initials: J
authors.lastname: Labaye
mesh_terms: D019867:Anti-Glomerular Basement Membrane Disease / Q000175:diagnosis*; D061067:Antibodies, Monoclonal, Humanized / Q000627:therapeutic use; D003937:Diagnosis, Differential; D006463:Hemolytic-Uremic Syndrome / Q000175:diagnosis*; D006470:Hemorrhage / Q000209:etiology; D006801:Humans; D007668:Kidney / Q000473:pathology*; D008171:Lung Diseases / Q000209:etiology*; D008297:Male; D008875:Middle Aged
chemical_list: D061067:Antibodies, Monoclonal, Humanized; C481642:eculizumab
keywords: Anti-GBM antibodies; Anticorps anti-MBG; Atypical hemolytic uremic syndrome; Eculizumab; Hémorragie intra-alvéolaire; Intra-alveolar hemorrhage; Plasma exchange; Pneumo-renal syndrome; Syndrome hémolytique et urémique atypique; Syndrome pneumo-rénal; Échanges plasmatiques; Éculizumab