title: Primary desmoplastic small round cell tumor of the testis: First case in India and review of the literature.
abstract: The purpose of this study is to describe the aggressive clinical behavior of desmoplastic small round cell tumor (DSRCT) of the testis and review of the literature. A 17-year-old male having painless testicular mass and neck swelling diagnosed to have metastatic DSRCT of the testis. Patient received aggressive chemotherapy with P6 protocol. The patient progressed on treatment and died due to extensive metastasis. Primary DSRCT of the testis is extremely rare mesenchymal tumor occurring in adolescence, with a tendency for extensive metastases. Management should be multimodal approach with aggressive polychemotherapy, surgical tumor debulking and radiotherapy. However the overall prognosis is very poor with <20% survival rates at 2 years.
authors.forename: M V
authors.initials: MV
authors.lastname: Manjula
authors.affiliation: Department of Radiation Oncology, Yashoda Cancer Institute, Somajiguda, Hyderabad, Andhra Pradesh, India.
authors.forename: Y S
authors.initials: YS
authors.lastname: Pawar
mesh_terms: D000293:Adolescent; D058405:Desmoplastic Small Round Cell Tumor / Q000175:diagnosis / Q000473:pathology / Q000628:therapy*; D006801:Humans; D008297:Male; D011379:Prognosis; D013736:Testicular Neoplasms / Q000175:diagnosis / Q000473:pathology / Q000628:therapy*