title: Anomalous Origin of One Pulmonary Artery From the Ascending Aorta: From Diagnosis to Treatment in Angola.
abstract: BACKGROUND
  Anomalous origin of one pulmonary artery is a rare congenital heart disease in which one pulmonary artery branch originates from the ascending aorta.
  
  
  OBJECTIVE
  To describe the experience of a cardiothoracic center in an African country to repair anomalous origin of one pulmonary artery in the context of Portugal-Angola collaboration.
  
  
  METHODS
  Between March 2011 and March 2015, four consecutive patients with anomalous origin of pulmonary artery branch underwent surgical correction. The mean age was 1.6 months. The mean weight was 4 kg. All had right pulmonary artery branch originating from the ascending aorta. All patients underwent direct implantation of right pulmonary branch to main pulmonary artery. Two patents had patent ductus arteriosus and one had atrial septal defect. Two patients had pulmonary hypertension.
  
  
  RESULTS
  There was no registration of death. The mean cardiopulmonary bypass time was 75.5 ± 4.5 minutes, mean aortic cross-clamping time was 40 ± 5.6 minutes, and mean duration of the postoperative intensive care unit stay was 6.8 ± 5.7 days. At discharge, one patient had residual gradient of 25 mm Hg, the remainder had no significant gradient. The mean follow-up time was 11 months (5-28 months). One week after discharge, one patient presented operative wound dehiscence. At the last follow-up, all patients were alive, and no significant residual gradient or stenosis at site of anastomosis was observed. No reintervention was required.
  
  
  CONCLUSIONS
  Anomalous origin of one pulmonary artery is a rare but potentially treatable lesion if operated early in life. Direct implantation was a good technique with good short-term results.
authors.affiliation: Cardio-Thoracic Center, Clínica Girassol, Luanda, Angola valdanympub@gmail.com.
authors.forename: Valdano
authors.initials: V
authors.lastname: Manuel
authors.affiliation: Cardio-Thoracic Center, Clínica Girassol, Luanda, Angola Hospital Cruz Vermelha, Lisbon, Portugal.
authors.forename: Miguel
authors.initials: M
authors.lastname: Sousa-Uva
authors.affiliation: Cardiology Department, Hospital Militar Principal/Instituto Superior, Luanda, Angola.
authors.forename: Humberto
authors.initials: H
authors.lastname: Morais
authors.affiliation: Cardio-Thoracic Center, Clínica Girassol, Luanda, Angola Hospital Cruz Vermelha, Lisbon, Portugal.
authors.forename: Manuel P
authors.initials: MP
authors.lastname: Magalhães
authors.affiliation: Cardio-Thoracic Center, Clínica Girassol, Luanda, Angola Hospital Cruz Vermelha, Lisbon, Portugal.
authors.forename: Albino
authors.initials: A
authors.lastname: Pedro
authors.affiliation: Cardio-Thoracic Center, Clínica Girassol, Luanda, Angola.
authors.forename: Gade
authors.initials: G
authors.lastname: Miguel
authors.affiliation: Cardio-Thoracic Center, Clínica Girassol, Luanda, Angola Hospital Cruz Vermelha, Lisbon, Portugal.
authors.forename: Maria A S
authors.initials: MA
authors.lastname: Nunes
authors.affiliation: Service of Pediatric Cardiology, Hospital Pediátrico David Bernardino, Luanda, Angola.
authors.forename: Sebastiana
authors.initials: S
authors.lastname: Gamboa
authors.affiliation: Cardio-Thoracic Center, Clínica Girassol, Luanda, Angola.
authors.forename: António P F
authors.initials: AP
authors.lastname: Júnior
mesh_terms: D000792:Angiography; D000810:Angola / Q000453:epidemiology; D001011:Aorta / Q000002:abnormalities* / Q000601:surgery; D003937:Diagnosis, Differential; D004452:Echocardiography; D005260:Female; D006801:Humans; D015994:Incidence; D007223:Infant; D007231:Infant, Newborn; D008297:Male; D008875:Middle Aged; D011651:Pulmonary Artery / Q000002:abnormalities* / Q000601:surgery; D015996:Survival Rate / Q000639:trends; D014057:Tomography, X-Ray Computed; D054079:Vascular Malformations / Q000175:diagnosis* / Q000601:surgery; D014656:Vascular Surgical Procedures / Q000379:methods*
keywords: aorta; congenital heart disease; congenital heart surgery; hemitruncus; pulmonary artery; pulmonary hypertension