title: A Case of Severe Unicuspid Aortic Valve Stenosis: Valve Repair With Tricuspidization in an Adult.
abstract: A 33-year-old male was referred to our institute with acute heart failure. The patient was found to have a unicuspid aortic valve (UAV) and severe aortic stenosis. He had been followed at a local university hospital during childhood. However, he stopped visiting the outpatient clinic after becoming an adult. His condition subsequently worsened, and he ultimately presented to our hospital with cardiogenic shock. In Japan, some adult congenital heart disease (ACHD) patients continue to be followed by pediatric cardiologists, though the patterns of practice are variable. This report describes the case of a patient who became lost to follow-up in early adulthood. We thus focus on this ACHD case as an example of the effects of inadequate communication among doctors and the need to establish better ACHD management protocols for treating this patient population.
authors.affiliation: Division of Cardiovascular Medicine, Toho University, Ohashi Medical Center, Meguro, Tokyo, Japan masahide.tokue@med.toho-u.ac.jp.
authors.forename: Masahide
authors.initials: M
authors.lastname: Tokue
authors.affiliation: Division of Cardiovascular Medicine, Toho University, Ohashi Medical Center, Meguro, Tokyo, Japan.
authors.forename: Hidehiko
authors.initials: H
authors.lastname: Hara
authors.affiliation: Division of Cardiovascular Medicine, Toho University, Ohashi Medical Center, Meguro, Tokyo, Japan.
authors.forename: Naohiko
authors.initials: N
authors.lastname: Sahara
authors.affiliation: Division of Cardiovascular Medicine, Toho University, Ohashi Medical Center, Meguro, Tokyo, Japan.
authors.forename: Kenji
authors.initials: K
authors.lastname: Yamazaki
authors.affiliation: Department of Cardiovascular Surgery, Toho University, Ohashi Medical Center, Meguro, Tokyo, Japan.
authors.forename: Hiromasa
authors.initials: H
authors.lastname: Yamashita
authors.affiliation: Department of Pathology, Toho University, Ohashi Medical Center, Meguro, Tokyo, Japan.
authors.forename: Kei
authors.initials: K
authors.lastname: Takahashi
authors.affiliation: Department of Cardiovascular Surgery, Toho University, Ohashi Medical Center, Meguro, Tokyo, Japan.
authors.forename: Shigeyuki
authors.initials: S
authors.lastname: Ozaki
authors.affiliation: Division of Cardiovascular Medicine, Toho University, Ohashi Medical Center, Meguro, Tokyo, Japan.
authors.forename: Kaoru
authors.initials: K
authors.lastname: Sugi
authors.affiliation: Division of Cardiovascular Medicine, Toho University, Ohashi Medical Center, Meguro, Tokyo, Japan.
authors.forename: Masato
authors.initials: M
authors.lastname: Nakamura
mesh_terms: D000328:Adult; D001021:Aortic Valve / Q000002:abnormalities* / Q000601:surgery; D001024:Aortic Valve Stenosis / Q000151:congenital* / Q000175:diagnosis / Q000601:surgery; D002648:Child; D015150:Echocardiography, Doppler; D019918:Heart Valve Prosthesis Implantation / Q000379:methods*; D006801:Humans; D008297:Male; D012720:Severity of Illness Index; D014261:Tricuspid Valve / Q000601:surgery*
keywords: adult congenital heart disease; aortic valve; calcification; heart failure; repair