title: Report of the European Respiratory Society/European Cystic Fibrosis Society task force on the care of adults with cystic fibrosis.
abstract: The improved survival in people with cystic fibrosis has led to an increasing number of patients reaching adulthood. This trend is likely to be maintained over the next decades, suggesting a need to increase the number of centres with expertise in the management of adult patients with cystic fibrosis. These centres should be capable of delivering multidisciplinary care addressing the complexity of the disease, in addition to addressing the psychological burden on patients and their families. Further issues that require attention are organ transplantation and end of life management.Lung disease in adults with cystic fibrosis drives most of the clinical care requirements, and major life-threatening complications, such as respiratory infection, respiratory failure, pneumothorax and haemoptysis, and the management of lung transplantation require expertise from trained respiratory physicians. The taskforce therefore strongly reccommends that medical leadership in multidisciplinary adult teams should be attributed to a respiratory physician adequately trained in cystic fibrosis management.The task force suggests the implementation of a core curriculum for trainees in adult respiratory medicine and the selection and accreditation of training centres that deliver postgraduate training to the standards of the HERMES programme.
authors.affiliation: School of Medicine, Dentistry and Biomedical Sciences, Queen's University of Belfast, Belfast, UK s.elborn@qub.ac.uk.
authors.forename: J Stuart
authors.initials: JS
authors.lastname: Elborn
authors.affiliation: Dept of Thoracic Medicine, The Prince Charles Hospital and QIMR Berghofer Medical Research Institute, Brisbane, Australia.
authors.forename: Scott C
authors.initials: SC
authors.lastname: Bell
authors.affiliation: Dept of Respiratory Medicine, Royal Brompton Hospital, London, UK.
authors.forename: Susan L
authors.initials: SL
authors.lastname: Madge
authors.affiliation: Dept of Respiratory Medicine, Cochin Hospital, Assistance Publique Hôpitaux de Paris and Université Paris Descartes, Sorbonne Paris Cité, Paris, France.
authors.forename: Pierre-Regis
authors.initials: PR
authors.lastname: Burgel
authors.affiliation: Cystic Fibrosis Center, Azienda Ospedaliera Universitaria Integrata, Verona, Italy.
authors.forename: Carlo
authors.initials: C
authors.lastname: Castellani
authors.affiliation: Paediatric and Adult CF Units, Leeds Teaching Hospitals Trust, Leeds, UK.
authors.forename: Steven
authors.initials: S
authors.lastname: Conway
authors.affiliation: Cystic Fibrosis Europe, Brussels, Belgium.
authors.forename: Karleen
authors.initials: K
authors.lastname: De Rijcke
authors.affiliation: Mukoviszidose eV, Berlin, Germany.
authors.forename: Birgit
authors.initials: B
authors.lastname: Dembski
authors.affiliation: Dept of Medical Microbiology, Motol University Hospital and 2nd Faculty of Medicine, Charles University, Prague, Czech Republic.
authors.forename: Pavel
authors.initials: P
authors.lastname: Drevinek
authors.affiliation: Haga Teaching Hospital, Dept of Pulmonology and Cystic Fibrosis, The Hague, The Netherlands.
authors.forename: Harry G M
authors.initials: HG
authors.lastname: Heijerman
authors.affiliation: Scottish Adult Cystic Fibrosis Service, Western General Hospital, Edinburgh, UK.
authors.forename: J Alistair
authors.initials: JA
authors.lastname: Innes
authors.affiliation: Dept of Paediatrics, Queen Silvia Children's Hospital, Sahlgrenska University Hospital, Gothenburg, Sweden.
authors.forename: Anders
authors.initials: A
authors.lastname: Lindblad
authors.affiliation: Cystic Fibrosis Foundation, Bethesda, MD, USA.
authors.forename: Bruce
authors.initials: B
authors.lastname: Marshall
authors.affiliation: CF Centre, Aarhus University Hospital, Aarhus, Denmark.
authors.forename: Hanne V
authors.initials: HV
authors.lastname: Olesen
authors.affiliation: Mukoviszidose Institut gGmbH, Bonn, Germany.
authors.forename: Andreas L
authors.initials: AL
authors.lastname: Reimann
authors.affiliation: Lung Transplant and Adult Cystic Fibrosis, Dept of Pneumology, University Hospital la FE, Valencia, Spain.
authors.forename: Ampara
authors.initials: A
authors.lastname: Solé
authors.affiliation: Dipartimento di Scienze Cliniche e di Comunità, Università degli Studi di Milano, Milan, Italy.
authors.forename: Laura
authors.initials: L
authors.lastname: Viviani
authors.affiliation: Christiane Herzog CF Centre, Dept of Respiratory Diseases, Goethe University Frankfurt am Main, Frankfurt am Main, Germany.
authors.forename: Thomas O F
authors.initials: TO
authors.lastname: Wagner
authors.affiliation: Dept of Respiratory Medicine, Hannover Medical School, Hanover, Germany.
authors.forename: Tobias
authors.initials: T
authors.lastname: Welte
authors.affiliation: Dept of Pathophysiology and Transplantation, University of Milan, IRCCS Fondazione Cà Granda, Milan, Italy francesco.blasi@unimi.it.
authors.forename: Francesco
authors.initials: F
authors.lastname: Blasi
mesh_terms: D000328:Adult; D026683:Advisory Committees; D003550:Cystic Fibrosis / Q000523:psychology / Q000628:therapy*; D019468:Disease Management; D005060:Europe; D006285:Health Planning; D006301:Health Services Needs and Demand; D006801:Humans; D016040:Lung Transplantation; D010349:Patient Compliance; D015272:Pulmonary Medicine / Q000193:education* / Q000458:organization & administration; D012944:Social Support; D012955:Societies, Medical; D013727:Terminal Care; D060305:Transition to Adult Care / Q000458:organization & administration; D000078329:Workforce