Massive Plexiform Neurofibroma of the Neck and Larynx.
Introduction Laryngeal neurofibromas are extremely rare, accounting for only 0.03 to 0.1% of benign tumors of the larynx. Objectives To report the first case of massive neck plexiform neurofibroma with intralaryngeal (supraglottic) extension in a 5-year-old boy with neurofibromatosis type 1 and to describe its treatment. Resumed Report This massive plexiform neurofibroma was surgically removed, relieving its significant respiratory obstructive symptoms without recurrence to date. Conclusion Massive neck plexiform neurofibroma with supraglottic part was found in a child with neurofibromatosis type 1; it should be included in differential diagnosis of stridor and neck mass in children. It was diagnosed and removed in early in childhood without recurrence.
Department of Otorhinolaryngology-Head and Neck Surgery, Zagazig University, Zagazig, Egypt.
Mohammad Kamal
MK
Mobashir
Department of Otorhinolaryngology-Head and Neck Surgery, Zagazig University, Zagazig, Egypt.
Abd ElRaof Said
AE
Mohamed
Department of Otorhinolaryngology-Head and Neck Surgery, Zagazig University, Zagazig, Egypt.
Mohammad Waheed
MW
El-Anwar
Department of Otorhinolaryngology-Head and Neck Surgery, Zagazig University, Zagazig, Egypt.
Ahmad Ebrahim
AE
El Sayed
Department of Pathology, Zagazig University, Zagazig, Egypt.
Mouhamad A
MA
Fouad
larynx; neck; plexiform neurofibroma