Persistent Truncus Arteriosus With Intact Ventricular Septum: Clinical, Hemodynamic and Short-term Surgical Outcome.
BACKGROUND
Truncus arteriosus with intact ventricular septum is a rare and unique variant of persistent truncus arteriosus (PTA) which usually presents with central cyanosis and congestive heart failure in neonate and early infancy. Associated cardiac and non-cardiac anomalies may affect morbidity and mortality of these patients.


METHODS
We describe clinical presentation, echocardiography and angiographic features of a 7-month old boy with PTA and intact ventricular septum who underwent surgical repair of the anomaly at our institution. Operative findings, surgical procedure and short-term outcome are reported.


CONCLUSIONS
While our patient had systemic pulmonary arterial pressure at the time of complete surgical repair, it was improved after surgery.
Cardiovascular and Neonatology Research Center, Shiraz University of Medical Sciences, Shiraz, IR Iran.
Gholamhossein
G
Ajami
Cardiothoracic Surgery Unit, Shiraz University of Medical Sciences, Shiraz, IR Iran.
Ahmad Ali
AA
Amirghofran
Cardiovascular and Neonatology Research Center, Shiraz University of Medical Sciences, Shiraz, IR Iran ; Department of Pediatrics, Namazi Hospital, Shiraz, IR Iran.
Hamid
H
Amoozgar
Cardiovascular and Neonatology Research Center, Shiraz University of Medical Sciences, Shiraz, IR Iran.
Mohammad
M
Borzouee
Intact Ventricular Septum; Outcome; Persistent; Truncus Arteriosus