Adult Form of Scimitar Syndrome Presenting as Severe Pulmonary Hypertension in a Child.
BACKGROUND
Scimitar syndrome is a rare association of congenital cardiopulmonary anomalies; the adult form is not usually is associated with pulmonary hypertension.


METHODS
6-year-old girl with recurrent episodes of cough and breathlessness, along with features of right heart enlargement. Computed tomography angiogram revealed right pulmonary veins draining into inferior vena cava with dextroposition of heart.


RESULTS
Successfully managed with surgical correction.


CONCLUSIONS
Scimitar syndrome should be considered in any child with unexplained pulmonary hypertension and dextroposed heart.
Department of Pulmonology, Institute of Child Health and Hospital for Children; and *Department of Pediatric Cardiac Surgery, Apollo Childrens Hospital; Chennai, India. Correspondence to: Dr Sivasambo Kalpana, Department of Pulmonology, Institute of Child Health and Hospital for Children, Halls road, Egmore, Chennai. drskalpana@yahoo.co.in.
Sivasambo
S
Kalpana
Sarath
S
Balaji B
Selladurai
S
Elilarasi
Neville A G
NA
Solomon
D000328:Adult; D000792:Angiography; D002648:Child; D003937:Diagnosis, Differential; D005260:Female; D006325:Heart Atria / Q000601:surgery; D006333:Heart Failure / Q000175:diagnosis / Q000209:etiology / Q000601:surgery; D006801:Humans; D006976:Hypertension, Pulmonary / Q000175:diagnosis* / Q000209:etiology / Q000601:surgery; D011667:Pulmonary Veins / Q000002:abnormalities / Q000601:surgery; D012587:Scimitar Syndrome / Q000175:diagnosis* / Q000601:surgery; D014057:Tomography, X-Ray Computed