Obstructive jaundice secondary to Morgagni hernia in an infant with Fontan circulation.
The vast majority of congenital diaphragmatic cases present with severe respiratory distress in the immediate neonatal period. Obstructive jaundice secondary to CDH is a rare presenting symptom, previously unreported with Morgagni type hernias which comprise 2% of all CDHs. Although the safety of minimally invasive repair for CDH has been shown previously, there has been little data on its safety for patients with complex congenital cardiac disease. In this case report, we present an 18-month old infant with Fontan circulation presenting with jaundice secondary to Morgagni hernia who ultimately underwent laparoscopic repair. A brief discussion of the safety of laparoscopic surgery in patients post-Fontan is included.
Section of Pediatric Surgery, Department of Surgery, University of Michigan, Ann Arbor, MI, USA.
Ihab
I
Halaweish
Section of Pediatric Surgery, Department of Surgery, University of Michigan, Ann Arbor, MI, USA.
Mathew
M
Ralls
Section of Pediatric Surgery, Department of Surgery, University of Michigan, Ann Arbor, MI, USA.
Sabina
S
Siddiqui
Section of Pediatric Gastroenterology, Department of Pediatrics, University of Michigan, Ann Arbor, MI, USA.
Chris
C
Dickinson
Section of Pediatric Surgery, Department of Surgery, University of Michigan, Ann Arbor, MI, USA. marjarbo@med.umich.edu.|C.S. Mott Children's Hospital, University of Michigan, 1540 E. Hospital Dr., SPC 4211, Ann Arbor, MI, 48109-0344, USA. marjarbo@med.umich.edu.
Marcus D
MD
Jarboe
D018729:Fontan Procedure; D065630:Hernias, Diaphragmatic, Congenital / Q000150:complications* / Q000601:surgery*; D006801:Humans; D007223:Infant; D041781:Jaundice, Obstructive / Q000150:complications*; D010535:Laparoscopy; D008297:Male; D016896:Treatment Outcome
Diaphragmatic; Fontan; Hernia; Jaundice; Morgagni; Pediatric