A Case of Extensive IgG4-Related Disease Presenting as Massive Pleural Effusion, Mediastinal Mass, and Mesenteric Lymphadenopathy in a 16-Year-Old Male.
IgG4-related disease is an immune-mediated fibro-inflammatory disease, characterized by lymphoplasmacytic infiltration composed of IgG4-positive plasma cells of various organs with elevated circulating levels of IgG4. This disease is now reported with increasing frequency and usually affects middle-aged men. Massive pleural effusion in children is an uncommon feature in IgG4-related disease. Here, we report a case of a 16-year-old male patient with extensive IgG4-related disease presenting with massive pleural effusion, mediastinal mass, and mesenteric lymphadenopathy.
Division of Pulmonology, Yonsei University College of Medicine, Seoul, Korea. ; Department of Internal Medicine, Yonsei University College of Medicine, Seoul, Korea.
Eun Kyong
EK
Goag
Division of Pulmonology, Yonsei University College of Medicine, Seoul, Korea. ; Department of Internal Medicine, Yonsei University College of Medicine, Seoul, Korea.
Ji Eun
JE
Park
Division of Pulmonology, Yonsei University College of Medicine, Seoul, Korea. ; Department of Internal Medicine, Yonsei University College of Medicine, Seoul, Korea.
Eun Hye
EH
Lee
Division of Pulmonology, Yonsei University College of Medicine, Seoul, Korea. ; Department of Internal Medicine, Yonsei University College of Medicine, Seoul, Korea.
Young Mok
YM
Park
Division of Pulmonology, Yonsei University College of Medicine, Seoul, Korea. ; Department of Internal Medicine, Yonsei University College of Medicine, Seoul, Korea.
Chi Young
CY
Kim
Division of Pulmonology, Yonsei University College of Medicine, Seoul, Korea. ; Department of Internal Medicine, Yonsei University College of Medicine, Seoul, Korea.
Jung Mo
JM
Lee
Department of Internal Medicine, Yonsei University College of Medicine, Seoul, Korea.
Young Joo
YJ
Kim
Division of Pulmonology, Yonsei University College of Medicine, Seoul, Korea. ; Department of Internal Medicine, Yonsei University College of Medicine, Seoul, Korea.
Young Sam
YS
Kim
Division of Pulmonology, Yonsei University College of Medicine, Seoul, Korea. ; Department of Internal Medicine, Yonsei University College of Medicine, Seoul, Korea.
Se Kyu
SK
Kim
Division of Pulmonology, Yonsei University College of Medicine, Seoul, Korea. ; Department of Internal Medicine, Yonsei University College of Medicine, Seoul, Korea.
Joon
J
Chang
Division of Pulmonology, Yonsei University College of Medicine, Seoul, Korea. ; Department of Internal Medicine, Yonsei University College of Medicine, Seoul, Korea.
Moo Suk
MS
Park
Division of Pulmonology, Yonsei University College of Medicine, Seoul, Korea. ; Department of Internal Medicine, Yonsei University College of Medicine, Seoul, Korea.
Kyung Soo
KS
Chung
Mediastinum; Pleural Effusion