title: [Cutaneous mastocytosis: A case report].
abstract: BACKGROUND
  Mastocytosis represents a group of diseases characterised by an excesive accumulation of mastocytes in one or multiple tissues. It can affect only the skin, or have a systemic involvement. It has a low prevalence, and the prognosis is benign in children.
  
  
  OBJECTIVE
  To report a case of urticaria pigmentosa as a subtype of cutaneous mastocytosis, and present a literature review focused on clinical findings, diagnosis and initial basic management.
  
  
  METHODS
  A child of six months of age presenting with multiple blemishes and light brown papules located on the trunk, arms and legs. The symptoms were compatible with urticaria pigmentosa, and was confirmed by biopsy. Tests to rule out systemic involvement were requested. The patient was treated with general measures, education, and antihistamines, with favourable results.
  
  
  CONCLUSIONS
  Cutaneous mastocytosis is a rare disease with a good prognosis. In childhood general measures and education are usually enough to obtain favourable results. Histamine H1 antagonists are the first line drug treatment.
authors.affiliation: Profesor asociado, Departamento de Dermatología, Facultad de Medicina, Pontificia Universidad Católica de Chile, Santiago, Chile.
authors.forename: María Soledad
authors.initials: MS
authors.lastname: Zegpi-Trueba
authors.affiliation: Médico Cirujano, CESFAM Laurita Vicuña, Puente Alto, Santiago, Chile.
authors.forename: Paula
authors.initials: P
authors.lastname: Hasbún-Acuña
authors.affiliation: Residente de Dermatología, Facultad de Medicina, Pontificia Universidad Católica de Chile, Santiago, Chile. Electronic address: dmberroeta@gmail.com.
authors.forename: Daniela
authors.initials: D
authors.lastname: Berroeta-Mauriziano
mesh_terms: D001706:Biopsy; D005260:Female; D006634:Histamine H1 Antagonists / Q000627:therapeutic use; D006801:Humans; D007223:Infant; D034701:Mastocytosis, Cutaneous / Q000175:diagnosis* / Q000473:pathology / Q000628:therapy; D011379:Prognosis; D014582:Urticaria Pigmentosa / Q000175:diagnosis* / Q000473:pathology / Q000628:therapy
chemical_list: D006634:Histamine H1 Antagonists
keywords: Antagonistas de los receptores de histamina H1; Histamine H1 antagonist; Mastocitoma; Mastocitosis; Mastocytoma; Mastocytosis; Urticaria pigmentosa