title: Mondini dysplasia with recurrent bacterial meningitis caused by three different pathogens.
abstract: Mondini dysplasia is rare, but has an important association with recurrent bacterial meningitis. We herein describe the case of a 3-year-old girl with unilateral sensorineural hearing loss who presented with three independent episodes of bacterial meningitis within 8 months. Temporal bone computed tomography indicated the characteristic features of Mondini dysplasia in the right inner ear. This was treated by surgical closure of the inner ear defect via oval window and additional vaccination was administered. Appropriate vaccination might prevent the recurrent bacterial meningitis associated with Mondini dysplasia.
authors.affiliation: Department of Pediatrics, Ogaki Municipal Hospital, Ogaki City, Gifu, Japan.
authors.forename: Hiroaki
authors.initials: H
authors.lastname: Shikano
authors.affiliation: Department of Pediatrics, Graduate School of Medicine, Gifu University, Gifu City, Gifu, Japan.
authors.forename: Hidenori
authors.initials: H
authors.lastname: Ohnishi
authors.affiliation: Department of Pediatrics, Ogaki Municipal Hospital, Ogaki City, Gifu, Japan.
authors.forename: Hisashi
authors.initials: H
authors.lastname: Fukutomi
authors.affiliation: Department of Pediatrics, Ogaki Municipal Hospital, Ogaki City, Gifu, Japan.
authors.forename: Kimiko
authors.initials: K
authors.lastname: Ito
authors.affiliation: Department of Pediatrics, Graduate School of Medicine, Gifu University, Gifu City, Gifu, Japan.
authors.forename: Masahiro
authors.initials: M
authors.lastname: Morimoto
authors.affiliation: Department of Pediatrics, Graduate School of Medicine, Gifu University, Gifu City, Gifu, Japan.
authors.forename: Takahide
authors.initials: T
authors.lastname: Teramoto
authors.affiliation: Department of Otolaryngology, Graduate School of Medicine, Gifu University, Gifu City, Gifu, Japan.
authors.forename: Mitsuhiro
authors.initials: M
authors.lastname: Aoki
authors.affiliation: Department of Otolaryngology, Graduate School of Medicine, Gifu University, Gifu City, Gifu, Japan.
authors.forename: Takezumi
authors.initials: T
authors.lastname: Nishihori
authors.affiliation: Research Institute for Microbial Diseases, Osaka University, Suita, Osaka, Japan.
authors.forename: Yukihiro
authors.initials: Y
authors.lastname: Akeda
authors.affiliation: Research Institute for Microbial Diseases, Osaka University, Suita, Osaka, Japan.|Infectious Disease Surveillance Center, National Institute of Infectious Diseases, Shinjuku, Tokyo, Japan.
authors.forename: Kazunori
authors.initials: K
authors.lastname: Oishi
authors.affiliation: Department of Pediatrics, Graduate School of Medicine, Gifu University, Gifu City, Gifu, Japan.
authors.forename: Toshiyuki
authors.initials: T
authors.lastname: Fukao
mesh_terms: D001419:Bacteria / Q000302:isolation & purification*; D002675:Child, Preschool; D005260:Female; D006319:Hearing Loss, Sensorineural / Q000150:complications* / Q000175:diagnosis; D006646:Histiocytosis, Langerhans-Cell / Q000150:complications* / Q000175:diagnosis; D006801:Humans; D016867:Immunocompromised Host; D016920:Meningitis, Bacterial / Q000150:complications* / Q000175:diagnosis / Q000382:microbiology; D014057:Tomography, X-Ray Computed
keywords: Mondini dysplasia; anomaly; bacterial meningitis; immunodeficiency; pneumococcal vaccine