title: Surgical management of a large cleft palate in a Pierre Robin sequence: A case report and review of literature.
abstract: Pierre Robin syndrome or Pierre Robin sequence (PRS) is a congenital etiologically heterogeneous condition presenting with various malformations. Here we are reporting the surgical management of an 18-month-old female baby who was referred from Department of Pediatrics with a complaint of a large cleft palate. She was taken up for palatoplasty with consent for elective tracheostomy. After genetic evaluation, the authors conclude that the presented case was a PRS in isolation with mild cardiac anomalies and an inferiorly placed hypoplastic epiglottis. Patient should be followed up and growth modifications of the jaws should be done.
authors.affiliation: Department of Oral and Maxillofacial Surgery, Armed Forces Hospital Southern Region, Kingdom of Saudi Arabia.
authors.forename: Sherry
authors.initials: S
authors.lastname: Andrews
authors.affiliation: Department of Oral and Maxillofacial Surgery, Armed Forces Hospital Southern Region, Kingdom of Saudi Arabia.
authors.forename: Mathew
authors.initials: M
authors.lastname: Sam
authors.affiliation: Department of Pedodontics, Vinayaka Missions Sankarachariyar Dental College, Salem, Tamil Nadu, India.
authors.forename: Ramesh
authors.initials: R
authors.lastname: Krishnan
authors.affiliation: Department of Oral Pathology, Vinayaka Missions Sankarachariyar Dental College, Salem, Tamil Nadu, India.
authors.forename: Maya
authors.initials: M
authors.lastname: Ramesh
authors.affiliation: Department of Orthodontics, Vinayaka Missions Sankarachariyar Dental College, Salem, Tamil Nadu, India.
authors.forename: Shiji M
authors.initials: SM
authors.lastname: Kunjappan
keywords: Cleft palate; Pierre Robin sequence; comparative genome hybridization-244 k gene; von Langenbeck technique