title: Morning Glory Syndrome with Carotid and Middle Cerebral Artery Vasculopathy.
abstract: OBJECTIVE
  To report a case of incidental asymptomatic atypical morning glory syndrome (MGS) with concomitant ipsilateral carotid and middle cerebral dysgenesis.
  
  
  METHODS
  A 6-year-old child was discovered to have incidental findings of MGS, with atypia. All visual functions were normal including vision and stereopsis. Neuroimaging revealed ipsilateral carotid and middle cerebral vascular narrowing without associated collateral vessels or cerebral ischemia commonly seen in Moyamoya disease. Subsequent annual examinations have been stable, without signs of progression.
  
  
  CONCLUSIONS
  This case demonstrates disparity between structural aberrations and final visual and neurological function and reinforces the association between MGS and intracranial vascular disruption. Full ancillary ophthalmic and neuroimaging studies should be performed in all patients with MGS with interval reassessments, even when the patient is asymptomatic and functionally intact.
authors.affiliation: *MD, FEBO †MD, FRCS, FRCOphth ‡MD Service d'Ophtalmologie, CHU de Clermont Ferrand, Clermont-Ferrand, France (HN, HD); Department of Ophthalmology, King Faisal Specialist Hospital and Research Center, Riyadh, Kingdom of Saudi Arabia (HN); Department of Surgery, North Bronx Health Network, Bronx, New York (JM); and Department of Ophthalmology and Visual Sciences, Albert Einstein College of Medicine of Yeshiva University, Bronx, New York (JM).
authors.forename: Hachemi
authors.initials: H
authors.lastname: Nezzar
authors.forename: Joyce N
authors.initials: JN
authors.lastname: Mbekeani
authors.forename: Helen
authors.initials: H
authors.lastname: Dalens
mesh_terms: D002343:Carotid Artery, Internal / Q000002:abnormalities*; D002648:Child; D003867:Depth Perception / Q000502:physiology; D005124:Eye Abnormalities / Q000175:diagnosis*; D005451:Fluorescein Angiography; D006801:Humans; D018810:Magnetic Resonance Angiography; D008297:Male; D020768:Middle Cerebral Artery / Q000002:abnormalities*; D009072:Moyamoya Disease / Q000175:diagnosis*; D009898:Optic Disk / Q000002:abnormalities*; D013577:Syndrome; D041623:Tomography, Optical Coherence; D014792:Visual Acuity / Q000502:physiology; D014794:Visual Fields