title: Idiopathic Hypertrophic Pachymeningitis in the Craniocervical Junction.
abstract: Idiopathic hypertrophic pachymeningitis (IHP) is a rare disease, and it is characterized by chronic progressive inflammatory fibrosis and thickening of the dura mater with resultant compression of the spinal cord or neural structure without any identifiable cause. It can occur in the intracranial or spinal dura mater alone or as a craniospinal form. The spinal form is rarer than the cranial form and the craniospinal form is extremely rare. We report a rare case of IHP in the craniocervical junction involving both the cranial and spinal dura mater and discuss the diagnosis and management of the disease.
authors.affiliation: Department of Neurosurgery, Dongguk University Ilsan Hospital, Goyang, Korea and Dongguk University, Seoul, Korea.
authors.forename: Jin Hyuk
authors.initials: JH
authors.lastname: Bang
authors.affiliation: Department of Neurosurgery, Dongguk University Ilsan Hospital, Goyang, Korea and Dongguk University, Seoul, Korea.
authors.forename: Keun-Tae
authors.initials: KT
authors.lastname: Cho
authors.affiliation: Department of Pathology, Dongguk University Ilsan Hospital, Goyang, Korea and Dongguk University, Seoul, Korea.
authors.forename: Eo Jin
authors.initials: EJ
authors.lastname: Kim
keywords: Craniocervical junction; Diagnosis; Idiopathic hypertrophic pachymeningitis; Treatment