title: Primary Pulmonary Sequestration With Secondary Hamartomatosis Change.
abstract: The radiologic features of intralobar pulmonary sequestration (ILPS) have been describe and include the identification of a feeding systemic artery with venous drainage through pulmonary veins. Primary sequestration associated with typical hamartoma signs is really rare and has been described only once. We describe a patient with ILPS whose radiographic findings were unusual for two reasons. First, computed tomography (CT) demonstrated a bulky mass in the pulmonary sequestration. The size of lesion and histopathology made it an unusual presentation. Final histology study demonstrated pulmonary hamartoma with predominantly adipose and cartilage differentiation, which is an unusual complication originated from ILPS. Another sign also explains the second unusual feature, intracranial cholesteatoma, occurring concurrently with ILPS.
authors.affiliation: Shandong Medical Imaging Research Institute, Affiliated to Shandong University, Jinan, P. R. China.
authors.forename: Changhu
authors.initials: C
authors.lastname: Liang
authors.affiliation: Department of Surgery, Provincial Hospital, Affiliated to Shandong University, Jinan, P. R. China.
authors.forename: Shifeng
authors.initials: S
authors.lastname: Xu
authors.affiliation: Shandong Medical Imaging Research Institute, Affiliated to Shandong University, Jinan, P. R. China.
authors.forename: Bin
authors.initials: B
authors.lastname: Zhao
authors.affiliation: Department of Thoracic Surgery, Provincial Hospital, Affiliated to Shandong University, Jinan, P. R. China.
authors.forename: Guoyuan
authors.initials: G
authors.lastname: Ma
authors.affiliation: Shandong Provincial Center for Disease Control and Prevention, Public Health Institute 72, Jinan, P. R. China.
authors.forename: Yinglin
authors.initials: Y
authors.lastname: Du
keywords: Hamartoma; Pulmonary Sequestration; Syndrome