title: Double-level osteotomy and one-stage reconstruction with long intramedullary femoral nail to correct a severe proximal and diaphyseal femur deformity in a patient with polyostotic fibrous dysplasia: case report and literatures review.
abstract: Proximal femur is often involved with varus and retroversion deformity in polyostotic fibrous dysplasia (PFD). Multiple corrective osteotomies with intramedullary nails in two stages is recommended procedure as some authors described. We report a case using double-level osteotomy and one-stage reconstruction with intramedullary nail in a patient with painful proximal femur and diaphysis varus deformity, the neck-shaft angle was corrected from 95° pre-operatively to 125° post-operatively, the patient was free of pain and no evidence of recurrence at the 24-month follow up. The operative design and method were described, and a review of related literatures about the treatment alteration for PFD and relevant operative selection were also performed.
authors.affiliation: The Department of Orthopedics, Huashan Hospital, Fudan University Shanghai, China.
authors.forename: Feiyan
authors.initials: F
authors.lastname: Chen
authors.affiliation: The Department of Orthopedics, Huashan Hospital, Fudan University Shanghai, China.
authors.forename: Yibing
authors.initials: Y
authors.lastname: Wei
authors.affiliation: The Department of Orthopedics, Huashan Hospital, Fudan University Shanghai, China.
authors.forename: Jun
authors.initials: J
authors.lastname: Xia
authors.affiliation: The Department of Orthopedics, Huashan Hospital, Fudan University Shanghai, China.
authors.forename: Jianguo
authors.initials: J
authors.lastname: Wu
authors.affiliation: The Department of Orthopedics, Huashan Hospital, Fudan University Shanghai, China.
authors.forename: Siqun
authors.initials: S
authors.lastname: Wang
authors.affiliation: The Department of Orthopedics, Huashan Hospital, Fudan University Shanghai, China.
authors.forename: Gangyong
authors.initials: G
authors.lastname: Huang
authors.affiliation: The Department of Orthopedics, Huashan Hospital, Fudan University Shanghai, China.
authors.forename: Jie
authors.initials: J
authors.lastname: Chen
authors.affiliation: The Department of Orthopedics, Huashan Hospital, Fudan University Shanghai, China.
authors.forename: Jingsheng
authors.initials: J
authors.lastname: Shi
keywords: Polyostotic fibrous dysplasia; Shepherd’s deformity; internal-fixation; osteotomy