title: [Febrile ulceronecrotic Mucha-Habermann disease].
abstract: Pityriasis lichenoides et varioliformis acuta (PLEVA) is an inflammatory skin disease that is unknown to pediatricians. The ulceronecrotic febrile form is a rare and potentially lethal variant. We report the case of a 7-year-old boy with a papulovesicular eruption lasting for 4 weeks, secondarily associated with ulcers and necrotic crusts, fever, and systemic signs. After exploring infectious causes such as chickenpox, we discussed and confirmed PLEVA with histological analysis. Systemic steroids and methotrexate improved the symptoms. It is necessary to mention PLEVA in case of prolonged papulovesicular eruption. Prompt diagnosis allows appropriate treatment, although there is no consensus on therapeutic guidelines.
authors.affiliation: Service de pédiatrie générale, CHU Ambroise-Paré, AP-HP, 9, avenue Charles-de-Gaulle, 92100 Boulogne-Billancourt, France.
authors.forename: A
authors.initials: A
authors.lastname: Dupin
authors.affiliation: Service de dermatologie, CHU Ambroise-Paré, AP-HP, 9, avenue Charles-de-Gaulle, 92100 Boulogne-Billancourt, France; UFR des sciences de la santé Simone-Veil, université de Versailles St. Quentin, 78180 Montigny-le-Bretonneux, France.
authors.forename: D
authors.initials: D
authors.lastname: Bosset
authors.affiliation: Service de pédiatrie générale, CHU Ambroise-Paré, AP-HP, 9, avenue Charles-de-Gaulle, 92100 Boulogne-Billancourt, France.
authors.forename: L
authors.initials: L
authors.lastname: Atger
authors.affiliation: Service de pédiatrie générale, CHU Ambroise-Paré, AP-HP, 9, avenue Charles-de-Gaulle, 92100 Boulogne-Billancourt, France; UFR des sciences de la santé Simone-Veil, université de Versailles St. Quentin, 78180 Montigny-le-Bretonneux, France.
authors.forename: B
authors.initials: B
authors.lastname: Chevallier
authors.affiliation: Service de dermatologie, CHU Ambroise-Paré, AP-HP, 9, avenue Charles-de-Gaulle, 92100 Boulogne-Billancourt, France; UFR des sciences de la santé Simone-Veil, université de Versailles St. Quentin, 78180 Montigny-le-Bretonneux, France.
authors.forename: P
authors.initials: P
authors.lastname: Saiag
authors.affiliation: Service de pédiatrie générale, CHU Ambroise-Paré, AP-HP, 9, avenue Charles-de-Gaulle, 92100 Boulogne-Billancourt, France. Electronic address: gregoire.benoist@aphp.fr.
authors.forename: G
authors.initials: G
authors.lastname: Benoist
mesh_terms: D002648:Child; D003879:Dermatologic Agents / Q000627:therapeutic use; D005334:Fever / Q000209:etiology; D006801:Humans; D008297:Male; D008727:Methotrexate / Q000627:therapeutic use; D063806:Myalgia / Q000209:etiology; D017514:Pityriasis Lichenoides / Q000188:drug therapy / Q000473:pathology*
chemical_list: D003879:Dermatologic Agents; D008727:Methotrexate