title: Clarifying the atrioventricular junctional anatomy in the setting of double outlet right atrium.
abstract: Double outlet atrium is a rare cardiac anomaly wherein one of the atriums, most frequently the right atrium, opens into both the ventricles. Although seen more commonly in the setting of atrioventricular septal defect, this arrangement can also be found when one of the atrioventricular connections is atretic due to absence of the atrioventricular connection and the other atrioventricular valve straddles the muscular ventricular septum. It is the specific anatomy and connections of the atrioventricular junction that clarifies the situation and distinguishes between these two types of double outlet atrium. In this report, we present a case of double outlet right atrium co-existing with the absence of left atrioventricular connection. We then discuss the morphologic aspects of this interesting anomaly.
authors.affiliation: Department of Cardiology, All India Institute of Medical Sciences, New Delhi, India.
authors.forename: Saurabh Kumar
authors.initials: SK
authors.lastname: Gupta
authors.affiliation: Department of Cardiology, All India Institute of Medical Sciences, New Delhi, India.
authors.forename: Anunay
authors.initials: A
authors.lastname: Gupta
authors.affiliation: Department of Cardiology, All India Institute of Medical Sciences, New Delhi, India.
authors.forename: Sivasubramanian
authors.initials: S
authors.lastname: Ramakrishnan
authors.affiliation: Institute of Genetic Medicine, University of Newcastle, Newcastle-upon-Tyne, United Kingdom.
authors.forename: Robert H
authors.initials: RH
authors.lastname: Anderson
keywords: Atrioventricular junction; atrioventricular septal defect; double outlet atrium; x plane imaging