title: Acquired neurocutaneous disorders.
abstract: A variety of neurologic diseases have cutaneous manifestations. These may precede, coincide with, or follow the neurologic findings. An array of autoimmune, genetic, and environmental factors play a role in expression and severity of the neurologic burden in these conditions. This chapter emphasizes congenital and genetic disorders, but we also discuss the pathophysiology and manifestation of various acquired neurocutaneous disorders with an emphasis Behcet's disease, dermatomyositis, Sjögren's syndrome, systemic lupus erythematosus, scleroderma, Parry-Romberg syndrome and Degos disease.
authors.affiliation: Department of Neurology, Hartford Hospital - University of Connecticut, Hartford CT, USA.
authors.forename: Amre
authors.initials: A
authors.lastname: Nouh
authors.affiliation: Section of Dermatopathology, Department of Pathology, Stritch School of Medicine, Loyola University Chicago, Maywood, IL, USA.
authors.forename: Jodi
authors.initials: J
authors.lastname: Speiser
authors.affiliation: Department of Neurology, Stritch School of Medicine, Loyola University Chicago, Maywood, IL, USA. Electronic address: jbiller@lumc.edu.
authors.forename: José
authors.initials: J
authors.lastname: Biller
mesh_terms: D001528:Behcet Syndrome / Q000503:physiopathology; D000013:Congenital Abnormalities / Q000503:physiopathology*; D003882:Dermatomyositis / Q000503:physiopathology; D030342:Genetic Diseases, Inborn / Q000150:complications*; D006801:Humans; D020752:Neurocutaneous Syndromes / Q000150:complications* / Q000235:genetics*; D012859:Sjogren's Syndrome / Q000503:physiopathology
keywords: Behçet's disease; Neurologic manifestations; Parry–Romberg syndrome and Degos disease; Sjögren syndrome; dermatologic manifestations; dermatomyositis; scleroderma; systemic lupus erythematosus (SLE)