title: Review of Congenital Mitral Valve Stenosis: Analysis, Repair Techniques and Outcomes.
abstract: The spectrum of congenital mitral valve stenosis (MS) consists of a complex of defects that result in obstruction to left ventricular inflow. This spectrum includes patients with underdeveloped left heart structures (Fig. 1) to those with isolated congenital MS. The specific mitral valve defects can further be divided into categories based on the relationship to the mitral valve annulus including valvar, supravalvar and subvalvar components. Clinically, these patients present based on the degree of obstruction, associated mitral regurgitation, secondary pulmonary hypertension, associated lung disease and/or associated cardiac lesions. There are a number of factors that contribute to the successful outcomes in these patients including pre-operative imaging, aggressive surgical techniques and peri-operative management.
authors.affiliation: Boston Children's Hospital, Boston, MA, USA. chris.baird@cardio.chboston.org.
authors.forename: Christopher W
authors.initials: CW
authors.lastname: Baird
authors.affiliation: Boston Children's Hospital, Boston, MA, USA.
authors.forename: Gerald R
authors.initials: GR
authors.lastname: Marx
authors.affiliation: Boston Children's Hospital, Boston, MA, USA.
authors.forename: Michele
authors.initials: M
authors.lastname: Borisuk
authors.affiliation: Boston Children's Hospital, Boston, MA, USA.
authors.forename: Sitram
authors.initials: S
authors.lastname: Emani
authors.affiliation: Boston Children's Hospital, Boston, MA, USA.
authors.forename: Pedro J
authors.initials: PJ
authors.lastname: del Nido
mesh_terms: D004452:Echocardiography; D006801:Humans; D008943:Mitral Valve / Q000002:abnormalities* / Q000000981:diagnostic imaging / Q000601:surgery*; D008946:Mitral Valve Stenosis / Q000151:congenital* / Q000000981:diagnostic imaging / Q000601:surgery*; D016896:Treatment Outcome
keywords: Anatomy; Congenital mitral stenosis; Repair