title: Are Auditory Steady-State Responses Useful to Evaluate Severe-to-Profound Hearing Loss in Children?
abstract: OBJECTIVE
  To evaluate Auditory Steady-State Responses (ASSR) at high intensities in pediatric cochlear implant candidates and to compare the results to behavioral tests responses.
  
  
  METHODS
  This prospective study evaluated 42 children with suspected severe-to-profound hearing loss, aged from 3 to 72 months. All had absent ABR and OAE responses. ASSR were evoked using binaural single frequency stimuli at 110 dB HL with a 10 dB down-seeking procedure. ASSR and behavioral test results were compared.
  
  
  RESULTS
  Forty-two subjects completed both ASSR and behavioral evaluation. Eleven children (26.2%) had bilateral responses. Four (9.5%) showed unilateral responses in at least two frequencies, all confirmed by behavioral results. Overall 61 ASSR responses were obtained, most (37.7%) in 500 Hz. Mean thresholds were between 101.3 and 104.2 dB HL. Among 27 subjects with absent ASSR, fifteen had no behavioral responses. Seven subjects showed behavioral responses with absent ASSR responses. No spurious ASSR responses were observed at 100 or 110 dB HL.
  
  
  CONCLUSIONS
  ASSR is a valuable tool to detect residual hearing. No false-positive ASSR results were observed among 42 children, but in seven cases with absent ASSR, the test underestimated residual hearing as compared to the behavioral responses.
authors.affiliation: Department of Otolaryngology, University of São Paulo, 255 Dr. Eneas de Carvalho Aguiar Avenue, 05403-900 São Paulo, SP, Brazil.
authors.forename: Signe Schuster
authors.initials: SS
authors.lastname: Grasel
authors.affiliation: Department of Otolaryngology, University of São Paulo, 255 Dr. Eneas de Carvalho Aguiar Avenue, 05403-900 São Paulo, SP, Brazil.
authors.forename: Edigar Rezende
authors.initials: ER
authors.lastname: de Almeida
authors.affiliation: Department of Otolaryngology, University of São Paulo, 255 Dr. Eneas de Carvalho Aguiar Avenue, 05403-900 São Paulo, SP, Brazil.
authors.forename: Roberto Miquelino de Oliveira
authors.initials: RM
authors.lastname: Beck
authors.affiliation: Department of Otolaryngology, University of São Paulo, 255 Dr. Eneas de Carvalho Aguiar Avenue, 05403-900 São Paulo, SP, Brazil.
authors.forename: Maria Valéria Schmidt
authors.initials: MV
authors.lastname: Goffi-Gomez
authors.affiliation: Department of Otolaryngology, University of São Paulo, 255 Dr. Eneas de Carvalho Aguiar Avenue, 05403-900 São Paulo, SP, Brazil.
authors.forename: Henrique Faria
authors.initials: HF
authors.lastname: Ramos
authors.affiliation: Department of Otolaryngology, University of São Paulo, 255 Dr. Eneas de Carvalho Aguiar Avenue, 05403-900 São Paulo, SP, Brazil.
authors.forename: Amanda Costa
authors.initials: AC
authors.lastname: Rossi
authors.affiliation: Department of Otolaryngology, University of São Paulo, 255 Dr. Eneas de Carvalho Aguiar Avenue, 05403-900 São Paulo, SP, Brazil.
authors.forename: Robinson
authors.initials: R
authors.lastname: Koji Tsuji
authors.affiliation: Department of Otolaryngology, University of São Paulo, 255 Dr. Eneas de Carvalho Aguiar Avenue, 05403-900 São Paulo, SP, Brazil.
authors.forename: Ricardo Ferreira
authors.initials: RF
authors.lastname: Bento
authors.affiliation: Department of Otolaryngology, University of São Paulo, 255 Dr. Eneas de Carvalho Aguiar Avenue, 05403-900 São Paulo, SP, Brazil.
authors.forename: Rubens
authors.initials: R
authors.lastname: de Brito
mesh_terms: D000161:Acoustic Stimulation / Q000379:methods; D001309:Auditory Threshold / Q000502:physiology; D002648:Child; D002675:Child, Preschool; D019929:Cochlear Implantation / Q000379:methods; D003054:Cochlear Implants; D016057:Evoked Potentials, Auditory, Brain Stem / Q000502:physiology; D005260:Female; D006309:Hearing / Q000502:physiology; D006319:Hearing Loss, Sensorineural / Q000175:diagnosis* / Q000503:physiopathology*; D006320:Hearing Tests / Q000379:methods; D006801:Humans; D007223:Infant; D008297:Male