title: Anesthetic Management of a Parturient with PHACE Syndrome for Cesarean Delivery.
abstract: PHACE syndrome is a disorder that features posterior fossa malformations, hemangiomas, arterial anomalies, coarctation of the aorta and cardiac defects, and eye abnormalities. PHACE syndrome includes abnormalities in several organ systems that may influence anesthetic management. We discuss the anesthetic management of a 26-year-old woman with PHACE syndrome presenting for cesarean delivery. Management included careful airway examination, slowly dosed epidural anesthesia, close hemodynamic monitoring aided by a radial arterial line, and continuous intraoperative neurologic assessment.
authors.affiliation: From the Department of Anesthesia, Ochsner Clinic Foundation, Jefferson, Louisiana.
authors.forename: Colleen
authors.initials: C
authors.lastname: Martel
authors.forename: Richard
authors.initials: R
authors.lastname: Robertson
authors.forename: Frank B
authors.initials: FB
authors.lastname: Williams
authors.forename: R Clifton
authors.initials: RC
authors.lastname: Moore
authors.forename: Allison
authors.initials: A
authors.lastname: Clark
mesh_terms: D000015:Abnormalities, Multiple; D000328:Adult; D000767:Anesthesia, Epidural / Q000379:methods*; D000773:Anesthesia, Obstetrical / Q000379:methods*; D001017:Aortic Coarctation; D001921:Brain / Q000002:abnormalities; D002585:Cesarean Section / Q000379:methods*; D003388:Cranial Fossa, Posterior / Q000002:abnormalities; D005124:Eye Abnormalities; D005260:Female; D006391:Hemangioma; D006801:Humans; D007231:Infant, Newborn; D008297:Male; D009072:Moyamoya Disease / Q000150:complications; D020752:Neurocutaneous Syndromes; D009460:Neurologic Examination; D011247:Pregnancy; D011256:Pregnancy Outcome