title: Recurrent pericardial effusion and tamponade in a patient with Erdheim-Chester disease (ECD).
abstract: Erdheim-Chester disease (ECD) is a rare xanthogranulomatous disorder characterised by the proliferation of lipid laden histiocytes along with infiltration of various organs of the body. Although commonly presenting with bone pains secondary to bony infiltration, cardiac involvement in the form of periaortic fibrosis and pericardial involvement may be seen in a subgroup of patients. We report a case of ECD presenting as recurrent pericardial effusion along with pericardial tamponade.
authors.affiliation: Department of Internal Medicine, Christian Medical College, Vellore, Tamil Nadu, India.
authors.forename: Ajay Kumar
authors.initials: AK
authors.lastname: Mishra
authors.affiliation: Department of Radiology, Christian Medical College, Vellore, Tamil Nadu, India.
authors.forename: Sunithi
authors.initials: S
authors.lastname: Mani
authors.affiliation: Department of Dermatology, Christian Medical College, Vellore, Tamil Nadu, India.
authors.forename: Anu Anna
authors.initials: AA
authors.lastname: George
authors.affiliation: Department of Internal Medicine Unit II, Christian Medical College, Vellore, Tamil Nadu, India.
authors.forename: Thambu David
authors.initials: TD
authors.lastname: Sudarsanam
mesh_terms: D001921:Brain / Q000473:pathology; D002305:Cardiac Tamponade / Q000150:complications / Q000000981:diagnostic imaging* / Q000188:drug therapy; D003937:Diagnosis, Differential; D031249:Erdheim-Chester Disease / Q000150:complications / Q000175:diagnosis* / Q000188:drug therapy; D017809:Fatal Outcome; D005269:Femur / Q000473:pathology; D005938:Glucocorticoids / Q000627:therapeutic use; D006801:Humans; D007372:Interferons / Q000627:therapeutic use; D008279:Magnetic Resonance Imaging; D008297:Male; D008875:Middle Aged; D010490:Pericardial Effusion / Q000150:complications / Q000000981:diagnostic imaging* / Q000188:drug therapy; D012008:Recurrence; D012272:Ribs / Q000473:pathology; D014057:Tomography, X-Ray Computed
chemical_list: D005938:Glucocorticoids; D007372:Interferons