title: Calcifying nested stromal-epithelial tumor (CNSET) of the liver: a newly recognized entity to be considered in the radiologist's differential diagnosis.
abstract: Calcifying nested stromal-epithelial tumor (CNSET), an extremely rare tumor found in the liver, was first described in 2001 by Ishak et al. The characteristic imaging features include large size, well-circumscribed, enhancing mass with calcification. To our knowledge, since 2001, there have been 29 reported. Typically arising from the right hepatic lobe, it is primarily found in children and shows clear predilection for females. Emphasizing imaging, we report a 14-year-old female with Beckwith-Wiedemann syndrome who presented with CNSET.
authors.affiliation: Children's Healthcare of Atlanta and Emory University, Department of Pathology.
authors.forename: Lauren R
authors.initials: LR
authors.lastname: Schaffer
authors.affiliation: Children's Healthcare of Atlanta and Emory University, Department of Pathology.
authors.forename: Bahig M
authors.initials: BM
authors.lastname: Shehata
authors.affiliation: Children's Healthcare of Atlanta and Emory University, Department of Pathology.
authors.forename: Julie
authors.initials: J
authors.lastname: Yin
authors.affiliation: Children's Healthcare of Atlanta and Emory University, Department of Pathology.
authors.forename: Erwin
authors.initials: E
authors.lastname: Schemankewitz
authors.affiliation: Children's Healthcare of Atlanta and Emory University, Departments of Pediatrics and Radiology and Imaging Sciences. Electronic address: adina.alazraki@choa.org.
authors.forename: Adina
authors.initials: A
authors.lastname: Alazraki
mesh_terms: D000293:Adolescent; D001506:Beckwith-Wiedemann Syndrome / Q000150:complications*; D002114:Calcinosis / Q000000981:diagnostic imaging; D003480:Cushing Syndrome / Q000150:complications*; D003937:Diagnosis, Differential; D005260:Female; D006801:Humans; D008099:Liver / Q000000981:diagnostic imaging / Q000601:surgery; D008113:Liver Neoplasms / Q000150:complications* / Q000175:diagnosis* / Q000601:surgery; D016031:Liver Transplantation; D018193:Neoplasms, Complex and Mixed / Q000150:complications* / Q000175:diagnosis* / Q000601:surgery; D017154:Stromal Cells / Q000000981:diagnostic imaging; D014057:Tomography, X-Ray Computed; D014463:Ultrasonography
keywords: Beckwith–Wiedmann; CT; Calcifying; Liver tumor; Stromal