title: Hypoglycemia due to 3β-Hydroxysteroid Dehydrogenase type II Deficiency in a Newborn.
abstract: BACKGROUND
  3β-hydroxysteroid dehydrogenase type II deficiency results in decreased production of all three groups of adrenal steroids. Recurrent hypoglycemia as a presenting feature of this disorder has not been reported earlier.
  
  
  METHODS
  A genotypically and phenotypically normal female newborn delivered by in-vitro fertilization presenting with recurrent hypoglycemia. Primary adrenal insufficiency with insignificant mineralocorticoid deficiency and slightly elevated levels of 17-hydro-xyprogesterone, dehydroepian-drosterone sulphate and testosterone.
  
  
  RESULTS
  Successfully managed only with corticosteroid replacement.
  
  
  CONCLUSIONS
  Congenital adrenal hyperplasia can rarely cause recurrent hypoglycemia in newborns.
authors.affiliation: Departments of Pediatrics and *Endocrinology, Nil Ratan Sircar Medical College and Hospital, Kolkata, West Bengal, India. Correspondence to: Dr Mithun Chandra Konar, DE- 290 -1, Giridhari V Apartment, Flat No 3B, 3rd floor, Narayantala (East), Baguiati, Kolkata 700 159, West Bengal, India. dr_mithun60589@yahoo.com.
authors.forename: M C
authors.initials: MC
authors.lastname: Konar
authors.forename: S
authors.initials: S
authors.lastname: Goswami
authors.forename: B G
authors.initials: BG
authors.lastname: Babu
authors.forename: A K
authors.initials: AK
authors.lastname: Mallick
mesh_terms: D000305:Adrenal Cortex Hormones / Q000627:therapeutic use; D000312:Adrenal Hyperplasia, Congenital / Q000150:complications / Q000175:diagnosis / Q000188:drug therapy; D006801:Humans; D007003:Hypoglycemia / Q000209:etiology; D007231:Infant, Newborn; D008297:Male
chemical_list: D000305:Adrenal Cortex Hormones