title: Left isomerism syndrome with total anomalous systemic connection.
abstract: We present a case of left isomerism with total anomalous systemic venous connection where the inferior vena cava was absent and all other systemic veins connected abnormally to the left atrium. The right atrium was hypoplastic with an intact atrial septum. Blood flow to the lungs was through a large ventricular septal defect. The diagnosis was made with echocardiography, angiography, and computed tomography. Complete repair was performed successfully, and the 7-year-old patient had an uneventful recovery.
authors.affiliation: Department of Cardiovascular Surgery, University Medical Center, University of Medicine and Pharmacy in Ho Chi Minh City, Ho Chi Minh City, Vietnam.
authors.forename: Anh Tuan
authors.initials: AT
authors.lastname: Vo
authors.affiliation: Department of Cardiovascular Surgery, University Medical Center, University of Medicine and Pharmacy in Ho Chi Minh City, Ho Chi Minh City, Vietnam.
authors.forename: Khang Dang
authors.initials: KD
authors.lastname: Cao
authors.affiliation: Department of Cardiovascular Surgery, University Medical Center, University of Medicine and Pharmacy in Ho Chi Minh City, Ho Chi Minh City, Vietnam.
authors.forename: Khoi Minh
authors.initials: KM
authors.lastname: Le
authors.affiliation: Department of Cardiovascular Surgery, University Medical Center, University of Medicine and Pharmacy in Ho Chi Minh City, Ho Chi Minh City, Vietnam.
authors.forename: Dinh Hoang
authors.initials: DH
authors.lastname: Nguyen
mesh_terms: D000015:Abnormalities, Multiple; D006348:Cardiac Surgical Procedures; D002648:Child; D000072226:Computed Tomography Angiography; D018618:Echocardiography, Doppler, Color; D005260:Female; D006330:Heart Defects, Congenital / Q000000981:diagnostic imaging / Q000503:physiopathology / Q000601:surgery; D006345:Heart Septal Defects, Ventricular / Q000000981:diagnostic imaging / Q000503:physiopathology / Q000601:surgery; D006352:Heart Ventricles / Q000002:abnormalities* / Q000000981:diagnostic imaging / Q000503:physiopathology / Q000601:surgery; D006439:Hemodynamics; D059446:Heterotaxy Syndrome / Q000000981:diagnostic imaging / Q000503:physiopathology / Q000601:surgery; D006801:Humans; D011652:Pulmonary Circulation; D016896:Treatment Outcome; D014682:Vena Cava, Inferior / Q000002:abnormalities* / Q000000981:diagnostic imaging / Q000503:physiopathology / Q000601:surgery
keywords: Heart atria; Heart defects; Heart septal defects; Vascular malformations; Vena cava; atrial; congenital; inferior; superior