title: Alveolar Capillary Dysplasia as a Cause of Persistent Pulmonary Hypertension.
abstract: BACKGROUND
  Persistent pulmonary hypertension (PPHN) in a term or late preterm has varied etiology.
  
  
  METHODS
  A late preterm neonate operated for esophageal atresia with tracheo-esophageal fistula was complicated by severe pulmonary hypertension and unable to be weaned off from respiratory support.
  
  
  RESULTS
  The neonate expired by 15 weeks of life; diagnosis was made on postmortem lung biopsy.
  
  
  CONCLUSIONS
  Alveolarcapillary dysplasia should be considered in a neonate with idiopathic refractory PPHN, if associated with anomalies.
authors.affiliation: Department of Neonatology, Manipal Hospital. Bangalore, India. Correspondence to: Dr N Karthik Nagesh, Head, Department of Neonatology, Manipal Group of Hospitals, Bangalore, India. drkarthiknagesh@gmail.com.
authors.forename: Abdul
authors.initials: A
authors.lastname: Razak
authors.forename: Pankaj Kumar
authors.initials: PK
authors.lastname: Mohanty
authors.forename: N Karthik
authors.initials: NK
authors.lastname: Nagesh
mesh_terms: D004933:Esophageal Atresia / Q000209:etiology*; D017809:Fatal Outcome; D006801:Humans; D007231:Infant, Newborn; D008297:Male; D010547:Persistent Fetal Circulation Syndrome / Q000150:complications / Q000175:diagnosis / Q000503:physiopathology; D011650:Pulmonary Alveoli / Q000002:abnormalities* / Q000503:physiopathology