title: Myxoid mesenchymal neoplasm presenting as massive arm and chest wall oedema with pleural effusion.
abstract: Myxoid mesenchymal tumours are a heterogeneous group of neoplasms characterised histologically by their abundant mucoid and myxoid extracellular matrix (ECM). Encompassing a broad spectrum of clinical behaviour ranging from benign to malignant, there are more than 60 reactive and neoplastic entities currently classified under its domain. Its varied clinical and histopathologic features continue to pose a diagnostic challenge to clinicians and pathologists. Here, we describe a rare case of myxoid mesenchymal tumour presenting as oedema of the upper extremity with pleural metastasis and partial response to chemotherapy, which to the best of our knowledge has not yet been described in the literature.
authors.affiliation: Department of Internal Medicine, Paediatrics, University of Arkansas For Medical Sciences, AR 72205, USA.
authors.forename: Vidya B
authors.initials: VB
authors.lastname: Pai
authors.affiliation: Department of Internal Medicine, University of Arkansas for Medical Sciences, AR 72205, USA.
authors.forename: Rahul
authors.initials: R
authors.lastname: Ravilla
authors.affiliation: Department of Pathology, University of Arkansas For Medical Sciences, AR 72205, USA.
authors.forename: Matthew
authors.initials: M
authors.lastname: Lindberg
authors.affiliation: Division of Thoracic Surgery, University of Arkansas For Medical Sciences, AR 72205, USA.
authors.forename: Matthew
authors.initials: M
authors.lastname: Steliga
authors.affiliation: Division of Haematology-Oncology, University of Arkansas For Medical Sciences, AR 72205, USA.
authors.forename: Konstantinos
authors.initials: K
authors.lastname: Arnaoutakis
keywords: extracellular matrix; malignant pleural effusion; neoplasms; sarcoma