title: [Bernard-Soulier syndrome and pregnancy: a case report].
abstract: Bernard-Soulier syndrome is an inherited bleeding disorder. Due to the rarity of the combination of this syndrome and pregnancy, data on the clinical course and outcome of pregnancy in women with Bernard-Soulier syndrome is scattered in individual case reports and there is no consensus in the management of SBS. In some patients, the pregnancy course was uneventful while in others post partum hemorrhage was the most common complication. We report our experience about the perioperative management of a pregnant woman with Bernard-Soulier syndrome.
authors.affiliation: Service d'anesthésie réanimation, Hôpital Hedi Chaker, Sfax, Tunisie.
authors.forename: Mohamed
authors.initials: M
authors.lastname: Smaoui
authors.affiliation: Service d'anesthésie réanimation, Hôpital Hedi Chaker, Sfax, Tunisie.
authors.forename: Sahar
authors.initials: S
authors.lastname: Elleuch
authors.affiliation: Service d'anesthésie réanimation, Hôpital Hedi Chaker, Sfax, Tunisie.
authors.forename: Sofien
authors.initials: S
authors.lastname: Abidi
authors.affiliation: Service d'anesthésie réanimation, Hôpital Hedi Chaker, Sfax, Tunisie.
authors.forename: Yasmine
authors.initials: Y
authors.lastname: Ellouze
authors.affiliation: Service de gynécologie obstétrique, Hôpital Hedi Chaker, Sfax, Tunisie.
authors.forename: Doulira
authors.initials: D
authors.lastname: Louati
authors.affiliation: Service d'hématologie, Hôpital Hedi Chaker, Sfax, Tunisie.
authors.forename: Moez
authors.initials: M
authors.lastname: Loumi
authors.affiliation: Service d'anesthésie réanimation, Hôpital Hedi Chaker, Sfax, Tunisie.
authors.forename: Kamel
authors.initials: K
authors.lastname: Kolsi
mesh_terms: D000328:Adult; D001606:Bernard-Soulier Syndrome / Q000150:complications / Q000473:pathology / Q000628:therapy*; D001803:Blood Transfusion; D002585:Cesarean Section; D005260:Female; D005313:Fetal Death; D006801:Humans; D020300:Intracranial Hemorrhages / Q000473:pathology; D006473:Postpartum Hemorrhage / Q000209:etiology / Q000628:therapy; D011247:Pregnancy; D011250:Pregnancy Complications, Hematologic / Q000473:pathology / Q000628:therapy*; D014148:Tranexamic Acid / Q000627:therapeutic use
chemical_list: D014148:Tranexamic Acid
keywords: Bernard-Soulier syndrome; bleeding; delivery; pregnancy