title: Anesthetic management of a pediatric patient with hypohidrotic ectodermal dysplasia undergoing emergency surgery.
abstract: Ectodermal dysplasias are rare conditions with a triad of hypotrichosis, anodontia and anhidrosis. In literature review there have been only a few reports of anesthetic management of patients with ectodermal dysplasias. Hyperthermia is a very serious risk which may occur due to the defect of sweat glands. The present case involves a 10-year-old child with ectodermal dysplasia who presented with an acute abdomen and was considered for an emergency surgery. Our aim was to demonstrate the successful management of this case using a combination of general and epidural anesthesia. It is important for anesthesiologist to have information about this syndrome in case of emergency operations, since it can prevent serious complications and even save lives.
authors.affiliation: Department of Anesthesiology and Reanimation, Regional Training and Research Hospital, Erzurum, Turkey. Electronic address: drelforl@hotmail.com.
authors.forename: Elif Oral
authors.initials: EO
authors.lastname: Ahiskalioglu
authors.affiliation: Department of Anesthesiology and Reanimation, Ataturk University School of Medicine, Erzurum, Turkey.
authors.forename: Ali
authors.initials: A
authors.lastname: Ahiskalioglu
authors.affiliation: Department of Pediatric Surgery, Regional Training and Research Hospital, Erzurum, Turkey.
authors.forename: Binali
authors.initials: B
authors.lastname: Firinci
authors.affiliation: Department of Anesthesiology and Reanimation, Ataturk University School of Medicine, Erzurum, Turkey.
authors.forename: Aysenur
authors.initials: A
authors.lastname: Dostbil
authors.affiliation: Department of Anesthesiology and Reanimation, Ataturk University School of Medicine, Erzurum, Turkey.
authors.forename: Mehmet
authors.initials: M
authors.lastname: Aksoy
mesh_terms: D000758:Anesthesia / Q000379:methods*; D001064:Appendicitis / Q000601:surgery*; D002648:Child; D053358:Ectodermal Dysplasia 1, Anhidrotic / Q000150:complications*; D004638:Emergency Treatment; D006801:Humans; D008297:Male
keywords: Abdome agudo; Acute abdomen; Anestesia regional; Displasia ectodérmica; Ectodermal dysplasia; Regional anesthesia