title: Bone-anchored hearing aid implantation in a patient with Goldenhar syndrome.
abstract: Patients with Goldenhar syndrome exhibit a number of characteristic symptoms, including middle and internal ear malformations that may cause profound hearing loss. Bone-anchored hearing aids have been used to treat these patients in the past, although complications may arise due to the nature of the disease. Herein we present the case of a pediatric patient with Goldenhar syndrome whose hearing aid abutment extruded spontaneously because of poor bone quality, despite adequate thickness. We provide a brief review of the literature and suggest a flexible surgical plan for any syndromic pediatric patient.
authors.affiliation: College of Medicine and Life Sciences, University of Toledo College of Medicine, Toledo, OH 43606, USA.
authors.forename: Griffin
authors.initials: G
authors.lastname: Santarelli
authors.forename: Roberta E
authors.initials: RE
authors.lastname: Redfern
authors.forename: Aaron G
authors.initials: AG
authors.lastname: Benson
mesh_terms: D002648:Child; D003638:Deafness / Q000534:rehabilitation* / Q000601:surgery*; D005260:Female; D006053:Goldenhar Syndrome / Q000534:rehabilitation* / Q000601:surgery* / Q000628:therapy; D006310:Hearing Aids; D006801:Humans; D019919:Prosthesis Implantation; D053441:Suture Anchors; D013701:Temporal Bone / Q000601:surgery