title: [Anesthetic management of a pediatric patient with hypohidrotic ectodermal dysplasia undergoing emergency surgery].
abstract: Ectodermal dysplasias are rare conditions with a triad of hypotrichosis, anodontia and anhidrosis. In literature review there have been only a few reports of anesthetic management of patients with ectodermal dysplasias. Hyperthermia is a very serious risk which may occur due to the defect of sweat glands. The present case involves a 10-year-old child with ectodermal dysplasia who presented with an acute abdomen and was considered for an emergency surgery. Our aim was to demonstrate the successful management of this case using a combination of general and epidural anesthesia. It is important for anesthesiologist to have information about this syndrome in case of emergency operations, since it can prevent serious complications and even save lives.
authors.affiliation: Departamento de Anestesiologia e Reanimação, Hospital Regional de Ensino e Pesquisa, Erzurum, Turquia. Electronic address: drelforl@hotmail.com.
authors.forename: Elif Oral
authors.initials: EO
authors.lastname: Ahiskalioglu
authors.affiliation: Departamento de Anestesiologia e Reanimação, Escola de Medicina da Universidade Ataturk, Erzurum, Turquia.
authors.forename: Ali
authors.initials: A
authors.lastname: Ahiskalioglu
authors.affiliation: Departamento de Pediatria Cirurgia, Hospital Regional de Ensino e Pesquisa, Erzurum, Turquia.
authors.forename: Binali
authors.initials: B
authors.lastname: Firinci
authors.affiliation: Departamento de Anestesiologia e Reanimação, Escola de Medicina da Universidade Ataturk, Erzurum, Turquia.
authors.forename: Aysenur
authors.initials: A
authors.lastname: Dostbil
authors.affiliation: Departamento de Anestesiologia e Reanimação, Escola de Medicina da Universidade Ataturk, Erzurum, Turquia.
authors.forename: Mehmet
authors.initials: M
authors.lastname: Aksoy
keywords: Abdome agudo; Acute abdomen; Anestesia regional; Displasia ectodérmica; Ectodermal dysplasia; Regional anesthesia