title: Sudden Cardiac Death Associated with Anomalous Origin of the Left Main Coronary Artery from the Right Sinus, with an Intramural Course.
abstract: Anomalous origin of the left main coronary artery from the right sinus of Valsalva is extremely rare and can lead to sudden cardiac death. We report a case in which an 18-year-old college student collapsed immediately after a long-distance run of 10 km. After cardiopulmonary resuscitation and electrical shock for ventricular fibrillation, she experienced a return of spontaneous circulation. Cardiac catheterization and cardiac computed tomographic angiography revealed an unusually long intramural course of the left main coronary artery from the right sinus of Valsalva. The young woman underwent a successful unroofing operation for coronary artery correction. She remained asymptomatic upon exercise during 2.5 years of follow-up.
authors.forename: Huai-Ren
authors.initials: HR
authors.lastname: Chang
authors.forename: Jen-Che
authors.initials: JC
authors.lastname: Hsieh
authors.forename: Shen-Feng
authors.initials: SF
authors.lastname: Chao
authors.forename: Ji-Hung
authors.initials: JH
authors.lastname: Wang
authors.forename: Shoei K
authors.initials: SK
authors.lastname: Stephen Huang
mesh_terms: D000293:Adolescent; D006328:Cardiac Catheterization; D006348:Cardiac Surgical Procedures; D016887:Cardiopulmonary Resuscitation; D017023:Coronary Angiography / Q000379:methods; D003330:Coronary Vessel Anomalies / Q000150:complications* / Q000175:diagnosis / Q000601:surgery; D016757:Death, Sudden, Cardiac / Q000209:etiology* / Q000517:prevention & control; D004554:Electric Countershock; D004562:Electrocardiography; D005260:Female; D006801:Humans; D061330:Multidetector Computed Tomography; D058687:Out-of-Hospital Cardiac Arrest / Q000175:diagnosis / Q000209:etiology* / Q000628:therapy; D020127:Recovery of Function; D012420:Running; D012850:Sinus of Valsalva / Q000002:abnormalities* / Q000000981:diagnostic imaging / Q000601:surgery; D016896:Treatment Outcome
keywords: Coronary vessel anomalies/radiography/surgery; death, sudden, cardiac/pathology; exercise, strenuous; heart defects, congenital; left main coronary artery/abnormalities; sinus of Valsalva/abnormalities; sports