title: Primary-care management of patients with congenital anomalies of the coronary arteries.
abstract: Congenital anomalies of the coronary arteries, although uncommon, have the potential to cause serious myocardial damage, ischaemic cardiomyopathy, and sudden cardiac death. This article summarises aspects of care for these patients in the outpatient setting, including clinical history and physical examination findings, ancillary testing, decision-making regarding the need for surgical intervention, and recommendations for physical activity. Although there are limited data regarding some of these recommendations, it is hoped that these can be used as an initial benchmark against which further data will lead to a more evidence-based approach.
authors.affiliation: Children's Hospital of Philadelphia,Perelman School of Medicine,University of Pennsylvania,Philadelphia,Pennsylvania,United States of America.
authors.forename: Jeffrey R
authors.initials: JR
authors.lastname: Boris
authors.affiliation: Children's Hospital of Philadelphia,Perelman School of Medicine,University of Pennsylvania,Philadelphia,Pennsylvania,United States of America.
authors.forename: Julie A
authors.initials: JA
authors.lastname: Brothers
mesh_terms: D000553:Ambulatory Care; D063748:Bland White Garland Syndrome / Q000175:diagnosis / Q000628:therapy; D006348:Cardiac Surgical Procedures; D000066491:Clinical Decision-Making; D054326:Coronary Sinus / Q000002:abnormalities / Q000000981:diagnostic imaging / Q000473:pathology; D003330:Coronary Vessel Anomalies / Q000175:diagnosis / Q000628:therapy*; D003331:Coronary Vessels / Q000000981:diagnostic imaging / Q000473:pathology; D016757:Death, Sudden, Cardiac / Q000517:prevention & control*; D019468:Disease Management; D004452:Echocardiography; D004562:Electrocardiography; D015444:Exercise; D006337:Heart Murmurs; D006801:Humans; D008279:Magnetic Resonance Imaging; D009043:Motor Activity; D010808:Physical Examination; D011320:Primary Health Care; D011651:Pulmonary Artery / Q000002:abnormalities / Q000000981:diagnostic imaging / Q000473:pathology; D014057:Tomography, X-Ray Computed
keywords: Ambulatory; anomalous aortic origin of a coronary artery; anomalous origin of the left coronary artery arising from the pulmonary artery; coronary fistula; outpatient