title: Functionally Univentricular Heart With Right Atrial Isomerism and Mixed Total Anomalous Pulmonary Venous Drainage.
abstract: Patients with right atrial isomerism and total anomalous pulmonary venous connection (TAPVC) in a functionally univentricular heart are a challenging subset with a high mortality rate. We present the case of a patient with univentricular heart who had right atrial isomerism and associated mixed TAPVC (supracardiac, cardiac, and infracardiac). The anatomy was delineated precisely, and the patient underwent first-stage univentricular palliation consisting of TAPVC repair and bilateral bidirectional superior cavopulmonary anastomosis.
authors.affiliation: Department of Cardiothoracic and Vascular Surgery, All India Institute of Medical Sciences, New Delhi, India sachintalwar@hotmail.com.
authors.forename: Sachin
authors.initials: S
authors.lastname: Talwar
authors.affiliation: Department of Cardiothoracic and Vascular Surgery, All India Institute of Medical Sciences, New Delhi, India.
authors.forename: Palkesh
authors.initials: P
authors.lastname: Agarwal
authors.affiliation: Department of Cardiothoracic and Vascular Surgery, All India Institute of Medical Sciences, New Delhi, India.
authors.forename: Shiv Kumar
authors.initials: SK
authors.lastname: Choudhary
authors.affiliation: Department of Cardiothoracic and Vascular Surgery, All India Institute of Medical Sciences, New Delhi, India.
authors.forename: Balram
authors.initials: B
authors.lastname: Airan
mesh_terms: D000714:Anastomosis, Surgical; D000072226:Computed Tomography Angiography; D005260:Female; D006352:Heart Ventricles / Q000002:abnormalities / Q000000981:diagnostic imaging / Q000601:surgery; D059446:Heterotaxy Syndrome / Q000000981:diagnostic imaging* / Q000601:surgery; D006801:Humans; D021621:Imaging, Three-Dimensional; D007231:Infant, Newborn; D011296:Prenatal Diagnosis; D011651:Pulmonary Artery / Q000002:abnormalities / Q000601:surgery; D012587:Scimitar Syndrome / Q000000981:diagnostic imaging* / Q000601:surgery; D014424:Turner Syndrome / Q000000981:diagnostic imaging / Q000601:surgery
keywords: atrial isomerism; heterotaxy; total anomalous pulmonary venous connection