title: The Congenital Heart Surgeons' Society Registry of Anomalous Aortic Origin of a Coronary Artery: an update.
abstract: The anomalous aortic origin of a coronary artery from the wrong sinus of Valsalva with an interarterial, intramural, and/or intraconal course is a relatively rare congenital defect of the heart that may be associated with an increased risk of ischaemia of the myocardium and sudden death, notably in children and young adults. Data are limited regarding stratification of risk and long-term outcomes of these patients. In 2009, the Anomalous Coronary Artery Working Group formed the Congenital Heart Surgeons' Society Registry of Anomalous Aortic Origin of a Coronary Artery to obtain information on large numbers of young patients with anomalous aortic origin of a coronary artery with the goal to better understand the natural and surgical history of this anomaly as well as to develop evidence-based treatment and management guidelines. In this report, we describe the data we have collected from the registry and the current state of the registry.
authors.affiliation: 1Division of Cardiology,The Children's Hospital of Philadelphia,Perelman School of Medicine,University of Pennsylvania,Philadelphia,Pennsylvania,United States of America.
authors.forename: Julie A
authors.initials: JA
authors.lastname: Brothers
authors.affiliation: 2Department of Cardiothoracic Surgery,The Children's Hospital of Philadelphia,Perelman School of Medicine,University of Pennsylvania,Philadelphia,Pennsylvania,United States of America.
authors.forename: J William
authors.initials: JW
authors.lastname: Gaynor
authors.affiliation: 3Division of Cardiovascular Surgery,Department of Surgery,Johns Hopkins All Children's Heart Institute,All Children's Hospital and Florida Hospital for Children,Saint Petersburg,Tampa,Orlando,Florida,United States of America.
authors.forename: Jeffrey P
authors.initials: JP
authors.lastname: Jacobs
authors.affiliation: 5Indiana University School of Medicine,United States of America.
authors.forename: Jeffrey A
authors.initials: JA
authors.lastname: Poynter
authors.affiliation: 3Division of Cardiovascular Surgery,Department of Surgery,Johns Hopkins All Children's Heart Institute,All Children's Hospital and Florida Hospital for Children,Saint Petersburg,Tampa,Orlando,Florida,United States of America.
authors.forename: Marshall L
authors.initials: ML
authors.lastname: Jacobs
mesh_terms: D000293:Adolescent; D000328:Adult; D001013:Aorta, Thoracic / Q000002:abnormalities*; D002648:Child; D002675:Child, Preschool; D003330:Coronary Vessel Anomalies / Q000150:complications / Q000175:diagnosis / Q000601:surgery*; D016757:Death, Sudden, Cardiac / Q000209:etiology; D005260:Female; D006801:Humans; D007223:Infant; D007231:Infant, Newborn; D008297:Male; D012042:Registries; D012955:Societies, Medical; D013903:Thoracic Surgery; D055815:Young Adult
keywords: Congenital cardiac disease; interarterial coronary artery; intraconal coronary artery; intramural coronary artery; paediatric cardiac disease