title: Dermatopathia Pigmentosa Reticularis with Salzmann's nodular degeneration of cornea: A rare association.
abstract: BACKGROUND
  Dermatopathia pigmentosa reticularis (DPR) is a very rare autosomal dominant disorder with the diagnostic triad of generalized reticulate hyperpigmentation, noncicatricial alopecia and onychodystrophy.
  
  
  OBJECTIVE
  To describe the occurrence of Salzmann's nodular degeneration of cornea with moderate dry eye in a patient with Dermatopathia pigmentosa reticularis.
  
  
  METHODS
  We present an 11 year old young Indian girl with DPR who had Salzmann's nodular degeneration of cornea with moderate dry eye. She was put on symptomatic treatment and counseled regarding the course of disease, familial nature and avoidance of exposure to sun.
  
  
  CONCLUSIONS
  In a patient of Salzmann`s nodular degeneration with generalized reticulate hyperpigmentation, noncicatricial alopecia and onychodystrophy the diagnosis of DPR must be kept in mind. A multidisciplinary approach is required for the management of such cases.
authors.affiliation: Gurunanak Eye Center, Maulana Azad Medical College, New Delhi.
authors.forename: R
authors.initials: R
authors.lastname: Goel
authors.forename: S A
authors.initials: SA
authors.lastname: Bodh
authors.forename: K
authors.initials: K
authors.lastname: Sardana
authors.forename: A
authors.initials: A
authors.lastname: Goel
mesh_terms: D000505:Alopecia / Q000150:complications* / Q000235:genetics; D002266:Carboxymethylcellulose Sodium / Q000008:administration & dosage; D002648:Child; D002886:Chromosomes, Human, Pair 17 / Q000235:genetics; D003317:Corneal Dystrophies, Hereditary / Q000150:complications* / Q000188:drug therapy / Q000235:genetics; D015352:Dry Eye Syndromes / Q000150:complications / Q000188:drug therapy / Q000235:genetics; D005260:Female; D006801:Humans; D017495:Hyperpigmentation / Q000150:complications* / Q000235:genetics; D007641:Keratolytic Agents / Q000008:administration & dosage; D009260:Nail Diseases / Q000150:complications* / Q000235:genetics; D009883:Ophthalmic Solutions / Q000008:administration & dosage; D012878:Skin Neoplasms / Q000150:complications* / Q000235:genetics; D014212:Tretinoin / Q000008:administration & dosage
chemical_list: D007641:Keratolytic Agents; D009883:Ophthalmic Solutions; D014212:Tretinoin; D002266:Carboxymethylcellulose Sodium