title: Unilateral orbital mass as an unusual presentation of IgG4-related disease.
abstract: IgG4-related diseases are a recently recognized systemic syndrome characterized by mass-forming lesions, in mainly exocrine tissue, that consist of lymphoplasmacytic infiltrates and sclerosis, which may mimic malignant neoplasm due to clinical and imaging features. We report an unusual case of a 62-year-old woman who presented with a left orbital mass, which histologically revealed to be an IgG4-sclerosing disease.
authors.affiliation: Department of pathology, Charles-Nicolle Hospital, Tunis, Tunisia.
authors.forename: S
authors.initials: S
authors.lastname: Rammeh
authors.affiliation: Department of pathology, Charles-Nicolle Hospital, Tunis, Tunisia.
authors.forename: W
authors.initials: W
authors.lastname: Ajouli
authors.affiliation: Department of maxillofacial surgery, Charles-Nicolle Hospital, Tunis, Tunisia.
authors.forename: A
authors.initials: A
authors.lastname: Landolsi
authors.affiliation: Department of pathology, Charles-Nicolle Hospital, Tunis, Tunisia. Electronic address: dr_sabbeghznaidinadia@yahoo.fr.
authors.forename: N
authors.initials: N
authors.lastname: Sabbegh Znaidi
authors.affiliation: Department of pathology, Charles-Nicolle Hospital, Tunis, Tunisia.
authors.forename: R
authors.initials: R
authors.lastname: Zermani
mesh_terms: D005260:Female; D006801:Humans; D007074:Immunoglobulin G / Q000276:immunology*; D008214:Lymphocytes / Q000166:cytology*; D008875:Middle Aged; D009918:Orbital Neoplasms / Q000175:diagnosis / Q000276:immunology / Q000473:pathology*; D012598:Sclerosis / Q000175:diagnosis / Q000276:immunology / Q000473:pathology*
chemical_list: D007074:Immunoglobulin G
keywords: IgG4-related disease; Maladie à IgG4; Orbit; Orbite; Tumeur; Tumor