title: A case of staged Norwood procedure for a unique form of truncus arteriosus, interrupted aortic arch with hypoplastic tricuspid valve and right ventricle and anomalous left coronary artery orifice: first reported case.
abstract: We present the first reported case of truncus arteriosus, interrupted aortic arch with hypoplastic tricuspid valve and right ventricle and anomalous left coronary artery orifice in a neonate in whom successful palliation was performed using two-staged procedure. The first-stage palliation was the bilateral pulmonary artery band at age 2 days. The second-stage palliation was a Norwood procedure concomitant with ASD creation and patch augmentation of the pulmonary artery confluence at 22 days. The patient is doing well, with unobstructed aortic arch and mild truncal valve regurgitation.
authors.affiliation: Department of the Cardiovascular Surgery, Faculty of Medicine, Shimane University, 89-1 Enya-cho, Izumo, Shimane, 693-8501, Japan. yoshi-sleepingcat@crest.ocn.ne.jp.|Department of the Pediatric Cardiac Surgery, Faculty of Medicine, Shimane University, 89-1 Enya-cho, Izumo, Shimane, 693-8501, Japan. yoshi-sleepingcat@crest.ocn.ne.jp.
authors.forename: Yoshifumi
authors.initials: Y
authors.lastname: Fujimoto
authors.affiliation: Department of the Cardiovascular Surgery, Faculty of Medicine, Shimane University, 89-1 Enya-cho, Izumo, Shimane, 693-8501, Japan. tcmaipee@yahoo.co.jp.|Department of the Pediatric Cardiac Surgery, Faculty of Medicine, Shimane University, 89-1 Enya-cho, Izumo, Shimane, 693-8501, Japan. tcmaipee@yahoo.co.jp.
authors.forename: Maiko
authors.initials: M
authors.lastname: Tachi
authors.affiliation: Department of the Cardiovascular Surgery, Faculty of Medicine, Shimane University, 89-1 Enya-cho, Izumo, Shimane, 693-8501, Japan.
authors.forename: Shoichi
authors.initials: S
authors.lastname: Suehiro
authors.affiliation: Department of the Cardiovascular Surgery, Faculty of Medicine, Shimane University, 89-1 Enya-cho, Izumo, Shimane, 693-8501, Japan.
authors.forename: Megumi
authors.initials: M
authors.lastname: Ito
authors.affiliation: Department of the Cardiovascular Surgery, Faculty of Medicine, Shimane University, 89-1 Enya-cho, Izumo, Shimane, 693-8501, Japan.
authors.forename: Teiji
authors.initials: T
authors.lastname: Oda
mesh_terms: D000015:Abnormalities, Multiple; D001013:Aorta, Thoracic / Q000002:abnormalities* / Q000601:surgery; D003330:Coronary Vessel Anomalies / Q000175:diagnosis / Q000601:surgery*; D003331:Coronary Vessels / Q000000981:diagnostic imaging*; D004452:Echocardiography; D005260:Female; D006352:Heart Ventricles / Q000002:abnormalities* / Q000000981:diagnostic imaging; D006801:Humans; D007231:Infant, Newborn; D058327:Norwood Procedures / Q000379:methods*; D011651:Pulmonary Artery / Q000002:abnormalities; D014057:Tomography, X-Ray Computed; D014261:Tricuspid Valve / Q000002:abnormalities* / Q000601:surgery; D014339:Truncus Arteriosus, Persistent / Q000175:diagnosis / Q000601:surgery*
keywords: Hypoplastic right ventricle; Hypoplastic tricuspid valve; Interrupted aortic arch; Norwood; Truncus arteriosus