title: Treatment of Virgin OHVIRA Syndrome with Haematometrocolpos by Complete Incision of Vaginal Septum without Hymenotomy.
abstract: Mullerian malformations result from defective fusion of the Mullerian ducts during development of the female reproductive system and have an incidence of 2-3%. The American Fertility Society classification of Mullerian anomalies is the most commonly utilized standardized classification. The least common form of these malformations is Herlyn-Werner-Wunderlich syndrome characterized by obstructed hemivagina and ipsilateral renal anomaly (OHVIRA). This syndrome has been described with case reports since 1922. Early diagnosis and surgery that include drainage of fluid and resection of the vaginal septum is necessary for OHVIRA to prevent late complications (i.e. pyocolpos, chronic cryptomenorrhea). Here in we report a case of Herlyn-Werner-Wunderlich syndrome that hymen has been preserved during the operation of non-fenestrated transverse vaginal septum resection with hysteroscopy.
authors.affiliation: Associate Professor, Department of Obstetrics and Gynecology, Fatih Sultan Mehmet Research and Training Hospital , Istanbul, Turkey .
authors.forename: Niyazi
authors.initials: N
authors.lastname: Tug
authors.affiliation: Specialist, Department of Obstetrics and Gynecology, Fatih Sultan Mehmet Research and Training Hospital , Istanbul, Turkey .
authors.forename: Mehmet Akif
authors.initials: MA
authors.lastname: Sargin
authors.affiliation: Specialist, Department of Obstetrics and Gynecology, Fatih Sultan Mehmet Research and Training Hospital , Istanbul, Turkey .
authors.forename: Ayhan
authors.initials: A
authors.lastname: Çelik
authors.affiliation: Specialist, Department of Urology, Fatih Sultan Mehmet Research and Training Hospital , Istanbul, Turkey .
authors.forename: Turgut
authors.initials: T
authors.lastname: Alp
authors.affiliation: Specialist, Department of Obstetrics and Gynecology, Fatih Sultan Mehmet Research and Training Hospital , Istanbul, Turkey .
authors.forename: Ilter
authors.initials: I
authors.lastname: Yenidede
keywords: Herlyn-Werner-Wunderlich syndrome; Hysteroscopy; Transverse vaginal septum