title: High-grade primary pulmonary leiomyosarcoma.
abstract: Primary sarcomas of the lung are rare and account for 0.5% of all primary lung tumors. There were approximately 300 cases described in the literature as of 2006. All histologic types of sarcoma were described, and the most common intrathoracic types reported were angiosarcoma, leiomyosarcoma, fibrosarcoma, hemangiopericytoma, and rhabdomyosarcoma. The biological behavior of these tumors is not well-known due to their low frequency. Leiomyosarcomas represent one of the most common subtypes encountered in the lungs, and usually occur during the sixth decade, with male predominance. Although the frequency of metastatic disease is not related to tumor size, prognosis was reported to be poorer in high-grade tumors. In comparison with other sarcomas, survival after complete resection of pulmonary leiomyosarcoma was reported as longer. We report on a patient with primary leiomyosarcoma originating from the bronchus with complete resection and long-term follow-up.
authors.affiliation: Hospital AC Camargo, São Paulo, SP, BR.
authors.forename: Rodrigo Afonso da Silva
authors.initials: RA
authors.lastname: Sardenberg
authors.affiliation: Hospital AC Camargo, São Paulo, SP, BR.
authors.forename: Renato
authors.initials: R
authors.lastname: Cangnaci Neto
authors.affiliation: Hospital Oswaldo Cruz, São Paulo, SP, BR.
authors.forename: Fernanda
authors.initials: F
authors.lastname: Cavalcanti
authors.affiliation: Instituto do Câncer do Estado de São Paulo - ICESP, São Paulo, SP, BR.
authors.forename: Riad Naim
authors.initials: RN
authors.lastname: Younes