title: Spectrum of Clinical Responses to Therapies in Infantile Bullous Pemphigoid.
abstract: Infantile bullous pemphigoid (BP) is a rare autoimmune dermatosis characterized by the presence of antibodies against basal membrane zone proteins. Histologic and immunologic features are similar to those of the adult disease, but its clinical features may vary in children. We report here four cases of infantile BP whose atypical presentation or progression shed new light on the disease.
authors.affiliation: Department of Dermatology, University Hospital of Nice, Nice, France.
authors.forename: Hélène
authors.initials: H
authors.lastname: Taquin
authors.affiliation: Department of Dermatology, University Hospital of Nice, Nice, France.|Department of Pediatrics, Nice Centre Hospitalier Universitaire Lenval Pediatric Hospital, Nice, France.
authors.forename: Christine
authors.initials: C
authors.lastname: Chiaverini
authors.affiliation: Department of Dermatology, University Hospital of Nice, Nice, France.
authors.forename: Jean Philippe
authors.initials: JP
authors.lastname: Lacour
mesh_terms: D001324:Autoantigens / Q000276:immunology; D001623:Betamethasone / Q000031:analogs & derivatives / Q000627:therapeutic use; D015153:Blotting, Western; D004797:Enzyme-Linked Immunosorbent Assay; D005076:Exanthema / Q000175:diagnosis / Q000209:etiology; D005260:Female; D019084:Fluorescent Antibody Technique, Indirect; D005938:Glucocorticoids / Q000627:therapeutic use*; D006801:Humans; D007223:Infant; D007231:Infant, Newborn; D008297:Male; D024041:Non-Fibrillar Collagens / Q000276:immunology; D010391:Pemphigoid, Bullous / Q000175:diagnosis / Q000188:drug therapy* / Q000276:immunology; D011239:Prednisolone / Q000627:therapeutic use; D012867:Skin / Q000473:pathology*; D016896:Treatment Outcome; D000097805:Collagen Type XVII
chemical_list: D001324:Autoantigens; D001623:Betamethasone; D005938:Glucocorticoids; D024041:Non-Fibrillar Collagens; D011239:Prednisolone; D000097805:Collagen Type XVII; C011175:betamethasone-17,21-dipropionate