title: Desmoplastic small round cell tumor of the lung: A case report and literature review.
abstract: Desmoplastic small round cell tumor (DSRCT) is a rare, aggressive and malignant tumor that is characterized by nests of small tumor cells surrounded by a cellular and vascular collagenous stroma and predominantly affects young adolescent males. This tumor most commonly originates in the abdomen; however, in rare cases, DSRCT can originate in other body regions. The main manifestations of DSRCT are chest pain and respiratory symptoms, and patients' average survival after diagnosis is less than two years. In this report, we describe a case involving DSRCT of the lung that proved to be difficult to diagnose, and we conduct a literature review.
authors.affiliation: Pulmonologist - Hospital Universitario Central de Asturias (HUCA), Instituto Nacional de Silicosis (INS), Área del Pulmón, Oviedo, Spain.
authors.forename: Miguel Angel
authors.initials: MA
authors.lastname: Ariza-Prota
authors.affiliation: Pulmonologist - Hospital Universitario Central de Asturias (HUCA), Instituto Nacional de Silicosis (INS), Área del Pulmón, Oviedo, Spain.
authors.forename: Ana
authors.initials: A
authors.lastname: Pando-Sandoval
authors.affiliation: Pulmonologist - Hospital Universitario Central de Asturias (HUCA), Instituto Nacional de Silicosis (INS), Área del Pulmón, Oviedo, Spain.
authors.forename: David
authors.initials: D
authors.lastname: Fole-Vázquez
authors.affiliation: Pulmonologist - Hospital Universitario Central de Asturias (HUCA), Instituto Nacional de Silicosis (INS), Área del Pulmón, Oviedo, Spain.
authors.forename: Pere
authors.initials: P
authors.lastname: Casan
keywords: Adenosine deaminase, ADA; Computed tomography, CT; Desmoplastic small round cell tumor; Desmoplastic small round cell tumor, DSRCT; Enzyme-linked immunosorbent assay, ELISA; Fluorodeoxyglucose positron emission tomography/CT, FDG-PET/CT; Human immunodeficiency virus, HIV; Lactate dehydrogenase, LDH; Leukocyte common antigen, LCA; Lung cancer; Magnetic resonance imaging, MRI; Pleural effusion; Polymerase chain reaction, PCR; Primitive neuroectodermal tumor, PNET; Smooth muscle actin, SMA; Transbronchial needle aspiration, TBNA