title: An atypical case of dermatomyositis associated with chromophobe renal cell carcinoma.
abstract: Dermatomyositis and polymyositis are the major idiopathic inflammatory myopathies in adults. They are associated with an elevated risk of malignancy. However, renal tumours have rarely been described in dermatomyositis patients. We report the case of a 27-year-old Caucasian man with chromophobe renal cell cancer (ChRCC) and antinuclear matrix protein (NXP-2)-associated dermatomyositis. To the best of our knowledge, there are no previous reports of ChRCC presenting with dermatomyositis.
authors.affiliation: University of Pennsylvania, Philadelphia, Pennsylvania, USA.
authors.forename: Michael David
authors.initials: MD
authors.lastname: George
authors.affiliation: Johns Hopkins University, Baltimore, Maryland, USA.
authors.forename: Arash H
authors.initials: AH
authors.lastname: Lahouti
authors.affiliation: Johns Hopkins University, Baltimore, Maryland, USA.
authors.forename: Lisa
authors.initials: L
authors.lastname: Christopher-Stine
mesh_terms: D000251:Adenosine Triphosphatases / Q000378:metabolism; D000328:Adult; D002292:Carcinoma, Renal Cell / Q000150:complications* / Q000473:pathology; D004268:DNA-Binding Proteins / Q000378:metabolism; D003882:Dermatomyositis / Q000209:etiology* / Q000378:metabolism; D006801:Humans; D007680:Kidney Neoplasms / Q000150:complications* / Q000473:pathology; D008297:Male; D009132:Muscles / Q000473:pathology*; D009220:Myositis / Q000209:etiology; D012867:Skin / Q000473:pathology*
chemical_list: D004268:DNA-Binding Proteins; D000251:Adenosine Triphosphatases; C551732:MORC3 protein, human