title: Case 226: Oval Window Atresia.
abstract: A 6-year-old girl presented with bilateral hearing loss. Her otologic, birth, and family histories were limited, given that she was adopted, but her parents reported that she had had difficulty hearing and speaking ever since they adopted her at 2 years of age. Her parents denied a history of acute otitis media, otorrhea, otalgia, vertigo, autophony, or tinnitus since her adoption. At 2.5 years of age, a diagnosis of hearing loss was made, and she was given hearing aids. Her parents believed that she had been doing well with both receptive and expressive language since she had received the hearing aids. At examination, she had small bilateral preauricular skin tags and normal pinna. Her external auditory canals were of a normal caliber bilaterally, with no otorrhea or lesions. The tympanic membranes were translucent and mobile at pneumatic otoscopy. There was no evidence of a middle ear lesion, nor was there a Schwartz sign. She had no nystagmus or vertigo at pneumatic otoscopy. Audiometry was performed and revealed moderate to severe conductive hearing loss bilaterally, with a mixed component present at 2000 KHz. She had normal bilateral middle ear pressure at tympanometry. Thin-section computed tomography (CT) of the temporal bone was performed.
authors.affiliation: From the Department of Otolaryngology and Communication Enhancement (A.H., E.A.) and Department of Radiology (A.D.), Boston Children's Hospital, 300 Longwood Ave, LO-367, Boston, MA 02115; and Department of Otology and Laryngology, Harvard Medical School, Boston, Mass (E.A.).
authors.forename: Amy
authors.initials: A
authors.lastname: Hughes
authors.affiliation: From the Department of Otolaryngology and Communication Enhancement (A.H., E.A.) and Department of Radiology (A.D.), Boston Children's Hospital, 300 Longwood Ave, LO-367, Boston, MA 02115; and Department of Otology and Laryngology, Harvard Medical School, Boston, Mass (E.A.).
authors.forename: Amy
authors.initials: A
authors.lastname: Danehy
authors.affiliation: From the Department of Otolaryngology and Communication Enhancement (A.H., E.A.) and Department of Radiology (A.D.), Boston Children's Hospital, 300 Longwood Ave, LO-367, Boston, MA 02115; and Department of Otology and Laryngology, Harvard Medical School, Boston, Mass (E.A.).
authors.forename: Eelam
authors.initials: E
authors.lastname: Adil
mesh_terms: D001844:Bone Conduction; D002648:Child; D003937:Diagnosis, Differential; D005260:Female; D006314:Hearing Loss, Conductive / Q000000981:diagnostic imaging* / Q000473:pathology; D006801:Humans; D010046:Oval Window, Ear / Q000000981:diagnostic imaging* / Q000473:pathology; D013701:Temporal Bone / Q000000981:diagnostic imaging* / Q000473:pathology; D014057:Tomography, X-Ray Computed