title: Unusual Outcome of a Right Ventricular Rhabdomyoma in an Infant.
abstract: Rhabdomyomas are the most common benign cardiac tumors. They may often be associated with tuberous sclerosis. In many cases, cardiac rhabdomyomas undergo spontaneous regression. Here, we report the unusual case of an infant with a large nonobstructive right ventricular rhabdomyoma at birth and at four months of age, which subsequently caused severe right ventricle outflow tract obstruction at six months of age, prompting surgery to remove the tumor. Close monitoring should be done in infants with large nonobstructive cardiac rhabdomyomas.
authors.affiliation: Children Hospital Gatien de Clocheville, Tours, France University François Rabelais, Tours, France INSERM UMR 1069 «nutrition, croissance et cancer», Tours, France bruno.lefort@univ-tours.fr.
authors.forename: Bruno
authors.initials: B
authors.lastname: Lefort
authors.affiliation: Children Hospital Gatien de Clocheville, Tours, France.
authors.forename: Julie
authors.initials: J
authors.lastname: Lothion
authors.affiliation: Children Hospital Gatien de Clocheville, Tours, France.
authors.forename: Jean-Marc El
authors.initials: JM
authors.lastname: Arid
authors.affiliation: University François Rabelais, Tours, France Department of Pathology, University Hospital of Tours, Tours, France.
authors.forename: Flore
authors.initials: F
authors.lastname: Tabareau-Delalande
authors.affiliation: University Hospital of Poitiers, Poitiers, France.
authors.forename: Alaeddin
authors.initials: A
authors.lastname: Nassimi
authors.affiliation: Children Hospital Gatien de Clocheville, Tours, France.
authors.forename: Paul
authors.initials: P
authors.lastname: Neville
authors.affiliation: Children Hospital Gatien de Clocheville, Tours, France University François Rabelais, Tours, France.
authors.forename: Alain
authors.initials: A
authors.lastname: Chantepie
mesh_terms: D018450:Disease Progression; D006338:Heart Neoplasms / Q000150:complications / Q000000981:diagnostic imaging* / Q000601:surgery; D006352:Heart Ventricles / Q000473:pathology; D006801:Humans; D007223:Infant; D008297:Male; D012207:Rhabdomyoma / Q000150:complications / Q000000981:diagnostic imaging* / Q000601:surgery; D016896:Treatment Outcome; D016216:Ultrasonography, Prenatal; D014694:Ventricular Outflow Obstruction / Q000000981:diagnostic imaging* / Q000209:etiology / Q000601:surgery
keywords: cardiac tumors (includes myxoma; echocardiography; emergency; infant; metastases); primary; surgery