title: An Unusual Type of Totally Anomalous Pulmonary Venous Connection to the Superior Cavoatrial Junction.
abstract: A neonate with cyanosis at birth was found to have a rare type of totally anomalous pulmonary venous connection. The pulmonary veins entered a confluence posterior to the left atrial wall, which drained into the right superior cavoatrial junction. There were no other major structural defects and no evidence of isomerism. Because of the severe cyanosis, and the restrictive nature of the interatrial communication, we performed balloon atrioseptostomy to improve oxygenation. We then achieved successful surgical repair when the baby was aged 7 months.
authors.affiliation: Pediatric and Congenital Cardiac Surgery Unit, Department of Surgery, School of Medical Sciences, Health Campus, Universiti Sains Malaysia, Kubang Kerian, Kelantan, Malaysia amahir@gmail.com.
authors.forename: Ahmad Mahir
authors.initials: AM
authors.lastname: Shamsuddin
authors.affiliation: Pediatric Cardiology Unit, Department of Pediatrics, Hospital Raja Perempuan Zainab II, Kota Bharu, Kelantan, Malaysia.
authors.forename: Abdul Rahim
authors.initials: AR
authors.lastname: Wong
authors.affiliation: Institute of Genetic Medicine, Newcastle University, International Centre for Life, Newcastle upon Tyne, United Kingdom.
authors.forename: Robert H
authors.initials: RH
authors.lastname: Anderson
authors.affiliation: Pediatric Cardiac Surgery Unit, East Midlands Congenital Heart Center, Glenfield Hospital, Leicester, United Kingdom.
authors.forename: Antonio F
authors.initials: AF
authors.lastname: Corno
mesh_terms: D006348:Cardiac Surgical Procedures / Q000379:methods; D003490:Cyanosis; D005260:Female; D006344:Heart Septal Defects, Atrial / Q000601:surgery*; D006801:Humans; D007231:Infant, Newborn; D011667:Pulmonary Veins / Q000002:abnormalities*; D016896:Treatment Outcome
keywords: cardiopulmonary bypass; congenital heart defects; congenital heart surgery; totally anomalous pulmonary venous connection