title: [A toddler with an itchy, brown rash].
abstract: An otherwise healthy 15-month-old boy presented with a pruritic rash that had gradually developed since birth, leaving brown pigmentation. Darier's sign was positive and the diagnosis of juvenile urticaria pigmentosa was made. Juvenile urticaria pigmentosa usually shows spontaneous remission before puberty. Progression to systemic mastocytosis is extremely rare.
authors.affiliation: Leids Universitair Medisch Centrum, afd. Dermatologie, Leiden.
authors.forename: Karlijn M
authors.initials: KM
authors.lastname: Mulder
authors.forename: Maarten H
authors.initials: MH
authors.lastname: Vermeer
mesh_terms: D005076:Exanthema; D006801:Humans; D007223:Infant; D008297:Male; D010808:Physical Examination; D012075:Remission, Spontaneous; D012741:Sexual Maturation; D014582:Urticaria Pigmentosa / Q000175:diagnosis*