title: [Inherited primitive and secondary polycythemia].
abstract: Myeloproliferative disorders and secondary polycythemia cover most of the polycythemia cases encountered in daily practice. Inherited polycythemias are rare entities that have to be suspected when the classical causes of acquired polycythemia have been ruled out. Recent advances were made in the understanding of these pathologies, which are still little known to the physicians. This review reports the state of knowledge and proposes an algorithm to follow when confronted to a possible case of inherited polycythemia.
authors.affiliation: Service de médecine interne, hôpital Édouard-Herriot, 5, place d'Arsonval, 69003 Lyon, France. Electronic address: tbarba19@gmail.com.
authors.forename: T
authors.initials: T
authors.lastname: Barba
authors.affiliation: Service d'hématologie-oncologie, faculté de médecine et des sciences de la santé, CHU de Sherbrooke, 2500, boulevard de l'Université, Sherbrooke, Canada.
authors.forename: J-C
authors.initials: JC
authors.lastname: Boileau
authors.affiliation: Service de médecine interne, hôpital d'instruction des armées Desgenettes, 108, boulevard Pinel, 69003 Lyon, France.
authors.forename: F
authors.initials: F
authors.lastname: Pasquet
authors.affiliation: Service de médecine interne, hôpital Édouard-Herriot, 5, place d'Arsonval, 69003 Lyon, France.
authors.forename: A
authors.initials: A
authors.lastname: Hot
authors.affiliation: Service d'hématologie-oncologie, faculté de médecine et des sciences de la santé, CHU de Sherbrooke, 2500, boulevard de l'Université, Sherbrooke, Canada.
authors.forename: M
authors.initials: M
authors.lastname: Pavic
mesh_terms: D000465:Algorithms; D003937:Diagnosis, Differential; D004912:Erythrocytes; D006454:Hemoglobins; D006801:Humans; D011086:Polycythemia / Q000175:diagnosis* / Q000235:genetics*
chemical_list: D006454:Hemoglobins
keywords: Chuvash polycythemia; Erythrocytosis; Hyperaffine hemoglobin; Hyperviscosity syndrome; Hémoglobine hyperaffine; Inherited polycythemia; Methemoglobinemia; Méthémoglobinémie; Polycythémie; Polyglobulie de Chuvash; Polyglobulie héréditaire; Syndrome d’hyperviscosité; Érythrocytose