title: Herlyn-Werner-Wunderlich Syndrome: A Rare Cause of Pelvic Pain and High CA 19-9 Levels in an Adolescent Girl.
abstract: Herlyn-Werner-Wunderlich (HWW) syndrome is a rare developmental anomaly that includes uterus didelphys with obstructed hemivagina and ipsilateral renal agenesis. A 13-year-old girl presented with chronic abdominal pain. Magnetic resonance imaging revealed uterus didelphys, hematometrocolpos and renal agenesis on the right side with imperforate hymen. Subsequently the patient was found to have Mullerian duct anomalies. CA 19-9 level was high. At laparoscopy combined with vaginoscopy hematocolpos was drained following which she improved clinically and CA 19-9 level returned to normal.
authors.affiliation: Department of Pediatric Hematology and Oncology, Ankara University School of Medicine, Ankara, Turkey.
authors.forename: Emel
authors.initials: E
authors.lastname: Unal
authors.affiliation: Department of Pediatric Hematology and Oncology, Ankara University School of Medicine, Ankara, Turkey.
authors.forename: Hikmet Gulsah
authors.initials: HG
authors.lastname: Tanyildiz
authors.affiliation: Department of Obstetrics and Gynecology, Ankara University School of Medicine, Ankara, Turkey.
authors.forename: Murat
authors.initials: M
authors.lastname: Sonmezer
authors.affiliation: Department of Pediatrics, Ankara University School of Medicine, Ankara, Turkey.
authors.forename: Hatice Gul
authors.initials: HG
authors.lastname: Erkol
authors.affiliation: Department of Radiology, Ankara University School of Medicine, Ankara, Turkey.
authors.forename: Suat
authors.initials: S
authors.lastname: Fitoz
keywords: CA 19-9; Herlyn-Werner-Wunderlich Syndrome; Mullerian duct anomaly; Renal agenesis
references.citation: J Emerg Med. 2013 Oct;45(4):541-3
references.pmid: 23810118
references.citation: Fertil Steril. 2008 Sep;90(3):849.e9-10
references.pmid: 18625502
references.citation: Pediatr Radiol. 2007 Jul;37(7):657-65
references.pmid: 17503029
references.citation: Clin Res Hepatol Gastroenterol. 2013 Jun;37(3):e85-8
references.pmid: 23562788
references.citation: Hepatobiliary Pancreat Dis Int. 2009 Dec;8(6):620-6
references.pmid: 20007080
references.citation: BMJ Case Rep. 2011 Jul 15;2011:null
references.pmid: 22689557