title: A case of the cerebellar cognitive affective syndrome in a 12-year-old boy with acute post-infectious cerebellar ataxia.
abstract: BACKGROUND
  The cerebellar cognitive affective syndrome (CCAS), is characterised by disturbances in executive functions, visuospatial difficulties, personality changes, and linguistic difficulties. It is well described in other diseases of the cerebellum such as tumour resection and cerebellar stroke but has not previously been described in detail in paediatric cases of acute post-infectious ataxia (APCA).
  
  
  METHODS
  Case study. A 12-year-old boy was admitted with severe ataxia, dysmetria, dysdiadokinesia, and dysarthria. He was diagnosed with acute post-infectious cerebellar ataxia (APCA). Besides motor symptoms, the patient showed signs of disturbances in executive functions, visiospatial difficulties, personality changes, and linguistic difficulties. These symptoms correspond to CCAS.
  
  
  CONCLUSIONS
  CCAS may be an overlooked complication to APCA. In addition, APCA is considered a transient, monophasic disease and studying CCAS in this disease may give insight into subtle cases of CCAS and thus provide new knowledge about CCAS.
authors.affiliation: Department of Paediatrics, Regional Hospital Viborg, Heibergs Alle 4, 8800 Viborg, Denmark. Electronic address: nadjrasm@rm.dk.
authors.forename: Nadja
authors.initials: N
authors.lastname: Lindberg Bonne
authors.affiliation: Hammel Neurorehabilitation Centre and University Research Clinic, Central Denmark Region, Voldbyvej 15, 8450 Hammel, Denmark. Electronic address: lars.evald@rm.dk.
authors.forename: Lars
authors.initials: L
authors.lastname: Evald
authors.affiliation: Department of Paediatrics, Regional Hospital Viborg, Heibergs Alle 4, 8800 Viborg, Denmark. Electronic address: jonas.hansen@midt.rm.dk.
authors.forename: Jonas Kjeldbjerg
authors.initials: JK
authors.lastname: Hansen
mesh_terms: D000208:Acute Disease; D002524:Cerebellar Ataxia / Q000209:etiology*; D002526:Cerebellar Diseases / Q000175:diagnosis* / Q000209:etiology / Q000523:psychology; D002648:Child; D003072:Cognition Disorders / Q000209:etiology*; D056344:Executive Function; D006801:Humans; D008297:Male; D014777:Virus Diseases / Q000150:complications*
keywords: Acute post-infectious cerebellar ataxia; Cerebellar cognitive affective syndrome; Children; Single-photon emission computed tomography