title: Recent Treatments of Interstitial Lung Disease with Systemic Sclerosis.
abstract: Systemic sclerosis (SSc) is a disorder characterized by immune dysfunction, microvascular injury, and fibrosis. Organ involvement in patients with SSc is variable; however, pulmonary involvement occurs in up to 90% of patients with SSc. Interstitial lung disease (ILD) is a major cause of mortality and, thus, a major determinant in the prognosis of patients with SSc. This review summarizes current findings about the characteristics of ILD in patients with SSc, selection of patients with SSc-ILD who are candidates for the treatment, and current treatment options.
authors.affiliation: Assistant Professor, Division of Rheumatology, Department of Internal Medicine, Keio University School of Medicine, Shinjuku, Tokyo, Japan.
authors.forename: Hidekata
authors.initials: H
authors.lastname: Yasuoka
keywords: interstitial lung disease; pulmonary hypertension; systemic sclerosis
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