title: Intestinal lymphangiectasia in children. A favorable response to dietary modifications.
abstract: Intestinal lymphangiectasia (IL) is a rare disease characterized by dilatation of intestinal lymphatics. It can be classified as primary or secondary according to the underlying etiology. The clinical presentations of IL are pitting edema, chylous ascites, pleural effusion, acute appendicitis, diarrhea, lymphocytopenia, malabsorption, and intestinal obstruction. The diagnosis is made by intestinal endoscopy and biopsies. Dietary modification is the mainstay in the management of IL with a variable response. Here we report 2 patients with IL in Bahrain who showed positive response to dietary modification.
authors.affiliation: Department of Pediatrics, Salmaniya Medical Complex, Manama, Bahrain. E-mail. halfaraj@hotmail.com.
authors.forename: Hasan M
authors.initials: HM
authors.lastname: Isa
authors.forename: Ghadeer G
authors.initials: GG
authors.lastname: Al-Arayedh
authors.forename: Afaf M
authors.initials: AM
authors.lastname: Mohamed
mesh_terms: D001445:Bahrain; D002648:Child; D018752:Diet, Fat-Restricted; D019587:Dietary Supplements; D004386:Duodenum / Q000473:pathology; D004487:Edema; D006801:Humans; D007223:Infant; D041943:Infant Formula; D008168:Lung / Q000000981:diagnostic imaging; D008201:Lymphangiectasis, Intestinal / Q000000981:diagnostic imaging / Q000178:diet therapy* / Q000473:pathology; D008297:Male; D014057:Tomography, X-Ray Computed; D014280:Triglycerides / Q000627:therapeutic use*; D014463:Ultrasonography
chemical_list: D014280:Triglycerides
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