title: Adult hemophagocytic lymphohistiocytosis causing multi organ dysfunction in a patient with multiple autoimmune disorders: when the immune system runs amok.
abstract: We report a case of several autoimmune disorders eventually presenting as severe multi organ dysfunction syndrome caused by adult hemophagocytic lymphohistiocytosis (HLH). Clinical and laboratory tests might lead to fatal misinterpretation without awareness of its diagnostic evaluation, as HLH shares common features with sepsis and immune-mediated systemic inflammatory response syndromes.
authors: Neurological Intensive Care Unit Department of Neurology Charité - Universitätsmedizin Berlin 10117 Berlin Germany.
authors: Robert
authors: R
authors: Fleischmann
authors: Neurological Intensive Care Unit Department of Neurology Charité - Universitätsmedizin Berlin 10117 Berlin Germany.
authors: Wolfgang
authors: W
authors: Böhmerle
authors: Department of Pathology Charité - Universitätsmedizin Berlin 10117 Berlin Germany.
authors: Maximilian
authors: M
authors: von Laffert
authors: Department of Pathology Charité - Universitätsmedizin Berlin 10117 Berlin Germany.
authors: Korinna
authors: K
authors: Jöhrens
authors: Neurological Intensive Care Unit Department of Neurology Charité - Universitätsmedizin Berlin 10117 Berlin Germany.
authors: Annerose
authors: A
authors: Mengel
authors: Neurological Intensive Care Unit Department of Neurology Charité - Universitätsmedizin Berlin 10117 Berlin Germany.
authors: Benjamin
authors: B
authors: Hotter
authors: Neurological Intensive Care Unit Department of Neurology Charité - Universitätsmedizin Berlin 10117 Berlin Germany.
authors: Robert
authors: R
authors: Lindenberg
authors: Neurological Intensive Care Unit Department of Neurology Charité - Universitätsmedizin Berlin 10117 Berlin Germany.
authors: Franziska
authors: F
authors: Scheibe
authors: Neurological Intensive Care Unit Department of Neurology Charité - Universitätsmedizin Berlin 10117 Berlin Germany.
authors: Martin
authors: M
authors: Köhnlein
authors: Childhood Cancer Research Unit Department of Women׳s and Children׳s Health Karolinska Institutet Karolinska University Hospital Solna 17176 Stockholm Sweden.
authors: Tatiana
authors: T
authors: von Bahr Greenwood
authors: Childhood Cancer Research Unit Department of Women׳s and Children׳s Health Karolinska Institutet Karolinska University Hospital Solna 17176 Stockholm Sweden.
authors: Jan Inge
authors: JI
authors: Henter
authors: Neurological Intensive Care Unit Department of Neurology Charité - Universitätsmedizin Berlin 10117 Berlin Germany.
authors: Andreas
authors: A
authors: Meisel
keywords: Hemophagocytic lymphohistiocytosis; MuSK‐Ab‐positive myasthenia gravis; macrophage activation syndrome; multi organ dysfunction; systemic lupus erythematosus