title: Single-Stage Repair of an Unusual Association: Congenital Gerbode Defect, Hypoplastic Aortic Arch, and Partially Anomalous Pulmonary Venous Return in an Infant.
abstract: We present the case of a two-month-old male with congenital Gerbode defect, hypoplastic aortic arch, and left-sided partially anomalous pulmonary venous return. The patient underwent single-stage surgical repair, which consisted of aortic arch advancement with resection of the coarctation segment, pulmonary vein repair, and primary closure of the Gerbode defect. The anomalous pulmonary vein posed a particular challenge due to its size and distance from the left atrium, which we approached with a posterior atrial wall trapdoor baffle technique, without mobilizing the affected vein. Postoperatively and at one year follow-up, there was no evidence of residual lesions and there was unobstructed flow pattern across the aortic arch and the affected pulmonary vein.
authors: Heart Institute, Cincinnati Children's Hospital Medical Center, Cincinnati, OH, USA saul.flores@cchmc.org.
authors: Saul
authors: S
authors: Flores
authors: UC Department of Pediatrics, Heart Institute, Cincinnati Children's Hospital Medical Center, Cincinnati, OH, USA.
authors: Thomas R
authors: TR
authors: Kimball
authors: UC Department of Pediatrics, Heart Institute, Cincinnati Children's Hospital Medical Center, Cincinnati, OH, USA.
authors: David P
authors: DP
authors: Nelson
authors: UC Department of Pediatrics, Heart Institute, Cincinnati Children's Hospital Medical Center, Cincinnati, OH, USA.
authors: David L S
authors: DL
authors: Morales
mesh_terms: D001013:Aorta, Thoracic / Q000002:abnormalities*; D001017:Aortic Coarctation / Q000601:surgery*; D006348:Cardiac Surgical Procedures / Q000379:methods*; D006345:Heart Septal Defects, Ventricular / Q000601:surgery*; D006801:Humans; D007223:Infant; D008297:Male; D011667:Pulmonary Veins / Q000002:abnormalities*; D012587:Scimitar Syndrome / Q000601:surgery*; D016896:Treatment Outcome
keywords: Gerbode defect; coarctation of the aorta; partially anomalous pulmonary venous return