title: Pulmonary artery aneurysm in an adult patient with idiopathic dilatation of the pulmonary artery.
abstract: Idiopathic dilatation of the pulmonary artery (IDPA) is a rare congenital heart disease. It has been described for almost one hundred years, and numerous definitions have been proposed. The IDPA diagnostic criteria have not been updated for years. Secondary to primary disease, pulmonary artery aneurism was recognised as a lethal defect; however, long-term follow-up of patients with IDPA has not been well researched. Thus, indications to medical or surgical treatment are not evidence based. Here, we present a rare case of a 54-year-old patient with IDPA, who remained under observation for 36 years without surgical intervention.
authors: Department of Cardiology, Military Institute of Medicine, Warsaw, Poland.
authors: Katarzyna
authors: K
authors: Betkier-Lipińska
authors: Department of Cardiac Surgery, Military Institute of Medicine, Warsaw, Poland.
authors: Grzegorz
authors: G
authors: Suwalski
authors: Department of Clinical Radiology, Military Institute of Medicine, Warsaw, Poland.
authors: Sebastian
authors: S
authors: Czarkowski
authors: Department of Cardiac Surgery, Military Institute of Medicine, Warsaw, Poland.
authors: Piotr
authors: P
authors: Hendzel
authors: Department of Cardiology, Military Institute of Medicine, Warsaw, Poland.
authors: Andrzej
authors: A
authors: Cwetsch
keywords: main pulmonary artery; pulmonary artery dilatation