title: Distal Esophageal Duplication Cyst with Gastro-Esophageal Reflux Disease: A Rare Association and a Management Challenge.
abstract: Esophageal duplication cysts are rare congenital abnormalities of the foregut and may be associated with other conditions. Association of esophageal duplication with Gastro-Esophageal Reflux Disease (GERD) has not been reported in children. We are reporting a case of a 16 months baby who had antenatal diagnosis of diaphragmatic hernia. Postnatal CTchest, however, suggested a distal esophageal duplication cyst and a contrast esophagogram showed grade-IV GER. A thoracoscopy in another hospital excluded esophageal duplication at that time. Later, he presented with hematemesis in our department and was re-evaluated. Repeat CTconfirmed a persistent 2.5 x 1.3 cm cyst in distal esophagus. Upper GI endoscopy suggested grade-II esophagitis with a wide patent gastro-esophageal junction. The child was treated with left thoracotomy, excision of the duplication cyst and thoracic fundoplication. He had an uneventful post-operative recovery and is doing well at 6 months follow-up.
authors.affiliation: Department of Pediatric Surgery, Zayed Military Hospital, Abu Dhabi, UAE.
authors.forename: Iftikhar Ahmad
authors.initials: IA
authors.lastname: Jan
authors.affiliation: Department of Pediatrics, Zayed Military Hospital, Abu Dhabi, UAE.
authors.forename: Asma
authors.initials: A
authors.lastname: Al Nuaimi
authors.affiliation: Department of Pediatrics, Zayed Military Hospital, Abu Dhabi, UAE.
authors.forename: Basma
authors.initials: B
authors.lastname: Al Hamoudi
authors.affiliation: Department of Radiology, Zayed Military Hospital, Abu Dhabi, UAE.
authors.forename: Khalid
authors.initials: K
authors.lastname: Al Naqbi
authors.affiliation: Department of Pediatrics, Zayed Military Hospital, Abu Dhabi, UAE.
authors.forename: Mohammad
authors.initials: M
authors.lastname: Bilal
mesh_terms: D003680:Deglutition Disorders / Q000209:etiology; D016145:Endoscopy, Digestive System; D004934:Esophageal Cyst / Q000150:complications / Q000151:congenital* / Q000000981:diagnostic imaging / Q000601:surgery; D004941:Esophagitis / Q000175:diagnosis* / Q000601:surgery; D004943:Esophagogastric Junction / Q000601:surgery; D004947:Esophagus / Q000002:abnormalities* / Q000601:surgery; D018662:Fundoplication; D005764:Gastroesophageal Reflux / Q000209:etiology; D006548:Hernia, Diaphragmatic; D006801:Humans; D007223:Infant; D008297:Male; D011859:Radiography; D012720:Severity of Illness Index; D013906:Thoracoscopy; D013908:Thoracotomy; D016896:Treatment Outcome