title: Management of Red Teeth in an International Patient with X-Linked Adrenoleukodystrophy.
abstract: Childhood cerebral X-linked adrenoleukodystrophy is a progressive, central nervous system, and endocrine disorder that typically leads to total neurologic disability and, eventually, death without appropriate, timely medical therapy. Hematopoietic stem cell transplantation has been found effective in slowing cerebral deterioration and improving long-term survival. The purpose of this case report was to describe the multidisciplinary management of red, discolored, pulpally treated primary molars identified in a nine-year-old Russian boy with childhood cerebral X-linked adrenoleukodystrophy preparing for myeloablative conditioning chemotherapy followed by hematopoietic stem cell transplantation.
authors.affiliation: Division of Pediatric Dentistry, Department of Developmental and Surgical Sciences, School of Dentistry, University of Minnesota, Minneapolis, Minn., USA. jmkarp@umn.edu.
authors.forename: Elena
authors.initials: E
authors.lastname: Petrova
authors.affiliation: Division of Blood and Marrow Transplantation, Department of Pediatrics, School of Medicine, University of Minnesota, Minneapolis, Minn., USA.
authors.forename: Weston P
authors.initials: WP
authors.lastname: Miller
authors.affiliation: Division of Basic Sciences, Department of Diagnostic and Biological Sciences, School of Dentistry, University of Minnesota, Minneapolis, Minn., USA.
authors.forename: Sandra L
authors.initials: SL
authors.lastname: Myers
authors.affiliation: Division of Pediatric Dentistry, Department of Developmental and Surgical Sciences, School of Dentistry, University of Minnesota, Minneapolis, Minn., USA.
authors.forename: Jeffrey M
authors.initials: JM
authors.lastname: Karp
mesh_terms: D000326:Adrenoleukodystrophy; D018380:Hematopoietic Stem Cell Transplantation; D006801:Humans; D008297:Male