title: Left bronchial compression and pulmonary hypertension related to anomalous right pulmonary artery.
abstract: Anomalous origin of a pulmonary artery from the ascending aorta is a congenital defect that can be complicated by pulmonary arterial hypertension, typically due to vascular disease if the anomaly is left uncorrected past 6 months of age. We describe a unique case of severe pulmonary arterial hypertension with this defect in a 1-month-old infant unexpectedly caused instead by bronchial compression from her dilated left pulmonary artery.
authors.affiliation: Department of Pediatrics,Division of Cardiology,Children's Hospital of Los Angeles,Los Angeles,California,United States of America.
authors.forename: Jennifer A
authors.initials: JA
authors.lastname: Su
authors.affiliation: Department of Pediatrics,Division of Cardiology,Children's Hospital of Los Angeles,Los Angeles,California,United States of America.
authors.forename: Andrew L
authors.initials: AL
authors.lastname: Cheng
authors.affiliation: Department of Pediatrics,Division of Cardiology,Children's Hospital of Los Angeles,Los Angeles,California,United States of America.
authors.forename: Jacqueline R
authors.initials: JR
authors.lastname: Szmuszkovicz
mesh_terms: D001011:Aorta / Q000002:abnormalities*; D001982:Bronchial Diseases / Q000000981:diagnostic imaging*; D000072226:Computed Tomography Angiography; D004452:Echocardiography; D005260:Female; D006801:Humans; D006976:Hypertension, Pulmonary / Q000209:etiology*; D007223:Infant; D011651:Pulmonary Artery / Q000002:abnormalities*; D054079:Vascular Malformations / Q000150:complications* / Q000000981:diagnostic imaging*
keywords: Anomalous origin of one pulmonary artery from the aorta; heart failure; infant; pulmonary arterial hypertension; pulmonary vascular disease