title: Using a Distant Abdominal Skin Flap to Treat Digital Constriction Bands: A Case Report for Vohwinkel Syndrome.
abstract: In this study, a Vohwinkel syndrome case is presented where in 5th digit constriction bands in the right hand were reconstructed using a distant abdominal skin flap. Vohwinkel syndrome, or keratoderma hereditarium mutilans, is a rare, autosomal dominant genetic skin condition that causes palmoplantar hyperkeratosis and constricts finger and/or toe bands. In a typical manifestation, the finger and toe constriction bands lead to progressive strangulation and autoamputation, which requires immediate clinical treatment. Topical keratolytics and systemic retinoids have been used to treat hyperkeratosis but without consistent results. Only 1 effective approach for autoamputation has been accepted, reconstructive surgery.Applying a distant abdominal skin flap produced satisfying postoperative effects at the 18-month follow-up.
authors.affiliation: From the Department of Plastic Surgery, Peking Union Medical College Hospital, Beijing (MZ, KS, YW); Department of Neurosurgery, Qingdao Huangdao District Hospital of Traditional Chinese Medicine, Qingdao, Shandong (ND); and Department of Dermatology, Peking Union Medical College Hospital, Beijing, China (CS).
authors.forename: Mingzi
authors.initials: M
authors.lastname: Zhang
authors.forename: Kexin
authors.initials: K
authors.lastname: Song
authors.forename: Ning
authors.initials: N
authors.lastname: Ding
authors.forename: Chang
authors.initials: C
authors.lastname: Shu
authors.forename: Youbin
authors.initials: Y
authors.lastname: Wang
mesh_terms: D000005:Abdomen; D000015:Abnormalities, Multiple / Q000601:surgery*; D003251:Constriction, Pathologic / Q000601:surgery; D005260:Female; D005385:Fingers / Q000002:abnormalities* / Q000601:surgery*; D006228:Hand Deformities, Congenital / Q000601:surgery*; D006319:Hearing Loss, Sensorineural / Q000601:surgery*; D006801:Humans; D007645:Keratoderma, Palmoplantar / Q000601:surgery*; D019651:Plastic Surgery Procedures / Q000379:methods; D013524:Surgical Flaps; D055815:Young Adult