title: Sigmoid vaginoplasty in testicular feminising syndrome: surgical technique, outcome and review of the literature.
abstract: Vaginal agenesis occurs in approximately 1:5000 live female births. It results from failure of the sinovaginal bulbs to develop and form the vaginal plate. Mayer-Rokitansky-Kuster-Hauser syndrome (MRKH) is the most common cause of vaginal absence followed by complete or partial androgen insensitivity syndrome. Treatment of these patients encompasses a spectrum from simple non-operative dilation to the more complicated surgical creation of a neovagina. We present a case of a patient with testicular feminising syndrome who was reared as a female and underwent bilateral gonadal excision and sigmoid vaginoplasty.
authors.affiliation: Department of Urology, King George's Medical University, Lucknow, Uttar Pradesh, India.
authors.forename: Rahul Janak
authors.initials: RJ
authors.lastname: Sinha
authors.affiliation: Department of Urology, King George's Medical University, Lucknow, Uttar Pradesh, India.
authors.forename: Ved
authors.initials: V
authors.lastname: Bhaskar
authors.affiliation: Department of Obs & Gyn, King George's Medical University, Lucknow, Uttar Pradesh, India.
authors.forename: Seema
authors.initials: S
authors.lastname: Mehrotra
authors.affiliation: Department of Urology, King George's Medical University, Lucknow, Uttar Pradesh, India.
authors.forename: Vishwajeet
authors.initials: V
authors.lastname: Singh
mesh_terms: D058489:46, XX Disorders of Sex Development / Q000175:diagnosis; D000293:Adolescent; D013734:Androgen-Insensitivity Syndrome / Q000175:diagnosis / Q000601:surgery*; D012809:Colon, Sigmoid / Q000601:surgery; D000013:Congenital Abnormalities / Q000175:diagnosis / Q000235:genetics / Q000601:surgery*; D003937:Diagnosis, Differential; D005260:Female; D006801:Humans; D008297:Male; D009095:Mullerian Ducts / Q000002:abnormalities; D019651:Plastic Surgery Procedures / Q000379:methods*; D019738:Surgically-Created Structures; D014621:Vagina / Q000002:abnormalities* / Q000601:surgery*