title: [Imaging and audiology analysis of the congenital inner ear malformations].
abstract: OBJECTIVE
  To investigate imaging and audiology features of temporal bone and analyze the classification and prevalence of inner ear abnormalities in children with sensorineural hearing loss.
  
  
  METHODS
  Children who were diagnosed with sensorineural hearing loss were examined by high resolution CT and the inner ear fluid of MRI. And each chart was retrospectively reviewed to determine the imaging and audiology features.
  
  
  RESULTS
  There were 125 patients(232 ears) found with inner ear malformation in 590 children with SNHL. About 21.71% of the inner ear malformation occurred in severe and profound hearing loss ears, and 12.85% occurred in r moderate hearing loss ears. The inner ear malformation rate in normal hearing ears were 13.59%.
  
  
  CONCLUSIONS
  CT and MRI examinations of temporal bone are important diagnostic tools to indentify inner ear malformations. Inner ear malformations are almost bilateral and hearing loss are profoud. Cochleo-vestibular malformations and large vestibular aqueduct are the 2 most frequent deformities. Among the children with SNHL, deformity rate in the severe and profound hearing loss ears is higher than that in moderate hearing loss ear. Inner ear malformations can exist in people with normal hearing.
authors.forename: Bao
authors.initials: B
authors.lastname: Zhou
authors.forename: Shaolian
authors.initials: S
authors.lastname: Lin
authors.forename: Youhui
authors.initials: Y
authors.lastname: Lin
authors.forename: Zheming
authors.initials: Z
authors.lastname: Fang
authors.forename: Shengnan
authors.initials: S
authors.lastname: Ye
authors.forename: Rong
authors.initials: R
authors.lastname: Zhang
mesh_terms: D001298:Audiology; D002648:Child; D007758:Ear, Inner / Q000002:abnormalities*; D006319:Hearing Loss, Sensorineural / Q000151:congenital* / Q000473:pathology*; D006801:Humans; D008279:Magnetic Resonance Imaging; D015995:Prevalence; D012189:Retrospective Studies; D013701:Temporal Bone; D014057:Tomography, X-Ray Computed; D014723:Vestibular Aqueduct / Q000002:abnormalities