title: Management Strategies in Rosai-Dorfman Disease: To Do or Not To Do.
abstract: Rosai-Dorfman disease or sinus histiocytosis with massive lymphadenopathy is an extremely rare non-Langerhans cell histiocytosis. Orbital involvement is even rarer and may be accompanied by lymph node involvement. Treatment options range from systemic steroids and immunosuppressants to radiation and debulking. We present a rare case of bilateral orbital sinus histiocytosis with massive lymphadenopathy with cervical and circumaortic lymphadenopathy.
authors.affiliation: Department of Orbit, Oculoplasty, Reconstructive and Aesthetic Services, Medical Research Foundation, Chennai, Tamil Nadu, India.
authors.forename: Neha
authors.initials: N
authors.lastname: Shrirao
authors.forename: Aditya
authors.initials: A
authors.lastname: Sethi
authors.forename: Bipasha
authors.initials: B
authors.lastname: Mukherjee
mesh_terms: D002648:Child; D015618:Histiocytosis, Sinus / Q000209:etiology / Q000628:therapy*; D006801:Humans; D000072281:Lymphadenopathy / Q000209:etiology / Q000628:therapy; D008297:Male; D009916:Orbital Diseases / Q000209:etiology / Q000628:therapy*