title: Satisfaction of Children with Auditory Neuropathy and Cochlear Implant.
abstract: OBJECTIVE
  In auditory neuropathy (AN) a dyssynchrony in the nerve conduction of the auditory nerve fibers is observed. Typically, patients with AN exhibit moderate to profound sensorineural hearing loss, and treatment using cochlear implants (CIs) or hearing aids should be performed as early as possible for a better hearing rehabilitation. The aim of this study is to evaluate the satisfaction level of patients with AN spectrum disorder treated using CIs. The Satisfaction with Amplification in Daily Life questionnaire was selected to evaluate 10 patients with AN treated using CIs.
  
  
  METHODS
  Clinical study of patients with AN spectrum disorder submitted to CI. A retrospective data analysis, genetic and clinical evaluation in a tertiary referral center was done.
  
  
  RESULTS
  The means of the subscales for positive effects, services and costs, negative factors, and personal image were 6.15, 4.6, 3.26, and 3.33, respectively.
  
  
  CONCLUSIONS
  Patients with AN treated using CIs consider themselves satisfied.
authors.affiliation: Department of Ear Nose Throat, Head and Neck Surgery, Campinas University, Campinas, São Paulo, Brazil. guimachadocarvalho@gmail.com.
authors.forename: Guilherme Machado
authors.initials: GM
authors.lastname: de Carvalho
authors.forename: Thiago M
authors.initials: TM
authors.lastname: Zago
authors.forename: Priscila Z
authors.initials: PZ
authors.lastname: Ramos
authors.forename: Arthur M
authors.initials: AM
authors.lastname: Castilho
authors.forename: Alexandre C
authors.initials: AC
authors.lastname: Guimarães
authors.forename: Edi L
authors.initials: EL
authors.lastname: Sartorato
mesh_terms: D000203:Activities of Daily Living; D002648:Child; D002675:Child, Preschool; D003054:Cochlear Implants; D000072259:Connexin 26; D017630:Connexins / Q000235:genetics; D005260:Female; D006313:Hearing Loss, Central / Q000235:genetics / Q000503:physiopathology / Q000601:surgery*; D006801:Humans; D008297:Male; D009154:Mutation; D017060:Patient Satisfaction; D012189:Retrospective Studies; D011795:Surveys and Questionnaires
chemical_list: D017630:Connexins; D000072259:Connexin 26