title: Staged Single Ventricle Palliation and Homozygous Sickle Cell Disease.
abstract: Hypoxemia is a well-known trigger for precipitating a sickling crisis in patients with sickle cell disease. Patients undergoing staged single ventricle palliation have hypoxemia during the initial stages of the Fontan pathway. The successful completion of staged single ventricle palliation in a child with a combination of homozygous sickle cell disease and a single ventricle physiology that tolerate prolonged hypoxemia during earlier stages of Fontan pathway is described.
authors.affiliation: Department of Cardiac Anesthesia, National Heart Center, Royal Hospital, Muscat, Oman.
authors.forename: Madan Mohan
authors.initials: MM
authors.lastname: Maddali
authors.affiliation: Department of Cardiac Anesthesia, National Heart Center, Royal Hospital, Muscat, Oman.
authors.forename: Minakshi Sandip
authors.initials: MS
authors.lastname: Junghare
authors.affiliation: Department of Cardiac Anesthesia, National Heart Center, Royal Hospital, Muscat, Oman.
authors.forename: Arora Ram
authors.initials: AR
authors.lastname: Nishant
authors.affiliation: Department of Cardiothoracic Surgery, National Heart Center, Royal Hospital, Muscat, Oman.
authors.forename: Pranav Subbaraya
authors.initials: PS
authors.lastname: Kandachar
authors.affiliation: Department of Cardiothoracic Surgery, National Heart Center, Royal Hospital, Muscat, Oman.
authors.forename: Johan
authors.initials: J
authors.lastname: Valliattu
mesh_terms: D000755:Anemia, Sickle Cell / Q000150:complications*; D002648:Child; D004452:Echocardiography; D005260:Female; D018729:Fontan Procedure / Q000379:methods; D006352:Heart Ventricles / Q000002:abnormalities* / Q000601:surgery; D006801:Humans; D000860:Hypoxia; D007431:Intraoperative Complications; D010166:Palliative Care; D018785:Tricuspid Atresia / Q000150:complications / Q000000981:diagnostic imaging / Q000601:surgery