title: Adult Presentation of Dyke-Davidoff-Masson Syndrome: A Case Report.
abstract: Dyke-Davidoff-Masson syndrome (DDMS) is a rare disease which is clinically characterized by hemiparesis, seizures, facial asymmetry, and mental retardation. The classical radiological findings are cerebral hemiatrophy, calvarial thickening, and hyperpneumatization of the frontal sinuses. This disease is a rare entity, and it mainly presents in childhood. Adult presentation of DDMS is unusual and has been rarely reported in the medical literature.
  
  
  CONCLUSIONS
  DDMS is a rare disease of childhood. However, it should be kept in mind as a diagnostic possibility in an adult who presents with a long duration of progressive hemiparesis with seizures and mental retardation. Cerebral hemiatrophy, calvarial thickening, and hyperpneumatization of the frontal sinuses are diagnostic for this illness on brain imaging.
authors.affiliation: Department of Neurology, Bangur Institute of Neurosciences, IPGMER, Kolkata, India.
authors.forename: Ujjawal
authors.initials: U
authors.lastname: Roy
authors.affiliation: King George's Medical University, Lucknow, India.
authors.forename: Ajay
authors.initials: A
authors.lastname: Panwar
authors.affiliation: Department of Neurology, Bangur Institute of Neurosciences, IPGMER, Kolkata, India.
authors.forename: Adreesh
authors.initials: A
authors.lastname: Mukherjee
authors.affiliation: Department of Neurology, Bangur Institute of Neurosciences, IPGMER, Kolkata, India.
authors.forename: Debsadhan
authors.initials: D
authors.lastname: Biswas
keywords: Calvarial thickening; Cerebral hemiatrophy; Dyke-Davidoff-Masson syndrome