title: [Clear cell sarcoma of kidney in children].
abstract: Clear cell sarcoma of the kidney (CCSK) is a rare tumor that is diagnosed most often in children between 2- and 4-years-old of age. Usually, patients with CCSK are treated in international study for intrarenal tumors, preferentially Wilms tumor, according to bad histopronostic group. The purpose of this paper is to review the most important features in 2015 about epidemiology, radiology, anatomopathology and genetic of CCSK, and above all a synthesis about successive treatment strategies with their results. Second most common pediatric renal tumor in children less than 5-years-old, its prognosis has improved dramatically in recent years with the use of anthracyclines.
authors.affiliation: Centre Oscar-Lambret, unité d'oncologie pédiatrique, 3, rue Frederic-Combemale, 59000 Lille, France. Electronic address: h-sudour@o-lambret.fr.
authors.forename: Hélène
authors.initials: H
authors.lastname: Sudour-Bonnange
authors.affiliation: Hôpital Femme-Mère-Enfant, département de pathologie, 69677 Bron, France; Université Claude-Bernard, Lyon 1, France.
authors.forename: Frédérique
authors.initials: F
authors.lastname: Dijoud
authors.affiliation: CHRU de Nantes, service de chirurgie infantile, 44000 Nantes, France.
authors.forename: Marc-David
authors.initials: MD
authors.lastname: Leclair
authors.affiliation: Centre Oscar-Lambret, département d'imagerie, 59000 Lille, France.
authors.forename: Nathalie
authors.initials: N
authors.lastname: Rocourt
authors.affiliation: Centre Léon-Bérard, institut d'hématologie et d'oncologie pédiatrique, 69008 Lyon, France.
authors.forename: Christophe
authors.initials: C
authors.lastname: Bergeron
mesh_terms: D018943:Anthracyclines / Q000627:therapeutic use; D000970:Antineoplastic Agents / Q000009:adverse effects / Q000627:therapeutic use; D001706:Biopsy / Q000379:methods; D002675:Child, Preschool; D006801:Humans; D007223:Infant; D007680:Kidney Neoplasms / Q000175:diagnosis / Q000453:epidemiology / Q000473:pathology / Q000628:therapy; D009364:Neoplasm Recurrence, Local / Q000175:diagnosis; D009392:Nephrectomy / Q000009:adverse effects; D011832:Radiation Injuries / Q000150:complications; D011879:Radiotherapy Dosage; D035583:Rare Diseases / Q000175:diagnosis / Q000453:epidemiology / Q000473:pathology / Q000628:therapy; D018227:Sarcoma, Clear Cell / Q000175:diagnosis / Q000453:epidemiology / Q000473:pathology / Q000628:therapy
chemical_list: D018943:Anthracyclines; D000970:Antineoplastic Agents
keywords: Anthracycline; Children; Clear cell sarcoma of kidney; Enfant; Renal tumor; Sarcomes cellules claires; Tumeurs rénales