title: Catecholaminergic Polymorphic Ventricular Tachycardia in Pregnancy.
abstract: BACKGROUND
  Catecholaminergic polymorphic ventricular tachycardia is a genetic disorder in which ventricular tachycardia occurs in the absence of structural heart disease or a prolonged QT interval. If untreated, there is a high incidence of sudden cardiac death. Management of this cardiac condition during pregnancy merits a multidisciplinary approach.
  
  
  METHODS
  A nulliparous woman with catecholaminergic polymorphic ventricular tachycardia presented at 15 weeks of gestation. Her care involved a multidisciplinary team including cardiology, maternal-fetal medicine, obstetric nursing, cardiac nursing, and anesthesia. A simulation scenario was designed to prepare for cardiac events during labor. A term intrapartum cesarean delivery was performed for fetal indications.
  
  
  CONCLUSIONS
  A multidisciplinary approach to the antepartum, intrapartum, and postpartum care of women with catecholaminergic polymorphic ventricular tachycardia is critical to a team-based successful pregnancy outcome.
authors.affiliation: Department of Obstetrics and Gynecology, the Division of Maternal-Fetal Medicine, Department of Obstetrics and Gynecology, the Division of Cardiology, Department of Medicine, and the Department of Anesthesia, Lehigh Valley Health Network, Allentown, Pennsylvania.
authors.forename: Matthew P
authors.initials: MP
authors.lastname: Romagano
authors.forename: Joanne N
authors.initials: JN
authors.lastname: Quiñones
authors.forename: Amy
authors.initials: A
authors.lastname: Ahnert
authors.forename: Rafael
authors.initials: R
authors.lastname: Martinez
authors.forename: John C
authors.initials: JC
authors.lastname: Smulian
mesh_terms: D000328:Adult; D002585:Cesarean Section; D005260:Female; D006801:Humans; D010348:Patient Care Team; D011247:Pregnancy; D011249:Pregnancy Complications, Cardiovascular / Q000209:etiology*; D011256:Pregnancy Outcome; D017180:Tachycardia, Ventricular / Q000150:complications*; D000098850:Polymorphic Catecholaminergic Ventricular Tachycardia