title: Intimomedial mucoid degeneration causing aortic and renal artery aneurysms in a young adult.
abstract: Intimomedial mucoid degeneration (IMMD) is characterised by aneurysm formation following mucin deposition in the intima and media, with elastic tissue degeneration of the arterial wall. We present a case of a young adult who developed a diffusely aneurysmal aorta and its major branches, which was histopathologically confirmed as intimomedial mucoid degeneration, and a review of the literature. This case report attempts to raise the awareness of the reader to this rare cause of aortic aneurysm and to the bleeding diathesis associated with IMMD that may complicate surgery.
authors.affiliation: Department of Medicine, Groote Schuur Hospital and University of Cape Town, South Africa. charleviljoen@gmail.com.
authors.forename: Charle
authors.initials: C
authors.lastname: Viljoen
authors.affiliation: Department of Medicine, Groote Schuur Hospital and University of Cape Town, South Africa.
authors.forename: Patryk
authors.initials: P
authors.lastname: Szymanski
authors.affiliation: Division of Anatomical Pathology, National Health Laboratory Service, Groote Schuur Hospital and University of Cape Town, South Africa.
authors.forename: Naeem
authors.initials: N
authors.lastname: Osman
authors.affiliation: Division of Radiology, Groote Schuur Hospital and University of Cape Town, South Africa.
authors.forename: Kristin Lorenc
authors.initials: KL
authors.lastname: Henning
authors.affiliation: Division of Radiology, Groote Schuur Hospital and University of Cape Town, South Africa.
authors.forename: Paul
authors.initials: P
authors.lastname: Scholtz
authors.affiliation: Division of Nephrology and Hypertension, Groote Schuur Hospital and University of Cape Town, South Africa.
authors.forename: Brian
authors.initials: B
authors.lastname: Rayner
authors.affiliation: Division of Vascular Surgery, Groote Schuur Hospital and University of Cape Town.
authors.forename: Nadraj
authors.initials: N
authors.lastname: Naidoo
mesh_terms: D000293:Adolescent; D001011:Aorta / Q000503:physiopathology / Q000601:surgery*; D001014:Aortic Aneurysm / Q000175:diagnosis / Q000473:pathology* / Q000601:surgery*; D006801:Humans; D008297:Male; D012077:Renal Artery / Q000473:pathology / Q000503:physiopathology / Q000601:surgery*; D016896:Treatment Outcome; D017539:Tunica Intima / Q000473:pathology* / Q000503:physiopathology; D017540:Tunica Media