title: Epithelioid Angiomyolipoma in a Pediatric Patient: Case Report and Review of Literature.
abstract: We report a case of a 17-year-old girl with tuberous sclerosis complex who underwent partial nephrectomy for a newly discovered 7.5-cm renal mass subsequently determined to be an epithelioid angiomyolipoma, a rare variant of angiomyolipoma that can be confused clinically, radiographically, and pathologically for renal cell carcinoma. Proper diagnosis and treatment are critical, especially in the pediatric patient. This case report and review of literature serve at increasing the awareness of this renal tumor, with its somewhat unpredictable outcome, reviewing the pertinent literature on the topic of epithelioid angiomyolipoma in the clinical setting of tuberous sclerosis complex.
authors.affiliation: Division of Urology, Department of Surgery, Washington University School of Medicine, Saint Louis, MO, USA.
authors.forename: Michael H
authors.initials: MH
authors.lastname: Johnson
authors.affiliation: Division of Urology, Department of Surgery, Washington University School of Medicine, Saint Louis, MO, USA.
authors.forename: Joseph B
authors.initials: JB
authors.lastname: Song
authors.affiliation: Department of Pathology Washington University School of Medicine, Saint Louis, MO, USA.
authors.forename: Louis P
authors.initials: LP
authors.lastname: Dehner
authors.affiliation: Division of Urology, Department of Surgery, Washington University School of Medicine, Saint Louis, MO, USA.
authors.forename: Robert Sherburne
authors.initials: RS
authors.lastname: Figenshau
keywords: Angiomyolipoma; Epithelioid angiomyolipoma; Kidney; Tuberous sclerosis complex