title: Lung clearance index response in patients with CF with class III CFTR mutations.
authors.affiliation: Division of Respiratory Medicine, Department of Pediatrics, Toronto, Ontario, Canada Physiology & Experimental Medicine, The Research Institute, The Hospital for Sick Children, Toronto, Ontario, Canada.
authors.forename: Mica
authors.initials: M
authors.lastname: Kane
authors.affiliation: Physiology & Experimental Medicine, The Research Institute, The Hospital for Sick Children, Toronto, Ontario, Canada Division of Gastroenterology and Nutrition, Department of Pediatrics, Toronto, Ontario, Canada Department of Pediatrics, University of Toronto, Ontario, Canada.
authors.forename: Tanja
authors.initials: T
authors.lastname: Gonska
authors.affiliation: Division of Respiratory Medicine, Department of Pediatrics, Toronto, Ontario, Canada Physiology & Experimental Medicine, The Research Institute, The Hospital for Sick Children, Toronto, Ontario, Canada.
authors.forename: Renee
authors.initials: R
authors.lastname: Jensen
authors.affiliation: Division of Respiratory Medicine, Department of Pediatrics, Toronto, Ontario, Canada Physiology & Experimental Medicine, The Research Institute, The Hospital for Sick Children, Toronto, Ontario, Canada Division of Gastroenterology and Nutrition, Department of Pediatrics, Toronto, Ontario, Canada.
authors.forename: Julie
authors.initials: J
authors.lastname: Avolio
authors.affiliation: Division of Respiratory Medicine, Department of Pediatrics, Toronto, Ontario, Canada Physiology & Experimental Medicine, The Research Institute, The Hospital for Sick Children, Toronto, Ontario, Canada.
authors.forename: Michelle
authors.initials: M
authors.lastname: Klingel
authors.affiliation: Division of Respiratory Medicine, Department of Pediatrics, Toronto, Ontario, Canada Physiology & Experimental Medicine, The Research Institute, The Hospital for Sick Children, Toronto, Ontario, Canada Institute of Health Policy, Management and Evaluation, University of Toronto, Ontario, Canada.
authors.forename: Sanja
authors.identifier: http://orcid.org/0000-0001-7931-8051
authors.initials: S
authors.lastname: Stanojevic
authors.affiliation: Division of Respiratory Medicine, Department of Pediatrics, Toronto, Ontario, Canada Physiology & Experimental Medicine, The Research Institute, The Hospital for Sick Children, Toronto, Ontario, Canada Department of Pediatrics, University of Toronto, Ontario, Canada.
authors.forename: Felix
authors.identifier: http://orcid.org/0000-0003-4057-6592
authors.initials: F
authors.lastname: Ratjen
mesh_terms: D000328:Adult; D000483:Alleles; D000627:Aminophenols / Q000627:therapeutic use*; D003550:Cystic Fibrosis / Q000175:diagnosis / Q000188:drug therapy* / Q000235:genetics*; D019005:Cystic Fibrosis Transmembrane Conductance Regulator / Q000187:drug effects* / Q000235:genetics; D005541:Forced Expiratory Volume / Q000187:drug effects; D006801:Humans; D008450:Maximal Midexpiratory Flow Rate; D009154:Mutation; D015363:Quinolones / Q000627:therapeutic use*; D012462:Saline Solution, Hypertonic / Q000627:therapeutic use; D012720:Severity of Illness Index; D013147:Spirometry; D016896:Treatment Outcome
chemical_list: D000627:Aminophenols; D015363:Quinolones; D012462:Saline Solution, Hypertonic; D019005:Cystic Fibrosis Transmembrane Conductance Regulator; C545203:ivacaftor
keywords: Cystic Fibrosis