title: [A nasal congenital malformation not published in the literature: About 5 cases].
abstract: OBJECTIVE
  Five cases of the same congenital malformation of the nose, affecting the nasal dorsum and the supra-tip, were supported in our university plastic surgery center. This malformation has not been described in the literature known to the authors. The aim of this study is to analyze this nasal deformity.
  
  
  METHODS
  Five children presented this congenital deformity between 1994 and 2014. The patients were examined and the malformation precisely described. Genetic and histological examinations were carried on. The diagnosis and treatment of this pathology were discussed.
  
  
  RESULTS
  This malformation associated 4 anomalies: hypertrophy of soft tissue of the dorsum located in the middle third of the nasal bridge, deformed alar cartilages turned back downward and outside, advanced support default and median skin brand similar to a scar. These patients showed no other abnormalities of the midline or respiratory disorders. No genetic disorder was found for these five patients, and no histological arguments were found. Three patients were operated, one until adulthood with a satisfying cosmetic result.
  
  
  CONCLUSIONS
  Bibliographic research has not allowed us to make an accurate diagnosis of this malformation that appears to be non-syndromic and to have a genetic origin. Our therapeutic approach became more clear and it now seems legitimate to propose early excision of fat mass to prevent alar deformations, associated with a cortico-cancellous graft, which in our experience grows with age, to support the tip.
authors.affiliation: Hôpital de la Conception, 147, boulevard Baille, 13005 Marseille, France. Electronic address: colson.t.r@gmail.com.
authors.forename: T R
authors.initials: TR
authors.lastname: Colson
authors.affiliation: Hôpital de la Conception, 147, boulevard Baille, 13005 Marseille, France. Electronic address: baptiste.bertrand@gmail.com.
authors.forename: B
authors.initials: B
authors.lastname: Bertrand
authors.affiliation: Hôpital de la Timone, 264, rue Saint-Pierre, 13385 Marseille, France. Electronic address: nathalie.degardin@gmail.com.
authors.forename: N
authors.initials: N
authors.lastname: Degardin
authors.affiliation: Hôpital de la Conception, 147, boulevard Baille, 13005 Marseille, France. Electronic address: jacques.bardot@ap-hm.fr.
authors.forename: J
authors.initials: J
authors.lastname: Bardot
authors.affiliation: Hôpital de la Conception, 147, boulevard Baille, 13005 Marseille, France. Electronic address: dominique.casanova@ap-hm.fr.
authors.forename: D
authors.initials: D
authors.lastname: Casanova
mesh_terms: D002648:Child; D005260:Female; D006785:Hospitals, University; D006801:Humans; D008297:Male; D009666:Nose / Q000002:abnormalities* / Q000000981:diagnostic imaging / Q000601:surgery*; D017060:Patient Satisfaction; D019651:Plastic Surgery Procedures / Q000379:methods; D012189:Retrospective Studies; D012225:Rhinoplasty / Q000379:methods; D013524:Surgical Flaps; D016896:Treatment Outcome
keywords: Congenital; Congénital; Deformity; Malformation; Nez; Nose; Rhinoplastie; Rhinoplasty