title: Pathological fracture dislocation of the acetabulum in a patient with neurofibromatosis-1.
abstract: Skeletal neurofibromatosis (NF) commonly manifests as scoliosis and tibial dysplasias. NF affecting the pelvic girdle is extremely rare. Pathological fracture of the acetabulum leading to anterior hip dislocation in a patient with NF-1 has never been reported in the literature. The paper presents the clinical symptomatology, the course of management and the successful outcome of such a rare case of NF-1. Histopathological and immunohistochemistry studies showing abundant spindle cells, which are S-100 positive and of neural origin are the classical hallmarks of neurofibromatous lesions. Tumor resection and iliofemoral arthrodesis can be considered as a valid option in young patients with pathological fracture dislocation of the acetabulum.
authors.affiliation: Department of Orthopaedics, Post Graduate Institute of Medical Education and Research, Chandigarh, India.
authors.forename: Balaji
authors.initials: B
authors.lastname: Saibaba
authors.affiliation: Department of Orthopaedics, Post Graduate Institute of Medical Education and Research, Chandigarh, India.
authors.forename: Ramesh Kumar
authors.initials: RK
authors.lastname: Sen
authors.affiliation: Department of Orthopaedics, Post Graduate Institute of Medical Education and Research, Chandigarh, India.
authors.forename: Manish
authors.initials: M
authors.lastname: Sharma
authors.affiliation: Department of Pathology, Post Graduate Institute of Medical Education and Research, Chandigarh, India.
authors.forename: Uma
authors.initials: U
authors.lastname: Nahar
keywords: Acetabulum; bone; fracture; neurofibromatosis; pathological; pathological fracture