title: Discontinuous Pulmonary Artery.
abstract: We describe the diagnosis and surgical repair of a five-month-old infant with a congenital discontinuous right pulmonary artery. Initial echocardiogram failed to show the right pulmonary artery and revealed systemic left pulmonary artery pressure based on the tricuspid regurgitation jet. Computed tomographic angiography confirmed the diagnosis of discontinuous right pulmonary artery. The right pulmonary artery appeared essentially normal in size, and there were no significant aortopulmonary collateral arteries. Using cardiopulmonary bypass and aortic transection, we created an anastomosis between the right and the main pulmonary arteries augmented anteriorly by a pericardial patch. Postoperative lung perfusion scan demonstrated balanced pulmonary blood flow to the lungs. Pulmonary hypertension resolved over three weeks in the postoperative period, an expected outcome in this age-group.
authors.affiliation: 1 Divisions of Cardiovascular-Thoracic Surgery, Ann & Robert H. Lurie Children's Hospital of Chicago, Chicago, IL, USA.|2 Department of Surgery, Feinberg School of Medicine, Northwestern University, Chicago, IL, USA.
authors.forename: Osama
authors.initials: O
authors.lastname: Eltayeb
authors.affiliation: 1 Divisions of Cardiovascular-Thoracic Surgery, Ann & Robert H. Lurie Children's Hospital of Chicago, Chicago, IL, USA.|2 Department of Surgery, Feinberg School of Medicine, Northwestern University, Chicago, IL, USA.
authors.forename: Michael C
authors.initials: MC
authors.lastname: Mongé
authors.affiliation: 3 Division of Medical Imaging, Ann & Robert H. Lurie Children's Hospital of Chicago, Chicago, IL, USA.
authors.forename: Andrada R
authors.initials: AR
authors.lastname: Popescu
authors.affiliation: 1 Divisions of Cardiovascular-Thoracic Surgery, Ann & Robert H. Lurie Children's Hospital of Chicago, Chicago, IL, USA.
authors.forename: Anne E
authors.initials: AE
authors.lastname: Sarwark
authors.affiliation: 4 Division of Cardiology, Ann & Robert H. Lurie Children's Hospital of Chicago, Chicago, IL, USA.
authors.forename: Tyler
authors.initials: T
authors.lastname: Harris
authors.affiliation: 1 Divisions of Cardiovascular-Thoracic Surgery, Ann & Robert H. Lurie Children's Hospital of Chicago, Chicago, IL, USA.|2 Department of Surgery, Feinberg School of Medicine, Northwestern University, Chicago, IL, USA.
authors.forename: Carl L
authors.initials: CL
authors.lastname: Backer
mesh_terms: D006348:Cardiac Surgical Procedures / Q000379:methods*; D000072226:Computed Tomography Angiography; D004452:Echocardiography; D006801:Humans; D007223:Infant; D008297:Male; D011651:Pulmonary Artery / Q000002:abnormalities* / Q000000981:diagnostic imaging / Q000601:surgery; D018633:Pulmonary Atresia / Q000175:diagnosis / Q000601:surgery*
keywords: congenital heart disease; congenital heart surgery; infant; pathophysiology; pediatric; pulmonary arteries; pulmonary atresia with intact ventricular septum