title: Presentation and management of pulmonary sequestration with total visceral inflow and outflow.
abstract: Two of the most common types of congenital thoracic malformations are congenital pulmonary airway malformations (CPAMs) and bronchopulmonary sequestrations (BPS). Here we present the first known case of a hybrid lesion, with coexisting features of an extralobar sequestration (ELS) and CPAM type 2, with arterial inflow from the celiac trunk and venous outflow to the portal vein. The clinical presentation, investigative imaging and timing of surgery are discussed.
authors.affiliation: Division of Pediatric Surgery, Department of Surgery, Emory University School of Medicine, Children's Healthcare of Atlanta, 1405 Clifton Road NE, 3rd Floor Surgical Suite, Atlanta, GA, 30322, USA.
authors.forename: Christopher L
authors.initials: CL
authors.lastname: Sudduth
authors.affiliation: Division of Pediatric Surgery, Department of Surgery, Emory University School of Medicine, Children's Healthcare of Atlanta, 1405 Clifton Road NE, 3rd Floor Surgical Suite, Atlanta, GA, 30322, USA.
authors.forename: Sarah J
authors.initials: SJ
authors.lastname: Hill
authors.affiliation: Division of Pediatric Surgery, Department of Surgery, Emory University School of Medicine, Children's Healthcare of Atlanta, 1405 Clifton Road NE, 3rd Floor Surgical Suite, Atlanta, GA, 30322, USA. mehulvraval@emory.edu.
authors.forename: Mehul V
authors.initials: MV
authors.lastname: Raval
mesh_terms: D000015:Abnormalities, Multiple; D001998:Bronchopulmonary Sequestration / Q000175:diagnosis* / Q000601:surgery; D006801:Humans; D007223:Infant; D008168:Lung / Q000002:abnormalities* / Q000000981:diagnostic imaging; D008297:Male; D011169:Portal Vein / Q000002:abnormalities* / Q000000981:diagnostic imaging; D020775:Thoracic Surgery, Video-Assisted / Q000379:methods*; D014057:Tomography, X-Ray Computed
keywords: Case report; Congenital pulmonary airway malformation; Congenital thoracic malformation; Failure to thrive; Pulmonary sequestration; Surgical management; Vascular supply