title: Nutritional intervention with hypocaloric diet for weight control in children and adolescents with Prader-Willi Syndrome.
abstract: Prader-Willi Syndrome (PWS) is a genetic disorder caused by the lack of expression of paternal alleles in the proximal region of the long arm of chromosome 15. Low inhibitory control and hyperphagia are two of the most severe neurobehavioral symptoms of the syndrome. The aim of the present study was to assess the efficiency of nutritional training program with the use hypocaloric diet for weight control in a group of five children and adolescents with PWS. The intervention program consisted of 10 sessions for parents' orientation during 8months. Patients had their anthropometric measures assessed (weight, height and body mass index - BMI). The main results indicate weight maintenance, height increase, and BMI decrease after intervention. These results were considered indicators of the program's efficiency.
authors.affiliation: Programa de Pós-graduação em Distúrbios do Desenvolvimento, Centro de Ciências Biológicas e da Saúde, Universidade Presbiteriana Mackenzie, São Paulo, SP, Brazil.
authors.forename: Vivian Penner de
authors.initials: VP
authors.lastname: Lima
authors.affiliation: Programa de Pós-graduação em Distúrbios do Desenvolvimento, Centro de Ciências Biológicas e da Saúde, Universidade Presbiteriana Mackenzie, São Paulo, SP, Brazil; Programa de Pós-Graduação em Psicologia Clínica, Instituto de Psicologia, Universidade de São Paulo (USP), São Paulo, SP, Brazil. Electronic address: deisy.remerich@usp.br.
authors.forename: Deisy Ribas
authors.initials: DR
authors.lastname: Emerich
authors.affiliation: Programa de Pós-graduação em Distúrbios do Desenvolvimento, Centro de Ciências Biológicas e da Saúde, Universidade Presbiteriana Mackenzie, São Paulo, SP, Brazil.
authors.forename: Maria Luiza Guedes de
authors.initials: ML
authors.lastname: Mesquita
authors.affiliation: Curso de Graduação em Nutrição, Centro de Ciências Biológicas e da Saúde, Universidade Presbiteriana Mackenzie, São Paulo, SP, Brazil.
authors.forename: Ana Carolina Almada Colucci
authors.initials: AC
authors.lastname: Paternez
authors.affiliation: Programa de Pós-graduação em Distúrbios do Desenvolvimento, Centro de Ciências Biológicas e da Saúde, Universidade Presbiteriana Mackenzie, São Paulo, SP, Brazil.
authors.forename: Luiz Renato Rodrigues
authors.initials: LR
authors.lastname: Carreiro
authors.affiliation: Faculdade de Medicina de Ribeirão Preto, Universidade de São Paulo (FMRP-USP), Ribeirão Preto, SP, Brazil.
authors.forename: João Monteiro de
authors.initials: JM
authors.lastname: Pina Neto
authors.affiliation: Programa de Pós-graduação em Distúrbios do Desenvolvimento, Centro de Ciências Biológicas e da Saúde, Universidade Presbiteriana Mackenzie, São Paulo, SP, Brazil.
authors.forename: Maria Cristina Triguero Veloz
authors.initials: MC
authors.lastname: Teixeira
mesh_terms: D000293:Adolescent; D015992:Body Mass Index; D001835:Body Weight; D002648:Child; D004038:Diet, Reducing / Q000191:economics; D005247:Feeding Behavior; D005260:Female; D006801:Humans; D006963:Hyperphagia / Q000150:complications / Q000178:diet therapy / Q000517:prevention & control; D008297:Male; D009765:Obesity / Q000150:complications* / Q000178:diet therapy* / Q000517:prevention & control; D011218:Prader-Willi Syndrome / Q000150:complications*
keywords: Nutritional intervention; Obesity; Prader–Willi Syndrome