title: [Dandy-Walker variant: Case report].
abstract: BACKGROUND
  Dandy Walker variant is defined by a variable hypoplasia of the cerebellar vermix with or without posterior fossa increase and without tentorium elevation.
  
  
  OBJECTIVE
  describe the case of a rare disease and emphasise the need to clarify the aetiology of prenatal malformations, as well as its multidisciplinary management.
  
  
  METHODS
  A male patient, 8 years of age, with a history of Infantile Cerebral Palsy and epilepsy, who was admitted with a history of tonic-clonic seizures. He was admitted due to psycho-motor developmental delay. During his hospitalisation, he had multiple seizure episodes, controlled with anticonvulsants. A computerized tomography was performed, in which communication was observed between the cisterna magna and fourth ventricle (the latter increased in size). In addition, the cerebellar vermix showed a partial hypoplasia. All these findings were compatible with a variant of the Dandy Walker syndrome.
  
  
  CONCLUSIONS
  Dandy Walker variant may be asymptomatic and the images found may not indicate them as the cause of developmental disorders, due to its association with multiple syndromes and chromosomal abnormalities. Clinical presentation and prognosis depends on the related disorders, and a multidisciplinary approach is important, because the treatment depends on the symptoms presented.
authors.affiliation: Medicina General, Facultad de Ciencias Médicas, Universidad Nacional Autónoma de Honduras, Tegucigalpa, Honduras. Electronic address: jose.cueva2311@gmail.com.
authors.forename: José E
authors.initials: JE
authors.lastname: Cueva-Núñez
authors.affiliation: Medicina General, Facultad de Ciencias Médicas, Universidad Nacional Autónoma de Honduras, Tegucigalpa, Honduras.
authors.forename: Alejandra
authors.initials: A
authors.lastname: Lozano-Bustillo
authors.affiliation: Medicina General, Facultad de Ciencias Médicas, Universidad Nacional Autónoma de Honduras, Tegucigalpa, Honduras.
authors.forename: Merlyn S
authors.initials: MS
authors.lastname: Irias-Álvarez
authors.affiliation: Radiología e Imagen, Neurorradiología, Radiología Intervencionista, Departamento de Radiología, Hospital Escuela Universitario, Tegucigalpa, Honduras.
authors.forename: Raúl F
authors.initials: RF
authors.lastname: Vásquez-Montes
authors.affiliation: Neurología Pediátrica, Hospital Materno Infantil, Departamento de Fisiología, Facultad de Ciencias Médicas, Universidad Nacional Autónoma de Honduras, Tegucigalpa, Honduras.
authors.forename: Douglas M
authors.initials: DM
authors.lastname: Varela-González
mesh_terms: D000927:Anticonvulsants / Q000627:therapeutic use; D002648:Child; D003616:Dandy-Walker Syndrome / Q000000981:diagnostic imaging* / Q000503:physiopathology; D006801:Humans; D008297:Male; D011379:Prognosis; D012640:Seizures / Q000188:drug therapy; D014057:Tomography, X-Ray Computed
chemical_list: D000927:Anticonvulsants
keywords: Complejo Dandy Walker; Dandy Walker complex; Dandy-Walker variant; Hipoplasia cerebelosa parcial; Hipoplasia de vermis aislada; Isolated vermian hypoplasia; Partial cerebellar hypoplasia; Variante de Dandy Walker