title: Multiple keratocystic odontogenic tumors in nevoid basal cell carcinoma syndrome.
abstract: Keratocystic odontogenic tumor (KCOT) is of particular interest because its recurrence rate is high and its behavior is aggressive. Nevoid basal cell carcinoma syndrome (NBCCS), which is also known as Gorlin syndrome, is a hereditary condition characterized by a wide range of developmental abnormalities and with a predisposition to neoplasms. These multiple KCOTs have warranted an aggressive treatment at the earliest because of the damage and possible complications. Recurrence of these lesions is a characteristic feature that has to be considered while explaining the prognosis to the patient. Here, we report a case of a 14-year-old boy with clinical features of basal cell nevus syndrome and multiple KCOTs. In addition to the other common features, congenitally missing third molars in all the four quadrants is a feature which has not been previously reported in association with NBCCS in Indian patients.
authors.affiliation: Department of Oral and Maxillofacial Pathology and Microbiology, Dr. D. Y. Patil Dental College and Hospital, Navi Mumbai, Maharashtra, India.
authors.forename: Treville
authors.initials: T
authors.lastname: Pereira
authors.affiliation: Department of Oral and Maxillofacial Pathology and Microbiology, Dr. D. Y. Patil Dental College and Hospital, Navi Mumbai, Maharashtra, India.
authors.forename: Avinash
authors.initials: A
authors.lastname: Tamgadge
authors.affiliation: Department of Oral and Maxillofacial Pathology and Microbiology, Dr. D. Y. Patil Dental College and Hospital, Navi Mumbai, Maharashtra, India.
authors.forename: Swati
authors.initials: S
authors.lastname: Sapdhare
authors.affiliation: Department of Oral and Maxillofacial Pathology and Microbiology, Dr. D. Y. Patil Dental College and Hospital, Navi Mumbai, Maharashtra, India.
authors.forename: Ashwini
authors.initials: A
authors.lastname: Pujar
keywords: Gorlin–Goltz; keratocystic odontogenic tumor; neoplasm; nevoid basal cell carcinoma