title: Platypnea-Orthodeoxia Syndrome Two Decades after Definitive Surgical Repair of Pulmonary Atresia with Intact Ventricular Septum.
abstract: A 20-year-old female had undergone definitive surgical repair for pulmonary atresia with intact ventricular septum soon after birth. She was referred to our institution with the chief complaint of clubbing fingers. A thorough examination revealed platypnea-orthodeoxia syndrome due to an interatrial right-to-left shunt through a secundum atrial septal defect. Percutaneous closure with an Amplatzer Septal Occluder resulted in resolution of the syndrome.
authors.affiliation: Department of Pediatrics, Division of Pediatric Cardiology, Changhua Christian Children's Hospital, Changhua, Taiwan. ferdielee@yahoo.com.
authors.forename: Meng-Luen
authors.initials: ML
authors.lastname: Lee
authors.affiliation: Department of Surgery, Division of Cardiovascular Surgery, Changhua Christian Children's Hospital, Changhua, Taiwan.|Department of Surgery, Division of Cardiovascular Surgery, College of Medicine, National Taiwan University Hospital, Taipei, Taiwan.
authors.forename: Ing-Sh
authors.initials: IS
authors.lastname: Chiu
mesh_terms: D004417:Dyspnea / Q000175:diagnosis* / Q000209:etiology* / Q000601:surgery; D005260:Female; D006330:Heart Defects, Congenital / Q000150:complications / Q000601:surgery*; D006344:Heart Septal Defects, Atrial / Q000150:complications* / Q000175:diagnosis* / Q000601:surgery; D006801:Humans; D000860:Hypoxia; D018633:Pulmonary Atresia / Q000150:complications / Q000601:surgery*; D055989:Septal Occluder Device; D013577:Syndrome; D016896:Treatment Outcome
keywords: Amplatzer Septal Occluder; Clubbing fingers; platypnea-orthodeoxia syndrome; secundum atrial septal defect