title: Clinical Practice Guidelines From the Cystic Fibrosis Foundation for Preschoolers With Cystic Fibrosis.
abstract: Cystic fibrosis (CF) clinical care guidelines exist for the care of infants up to age 2 years and for individuals ≥6 years of age. An important gap exists for preschool children between the ages of 2 and 5 years. This period marks a time of growth and development that is critical to achieve optimal nutritional status and maintain lung health. Given that disease often progresses in a clinically silent manner, objective and sensitive tools that detect and track early disease are important in this age group. Several challenges exist that may impede the delivery of care for these children, including adherence to therapies. A multidisciplinary committee was convened by the CF Foundation to develop comprehensive evidence-based and consensus recommendations for the care of preschool children, ages 2 to 5 years, with CF. This document includes recommendations in the following areas: routine surveillance for pulmonary disease, therapeutics, and nutritional and gastrointestinal care.
authors.affiliation: Pediatric Pulmonology, University of Vermont Children's Hospital and Department of Pediatrics, University of Vermont College of Medicine, Burlington, Vermont; Thomas.Lahiri@uvmhealth.org.
authors.forename: Thomas
authors.initials: T
authors.lastname: Lahiri
authors.affiliation: The Dartmouth Institute for Health Policy and Clinical Practice, Lebanon, New Hampshire; Geisel School of Medicine at Dartmouth, Lebanon, New Hampshire;
authors.forename: Sarah E
authors.initials: SE
authors.lastname: Hempstead
authors.affiliation: Children's Respiratory and Critical Care Specialists and Children's Hospitals and Clinics of Minnesota, Minneapolis, Minnesota;
authors.forename: Cynthia
authors.initials: C
authors.lastname: Brady
authors.affiliation: Texas A&M Health Science Center, College Station, Texas;
authors.forename: Carolyn L
authors.initials: CL
authors.lastname: Cannon
authors.affiliation: Department of Pediatrics, University of North Carolina, Charlotte, North Carolina;
authors.forename: Kelli
authors.initials: K
authors.lastname: Clark
authors.affiliation: University of Oklahoma College of Pharmacy and School of Community Medicine, Tulsa, Oklahoma;
authors.forename: Michelle E
authors.initials: ME
authors.lastname: Condren
authors.affiliation: Geisel School of Medicine at Dartmouth, Lebanon, New Hampshire; Allergy and Pediatric Pulmonology, Dartmouth-Hitchcock Medical Center, Lebanon, New Hampshire;
authors.forename: Margaret F
authors.initials: MF
authors.lastname: Guill
authors.affiliation: Department of Radiology, Baylor College of Medicine and Department of Pediatric Radiology, Texas Children's Hospital, Houston, Texas;
authors.forename: R Paul
authors.initials: RP
authors.lastname: Guillerman
authors.affiliation: Cystic Fibrosis Center, Children's Hospital Colorado, Aurora, Colorado;
authors.forename: Christina G
authors.initials: CG
authors.lastname: Leone
authors.affiliation: Section of Pediatric Pulmonology, Allergy and Sleep Medicine, Department of Pediatrics, Riley Hospital for Children, Indiana University School of Medicine, Indianapolis, Indiana ;
authors.forename: Karen
authors.initials: K
authors.lastname: Maguiness
authors.affiliation: Armond V. Mascia, MD Cystic Fibrosis Center, Maria Fareri Children's Hospital at Westchester Medical Center, Valhalla, New York;
authors.forename: Lisa
authors.initials: L
authors.lastname: Monchil
authors.affiliation: Department of Pediatrics and Cincinnati Children's Research Foundation, University of Cincinnati College of Medicine and Division of Behavioral Medicine and Clinical Psychology, Cincinnati Children's Hospital, Cincinnati, Ohio;
authors.forename: Scott W
authors.initials: SW
authors.lastname: Powers
authors.affiliation: Division of Pulmonary Medicine, Seattle Children's Hospital and Department of Pediatrics, University of Washington School of Medicine, Seattle, Washington;
authors.forename: Margaret
authors.initials: M
authors.lastname: Rosenfeld
authors.affiliation: Pediatric Gastroenterology, Hepatology and Nutrition, University of Minnesota Masonic Children's Hospital, Minneapolis, Minnesota;
authors.forename: Sarah Jane
authors.initials: SJ
authors.lastname: Schwarzenberg
authors.affiliation: Department of Rehabilitation and Movement Sciences, University of Vermont College of Nursing and Health Sciences, Burlington, Vermont; and.
authors.forename: Connie L
authors.initials: CL
authors.lastname: Tompkins
authors.affiliation: Department of Pediatrics, University of Colorado School of Medicine, Aurora, Colorado.
authors.forename: Edith T
authors.initials: ET
authors.lastname: Zemanick
authors.affiliation: Section of Pediatric Pulmonology, Allergy and Sleep Medicine, Department of Pediatrics, Riley Hospital for Children, Indiana University School of Medicine, Indianapolis, Indiana ;
authors.forename: Stephanie D
authors.initials: SD
authors.lastname: Davis
mesh_terms: D002675:Child, Preschool; D003550:Cystic Fibrosis / Q000175:diagnosis* / Q000628:therapy*; D005260:Female; D005582:Foundations / Q000592:standards*; D006801:Humans; D008297:Male; D017410:Practice Guidelines as Topic / Q000592:standards*