title: Anesthetic considerations in a parturient with Freeman-Sheldon syndrome.
abstract: Freeman-Sheldon syndrome is a rare genetic disorder characterized by malformations of the face, oral cavity and musculoskeletal system. This case report describes the anesthetic management of a parturient with Freeman-Sheldon syndrome, kyphoscoliosis and a cardiac pacemaker for a cesarean delivery and tubal ligation. With a predicted difficult airway, our team decided to provide a combined spinal-epidural anesthetic. Problems encountered included difficult intravenous access, failure to identify the subarachnoid space and patient discomfort during surgery.
authors.affiliation: Department of Anesthesia and Perioperative Medicine, London Health Sciences Centre, London, Ontario, Canada. Electronic address: kfishe2@uwo.ca.
authors.forename: K
authors.initials: K
authors.lastname: Fisher
authors.affiliation: Department of Anesthesia and Perioperative Medicine, London Health Sciences Centre, London, Ontario, Canada.
authors.forename: F
authors.initials: F
authors.lastname: Qasem
authors.affiliation: Department of Anesthesia and Perioperative Medicine, London Health Sciences Centre, London, Ontario, Canada.
authors.forename: P
authors.initials: P
authors.lastname: Armstrong
authors.affiliation: Department of Anesthesia and Perioperative Medicine, London Health Sciences Centre, London, Ontario, Canada.
authors.forename: I
authors.initials: I
authors.lastname: McConachie
mesh_terms: D000328:Adult; D058109:Airway Management; D000773:Anesthesia, Obstetrical / Q000379:methods*; D000775:Anesthesia, Spinal / Q000379:methods*; D002585:Cesarean Section; D003394:Craniofacial Dysostosis / Q000150:complications*; D005260:Female; D006801:Humans; D008305:Malignant Hyperthermia / Q000209:etiology; D011247:Pregnancy; D011248:Pregnancy Complications
keywords: Anesthesia; Cesarean delivery; Combined spinal–epidural; Freeman–Sheldon syndrome