title: Cutaneous perivascular epithelioid cell tumors: A review on an infrequent neoplasm.
abstract: "Perivascular epithelioid cutaneous" cell tumors (PEComa) are a family of mesenchymal tumors with shared microscopic and immunohistochemical properties: They exhibit both smooth muscle cell and melanocytic differentiation. Non-neoplastic counterpart of PEComa's cells are unknown, as well as the relationship between extracutaneous PEComa and primary cutaneous ones. We will review the clinical setting, histopathologic features, chromosomal abnormalities, differential diagnosis and treatment options for cutaneous PEComa.
authors.affiliation: Mar Llamas-Velasco, Department of Dermatology, Hospital Universitario de La Princesa, 28006 Madrid, Spain.
authors.forename: Mar
authors.initials: M
authors.lastname: Llamas-Velasco
authors.affiliation: Mar Llamas-Velasco, Department of Dermatology, Hospital Universitario de La Princesa, 28006 Madrid, Spain.
authors.forename: Luis
authors.initials: L
authors.lastname: Requena
authors.affiliation: Mar Llamas-Velasco, Department of Dermatology, Hospital Universitario de La Princesa, 28006 Madrid, Spain.
authors.forename: Thomas
authors.initials: T
authors.lastname: Mentzel
keywords: Clear cell myomelanocytic tumor; Cutaneous perivascular epithelioid cell tumors; Perivascular epithelioid cell tumor; Skin