title: Siblings with Idiopathic Left Atrial Appendage Ostial Stenosis and Cor Triatriatum.
abstract: Isolated left atrial appendage (LAA) ostial stenosis is a very rare entity found coincidentally in adults by transesophageal echocardiography. A 3-month-old healthy infant was suspected as having cor triatriatum. His brother had a history of surgical treatment of cor triatriatum. A cardiac catheterization revealed a narrowed ostium of the LAA and confirmed the echocardiographic diagnosis of isolated LAA ostial stenosis. This is the first pediatric case of idiopathic LAA ostial stenosis. The siblings called our attention to the differential diagnosis and the etiopathogenesis between LAA ostial stenosis and cor triatriatum.
authors.affiliation: Department of Pediatric Cardiology, Hiroshima City Hiroshima Citizens Hospital, Hiroshima, Japan.|Department of Pediatrics, Yamaguchi University Graduate School of Medicine, Yamaguchi, Japan.
authors.forename: Seigo
authors.initials: S
authors.lastname: Okada
authors.affiliation: Department of Pediatric Cardiology, Hiroshima City Hiroshima Citizens Hospital, Hiroshima, Japan.
authors.forename: Yukiko
authors.initials: Y
authors.lastname: Ishiguchi
authors.affiliation: Department of Pediatric Cardiology, Hiroshima City Hiroshima Citizens Hospital, Hiroshima, Japan.
authors.forename: Yuji
authors.initials: Y
authors.lastname: Moritoh
authors.affiliation: Department of Pediatric Cardiology, Hiroshima City Hiroshima Citizens Hospital, Hiroshima, Japan.
authors.forename: Mayuko
authors.initials: M
authors.lastname: Shohi
authors.affiliation: Department of Pediatric Cardiology, Hiroshima City Hiroshima Citizens Hospital, Hiroshima, Japan.
authors.forename: Naomi
authors.initials: N
authors.lastname: Nakagawa
authors.affiliation: Department of Pediatric Cardiology, Hiroshima City Hiroshima Citizens Hospital, Hiroshima, Japan.
authors.forename: Kengo
authors.initials: K
authors.lastname: Okamoto
authors.affiliation: Department of Pediatric Cardiology, Hiroshima City Hiroshima Citizens Hospital, Hiroshima, Japan.
authors.forename: Masahiro
authors.initials: M
authors.lastname: Kamada
keywords: congenital heart disease; cor triatriatum; left atrial appendage function; left atrium; ostial stenosis