title: A Rare Coexistence of Bilateral Congenital Wilms Tumor with Ductal Plate Malformation at Autopsy.
abstract: Congenital Wilms tumor is a tumor of childhood. Here we present an unusual case of bilateral congenital Wilms tumor with associated ductal plate malformation. In addition, there was also associated oligohydramnios, pulmonary hypoplasia, and multiple skeletal anomalies in this index case. Although various syndromic associations of Wilms tumor are well described in the literature, an association of congenital Wilms tumor with ductal plate malformation, polysplenia, and skeletal malformations is not reported. We believe that this is the first reported case of such an association.
authors.affiliation: a Department of Pathology , Post Graduate Institute of Medical Education and Research , Chandigarh , India.
authors.forename: Suvradeep
authors.initials: S
authors.lastname: Mitra
authors.affiliation: a Department of Pathology , Post Graduate Institute of Medical Education and Research , Chandigarh , India.
authors.forename: Debajyoti
authors.initials: D
authors.lastname: Chatterjee
authors.affiliation: a Department of Pathology , Post Graduate Institute of Medical Education and Research , Chandigarh , India.
authors.forename: Kiran
authors.initials: K
authors.lastname: Gowda
authors.affiliation: b Department of Histopathology , Post Graduate Institute of Medical Education and Research , Chandigarh , India.
authors.forename: Ashim
authors.initials: A
authors.lastname: Das
mesh_terms: D001344:Autopsy; D005260:Female; D006801:Humans; D007231:Infant, Newborn; D007674:Kidney Diseases / Q000150:complications / Q000473:pathology; D008297:Male; D018482:Muscle, Skeletal / Q000473:pathology*; D011247:Pregnancy; D009396:Wilms Tumor / Q000150:complications / Q000175:diagnosis / Q000473:pathology*
keywords: Wilms tumor; autopsy; ductal plate malformation; pulmonary hypoplasia; skeletal malformations