title: Bimaxillary Osteotomy for Jaw Deformity With Facioscapulohumeral Muscular Dystrophy.
abstract: Facioscapulohumeral muscular dystrophy (FSHD) is a subtype of muscular dystrophies which reduces the muscle strength, especially the regions of scapular, shoulder, and upper arms, progressively. According to progressive muscle weakness in FSHD, postoperative stability of patient with FSHD after orthognathic surgery is not reliably acquired same as healthy subjects. A 32-year-old woman with FSHD underwent orthodontic and orthognathic surgical treatment due to jaw deformity. She has been followed up more than 3 years after surgery and acquired skeletal stability. This patient is the first report that showed long-term skeletal stability after orthognathic surgery in patient with FSHD. This patient report suggests that it is possible to apply orthognathic surgical treatment to patients with FSHD.
authors.affiliation: *Department of Regenerative Oral Surgery†Department of Orthodontics and Dentofacial Orthopedics, Nagasaki University Graduate School of Biomedical Sciences, Nagasaki, Japan.
authors.forename: Takako
authors.initials: T
authors.lastname: Kawasaki
authors.forename: Seigo
authors.initials: S
authors.lastname: Ohba
authors.forename: Yuji
authors.initials: Y
authors.lastname: Fujimura
authors.forename: Izumi
authors.initials: I
authors.lastname: Asahina
mesh_terms: D000328:Adult; D002508:Cephalometry; D005260:Female; D005500:Follow-Up Studies; D006801:Humans; D007569:Jaw Abnormalities / Q000601:surgery*; D008312:Malocclusion, Angle Class II / Q000175:diagnosis / Q000601:surgery; D008334:Mandible / Q000601:surgery; D008437:Maxilla / Q000002:abnormalities* / Q000601:surgery*; D020391:Muscular Dystrophy, Facioscapulohumeral / Q000175:diagnosis / Q000601:surgery*; D024343:Open Bite / Q000175:diagnosis / Q000601:surgery; D056948:Orthognathic Surgical Procedures / Q000379:methods*; D010027:Osteotomy / Q000379:methods*; D019340:Osteotomy, Le Fort / Q000379:methods; D019651:Plastic Surgery Procedures / Q000379:methods*