title: Cone Reconstruction of Atypical Ebstein Anomaly Associated with Right Ventricular Apical Hypoplasia.
abstract: Cone reconstruction for tricuspid valve repair has revolutionized the surgical treatment of Ebstein anomaly. We present the case of a 58-year-old woman with atypical Ebstein anomaly and right ventricular apical hypoplasia who was spared from palliative shunt physiology by our use of cone reconstruction. Compared with other techniques, cone reconstruction of the tricuspid valve more closely replicates normal valvular anatomy and function. This surgical procedure can be applied to many anatomic variations of Ebstein anomaly, as in our patient's apparently unique instance of atypical Ebstein anomaly with right ventricular apical hypoplasia.
authors.forename: Gemma
authors.initials: G
authors.lastname: Reddin
authors.forename: Joseph T
authors.initials: JT
authors.lastname: Poterucha
authors.forename: Joseph A
authors.initials: JA
authors.lastname: Dearani
authors.forename: Carole A
authors.initials: CA
authors.lastname: Warnes
authors.forename: Frank
authors.initials: F
authors.lastname: Cetta
mesh_terms: D000015:Abnormalities, Multiple; D006348:Cardiac Surgical Procedures / Q000379:methods*; D004437:Ebstein Anomaly / Q000175:diagnosis* / Q000601:surgery; D004452:Echocardiography; D005260:Female; D006330:Heart Defects, Congenital / Q000175:diagnosis* / Q000601:surgery; D006352:Heart Ventricles / Q000002:abnormalities* / Q000601:surgery; D006801:Humans; D019028:Magnetic Resonance Imaging, Cine; D008875:Middle Aged; D019651:Plastic Surgery Procedures / Q000379:methods*
keywords: Cardiac surgical techniques; Ebstein anomaly/surgery; heart defects, congenital/complications; heart ventricles/abnormalities; reconstructive surgical procedures; treatment outcome; tricuspid valve/abnormalities/physiopathology/surgery; ventricular dysfunction, right