title: Management of unusual dysplastic gangliocytoma of the cerebellum (Lhermitte-Duclos disease) in a developing country: Case report and review of the literature.
abstract: Dysplastic cerebellar gangliocytoma or Lhermitte-Duclos disease (LDD) especially in children are extremely rare. In this report we add one further case to this rare entity. A three year old boy with a history of cerebellar and brain stem compression signs was presented in unconscious condition. Computerized tomography (CT) scan revealed a well defined lesion mixed with area of calcification in the right cerebellum and severe obstructive hydrocephalus. Ventricular shunting was performed followed by gross total tumor removal three days after shunting. In the follow up period, the patient showed almost total resolution of all neurological deficits. MRI has been an imaging tool to preoperatively diagnose this disease; otherwise it would be uncertain preoperative diagnosis. However, in this report we would like to emphasize that not all uncertain diagnosis of LDD leads to palliative treatment. Well demarcated lesion may account for the safe surgical resection of this disease.
authors.affiliation: Department of Neurosurgery, Sanglah General Hospital, School of Medicine, Udayana University, Denpasar, Bali, Indonesia.
authors.forename: Nyoman
authors.initials: N
authors.lastname: Golden
authors.affiliation: Department of Neurosurgery, Sanglah General Hospital, School of Medicine, Udayana University, Denpasar, Bali, Indonesia.
authors.forename: Mahadewa G B
authors.initials: MG
authors.lastname: Tjokorda
authors.affiliation: Department of Neurosurgery, Sanglah General Hospital, School of Medicine, Udayana University, Denpasar, Bali, Indonesia.
authors.forename: Maliawan
authors.initials: M
authors.lastname: Sri
authors.affiliation: Department of Neurosurgery, Sanglah General Hospital, School of Medicine, Udayana University, Denpasar, Bali, Indonesia.
authors.forename: Wayan
authors.initials: W
authors.lastname: Niryana
authors.affiliation: Department of Pathology, Sanglah General Hospital, School of Medicine, Udayana University, Denpasar, Bali, Indonesia.
authors.forename: Saputra
authors.initials: S
authors.lastname: Herman
keywords: Cerebellar tumor; Lhermitte-Duclos disease; dysplastic gangliocytoma; surgical resection