title: Congenital pulmonary airway malformation with atrial septal defect and pulmonary hypertension for lobectomy-anesthetic considerations.
abstract: The association of congenital pulmonary airway malformation (CPAM) with congenital heart disease is rare. We present the case of a 6-month-old child with atrial septal defect and pulmonary hypertension (PH) who presented with severe respiratory distress and hypoxia. The patient underwent right lobectomy for CPAM. With timely management, real-time monitoring, one lung ventilation, and adequate analgesia, we were able to extubate the child in the immediate postoperative period. We conclude that with meticulous planning and multidisciplinary team approach, such complex cases can be managed successfully.
authors.affiliation: Department of Pediatric Anaesthesiology, Seth G.S. Medical College and K.E.M. Hospital, Parel, Mumbai, Maharashtra, India.
authors.forename: Swapna A
authors.initials: SA
authors.lastname: Chiluveru
authors.forename: Nandini M
authors.initials: NM
authors.lastname: Dave
authors.forename: Raylene J
authors.initials: RJ
authors.lastname: Dias
authors.forename: Madhu B
authors.initials: MB
authors.lastname: Garasia
mesh_terms: D060666:Airway Extubation; D000758:Anesthesia; D015615:Cystic Adenomatoid Malformation of Lung, Congenital / Q000601:surgery; D005260:Female; D006344:Heart Septal Defects, Atrial / Q000150:complications*; D006345:Heart Septal Defects, Ventricular / Q000150:complications / Q000601:surgery; D006801:Humans; D006976:Hypertension, Pulmonary / Q000150:complications*; D007223:Infant; D008168:Lung / Q000002:abnormalities* / Q000601:surgery*; D008171:Lung Diseases / Q000151:congenital*; D061810:One-Lung Ventilation; D010347:Patient Care Planning; D010348:Patient Care Team