title: Intracerebellar haemorrage in a haemophilia child.
abstract: Hemophilia A is an inherited, X-linked, recessive disorder caused by deficiency of clotting factor VIII. Intracranial hemorrhage is the leading cause of morbidity and mortality in these patients. Use of factor replacement products and medications had improved outcome in these patients. But in developing countries many such patients are not able to afford factor replacement products. We report a case of traumatic intracerebellar hemorrage in a hemophilia child. This child presented to us as a case of sub-acute intracerebellar hemorrage, he was managed conservatively with six units of fresh frozen plasma transfusion. He improved clinically and on follow-up investigation hematoma was found to have dissolved spontaneously. Through this report we want to emphasize that those cases of hemophilia presenting with acute or sub-acute intracranial bleed, conservative approach through procoagulant transfusion and intravenous fibrinolysis inhibitors should be tried as first line of management. Before daring for surgery sufficient amount of factor replacement should be kept available.
authors.affiliation: Department of Neurosurgery, SCB Medical College and Hospital, Cuttack, Odisha, India.
authors.forename: Satya Bhusan
authors.initials: SB
authors.lastname: Senapati
authors.affiliation: Department of Neurosurgery, SCB Medical College and Hospital, Cuttack, Odisha, India.
authors.forename: Sudhansu Sekhar
authors.initials: SS
authors.lastname: Mishra
authors.affiliation: Department of Neurosurgery, SCB Medical College and Hospital, Cuttack, Odisha, India.
authors.forename: Manmath Kumar
authors.initials: MK
authors.lastname: Dhir
authors.affiliation: Department of Neurosurgery, SCB Medical College and Hospital, Cuttack, Odisha, India.
authors.forename: Srikanta
authors.initials: S
authors.lastname: Das
keywords: Conservative approach; Hemophilia; intracerebellar bleed