title: Von Meyenburg complex and complete ductal plate malformation along with Klatskin tumour: a rare association.
abstract: Von Meyenburg complexes (VMCs), or bile duct microhamartomas, are among the constellation of defects of ductal plate malformation. These present as multiple small intrahepatic cysts and are diagnosed incidentally. Association of intrahepatic VMCs with a bile duct cancer has rarely been reported. We describe a case of a 53-year-old man presenting with obstructive jaundice. Biochemistry and radiology gave a provisional diagnosis of a resectable Klatskin tumour. The patient underwent right hepatectomy with common bile duct and caudate lobe excision. The histopathological examination demonstrated intrahepatic VMCs with complete ductal malformation and malignancy at the hilum.
authors.affiliation: PGIMER, Chandigarh, India.
authors.forename: Ashish
authors.initials: A
authors.lastname: Gupta
authors.affiliation: PGIMER, Chandigarh, India.
authors.forename: Bramhadatta
authors.initials: B
authors.lastname: Pattnaik
authors.affiliation: Department of Histopathology, PGIMER, Chandigarh, India.
authors.forename: Ashim
authors.initials: A
authors.lastname: Das
authors.affiliation: Department of General Surgery, PGIMER, Chandigarh, India.
authors.forename: Lileswar
authors.initials: L
authors.lastname: Kaman
mesh_terms: D001649:Bile Duct Diseases / Q000150:complications* / Q000151:congenital; D001650:Bile Duct Neoplasms / Q000209:etiology* / Q000601:surgery; D001652:Bile Ducts / Q000002:abnormalities*; D006222:Hamartoma / Q000150:complications* / Q000151:congenital; D006498:Hepatectomy; D006801:Humans; D018285:Klatskin Tumor / Q000209:etiology* / Q000601:surgery; D008297:Male; D008875:Middle Aged