title: Bilateral Macular Edema: A New Ocular Feature of Dandy-Walker Syndrome.
abstract: To describe a case of bilateral cystoid macular edema in a patient with Dandy-Walker syndrome. An 18-year-old male was referred to our tertiary referral center for evaluation of his decreased visual acuity. Detailed ophthalmic examination and imaging revealed the presence of bilateral cystoid macular edema, which was successfully treated with intravitreal triamcinolone injections (2 mg in 0.05 ml). Recurrence of macular edema developed after a period of approximately four months. This is an unusual ophthalmic manifestation of Dandy-Walker syndrome. Cystoid macular edema should be included in the differential diagnosis of subjects with Dandy-Walker syndrome presenting with decreased vision. The pathogenetic mechanism for the development macular edema in this case is not clear. Intravitreal triamcinolone is an effective treatment, but edema was recurrent in our case. Other approaches (such as oral Acetazolamide or intravitreal Anti-VEGF) have to be considered as well.
authors.affiliation: a Ophthalmica Eye Institute , Thessaloniki , Greece.
authors.forename: P
authors.initials: P
authors.lastname: Tranos
authors.affiliation: a Ophthalmica Eye Institute , Thessaloniki , Greece.
authors.forename: N
authors.identifier: http://orcid.org/0000-0002-7269-2785
authors.initials: N
authors.lastname: Dervenis
authors.affiliation: a Ophthalmica Eye Institute , Thessaloniki , Greece.
authors.forename: S
authors.initials: S
authors.lastname: Kiouras
mesh_terms: D000293:Adolescent; D003616:Dandy-Walker Syndrome / Q000150:complications* / Q000175:diagnosis; D005938:Glucocorticoids / Q000008:administration & dosage; D006801:Humans; D058449:Intravitreal Injections; D008269:Macular Edema / Q000175:diagnosis / Q000188:drug therapy / Q000209:etiology*; D008279:Magnetic Resonance Imaging; D008297:Male; D041623:Tomography, Optical Coherence / Q000379:methods; D014222:Triamcinolone Acetonide / Q000008:administration & dosage*; D014792:Visual Acuity
chemical_list: D005938:Glucocorticoids; D014222:Triamcinolone Acetonide
keywords: Dandy–Walker syndrome; intravitreal triamcinolone; macular edema