title: Physiotherapy for cystic fibrosis in Australia and New Zealand: A clinical practice guideline.
abstract: Physiotherapy management is a key element of care for people with cystic fibrosis (CF) throughout the lifespan. Although considerable evidence exists to support physiotherapy management of CF, there is documented variation in practice. The aim of this guideline is to optimize the physiotherapy management of people with CF in Australia and New Zealand. A systematic review of the literature in key areas of physiotherapy practice for CF was undertaken. Recommendations were formulated based on National Health and Medical Research Council (Australia) guidelines and considered the quality, quantity and level of the evidence; the consistency of the body of evidence; the likely clinical impact; and applicability to physiotherapy practice in Australia and New Zealand. A total of 30 recommendations were made for airway clearance therapy, inhalation therapy, exercise assessment and training, musculoskeletal management, management of urinary incontinence, managing the newly diagnosed patient with CF, delivery of non-invasive ventilation, and physiotherapy management before and after lung transplantation. These recommendations can be used to underpin the provision of evidence-based physiotherapy care to people with CF in Australia and New Zealand.
authors.affiliation: Alfred Hospital, Victoria.
authors.forename: Brenda M
authors.initials: BM
authors.lastname: Button
authors.affiliation: The Royal Children's Hospital, Victoria.
authors.forename: Christine
authors.initials: C
authors.lastname: Wilson
authors.affiliation: Royal Prince Alfred Hospital, NSW.
authors.forename: Ruth
authors.initials: R
authors.lastname: Dentice
authors.affiliation: La Trobe University, Victoria.
authors.forename: Narelle S
authors.initials: NS
authors.lastname: Cox
authors.affiliation: The Children's Hospital at Westmead, NSW.
authors.forename: Anna
authors.initials: A
authors.lastname: Middleton
authors.affiliation: Westmead Hospital, NSW.
authors.forename: Esta
authors.initials: E
authors.lastname: Tannenbaum
authors.affiliation: The Prince Charles Hospital, Queensland.
authors.forename: Jennifer
authors.initials: J
authors.lastname: Bishop
authors.affiliation: Lady Cilento Children's Hospital, Brisbane.
authors.forename: Robyn
authors.initials: R
authors.lastname: Cobb
authors.affiliation: Lady Cilento Children's Hospital, Brisbane.
authors.forename: Kate
authors.initials: K
authors.lastname: Burton
authors.affiliation: Lady Cilento Children's Hospital, Brisbane.
authors.forename: Michelle
authors.initials: M
authors.lastname: Wood
authors.affiliation: Westmead Hospital, NSW.
authors.forename: Fiona
authors.initials: F
authors.lastname: Moran
authors.affiliation: The Royal Children's Hospital, Victoria.
authors.forename: Ryan
authors.initials: R
authors.lastname: Black
authors.affiliation: Princess Margaret Hospital, Western Australia.
authors.forename: Summar
authors.initials: S
authors.lastname: Bowen
authors.affiliation: John Hunter Children's Hospital, NSW.
authors.forename: Rosemary
authors.initials: R
authors.lastname: Day
authors.affiliation: Princess Margaret Hospital, Western Australia.
authors.forename: Julie
authors.initials: J
authors.lastname: Depiazzi
authors.affiliation: Bond University/Pindara Private Hospital, Queensland.
authors.forename: Katherine
authors.initials: K
authors.lastname: Doiron
authors.affiliation: Sydney Children's Hospital, NSW.
authors.forename: Michael
authors.initials: M
authors.lastname: Doumit
authors.affiliation: Royal Prince Alfred Hospital, NSW.|University of Sydney, Sydney, NSW.
authors.forename: Tiffany
authors.initials: T
authors.lastname: Dwyer
authors.affiliation: The Children's Hospital at Westmead, NSW.
authors.forename: Alison
authors.initials: A
authors.lastname: Elliot
authors.affiliation: Alfred Hospital, Victoria.
authors.forename: Louise
authors.initials: L
authors.lastname: Fuller
authors.affiliation: Lady Cilento Children's Hospital, Brisbane.
authors.forename: Kathleen
authors.initials: K
authors.lastname: Hall
authors.affiliation: Mater Health Services, Brisbane.
authors.forename: Matthew
authors.initials: M
authors.lastname: Hutchins
authors.affiliation: Westmead Hospital, NSW.
authors.forename: Melinda
authors.initials: M
authors.lastname: Kerr
authors.affiliation: Alfred Hospital, Victoria.
authors.forename: Annemarie L
authors.initials: AL
authors.lastname: Lee
authors.affiliation: Waikato DHB, Hamilton, New Zealand.
authors.forename: Christina
authors.initials: C
authors.lastname: Mans
authors.affiliation: Gold Coast University Hospital, Gold Coast, Queensland.
authors.forename: Lauren
authors.initials: L
authors.lastname: O'Connor
authors.affiliation: Alfred Hospital, Victoria.
authors.forename: Ranjana
authors.initials: R
authors.lastname: Steward
authors.affiliation: Women's & Children's Hospital, SA.
authors.forename: Angela
authors.initials: A
authors.lastname: Potter
authors.affiliation: Alfred Hospital, Victoria.
authors.forename: Tshepo
authors.initials: T
authors.lastname: Rasekaba
authors.affiliation: Starship Children's Health, New Zealand.
authors.forename: Rebecca
authors.initials: R
authors.lastname: Scoones
authors.affiliation: Alfred Hospital, Victoria.
authors.forename: Ben
authors.initials: B
authors.lastname: Tarrant
authors.affiliation: Royal Adelaide Hospital, South Australia.
authors.forename: Nathan
authors.initials: N
authors.lastname: Ward
authors.affiliation: The Prince Charles Hospital, Queensland.
authors.forename: Samantha
authors.initials: S
authors.lastname: West
authors.affiliation: Royal Adelaide Hospital, South Australia.
authors.forename: Dianne
authors.initials: D
authors.lastname: White
authors.affiliation: Alfred Hospital, Victoria.
authors.forename: Lisa
authors.initials: L
authors.lastname: Wilson
authors.affiliation: Sir Charles Gairdner Hospital and Institute for Respiratory Health, Western Australia.
authors.forename: Jamie
authors.initials: J
authors.lastname: Wood
authors.affiliation: La Trobe University, Victoria.
authors.forename: Anne E
authors.initials: AE
authors.lastname: Holland
mesh_terms: D001315:Australia / Q000453:epidemiology; D032921:Consensus; D003550:Cystic Fibrosis / Q000453:epidemiology / Q000503:physiopathology / Q000628:therapy*; D015444:Exercise; D019983:Guideline Adherence; D007722:Health Knowledge, Attitudes, Practice; D006801:Humans; D009079:Mucociliary Clearance; D009520:New Zealand / Q000453:epidemiology; D063087:Noninvasive Ventilation; D010349:Patient Compliance / Q000706:statistics & numerical data*; D017060:Patient Satisfaction / Q000706:statistics & numerical data*; D026741:Physical Therapy Modalities; D017410:Practice Guidelines as Topic; D011788:Quality of Life; D012129:Respiratory Function Tests; D012138:Respiratory Therapy; D016896:Treatment Outcome
keywords: airway clearance; cystic fibrosis; exercise; inhalation therapy; physiotherapy