title: Unusual presentation of total anomalous systemic venous connection.
abstract: A 9-year-old girl who presented with dyspnea on exertion was diagnosed with total anomalous systemic venous connection to the left atrium (both venae cavae), no left superior vena cava, and a moderate-sized atrial septal defect with severe pulmonary arterial hypertension and ectopic atrial rhythm. She underwent septation of the common atrium using autologous pericardium, thereby rerouting the superior vena cava, inferior vena cava, and coronary sinus to the right atrium. Her postoperative course was uneventful. This case is reported for its rarity of presentation with severe pulmonary arterial hypertension and ectopic atrial rhythm.
authors.affiliation: 1 Department of Cardiac Surgery, Madras Medical Mission, Chennai, India.
authors.forename: Swaminathan
authors.initials: S
authors.lastname: Vaidyanathan
authors.affiliation: 2 Department of Pediatric Cardiology, Madras Medical Mission, Chennai, India.
authors.forename: Sivakumar
authors.initials: S
authors.lastname: Kothandam
authors.affiliation: 2 Department of Pediatric Cardiology, Madras Medical Mission, Chennai, India.
authors.forename: Rajesh
authors.initials: R
authors.lastname: Kumar
authors.affiliation: 2 Department of Pediatric Cardiology, Madras Medical Mission, Chennai, India.
authors.forename: Priya M
authors.initials: PM
authors.lastname: Pradhan
authors.affiliation: 1 Department of Cardiac Surgery, Madras Medical Mission, Chennai, India.
authors.forename: Ravi
authors.initials: R
authors.lastname: Agarwal
mesh_terms: D018880:Atrial Premature Complexes / Q000175:diagnosis / Q000209:etiology* / Q000601:surgery; D006348:Cardiac Surgical Procedures; D002648:Child; D004417:Dyspnea / Q000175:diagnosis / Q000209:etiology; D005260:Female; D006801:Humans; D006976:Hypertension, Pulmonary / Q000175:diagnosis / Q000209:etiology* / Q000601:surgery; D010690:Phlebography; D012587:Scimitar Syndrome / Q000150:complications* / Q000000981:diagnostic imaging / Q000601:surgery; D012720:Severity of Illness Index; D016896:Treatment Outcome
keywords: Anomolous; Atrial septal defects; Complex; Isomerism; TASVC; congenital; superior