title: Osteopathia striata with cranial sclerosis (OSCS): review of the literature and case report demonstrating challenges of spinal fusion after trauma.
abstract: Osteopathia striata with cranial sclerosis (OSCS) is a rare but well-described pathology characterized by abnormalities in bone deposition in the axial and cranial skeleton as well as other abnormalities and associated deficits. These skeletal abnormalities can lead to significant intra-operative challenges for the surgeon and influence outcomes for the patient. In this report, we present a case of a patient with OSCS who was involved in a traumatic motor vehicle crash and underwent posterior cervico-thoracic fusion for a T4 chance fracture. Bony abnormalities in the cervico-thoracic spine presented a significant operative challenge due to alterations in bony anatomy and bone architecture. This case serves as an example of the challenges that the spine surgeon faces when dealing with OSCS, and highlights the differences between OSCS and commoner skeletal hyperplasias such as osteopetrosis.
authors.affiliation: Department of Neurosurgery, West Virginia University School of Medicine, One Medical Center Drive Suite 4300, Morgantown, WV, 26506, USA.|Center for Neuroscience, West Virginia University School of Medicine, Morgantown, WV, 26506, USA.
authors.forename: Gennadiy A
authors.initials: GA
authors.lastname: Katsevman
authors.affiliation: Department of Neurosurgery, West Virginia University School of Medicine, One Medical Center Drive Suite 4300, Morgantown, WV, 26506, USA.|Center for Neuroscience, West Virginia University School of Medicine, Morgantown, WV, 26506, USA.
authors.forename: Ryan C
authors.initials: RC
authors.lastname: Turner
authors.affiliation: Department of Neurosurgery, West Virginia University School of Medicine, One Medical Center Drive Suite 4300, Morgantown, WV, 26506, USA.|Center for Neuroscience, West Virginia University School of Medicine, Morgantown, WV, 26506, USA.
authors.forename: Brandon P
authors.initials: BP
authors.lastname: Lucke-Wold
authors.affiliation: Department of Neurosurgery, West Virginia University School of Medicine, One Medical Center Drive Suite 4300, Morgantown, WV, 26506, USA.|Center for Neuroscience, West Virginia University School of Medicine, Morgantown, WV, 26506, USA.
authors.forename: Cara L
authors.initials: CL
authors.lastname: Sedney
authors.affiliation: Department of Neurosurgery, West Virginia University School of Medicine, One Medical Center Drive Suite 4300, Morgantown, WV, 26506, USA. sbhatia@hsc.wvu.edu.|Center for Neuroscience, West Virginia University School of Medicine, Morgantown, WV, 26506, USA. sbhatia@hsc.wvu.edu.
authors.forename: Sanjay
authors.initials: S
authors.lastname: Bhatia
mesh_terms: D005260:Female; D050723:Fractures, Bone / Q000150:complications* / Q000473:pathology; D006801:Humans; D008875:Middle Aged; D010026:Osteosclerosis / Q000150:complications / Q000601:surgery*; D013123:Spinal Fusion / Q000009:adverse effects* / Q000379:methods
keywords: Image-based navigation; Osteopathia striata with cranial sclerosis; T4 chance fracture