title: Unilateral Absence of the Left Pulmonary Artery With an Associated Vascular Anomaly in Adulthood.
abstract: Left-sided pulmonary artery agenesis is a rare malformation that commonly requires childhood intervention secondary to associated congenital cardiovascular anomalies. We present an uncommon case of left-sided agenesis with an associated right-sided aortic arch and significant hypoplasia of the ipsilateral lung. Additionally, there is radiographic evidence of emphysema and pulmonary artery hypertension. Pulmonary artery agenesis is not a common entity, but should be considered in adult patients presenting with recurrent pneumonias and radiographic evidence suggestive of pulmonary hypoplasia. A prompt diagnosis is beneficial for affected individuals who may be candidates for a revascularization procedure or embolization of collaterals. Earlier diagnosis also allows for proper management and follow-up care, considering pulmonary artery hypertension is a severe complication of pulmonary artery agenesis.
authors.affiliation: Diagnostic Radiology, Florida Hospital-Orlando.
authors.forename: Miguel
authors.initials: M
authors.lastname: Flores
authors.affiliation: Diagnostic Radiology, Florida Hospital-Orlando.
authors.forename: Haley
authors.initials: H
authors.lastname: Letter
authors.affiliation: Diagnostic Radiology, Florida Hospital-Orlando.
authors.forename: Edward
authors.initials: E
authors.lastname: Derrick
authors.affiliation: Diagnostic Radiology, Florida Hospital-Orlando.
authors.forename: Ibrahim
authors.initials: I
authors.lastname: Koury
keywords: cardiovascular anomaly; congenital; pulmonary artery agenesis; uapa