Surgical Closure of Aortopulmonary Window in a Topsy-Turvy Heart: A Surgical Challenge.
Topsy-turvy heart is a rare congenital cardiac anomaly characterized by a 90° rotation of the heart along its long axis. The great vessels originate posteroinferiorly, and the arch vessels are elongated and join the aorta well below the carina. It is usually associated with aortic arch and tracheobronchial anomalies. Cardiopulmonary bypass is challenging in these patients because of the abnormal position of the great vessels. We describe the surgical management of aortopulmonary window in a topsy-turvy heart in a 14-day-old girl.
Department of Cardiology, Sree Chitra Tirunal Institute for Medical Sciences and Technology, Trivandrum, India. Electronic address: deepaskumar@yahoo.com.
Deepa
D
Sasikumar
Department of Cardiothoracic Surgery, Sree Chitra Tirunal Institute for Medical Sciences and Technology, Trivandrum, India.
Baiju S
BS
Dharan
Department of Cardiothoracic Surgery, Sree Chitra Tirunal Institute for Medical Sciences and Technology, Trivandrum, India.
Sabarinath
S
Menon
Department of Cardiology, Sree Chitra Tirunal Institute for Medical Sciences and Technology, Trivandrum, India.
Sivasankaran
S
Sivasubramanian
Department of Radiology, Sree Chitra Tirunal Institute for Medical Sciences and Technology, Trivandrum, India.
T R
TR
Kapilamoorthy
D001013:Aorta, Thoracic / Q000002:abnormalities / Q000000981:diagnostic imaging / Q000601:surgery*; D001159:Arterio-Arterial Fistula / Q000151:congenital / Q000000981:diagnostic imaging / Q000601:surgery*; D001980:Bronchi / Q000002:abnormalities; D000072226:Computed Tomography Angiography; D005260:Female; D006330:Heart Defects, Congenital / Q000000981:diagnostic imaging / Q000601:surgery*; D006801:Humans; D006976:Hypertension, Pulmonary / Q000209:etiology; D021621:Imaging, Three-Dimensional; D007231:Infant, Newborn; D011651:Pulmonary Artery / Q000002:abnormalities / Q000000981:diagnostic imaging / Q000601:surgery*; D012399:Rotation; D014057:Tomography, X-Ray Computed