High Le Fort I osteotomy for correction of mid-face deformity in Crouzon syndrome.
An 18-year-old woman with mild Crouzon syndrome was referred with malocclusion and mandibular protrusion. Examination revealed Class III canine and molar relationships, hypoplastic maxilla, 1-mm overbite, and -2-mm overjet. Analysis showed 69° sella-nasion-A, 73.6° sella-nasion-B, and -4.6° A point-nasion-B point angles. Polysomnography revealed respiratory disturbance and 6.3% oxygen desaturation indices of 5.4/h and 9.0/h. We performed double-jaw surgery using high Le Fort I osteotomy and bilateral sagittal split ramus osteotomy for midfacial deformity correction. Twelve months post-surgery, her measures were 70.8°, 72°, -1.2°, 3.0/h, and 6.1/h, respectively. Esthetics were satisfactory. High Le Fort I osteotomy is effective for midfacial deformity correction in patients with Crouzon syndrome.
Section of Oral and Maxillofacial Surgery, Division of Maxillofacial Diagnostic and Surgical Sciences, Faculty of Dental Science, Kyushu University, Fukuoka, Japan.
Yasumichi
Y
Nakajima
Section of Oral and Maxillofacial Surgery, Division of Maxillofacial Diagnostic and Surgical Sciences, Faculty of Dental Science, Kyushu University, Fukuoka, Japan.|Dental and Maxillofacial Center, Kyushi University Hospital, Fukuoka, Japan.
Hiroyuki
H
Nakano
Section of Oral and Maxillofacial Surgery, Division of Maxillofacial Diagnostic and Surgical Sciences, Faculty of Dental Science, Kyushu University, Fukuoka, Japan.|Dental and Maxillofacial Center, Kyushi University Hospital, Fukuoka, Japan.
Tomoki
T
Sumida
Section of Oral and Maxillofacial Surgery, Division of Maxillofacial Diagnostic and Surgical Sciences, Faculty of Dental Science, Kyushu University, Fukuoka, Japan.|Dental and Maxillofacial Center, Kyushi University Hospital, Fukuoka, Japan.
Tomohiro
T
Yamada
Section of Oral and Maxillofacial Surgery, Division of Maxillofacial Diagnostic and Surgical Sciences, Faculty of Dental Science, Kyushu University, Fukuoka, Japan.
Kazuya
K
Inoue
Section of Oral and Maxillofacial Surgery, Division of Maxillofacial Diagnostic and Surgical Sciences, Faculty of Dental Science, Kyushu University, Fukuoka, Japan.
Goro
G
Sugiyama
Department of Oral and Maxillofacial Surgery, Yamaguchi University Graduate School of Medicine, Yamaguchi, Japan.
Katsuaki
K
Mishima
Section of Oral and Maxillofacial Surgery, Division of Maxillofacial Diagnostic and Surgical Sciences, Faculty of Dental Science, Kyushu University, Fukuoka, Japan.|Dental and Maxillofacial Center, Kyushi University Hospital, Fukuoka, Japan.
Yoshihide
Y
Mori
D000293:Adolescent; D002508:Cephalometry; D003394:Craniofacial Dysostosis / Q000175:diagnosis* / Q000601:surgery*; D005260:Female; D006801:Humans; D008437:Maxilla / Q000002:abnormalities* / Q000601:surgery*; D019340:Osteotomy, Le Fort / Q000379:methods; D010641:Phenotype; D014057:Tomography, X-Ray Computed; D016896:Treatment Outcome
Crouzon syndrome; airway; high Le Fort I osteotomy; midfacial deformity; obstructive sleep apnea syndrome