Melanotic neuroectodermal tumor of infancy.
Melanotic neuroectodermal tumor of infancy (MNTI) is a rare pigmented craniofacial tumor of newborns and infants. We report the imaging findings of a 3-month old male patient with a maxillary MNTI. Detailed discussion on imaging features on various magnetic resonance sequences and CT scan are included. Characteristic radiographic appearance is also described. MNTI, of neural crest origin, display a biphasic population of melanin containing cells and neuroblastic cells, within a moderately vascularized fibrous stroma. The child underwent complete surgical excision with no evidence of recurrence at one year follow up. MNTI is an unusual tumor occurring in early childhood with a predilection for the maxilla. Clinical findings, CT scan and MRI may allow a preoperative diagnosis.
Department of Diagnostic Radiology, Yale School of Medicine, BOX 208042, Tompkins East 2, 333 Cedar Street, New Haven, CT 06520-8042, USA.
Xiao
X
Wu
Department of Diagnostic Radiology, Yale School of Medicine, BOX 208042, Tompkins East 2, 333 Cedar Street, New Haven, CT 06520-8042, USA.
Samantha
S
Shankar
Department of Pathology, Yale School of Medicine, New Haven, CT, USA.
William R
WR
Munday
Department of Diagnostic Radiology, Yale School of Medicine, BOX 208042, Tompkins East 2, 333 Cedar Street, New Haven, CT 06520-8042, USA. Electronic address: ajay.malhotra@yale.edu.
Ajay
A
Malhotra
D003937:Diagnosis, Differential; D006801:Humans; D007223:Infant; D008279:Magnetic Resonance Imaging; D008297:Male; D008441:Maxillary Neoplasms / Q000000981:diagnostic imaging* / Q000473:pathology; D017600:Neuroectodermal Tumor, Melanotic / Q000000981:diagnostic imaging* / Q000473:pathology; D014057:Tomography, X-Ray Computed
CT scan; Diagnostic imaging; Infants; Magnetic resonance; Maxillary tumor; Melanotic neuroectodermal tumor