Anterior Cranial Vault Distraction for the Treatment of Normocephalic Pancraniosynostosis.
Normocephalic pancraniosynostosis is a rare form of craniosynostosis that usually presents later in life secondary to a delayed onset of symptoms and the presence of a normal head shape. Since its initial description in the literature in 2010, normocephalic pancraniosynostosis remains a rare clinical entity that has only been reported in 6 patients. Surgical treatment in the 2 published reports has been by staged total calvarial reconstruction or anterior cranial vault remodeling with bilateral frontoorbital advancement. In this case report, the authors present 1 patient with normocephalic pancraniosynostosis and propose surgical treatment by anterior cranial vault expansion with distraction osteogenesis.
*Division of Plastic and Reconstructive Surgery, University of Nebraska Medical Center†University of Nebraska College of Medicine, Omaha, NE.
Shannon
S
Wong
Eric S
ES
Nagengast
Jason
J
Miller
D002675:Child, Preschool; D003398:Craniosynostoses / Q000175:diagnosis / Q000601:surgery*; D005260:Female; D006801:Humans; D019857:Osteogenesis, Distraction / Q000379:methods*; D019651:Plastic Surgery Procedures / Q000379:methods*; D012886:Skull / Q000000981:diagnostic imaging / Q000601:surgery*; D014057:Tomography, X-Ray Computed; D016896:Treatment Outcome