Orbital Malignant Peripheral Nerve Sheath Tumor With Heterologous Elements in a 15-Year-Old Girl.
A 15-year-old girl presented with painful proptosis in the right eye. Imaging studies demonstrated an inferiorly located orbital mass. Histopathological examination of the exenteration specimen was consistent with malignant peripheral nerve sheath tumor. This case is a rare example of orbital malignant peripheral nerve sheath tumor presumably arising from the infraorbital nerve with heterologous histologic elements.
Hayyam
H
Kiratli
Irem
I
Koç
Diclehan
D
Orhan
D000293:Adolescent; D000971:Antineoplastic Combined Chemotherapy Protocols / Q000627:therapeutic use; D059248:Chemoradiotherapy; D005094:Exophthalmos; D005260:Female; D006801:Humans; D008279:Magnetic Resonance Imaging; D018317:Nerve Sheath Neoplasms / Q000473:pathology* / Q000628:therapy; D009918:Orbital Neoplasms / Q000473:pathology* / Q000628:therapy; D061766:Proton Therapy; D014792:Visual Acuity / Q000502:physiology