Double-Lumen Aortic Arch: Persistence of the Fifth Aortic Arch.
A persistent fifth aortic arch is exceptionally rare. We report a patient with a double-lumen aortic arch in association with a perimembranous ventricular septal defect and Cornelia de Lange syndrome. We also discuss the morphologic consequences of persistent fifth aortic, arch, which may not be limited to the double-lumen aorta but in fact may be more common.
Royal Children's Hospital, Melbourne, Australia; Murdoch Children's Research Institute, Melbourne, Australia; University of Melbourne, Melbourne, Australia.
Phillip S
PS
Naimo
Royal Children's Hospital, Melbourne, Australia; Murdoch Children's Research Institute, Melbourne, Australia.
Maria Del Carmen
Mdel C
Vazquez-Alvarez
Royal Children's Hospital, Melbourne, Australia; Murdoch Children's Research Institute, Melbourne, Australia; University of Melbourne, Melbourne, Australia.
Yves
Y
d'Udekem
Royal Children's Hospital, Melbourne, Australia; Murdoch Children's Research Institute, Melbourne, Australia; University of Melbourne, Melbourne, Australia.
Bryn
B
Jones
Royal Children's Hospital, Melbourne, Australia; Murdoch Children's Research Institute, Melbourne, Australia; University of Melbourne, Melbourne, Australia. Electronic address: igor.konstantinov@rch.org.au.
Igor E
IE
Konstantinov
D001013:Aorta, Thoracic / Q000002:abnormalities* / Q000473:pathology; D003635:De Lange Syndrome / Q000150:complications*; D005260:Female; D006345:Heart Septal Defects, Ventricular / Q000150:complications*; D006801:Humans; D007223:Infant