Late-Onset Cyanosis and Finger Clubbing in a 37-Year-Old Female with Ebstein's Anomaly and Atrial Septal Defect.
It is common to suspect Eisenmenger syndrome when patients with atrial septal defect (ASD) show cyanosis and clubbing. However, ASD accompanying Ebstein's anomaly frequently shows cyanosis without severe pulmonary hypertension, especially in the early period after birth. So the medical decision to decline surgical treatment in those patients should not be determined merely by clinical features such as cyanosis and clubbing. We report a case of a 37-year-old female with Ebstein's anomaly and secundum ASD who showed lip cyanosis and finger clubbing, but maintained normal pulmonary artery pressure and thus underwent successful surgical correction.


BACKGROUND
Atrial septal defect; Cyanosis; Ebstein's anomaly; Eisenmenger syndrome.
Division of Cardiology, Department of Internal Medicine;
Kook-Jin
KJ
Chun
Division of Cardiology, Department of Internal Medicine;
Dong Cheul
DC
Han
Division of Cardiology, Department of Internal Medicine;
Yong Hyun
YH
Park
Department of Thoracic Surgery, Pusan National University Yangsan Hospital, South Korea.
Sang-Kwon
SK
Lee