title: Congenital intrahepatic portosystemic shunt diagnosed during intrauterine life.
abstract: OBJECTIVE
  To report a patient with prenatal diagnosis of portosystemic shunt; a rare condition in humans.
  
  
  METHODS
  17-day-old female infant admitted for investigation of suspected diagnosis of portosystemic shunt, presumed in obstetric ultrasound. The hypothesis was confirmed after abdominal angiography and liver Doppler. Other tests such as echocardiography and electroencephalogram were performed to investigate possible co-morbidities or associated complications, and were normal. We chose conservative shunt treatment, as there were no disease-related complications and this was intrahepatic shunt, which could close spontaneously by the age of 2 years.
  
  
  CONCLUSIONS
  Portosystemic shunt can lead to various complications such as hepatic encephalopathy, hypergalactosemia, liver tumors, and hepatopulmonary syndrome. Most diagnoses are done after one month of age, after such complications occur. The prenatal diagnosis of this patient provided greater security for the clinical picture management, as well as regular monitoring, which allows the anticipation of possible complications and perform interventional procedures when needed.
authors.affiliation: Hospital Pequeno Príncipe, Curitiba, PR, Brasil. Electronic address: camila.bellettini@gmail.com.
authors.forename: Camila Vieira
authors.initials: CV
authors.lastname: Bellettini
authors.affiliation: Hospital Pequeno Príncipe, Curitiba, PR, Brasil.
authors.forename: Rafaela
authors.initials: R
authors.lastname: Wagner
authors.affiliation: Pontifícia Universidade Católica do Paraná, Curitiba, PR, Brasil.
authors.forename: Aleocídio
authors.initials: A
authors.lastname: Sette Balzanelo
authors.affiliation: Pontifícia Universidade Católica do Paraná, Curitiba, PR, Brasil.
authors.forename: André Luis
authors.initials: AL
authors.lastname: de Souza Andretta
authors.affiliation: Pontifícia Universidade Católica do Paraná, Curitiba, PR, Brasil.
authors.forename: Arthur
authors.initials: A
authors.lastname: Nascimento de Moura
authors.affiliation: Pontifícia Universidade Católica do Paraná, Curitiba, PR, Brasil.
authors.forename: Catia Carolina
authors.initials: CC
authors.lastname: Fabris
authors.affiliation: Pontifícia Universidade Católica do Paraná, Curitiba, PR, Brasil.
authors.forename: Eduardo
authors.initials: E
authors.lastname: Maranhão Gubert
mesh_terms: D005260:Female; D006801:Humans; D007231:Infant, Newborn; D008099:Liver; D011169:Portal Vein / Q000002:abnormalities* / Q000000981:diagnostic imaging; D016216:Ultrasonography, Prenatal; D054079:Vascular Malformations / Q000000981:diagnostic imaging*
keywords: Anormalidades congênitas; CT scan; Congenital abnormalities; Diagnóstico pré‐natal; Doppler ultrasound; Prenatal diagnosis; Tomografia computadorizada; Ultrassonografia Doppler