title: A CASE OF UNILATERAL RETINAL PIGMENT EPITHELIUM DYSGENESIS.
abstract: OBJECTIVE
  To report a case of unilateral retinal pigment epithelium dysgenesis.
  
  
  METHODS
  An 8-year-old boy with a large grayish lesion and leopard-spot pattern lesion at its periphery in his left eye underwent fluorescein angiography, fundus autofluorescence imaging, optical coherence tomography, and electroretinography.
  
  
  RESULTS
  Fluorescein angiography showed an area of geographic hyperfluorescence with a peripheral pattern of dark spots. The area of retinal pigment epithelial atrophy showed hypofluorescence on fundus autofluorescence. Optical coherence tomography of the left eye showed attenuation of the inner segment-outer segment junction and choroidal thinning. Single-flash electroretinography and scotopic electroretinography showed normal results and did not differ between both the eyes. The 30-Hz flicker test and photopic electroretinography showed a decrease in amplitude in the left eye.
  
  
  CONCLUSIONS
  Unilateral retinal pigment epithelium dysgenesis is very rare, and its prognosis is still unknown. Careful follow-up of the patient seems to be essential.
authors.affiliation: Division of Ophthalmology and Visual Science, Faculty of Medicine, Tottori University, Tottori, Japan.
authors.forename: Atsushi
authors.initials: A
authors.lastname: Yamasaki
authors.forename: Takeshi
authors.initials: T
authors.lastname: Tominaga
authors.forename: Ryoko
authors.initials: R
authors.lastname: Ishikura
authors.forename: Hiroshi
authors.initials: H
authors.lastname: Ohmatsu
authors.forename: Yoshitsugu
authors.initials: Y
authors.lastname: Inoue
mesh_terms: D001284:Atrophy; D002648:Child; D003937:Diagnosis, Differential; D006801:Humans; D008297:Male; D012164:Retinal Diseases / Q000175:diagnosis*; D055213:Retinal Pigment Epithelium / Q000473:pathology*