title: Successful One-Stage Operative Resection of an Intravenous Leiomyomatosis Involving the Right-Sided Heart Chambers and Pulmonary Artery.
abstract: Intravenous leiomyomatosis (IVL) is a rare neoplastic disorder. It may extend into the right cardiac chambers, which are named after intracardiac leiomyomatosis (ICL). We describe a case of IVL extending into the right heart and pulmonary artery in a 46-year-old woman. The patient successfully underwent a one-stage operation under cardiopulmonary bypass (CPB) with deep hypothermic circulatory arrest. The patient fully recovered without major complications and did not exhibit any recurrence at the 9-month follow-up. The unique feature of this case is its involvement with the pulmonary artery, which is uncommon but potentially lethal.
authors.affiliation: Department of Cardiac Surgery, Peking Union Medical College Hospital, Peking Union Medical College, Chinese Academy of Medical Sciences, Beijing. xrj3408@163.com.
authors.forename: Rongjian
authors.initials: R
authors.lastname: Xu
authors.affiliation: Department of Cardiac Surgery, Peking Union Medical College Hospital, Peking Union Medical College, Chinese Academy of Medical Sciences, Beijing. miaoqipumc@hotmail.com.
authors.forename: Qi
authors.initials: Q
authors.lastname: Miao
authors.affiliation: Department of Cardiac Surgery, Peking Union Medical College Hospital, Peking Union Medical College, Chinese Academy of Medical Sciences, Beijing. dragon087@163.com.
authors.forename: Xingrong
authors.initials: X
authors.lastname: Liu
authors.affiliation: Department of Cardiac Surgery, Peking Union Medical College Hospital, Peking Union Medical College, Chinese Academy of Medical Sciences, Beijing. 1529382688@qq.com.
authors.forename: Chaoji
authors.initials: C
authors.lastname: Zhang
authors.affiliation: Department of Cardiac Surgery, Peking Union Medical College Hospital, Peking Union Medical College, Chinese Academy of Medical Sciences, Beijing. zhaom_1024@yeah.net.
authors.forename: Guotao
authors.initials: G
authors.lastname: Ma
mesh_terms: D006348:Cardiac Surgical Procedures / Q000379:methods*; D004452:Echocardiography; D005260:Female; D005500:Follow-Up Studies; D006325:Heart Atria; D006338:Heart Neoplasms / Q000175:diagnosis / Q000601:surgery*; D006352:Heart Ventricles; D006801:Humans; D018231:Leiomyomatosis / Q000175:diagnosis / Q000601:surgery*; D008875:Middle Aged; D009361:Neoplasm Invasiveness; D011651:Pulmonary Artery; D014057:Tomography, X-Ray Computed; D019043:Vascular Neoplasms / Q000175:diagnosis / Q000601:surgery*