title: Idiopathic pleuroparenchymal fibroelastosis - A rare idiopathic interstitial pneumonia.
abstract: Idiopathic pleuroparenchymal fibroelastosis is a rare idiopathic interstitial pneumonia. It was first described in 2004 and subsequently included in the ATS/ERS classification of idiopathic interstitial pneumonia in 2013. There have been few cases reported so far. The diagnostic criteria is still emerging and its etiology is being questioned. We report a case of pleuroparenchymal fibroelastosis probably idiopathic, the first of its kind to be reported from India, and a brief review of the literature.
authors.affiliation: Department of Pulmonary Medicine, Christian Medical College, Vellore, India.
authors.forename: Balamugesh
authors.initials: B
authors.lastname: Thangakunam
authors.affiliation: Department of Pulmonary Medicine, Christian Medical College, Vellore, India.
authors.forename: Barney T J
authors.initials: BT
authors.lastname: Isaac
authors.affiliation: Department of Pulmonary Medicine, Christian Medical College, Vellore, India.
authors.forename: Devasahayam Jesudas
authors.initials: DJ
authors.lastname: Christopher
authors.affiliation: Department of General Pathology, Christian Medical College, Vellore, India.
authors.forename: Deepak
authors.initials: D
authors.lastname: Burad
keywords: Idiopathic interstitial pneumonia; Interstitial lung disease; Pleuroparenchymal fibroelastosis