title: Wünderlich ist nicht so Wunderbar: Bilateral Angiomyolipomas and Wünderlich Syndrome Requiring Emergency Embolization in a Patient without Tuberous Sclerosis.
abstract: Bilateral renal angiomyolipomata are rare and usually associated with tuberous sclerosis. Renal angiomyolipomata can rupture spontaneously giving rise to (potentially catastrophic) retroperitoneal hemorrhage (Wünderlich syndrome). We present a very rare case of bilateral renal angiomyolipomata in an individual without tuberous sclerosis, presenting with life-threatening hemorrhage. The patient had emergency embolization of the bleeding angiomyolipoma and received elective embolization of a contralateral lesion. A follow-up brain magnetic resonance imaging showed no tubers but revealed a pituitary adenoma of uncertain significance.
authors.affiliation: Department of Radiology, Horton Hospital, Oxford University Hospitals NHS Trust, Oxford, UK. Electronic address: benjamin.harris@oncology.ox.ac.uk.
authors.forename: Benjamin Howell
authors.initials: BH
authors.lastname: Lole Harris
authors.affiliation: American University of Beirut Medical Centre, Vascular Medicine Program, Beirut, Lebanon.
authors.forename: Jason Leo
authors.initials: JL
authors.lastname: Walsh
authors.affiliation: Department of Radiology, Horton Hospital, Oxford University Hospitals NHS Trust, Oxford, UK.
authors.forename: Sarfraz Ahmed
authors.initials: SA
authors.lastname: Nazir
mesh_terms: D018207:Angiomyolipoma / Q000150:complications* / Q000000981:diagnostic imaging; D004621:Embolization, Therapeutic; D004630:Emergencies; D006470:Hemorrhage / Q000000981:diagnostic imaging / Q000209:etiology / Q000628:therapy*; D006801:Humans; D007680:Kidney Neoplasms / Q000150:complications* / Q000000981:diagnostic imaging; D008297:Male; D008875:Middle Aged; D012187:Retroperitoneal Space; D012422:Rupture, Spontaneous; D014057:Tomography, X-Ray Computed; D016896:Treatment Outcome