title: A Rare Case of Mayer-Rokitansky-Kuster-Hauser Syndrome Presenting with Acute Psychosis.
abstract: The psychiatric co-morbidities in female population with mullerian agenesis is an area with limited research. This is probably due to the fact that when those patients are diagnosed not much attention or information is given for long term psychiatric follow-up. Owing to their inability to bear children, these subjects often become socially harassed. Thus these constant stressors may lead to development of psychopathology in future. Mayer-Rokitansky-Kuster-Hauser (MRKH) syndrome is a congenital abnormality with absence of uterus, cervix and vagina, but normal secondary sexual characteristics and external genitalia and occurs in every 1 out of 4000-10,000 females. There is also limited literature on the probable common chromosomal aetiology for both psychosis and MRKH patients. We, present here a case of MRKH syndrome, whose initial presentation was psychosis only. In this respect, we also highlight the much neglected need of appropriate psychiatric screening and provision of psychiatric care in this population.
authors.affiliation: Associate Professor, Department of Psychiatry, Silchar Medical College and Hospital , Silchar, Assam, India .
authors.forename: Kamal
authors.initials: K
authors.lastname: Nath
authors.affiliation: Postgraduate Trainee, Department of Psychiatry, Silchar Medical College and Hospital , Silchar, Assam, India .
authors.forename: Bhanita
authors.initials: B
authors.lastname: Boro
authors.affiliation: Postgraduate Trainee, Department of Psychiatry, Silchar Medical College and Hospital , Silchar, Assam, India .
authors.forename: Subrata
authors.initials: S
authors.lastname: Naskar
keywords: Congenital anomaly; Mullerian agenesis; Primary amenorrhea; Psychological distress; Psychosis NOS