title: Survival of a very low-birthweight infant with Potter sequence on long-term hemodialysis.
abstract: Recent advances in neonatal cardiorespiratory management and neonatal renal replacement therapy have led to occasional reports of favorable short-term and long-term outcomes for Potter sequence, once thought to be fatal. The present patient was a girl born at a gestational age of 34 weeks 4 days with a birthweight of 1398 g. She was diagnosed with Potter sequence complicated by pulmonary hypoplasia due to left renal agenesis and small right kidney. Hemodialysis was started because anuria persisted even after persistent pulmonary hypertension receded and cardiorespiratory status improved. Peritoneal dialysis during the clinical course failed to achieve stability because of pericatheter leakage and frequent obstruction of the peritoneal dialysis catheter; in the meantime, hemodialysis was also performed. Once bodyweight passed 3.5 kg, peritoneal dialysis became more feasible with stability; the patient was discharged at 9 months and at the time of writing was on peritoneal dialysis at home, and renal transplantation was planned.
authors.affiliation: Department of Neonatology, Seirei-Hamamatsu General Hospital, Hamamatsu City, Shizuoka, Japan.
authors.forename: Jun
authors.initials: J
authors.lastname: Miyahara
authors.affiliation: Department of Pediatrics, Seirei-Hamamatsu General Hospital, Hamamatsu City, Shizuoka, Japan.
authors.forename: Masaki
authors.initials: M
authors.lastname: Yamamoto
authors.affiliation: Department of Neonatology, Seirei-Hamamatsu General Hospital, Hamamatsu City, Shizuoka, Japan.
authors.forename: Kyoko
authors.initials: K
authors.lastname: Motoshige
authors.affiliation: Department of Pediatrics, Seirei-Hamamatsu General Hospital, Hamamatsu City, Shizuoka, Japan.
authors.forename: Naoya
authors.initials: N
authors.lastname: Fujita
authors.affiliation: Department of Neonatology, Seirei-Hamamatsu General Hospital, Hamamatsu City, Shizuoka, Japan.
authors.forename: Shigeru
authors.initials: S
authors.lastname: Ohki
mesh_terms: D000293:Adolescent; D000013:Congenital Abnormalities / Q000175:diagnosis / Q000628:therapy; D005260:Female; D005500:Follow-Up Studies; D006801:Humans; D007231:Infant, Newborn; D019102:Infant, Very Low Birth Weight; D007668:Kidney / Q000002:abnormalities*; D007674:Kidney Diseases / Q000150:complications / Q000151:congenital* / Q000175:diagnosis / Q000628:therapy; D007676:Kidney Failure, Chronic / Q000175:diagnosis / Q000209:etiology / Q000628:therapy*; D011247:Pregnancy; D011860:Radiography, Abdominal; D006435:Renal Dialysis; D013997:Time Factors
keywords: Potter syndrome; dialysis; infant; very low-birthweight