title: IgG4-related disease presenting as a lung mass and weight loss: Case report and review of the literature.
abstract: We describe a case of IgG4-related lung disease presenting as a lung mass with associated weight loss. IgG4-related disease is a systemic sclerosing disorder that causes fibrotic, often tumor-like manifestations that variably effect different organ systems. The clinical presentation of IgG4-related disease is protean. Timely recognition and diagnosis requires awareness on the part of clinicians and pathologists to the variable manifestations of this newly recognized disorder. We offer a concise review of the pulmonary manifestations, diagnosis and treatment of IgG4-related lung disease.
authors.affiliation: Section of Pulmonary, Critical Care and Sleep Medicine, Bridgeport Hospital, Bridgeport, CT, USA.
authors.forename: Kevin
authors.initials: K
authors.lastname: Grewal
authors.affiliation: Department of Pathology, Bridgeport Hospital, Bridgeport, CT, USA.
authors.forename: Paul
authors.initials: P
authors.lastname: Cohen
authors.affiliation: Section of Pulmonary, Critical Care and Sleep Medicine, Bridgeport Hospital, Bridgeport, CT, USA.
authors.forename: Jeff S
authors.initials: JS
authors.lastname: Kwon
authors.affiliation: Section of Pulmonary, Critical Care and Sleep Medicine, Bridgeport Hospital, Bridgeport, CT, USA.
authors.forename: David A
authors.initials: DA
authors.lastname: Kaufman
keywords: Fibrosis; IgG4; Lung; Mass