title: A Second Case of Gobello Nevus Syndrome.
abstract: An uncommon type of epidermal nevus characterized by hyperpigmented hyperkeratotic bands following a Blaschko-linear pattern and generalized follicular hyperkeratosis were observed in a 17-year-old male patient who additionally showed tufted hair folliculitis on the scalp and clinodactyly of the fifth finger of both hands. The combination of epidermal nevus with skeletal abnormalities was first described by Gobello et al. [Dermatology 2000;201:51-55] as a new epidermal nevus syndrome that was named after the first author of this work. Our case shows identical clinical and histopathological features and represents the second case of this rare syndrome reported in the literature.
authors.affiliation: Dermatology Unit, Fondazione IRCCS Ca' Granda, Ospedale Maggiore Policlinico, University of Milan, Milan, Italy; Pediatric Highly Intensive Care Unit, Department of Pathophysiology and Transplantation, Fondazione IRCCS Ca' Granda, Ospedale Maggiore Policlinico, University of Milan, Milan, Italy.
authors.forename: Gianluca
authors.initials: G
authors.lastname: Tadini
authors.affiliation: Dermatology Unit, Fondazione IRCCS Ca' Granda, Ospedale Maggiore Policlinico, University of Milan, Milan, Italy.
authors.forename: Luisa Carlotta
authors.initials: LC
authors.lastname: Rossi
authors.affiliation: Dermatology Unit, Fondazione IRCCS Ca' Granda, Ospedale Maggiore Policlinico, University of Milan, Milan, Italy.
authors.forename: Elisa
authors.initials: E
authors.lastname: Faure
authors.affiliation: Section of Dermatology, Department of Clinical and Experimental Medicine, Parma University, Parma, Italy.
authors.forename: Francesca
authors.initials: F
authors.lastname: Besagni
authors.affiliation: Dermatology Unit, Fondazione IRCCS Ca' Granda, Ospedale Maggiore Policlinico, University of Milan, Milan, Italy.
authors.forename: Vinicio
authors.initials: V
authors.lastname: Boneschi
authors.affiliation: Pediatric Highly Intensive Care Unit, Department of Pathophysiology and Transplantation, Fondazione IRCCS Ca' Granda, Ospedale Maggiore Policlinico, University of Milan, Milan, Italy.
authors.forename: Susanna
authors.initials: S
authors.lastname: Esposito
authors.affiliation: Dermatology Unit, Fondazione IRCCS Ca' Granda, Ospedale Maggiore Policlinico, University of Milan, Milan, Italy.
authors.forename: Michela
authors.initials: M
authors.lastname: Brena
keywords: Bone abnormalities; Clinodactyly; Epidermal nevus syndrome; Follicular hyperkeratosis; Tufted hair folliculitis