title: A Young Man With Progressive Vision and Hearing Loss.
abstract: A 37-year-old man with a history of progressive bilateral sensorineural hearing loss presented to a neuro-ophthalmology clinic with an acute left homonymous hemianopsia. In this article, we discuss the clinical approach and differential diagnosis of progressive combined vision and hearing loss and guide the reader to discover the patient's ultimate diagnosis.
authors.affiliation: Department of Neurology, Washington University in St Louis, St Louis, Missouri.
authors.forename: Nathan H
authors.initials: NH
authors.lastname: Kung
authors.affiliation: Department of Neurology, Washington University in St Louis, St Louis, Missouri.
authors.forename: Robert C
authors.initials: RC
authors.lastname: Bucelli
authors.affiliation: Department of Neurology, Washington University in St Louis, St Louis, Missouri.
authors.forename: Renee B
authors.initials: RB
authors.lastname: Van Stavern
authors.affiliation: Department of Otolaryngology-Head and Neck Surgery, Washington University in St Louis, St Louis, Missouri.
authors.forename: Joel A
authors.initials: JA
authors.lastname: Goebel
authors.affiliation: Department of Ophthalmology, Washington University in St Louis, St Louis, Missouri.
authors.forename: Gregory P
authors.initials: GP
authors.lastname: Van Stavern
mesh_terms: D000328:Adult; D054062:Deaf-Blind Disorders / Q000000981:diagnostic imaging / Q000235:genetics / Q000378:metabolism / Q000628:therapy; D018450:Disease Progression; D003576:Electron Transport Complex IV / Q000378:metabolism; D006801:Humans; D008297:Male; D018485:Muscle Fibers, Skeletal / Q000378:metabolism / Q000473:pathology; D009154:Mutation / Q000235:genetics; D013385:Succinate Dehydrogenase / Q000235:genetics / Q000378:metabolism; D015898:Tomography Scanners, X-Ray Computed
chemical_list: D013385:Succinate Dehydrogenase; D003576:Electron Transport Complex IV