title: A case of portal hypertension by presumed as plexiform neurofibroma at the hepatic hilum.
abstract: Neurofibromas can occur anywhere in the body, but they usually involve the head, neck, pelvis, and extremities. Abdominal visceral involvement is rare, and intrahepatic involvement is even less common. We describe a patient who suffered from plexiform neurofibromatosis with liver involvement. A 49-year-old man, who had previously been diagnosed with neurofibromatosis, underwent esophagogastroduodenoscopy and abdominal ultrasonography for screening purposes. Esophagogastroduodenoscopy showed grade 2 esophageal varices and abdominal ultrasonography showed conglomerated nodules with echogenic appearances in the perihepatic space. Magnetic resonance imaging showed presumed plexiform neurofibroma involving the lesser sac and hepatic hilum and encasing the common hepatic artery celiac trunk and superior mesenteric artery left portal triad. We report an unusual case of portal hypertension attributed to the compressive narrowing of the portal vein by presumed as plexiform neurofibroma at the lesser sac and hepatic hilum.
authors.affiliation: Hepatology Center, Department of Internal Medicine, Bundang Jesaeng General Hospital, Seongnam, Korea.
authors.forename: Kyung Han
authors.initials: KH
authors.lastname: Lee
authors.affiliation: Hepatology Center, Department of Internal Medicine, Bundang Jesaeng General Hospital, Seongnam, Korea.
authors.forename: Sun Hong
authors.initials: SH
authors.lastname: Yoo
authors.affiliation: Hepatology Center, Department of Internal Medicine, Bundang Jesaeng General Hospital, Seongnam, Korea.
authors.forename: Gi Tark
authors.initials: GT
authors.lastname: Noh
authors.affiliation: Hepatology Center, Department of Internal Medicine, Bundang Jesaeng General Hospital, Seongnam, Korea.
authors.forename: Won Suk
authors.initials: WS
authors.lastname: Heo
authors.affiliation: Hepatology Center, Department of Internal Medicine, Bundang Jesaeng General Hospital, Seongnam, Korea.
authors.forename: Byung Seong
authors.initials: BS
authors.lastname: Ko
authors.affiliation: Hepatology Center, Department of Internal Medicine, Bundang Jesaeng General Hospital, Seongnam, Korea.
authors.forename: Jung Ah
authors.initials: JA
authors.lastname: Chio
authors.affiliation: Hepatology Center, Department of Internal Medicine, Bundang Jesaeng General Hospital, Seongnam, Korea.
authors.forename: Hyo Jin
authors.initials: HJ
authors.lastname: Cho
authors.affiliation: Hepatology Center, Department of Internal Medicine, Bundang Jesaeng General Hospital, Seongnam, Korea.
authors.forename: Jin Young
authors.initials: JY
authors.lastname: Choi
authors.affiliation: Hepatology Center, Department of Internal Medicine, Bundang Jesaeng General Hospital, Seongnam, Korea.
authors.forename: Hee Jun
authors.initials: HJ
authors.lastname: Kim
authors.affiliation: Hepatology Center, Department of Internal Medicine, Bundang Jesaeng General Hospital, Seongnam, Korea.
authors.forename: Won
authors.initials: W
authors.lastname: Sohn
authors.affiliation: Hepatology Center, Department of Internal Medicine, Bundang Jesaeng General Hospital, Seongnam, Korea.
authors.forename: Sang Jong
authors.initials: SJ
authors.lastname: Park
authors.affiliation: Hepatology Center, Department of Internal Medicine, Bundang Jesaeng General Hospital, Seongnam, Korea.
authors.forename: Young Min
authors.initials: YM
authors.lastname: Park
mesh_terms: D000005:Abdomen / Q000000981:diagnostic imaging; D016145:Endoscopy, Digestive System; D004932:Esophageal and Gastric Varices / Q000473:pathology; D006499:Hepatic Artery / Q000000981:diagnostic imaging; D006801:Humans; D006975:Hypertension, Portal / Q000175:diagnosis*; D008099:Liver / Q000000981:diagnostic imaging; D008279:Magnetic Resonance Imaging; D008297:Male; D008875:Middle Aged; D018318:Neurofibroma, Plexiform / Q000175:diagnosis* / Q000000981:diagnostic imaging; D014057:Tomography, X-Ray Computed; D014463:Ultrasonography
keywords: Esophageal varix; Plexiform neurofibroma; Portal hypertension