title: Dermatofibrosarcoma Protuberans: Insights into a Rare Soft Tissue Tumor.
abstract: Dermatofibrosarcoma protuberans (DFSP) is a rare soft tumor which originally represents a cutaneous sarcoma. It grows slowly and presents usually as nodular superficial lesion on the trunk or the extremities. Although these tumors are locally aggressive with high rate of recurrence following surgery; the prognosis is considered excellent when it is effectively treated. The radiological appearance of this tumor has rarely been studied and findings infrequently discussed in the literature probably because many lesions underwent resection before imaging. Although imaging is infrequently performed for this lesion; it can show characteristic features and demonstrate the full extent. Imaging may also play a role in the differentiation of this tumor from more serious soft tissue lesions such as more aggressive sarcomas and hemangioma. In this article, we discuss the imaging findings of DFSP that can aid in its diagnosis and its variable appearances. In addition; the clinical presentation and treatment options are also described with review of the previous literature.
authors.affiliation: Department of Radiology, Khoula Hospital, Muscat, Sultanate of Oman.
authors.forename: Aliya Sarhan
authors.initials: AS
authors.lastname: Al Barwani
authors.affiliation: Department of Radiology, Khoula Hospital, Muscat, Sultanate of Oman.
authors.forename: Sawsan
authors.initials: S
authors.lastname: Taif
authors.affiliation: Oman Medical Speciality Board, Radiology Training Program, Sultanate of Oman.
authors.forename: Reem Ahmed
authors.initials: RA
authors.lastname: Al Mazrouai
authors.affiliation: Department of Radiology, Khoula Hospital, Muscat, Sultanate of Oman.
authors.forename: Khamis Salim
authors.initials: KS
authors.lastname: Al Muzahmi
authors.affiliation: The James Cook University Hospital, South Tees Hospitals NHS, UK.
authors.forename: Asif
authors.initials: A
authors.lastname: Alrawi
keywords: Dermatofibrosarcoma protuberans; literature review; low-grade tumor; soft tissue sarcoma