title: Recurrent spontaneous scleral rupture in Marfan's syndrome.
abstract: The ocular manifestations of Marfan's syndrome (MS) range from ectopia lentis, microspherophakia, myopia, glaucoma and retinal detachment. Spontaneous scleral rupture is a rare complication and recurrent scleral perforation is extremely rare. We report a rare case of a 26-year-old male with MS who had sequential recurrent spontaneous scleral rupture which required surgical repair. He suffered from a similar problem 4 years later in both eyes in a different location, with overlying thin cystic blebs and hypotony maculopathy. Surgical repair with preserved scleral donor patch graft and conjunctival autograft in one eye, and conjunctival advancement in the other eye was performed. This helped stabilise the eyes, and resulted in complete visual recovery in both eyes.
authors.affiliation: Department of Glaucoma, L V Prasad Eye Institute, Hyderabad, Andhra Pradesh, India.
authors.forename: Kiranmaye
authors.initials: K
authors.lastname: Turaga
authors.affiliation: Department of Glaucoma, L V Prasad Eye Institute, Hyderabad, Andhra Pradesh, India.
authors.forename: Sirisha
authors.initials: S
authors.lastname: Senthil
authors.affiliation: Department of Retina and Vitreous Services, LV Prasad Eye Institute, Hyderabad, Telangana, India.
authors.forename: Subhadra
authors.initials: S
authors.lastname: Jalali
mesh_terms: D000328:Adult; D064592:Autografts; D003228:Conjunctiva / Q000637:transplantation*; D006801:Humans; D008297:Male; D008382:Marfan Syndrome / Q000150:complications*; D012422:Rupture, Spontaneous; D012590:Sclera / Q000637:transplantation*; D015422:Scleral Diseases / Q000209:etiology / Q000628:therapy*; D016896:Treatment Outcome; D014792:Visual Acuity