title: Congenital Aural Stenosis: Clinical Features and Long-term Outcomes.
abstract: The aim of the present study was to comprehensively evaluate the clinical features and long-term outcomes of congenital aural stenosis (CAS). This study presents a retrospective review of patients who underwent meatoplasty for CAS at a tertiary referral hospital from 2008 to 2015. A total of 246 meatoplasty procedures were performed on 232 patients in the present study. We performed multivariate regression analysis. Except in the age < 6 years group, no significant difference was observed among different age groups for cholesteatoma formation, p > 0.05. Except for the stenosis of the external auditory canal (EAC) (>4 mm) group, the other stenosis of EAC groups were not associated with cholesteatoma formation, p > 0.05. Postoperative air-bone gaps (ABG) less than 30 dB occurred in 77.3% (99/128) of the patients, and the Jahrsdoerfer score was associated with postoperative ABG, p < 0.001. The complication rate of CAS was 13.8% (20/144), and males showed a higher risk for postoperative complications (OR, 6.563; 95% CI, 1.268-33.966, p = 0.025). These results indicate that meatoplasty was an effective surgical intervention for CAS, showing a stable hearing outcome with prolonged follow-up. There was no significant difference between the cholesteatoma and no cholesteatoma groups for hearing outcomes, p > 0.05.
authors.affiliation: Eye &ENT Hospital, Fudan University, Department of Otolaryngology-Head and Neck Surgery, Shanghai, 200032, China.
authors.forename: Chen-Long
authors.initials: CL
authors.lastname: Li
authors.affiliation: Eye &ENT Hospital, Fudan University, Department of Otolaryngology-Head and Neck Surgery, Shanghai, 200032, China.
authors.forename: Ying
authors.initials: Y
authors.lastname: Chen
authors.affiliation: Eye &ENT Hospital, Fudan University, Department of Otolaryngology-Head and Neck Surgery, Shanghai, 200032, China.
authors.forename: Yong-Zheng
authors.initials: YZ
authors.lastname: Chen
authors.affiliation: Eye &ENT Hospital, Fudan University, Department of Otolaryngology-Head and Neck Surgery, Shanghai, 200032, China.
authors.forename: Yao-Yao
authors.initials: YY
authors.lastname: Fu
authors.affiliation: Eye &ENT Hospital, Fudan University, Department of Otolaryngology-Head and Neck Surgery, Shanghai, 200032, China.|National Ministry of Public Health, Hearing Medicine Key Laboratory, Shanghai, 200032, China.
authors.forename: Tian-Yu
authors.initials: TY
authors.lastname: Zhang
mesh_terms: D000293:Adolescent; D000328:Adult; D001301:Audiometry, Pure-Tone; D002648:Child; D002675:Child, Preschool; D018424:Cholesteatoma, Middle Ear / Q000175:diagnosis / Q000209:etiology / Q000473:pathology; D000013:Congenital Abnormalities / Q000503:physiopathology / Q000601:surgery*; D004423:Ear / Q000002:abnormalities* / Q000503:physiopathology / Q000601:surgery; D004424:Ear Canal / Q000002:abnormalities / Q000503:physiopathology / Q000601:surgery*; D005260:Female; D005500:Follow-Up Studies; D006801:Humans; D008297:Male; D008875:Middle Aged; D015999:Multivariate Analysis; D011183:Postoperative Complications; D019651:Plastic Surgery Procedures / Q000379:methods*; D016896:Treatment Outcome