title: [The differential diagnosis of Erdheim-Chester disease and IgG4-related diseases].
abstract: The paper describes Russia's first diagnosed case of Erdheim--Chester disease (systemic histiocytosis) in a 65-year-old man who has been long treated for Ormond's disease (idiopathic retroperitoneal fibrosis). It also gives the data available in the literature on the pathogenetic components of these diseases and on the similarity of many clinical, laboratory, and morphological characteristics of these two immunoinflammatory diseases and covers the issues of their differential diagnosis. Invasive procedures with a careful morphological/immunomorphological examination of biopsy specimens obtained from affected tissues are shown to be necessary for accurate diagnosis.
authors.affiliation: V.A. Nasonova Research Institute of Rheumatology, Moscow, Russia.
authors.forename: V I
authors.initials: VI
authors.lastname: Vasilyev
authors.affiliation: V.A. Nasonova Research Institute of Rheumatology, Moscow, Russia.
authors.forename: E V
authors.initials: EV
authors.lastname: Sokol
authors.affiliation: N.N. Blokhin Russian Cancer Research Center, Ministry of Health of Russia, Moscow, Russia.
authors.forename: N V
authors.initials: NV
authors.lastname: Kokosadze
authors.affiliation: N.N. Blokhin Russian Cancer Research Center, Ministry of Health of Russia, Moscow, Russia.
authors.forename: A I
authors.initials: AI
authors.lastname: Pavlovskaya
authors.affiliation: N.N. Blokhin Russian Cancer Research Center, Ministry of Health of Russia, Moscow, Russia.
authors.forename: D V
authors.initials: DV
authors.lastname: Komov
authors.affiliation: V.A. Nasonova Research Institute of Rheumatology, Moscow, Russia.
authors.forename: S G
authors.initials: SG
authors.lastname: Palshina
authors.affiliation: A.N. Bakulev Research Center of Cardiovascular Surgery, Moscow, Russia.
authors.forename: O V
authors.initials: OV
authors.lastname: Mukhortova
authors.affiliation: Research Institute of Eye Diseases, Moscow, Russia.
authors.forename: T N
authors.initials: TN
authors.lastname: Safonova
mesh_terms: D000368:Aged; D003937:Diagnosis, Differential; D003951:Diagnostic Errors; D031249:Erdheim-Chester Disease / Q000175:diagnosis*; D006801:Humans; D007074:Immunoglobulin G / Q000276:immunology*; D008297:Male; D012185:Retroperitoneal Fibrosis / Q000175:diagnosis*; D012426:Russia
chemical_list: D007074:Immunoglobulin G