Transcatheter intervention in a child with scimitar syndrome.
Scimitar syndrome is a rare congenital heart disease characterised by anomalous pulmonary venous drainage to the inferior vena cava, aortopulmonary collaterals, hypoplasia of the right lung and intracardiac defects. Surgical correction remains the gold-standard therapy. However, non-surgical intervention has been reported effective in selected cases with scimitar syndrome. We report on a one-year-old boy with scimitar syndrome who underwent stepwise transcatheter intervention as an alternative treatment. Embolisation of the aortopulmonary collaterals and occlusion of the atrial septal defect were performed using detachable coils and an Amplatzer septal occluder, respectively. The patient's postcathetherisation course was uneventful. The right cardiac chamber and pulmonary arterial pressure returned to normal during follow up.
Department of Cardiology, Guangzhou Women and Children's Medical Centre, Guangzhou, Guangdong Province, China. Email: freebirdwzp@sohu.com.
Zhouping
Z
Wang
Department of Cardiology, Guangzhou Women and Children's Medical Centre, Guangzhou, Guangdong Province, China.
Xiaoyi
X
Cai
D001011:Aorta / Q000503:physiopathology; D062186:Arterial Pressure; D006328:Cardiac Catheterization / Q000295:instrumentation; D003097:Collateral Circulation; D000072226:Computed Tomography Angiography; D004621:Embolization, Therapeutic; D006344:Heart Septal Defects, Atrial / Q000000981:diagnostic imaging / Q000503:physiopathology / Q000628:therapy*; D006801:Humans; D007223:Infant; D008297:Male; D010690:Phlebography / Q000379:methods; D011651:Pulmonary Artery / Q000000981:diagnostic imaging / Q000503:physiopathology*; D011652:Pulmonary Circulation; D011667:Pulmonary Veins / Q000002:abnormalities / Q000000981:diagnostic imaging / Q000503:physiopathology*; D020127:Recovery of Function; D012587:Scimitar Syndrome / Q000000981:diagnostic imaging / Q000503:physiopathology / Q000628:therapy*; D055989:Septal Occluder Device; D016896:Treatment Outcome