Multiple cerebral arteriovenous malformations associated to rostral hypoplasia of the superior sagittal sinus: a case report.
Multiple cerebral arteriovenous malformations (AVMs) are a rare occurrence usually associated with defined genetic disorders or a family history of cerebrovascular disease. The remaining cases cannot be associated to a genetic pathogenesis and are considered idiopathic. We report an extremely unusual case nor genetic neither idiopathic, but linked to an anatomical intracranial venous variation. The patient presented two independent frontal AVMs associated with rostral hypoplasia of the superior sagittal sinus. This anatomical variation may have induced frontal venous hypertension (VHT) triggering the development of the two AVMs. Throughout this intriguing case, we discuss the role of VHT in AVM development.
Department of Neurological Surgery, Vall d'Hebron University Hospital, Universidad Autónoma de Barcelona, Barcelona, Spain - ramtorne@me.com.
Ramon
R
Torné
Department of Neurological Surgery, Vall d'Hebron University Hospital, Universidad Autónoma de Barcelona, Barcelona, Spain.
Felipe A
FA
Molina Jaque
Department of Neurological Surgery, Vall d'Hebron University Hospital, Universidad Autónoma de Barcelona, Barcelona, Spain.
Ana
A
Rodríguez-Hernández
Department of Neurological Surgery, Vall d'Hebron University Hospital, Universidad Autónoma de Barcelona, Barcelona, Spain.
Fuat
F
Arikan
Department of Neurological Surgery, Vall d'Hebron University Hospital, Universidad Autónoma de Barcelona, Barcelona, Spain.
Diego
D
López Bermeo
Department of Neurological Surgery, Vall d'Hebron University Hospital, Universidad Autónoma de Barcelona, Barcelona, Spain.
Alejandro
A
Tomasello
D000328:Adult; D002533:Cerebral Angiography / Q000379:methods; D002561:Cerebrovascular Disorders / Q000175:diagnosis / Q000473:pathology / Q000503:physiopathology*; D004388:Dura Mater / Q000473:pathology / Q000503:physiopathology* / Q000601:surgery; D005260:Female; D006801:Humans; D002538:Intracranial Arteriovenous Malformations / Q000150:complications / Q000503:physiopathology* / Q000601:surgery; D008297:Male; D054063:Superior Sagittal Sinus / Q000000981:diagnostic imaging / Q000503:physiopathology* / Q000601:surgery; D016896:Treatment Outcome