RHEGMATOGENOUS RETINAL DETACHMENT: A RARE OCULAR MANIFESTATION OF PROTEUS SYNDROME.
OBJECTIVE
To present a case report of a rare ocular manifestation of Proteus syndrome-rhegmatogenous retinal detachment.


METHODS
Retrospective review of the patient's medical record and a review of the literature.


RESULTS
A 16-year-old boy with Proteus syndrome who presented with a total retinal detachment because of an operculated retinal tear. This patient underwent successful surgical repair of the retinal detachment and subsequent cataract surgery.


CONCLUSIONS
Proteus syndrome may be complicated by the development of rhegmatogenous retinal detachment, which can present in childhood.
Department of Ophthalmology, Addenbrooke's Hospital, Cambridge University Hospitals NHS Foundation Trust, Cambridge, United Kingdom.
Dawn S
DS
Russell-Hermanns
Douglas K
DK
Newman
D000293:Adolescent; D017679:Cryotherapy / Q000379:methods*; D058450:Endotamponade / Q000379:methods*; D006801:Humans; D008297:Male; D016715:Proteus Syndrome / Q000150:complications*; D012163:Retinal Detachment / Q000175:diagnosis / Q000209:etiology* / Q000628:therapy; D014821:Vitrectomy / Q000379:methods*