Retroperitoneal fibrosis: case series of five patients and review of the literature.
Chronic periaortitis (CP) is an umbrella term used to describe a group of nosologically allied conditions that include idiopathic retroperitoneal fibrosis (Ormond's disease), inflammatory abdominal aortic aneurysm, and perianeurysmal retroperitoneal fibrosis. Retroperitoneal fibrosis encompasses a range of diseases characterized by the presence of a fibro-inflammatory tissue, which usually surrounds the abdominal aorta and the iliac arteries and extends into the retroperitoneum to envelop neighboring structures-ureters. Retroperitoneal fibrosis is generally idiopathic, but can also be secondary to the use of certain drugs, malignant diseases, infections, and surgery. Here we describe a 5 years follow-up (2006-2011) of 5 patients admitted to our hospital with symptoms, laboratory, imaging and pathologic finding compatible with retroperitoneal fibrosis. We review our clinical course of our patient with respect to the literature.
Rheumatology Unit, Rabin Medical Center, Petach Tikva, Israel; Sackler Faculty of Medicine, Tel Aviv University, Tel Aviv, Israel. Electronic address: sofereret@gmail.com.
Shacahf
S
Shiber
Sackler Faculty of Medicine, Tel Aviv University, Tel Aviv, Israel; Department of Medicine, Rabin Medical Center, Beilinson Hospital, Petah Tikva, Israel.
Noa
N
Eliakim-Raz
Rheumatology Unit, Rabin Medical Center, Petach Tikva, Israel; Sackler Faculty of Medicine, Tel Aviv University, Tel Aviv, Israel.
Molad
M
Yair
D001012:Aorta, Abdominal; D017544:Aortic Aneurysm, Abdominal / Q000175:diagnosis* / Q000473:pathology / Q000601:surgery; D006801:Humans; D012185:Retroperitoneal Fibrosis / Q000175:diagnosis* / Q000473:pathology / Q000601:surgery*; D012187:Retroperitoneal Space
Fibrose retroperitoneal; IgG4; Insuficiência renal; Prednisona; Prednisone; Renal failure; Retroperitoneal fibrosis; Tamoxifen; Tamoxifeno