Prenatal diagnosis of persistent left and absent right superior vena cava.
We report a case of persistent left superior vena cava (LSVC) with absent right superior vena cava (RSVC) diagnosed prenatally. At 27 weeks' gestation, routine fetal ultrasonography showed an abnormal four-chamber view. Fetal echocardiography revealed a markedly enlarged coronary sinus in the four-chamber view. An absent RSVC and a persistent LSVC were demonstrated in the three-vessel view. No additional cardiac malformations were seen before birth. Postnatal imaging confirmed the prenatal diagnosis. The combination of persistent LSVC and absent RSVC without any other cardiac malformations is an extremely rare cardiac anomaly and less commonly detected in utero. Identification of a dilated coronary sinus in the four-chamber view, with atypical features in the three-vessel view, may lead to the antenatal diagnosis of this condition.
Department of Obstetrics and Gynecology, Kawasaki Municipal Hospital, 12-1 Shinkawadori, Kawasaki, Kanagawa, 210-0013, Japan. higu@kmh.gr.jp.
Takayuki
T
Higuchi
Department of Obstetrics and Gynecology, Kawasaki Municipal Hospital, 12-1 Shinkawadori, Kawasaki, Kanagawa, 210-0013, Japan.
Keiko
K
Kuroda
Department of Obstetrics and Gynecology, Kawasaki Municipal Hospital, 12-1 Shinkawadori, Kawasaki, Kanagawa, 210-0013, Japan.
Miho
M
Iida
Department of Obstetrics and Gynecology, Kawasaki Municipal Hospital, 12-1 Shinkawadori, Kawasaki, Kanagawa, 210-0013, Japan.
Yukitaka
Y
Murakoshi
Department of Pediatrics, Kawasaki Municipal Hospital, Kawasaki, Kanagawa, Japan.
Ritsuko
R
Furukawa
Department of Pediatrics, Kawasaki Municipal Hospital, Kawasaki, Kanagawa, Japan.
Megumi
M
Matsuoka
Department of Obstetrics and Gynecology, St. Marianna University School of Medicine, Kawasaki, Kanagawa, Japan.
Mamoru
M
Tanaka
Absent right superior vena cava; Fetal echocardiography; Persistent left superior vena cava