A case with double-chambered right ventricle and left ventricular-right atrial communication (Gerbode defect): potential pitfall for Eisenmenger syndrome.
The ventricular septal defect (VSD) can rarely be associated with other malformations such as double-chambered right ventricle (DCRV) in which hypertrophied muscle bundles divide the right ventricle into two chambers causing progressive obstruction (Mao et al., Asia Pac J Thorac Cardiovasc Surg 5:14-17, 1996). Most VSDs close spontaneously by apposition of the tricuspid leaflets, but the process is rarely disrupted, resulting in communication between left ventricle and right atrium called Gerbode defect [Cho et al., J Cardiovasc Ultrasound 19(3):148-151, 2011]. Hence, the Gerbode defect involves potential misinterpretation of its high-velocity shunt as pulmonary hypertension. Here we present a case with DCRV and Gerbode defect initially misdiagnosed to have Eisenmenger syndrome.
Tekirdag State Hospital, Tekirdağ, Turkey. dozkarm@yahoo.com.|, Hurriyet Mah. Kar Sokak Royal Hill Sitesi A Blok D:9, Tekirdağ, Turkey. dozkarm@yahoo.com.
Demet Ozkaramanli
DO
Gur
Department of Cardiovascular Surgery, Namık Kemal University, Tekirdağ, Turkey.
Ozcan
O
Gur
Eskisehir Sakarya Hospital, Eskisehir, Turkey.
Huseyin
H
Goksuluk
Ankara Umut Hospital, Ankara, Turkey.
Dervis
D
Oral
Double-chambered right ventricle; Eisenmenger syndrome; Gerbode defect; Pulmonary hypertension