Congenital cholesteatoma together with ossicular chain anomaly.
Cholesteatomas that occur under an intact tympanic membrane in the absence of prior surgical procedures or perforation are defined as congenital cholesteatomas. These entities are rarely seen, because they do not cause any major symptoms unless they touch the ossicular chain. Likewise, isolated congenital ossicular anomalies that occur independently of external ear anomalies and craniofacial dysplasia are also rarely seen. Here, we report a patient who presented with congenital cholesteatoma associated with anomalies of the ossicular chain and discuss its pathogenesis.
Department of Otolaryngology-Head and Neck Surgery, Baskent University, Ankara, Turkey. leylakansu@hotmail.com.|Department of Otolaryngology-Head and Neck Surgery, Alanya Medical and Research Center, Baskent University, Alanya, Antalya, Turkey. leylakansu@hotmail.com.
Leyla
L
Kansu
Department of Otolaryngology-Head and Neck Surgery, Baskent University, Ankara, Turkey.
Levent N
LN
Ozluoglu
D018424:Cholesteatoma, Middle Ear / Q000150:complications / Q000151:congenital / Q000175:diagnosis*; D004429:Ear Ossicles / Q000002:abnormalities*; D005260:Female; D006801:Humans; D055815:Young Adult
Conductive hearing loss; Congenital cholesteatoma; Ossicular chain anomalies; Stapes agenesis