Displacement of the anterior leaflet of the tricuspid valve: Rare variant of Ebstein's anomaly.
In Ebstein's anomaly, the points of attachment, or hinges, of the septal and mural leaflets in the right ventricle are displaced away from the atrioventricular junction. In contrast, the junctional hinge of the anterior leaflet usually retains a normal position. Here, we report a case of giant right atrial aneurysm due to isolated displacement of the anterior leaflet of the tricuspid valve in an infant, a rare variant of Ebstein's anomaly. Enlargement of the right atrium, which was initially diagnosed during the fetal period, progressively and markedly dilated after birth and was successfully treated with surgical resection. Isolated displacement of the anterior leaflet should be recognized as a variant of Ebstein's anomaly.
Department of Pediatric Cardiology, National Cerebral and Cardiovascular Center, Osaka, Japan.|Department of Pediatrics, Nara Medical University, Nara, Japan.
Nobuyuki
N
Tsujii
Department of Pediatric Cardiology, National Cerebral and Cardiovascular Center, Osaka, Japan.
Kenichi
K
Kurosaki
Department of Pediatric Cardiology, National Cerebral and Cardiovascular Center, Osaka, Japan.
Kenji
K
Yasuda
Department of Pediatric Cardiology, National Cerebral and Cardiovascular Center, Osaka, Japan.
Masanori
M
Mizuno
Department of Pediatric Cardiology, National Cerebral and Cardiovascular Center, Osaka, Japan.
Heima
H
Sakaguchi
Department of Pediatric Cardiac Surgery, National Cerebral and Cardiovascular Center, Osaka, Japan.
Takaya
T
Hoashi
Department of Pediatric Cardiac Surgery, National Cerebral and Cardiovascular Center, Osaka, Japan.
Hajime
H
Ichikawa
Department of Pediatric Cardiology, National Cerebral and Cardiovascular Center, Osaka, Japan.
Isao
I
Shiraishi
D000328:Adult; D000792:Angiography; D006328:Cardiac Catheterization; D006348:Cardiac Surgical Procedures; D004437:Ebstein Anomaly / Q000175:diagnosis* / Q000196:embryology / Q000601:surgery; D004452:Echocardiography; D005260:Female; D006325:Heart Atria / Q000002:abnormalities / Q000000981:diagnostic imaging*; D006352:Heart Ventricles / Q000002:abnormalities / Q000000981:diagnostic imaging*; D006801:Humans; D007231:Infant, Newborn; D008297:Male; D011296:Prenatal Diagnosis; D014261:Tricuspid Valve / Q000002:abnormalities* / Q000000981:diagnostic imaging
Ebstein's anomaly; anterior leaflet; atrial aneurysm; variant