Ewing Sarcoma of the External Ear Canal.
Background. Ewing sarcoma (ES) is a high-grade malignant tumor that has skeletal and extraskeletal forms and consists of small round cells. In the head and neck region, reported localization of extraskeletal ES includes the larynx, thyroid gland, submandibular gland, nasal fossa, pharynx, skin, and parotid gland, but not the external ear canal. Methods. We present the unique case of a 2-year-old boy with extraskeletal ES arising from the external ear canal, mimicking auricular hematoma. Results. Surgery was performed and a VAC/IE (vincristine, adriamycin, cyclophosphamide alternating with ifosfamide, and etoposide) regimen was used for adjuvant chemotherapy for 12 months. Conclusion. The clinician should consider extraskeletal ES when diagnosing tumors localized in the head and neck region because it may be manifested by a nonspecific clinical picture mimicking common otorhinolaryngologic disorders.
Department of Otorhinolaryngology-Head and Neck Surgery, Marmara University Pendik Training and Research Hospital, 34899 Istanbul, Turkey.
Adem
0000-0002-2797-0248
A
Binnetoglu
Department of Otorhinolaryngology-Head and Neck Surgery, Marmara University Pendik Training and Research Hospital, 34899 Istanbul, Turkey.
Tekin
0000-0001-5056-6852
T
Baglam
Department of Pediatric Oncology Clinic, Marmara University Pendik Training and Research Hospital, 34899 Istanbul, Turkey.
Gulnur
0000-0001-5291-2923
G
Tokuc
Department of Pediatrics, Marmara University Pendik Training and Research Hospital, 34899 Istanbul, Turkey.
Kiymet
K
Kecelioglu Binnetoglu
Department of Pathology, Marmara University Pendik Training and Research Hospital, 34899 Istanbul, Turkey.
Fatma
F
Gerin
Department of Otorhinolaryngology-Head and Neck Surgery, Marmara University Pendik Training and Research Hospital, 34899 Istanbul, Turkey.
Murat
M
Sari