Ameloblastic Fibrosarcoma Arising in the Maxilla.
BACKGROUND
Ameloblastic fibrosarcoma (AFS) is a rare odontogenic neoplasm of the jaw that usually arises de novo or through a malignant change in the mesenchymal component of a preexisting or recurrent benign fibroma. The majority of AFS cases reported in the literature arise in the mandible.


METHODS
A 35-year-old male presented with an asymptomatic left maxillary mass that on imaging was found to be effacing most of his maxillary sinus. He underwent a left maxillectomy with free-flap reconstruction and adjuvant radiotherapy to the tumor bed.


CONCLUSIONS
Wide local excision remains the treatment of choice for AFS, given the poor survival rates of patients with recurrent disease. However, long-term studies and follow-up are needed to elucidate the role of adjuvant therapies in the primary treatment of AFS.
Department of Maxillofacial Surgery, Royal Brisbane and Women's Hospital, Herston, Queensland, Australia; Translational Research Institute - Diamantina Institute, The University of Queensland, Woolloongabba, Queensland, Australia.
Rachael R
RR
Pillay
Department of Maxillofacial Surgery, Lismore Base Hospital, Lismore, Queensland, Australia.
Arthur
A
Bilski
Department of Maxillofacial Surgery, Royal Brisbane and Women's Hospital, Herston, Queensland, Australia.
Martin
M
Batstone
Ameloblasts; fibrosarcoma; maxilla; odontogenic tumors