title: [Birdshot retinochoroidopathy: Key messages].
abstract: Birdshot retinochoroidopathy (BRC) is a potentially blinding posterior autoimmune uveitis that affects Caucasian patients in their fifties. Strongly associated with the HLA A 29 phenotype, BRC is characterized by the presence of suggestive choroidal lesions on the fundus, but their apparition can be delayed. Visual acuity is not a good descriptive factor of visual function. Ancillary tests can therefore help establish the diagnosis and allow proper follow-up of BRC patients: optical coherence tomography can reveal either oedema or atrophy of the macula. Fluorescein and infracyanine green angiograms can show signs of inflammatory activity and give further diagnostic clues. Electroretinograms and visual fields can be useful for the diagnosis and follow-up. BCR patients should be examined periodically and undergo exhaustive clinical and paraclinical tests to insure the best prognosis. Corticosteroids should be associated with immunosuppressive treatments as early as possible in the presence of factors that are predictive of the worse prognoses.
authors.affiliation: Service d'ophtalmologie, hôpital de la Pitié Salpêtrière, centre de référence des maladies rares, université Paris VI, DHU « Sight Restore », 47-83, boulevard de l'Hôpital, 75013, Paris, France. Electronic address: saratouhami@gmail.com.
authors.forename: S
authors.initials: S
authors.lastname: Touhami
authors.affiliation: Service d'ophtalmologie, hôpital de la Pitié Salpêtrière, centre de référence des maladies rares, université Paris VI, DHU « Sight Restore », 47-83, boulevard de l'Hôpital, 75013, Paris, France.
authors.forename: C
authors.initials: C
authors.lastname: Fardeau
authors.affiliation: Service d'ophtalmologie, centre hospitalier intercommunal de Créteil, 40, avenue de Verdun, 94000, Créteil, France.
authors.forename: O
authors.initials: O
authors.lastname: Zambrowski
authors.affiliation: Service d'ophtalmologie, CHNO Quinze-Vingts, 28, rue de Charenton, 75012 Paris, France.
authors.forename: C
authors.initials: C
authors.lastname: Bonnet
authors.affiliation: Service d'ophtalmologie, hôpital de la Pitié Salpêtrière, centre de référence des maladies rares, université Paris VI, DHU « Sight Restore », 47-83, boulevard de l'Hôpital, 75013, Paris, France.
authors.forename: B
authors.initials: B
authors.lastname: Bodaghi
authors.affiliation: Service d'ophtalmologie, hôpital de la Pitié Salpêtrière, centre de référence des maladies rares, université Paris VI, DHU « Sight Restore », 47-83, boulevard de l'Hôpital, 75013, Paris, France.
authors.forename: V
authors.initials: V
authors.lastname: Touitou
authors.affiliation: Service d'ophtalmologie, hôpital de la Pitié Salpêtrière, centre de référence des maladies rares, université Paris VI, DHU « Sight Restore », 47-83, boulevard de l'Hôpital, 75013, Paris, France.
authors.forename: P
authors.initials: P
authors.lastname: Lehoang
mesh_terms: D002833:Choroiditis / Q000175:diagnosis / Q000453:epidemiology / Q000209:etiology / Q000628:therapy; D004596:Electroretinography; D005451:Fluorescein Angiography; D005654:Fundus Oculi; D006801:Humans; D000080364:Multifocal Choroiditis; D041623:Tomography, Optical Coherence; D014792:Visual Acuity; D058609:Visual Field Tests
keywords: Acuité visuelle; Angiogram; Angiographie; Birdshot retinochoroidopathy; Champs visuels; Electro-oculogram; Electroretinogram; Inflammation; Optical coherence tomography; Perimetry; Rétinochoroïdopathie de Birdshot; Tomographie par cohérence optique; Uveitis; Uvéite; Visual acuity; Électro-oculographie; Électrorétinographie