title: Anaesthetic Management of a Patient with Hereditary Angioedema.
abstract: Hereditary angioedema (HAE) is a rare autosomal dominant disorder caused by reduced activity of the C1 esterase inhibitor. Clinically, angioedema most often involves the upper extremities, face, neck and larynx. The most common cause of death is asphyxia related to laryngeal oedema. Attacks are triggered by many factors such as trauma, stress, infections and hormonal fluctuations. C1 esterase inhibitor concentrates, fresh frozen plasma (FFP), androgen steroids, quinine pathway inhibitors and antifibrinolytics can be used as treatment. In this case report, the anaesthetic management of a patient with hereditary angioedema undergoing laminectomy surgery is reported.
authors.affiliation: Department of Anaesthesiology and Reanimation, Çukurova University Faculty of Medicine, Adana, Turkey.
authors.forename: Mediha
authors.initials: M
authors.lastname: Türktan
authors.affiliation: Department of Anaesthesiology and Reanimation, Çukurova University Faculty of Medicine, Adana, Turkey.
authors.forename: Ersel
authors.initials: E
authors.lastname: Güleç
authors.affiliation: Department of Anaesthesiology and Reanimation, Çukurova University Faculty of Medicine, Adana, Turkey.
authors.forename: Zehra
authors.initials: Z
authors.lastname: Hatipoğlu
authors.affiliation: Department of Anaesthesiology and Reanimation, Çukurova University Faculty of Medicine, Adana, Turkey.
authors.forename: Çağatay
authors.initials: Ç
authors.lastname: Küçükbingöz
authors.affiliation: Department of Paediatric Allergy and Immunology, Çukurova University Faculty of Medicine, Adana, Turkey.
authors.forename: Mustafa
authors.initials: M
authors.lastname: Yılmaz
authors.affiliation: Department of Anaesthesiology and Reanimation, Çukurova University Faculty of Medicine, Adana, Turkey.
authors.forename: Yasemin
authors.initials: Y
authors.lastname: Güneş
keywords: C1 esterase inhibitor; Hereditary angioedema; laminectomy