title: Anaesthesia Management and Use of Sugammadex in a Patient with Ullrich's Disease.
abstract: Here, we report anaesthesia management and the successful use of total intravenous anaesthesia and sugammadex in a patient with Ullrich's disease. Propofol and remifentanyl infusion was used for anaesthesia. After the end of the surgery, when the train-of-four value was 0%, 4 mg kg(-1) sugammadex was administered, and the patient was successfully extubated after 36 s. No adverse effects or safety concerns were observed. In conclusion, we suggest that the use of propofol infusion to avoid the use of inhalation anaesthetics and the use of sugammadex for the reversal of the effects of rocuronium is safe in patients with Ullrich's disease.
authors.affiliation: Department of Anaesthesiology and Reanimation, İstanbul University Cerrahpaşa Faculty of Medicine, İstanbul, Turkey.
authors.forename: Emre
authors.initials: E
authors.lastname: Erbabacan
authors.affiliation: Department of Anaesthesiology and Reanimation, İstanbul University Cerrahpaşa Faculty of Medicine, İstanbul, Turkey.
authors.forename: Güniz M
authors.initials: GM
authors.lastname: Köksal
authors.affiliation: Department of Anaesthesiology and Reanimation, İstanbul University Cerrahpaşa Faculty of Medicine, İstanbul, Turkey.
authors.forename: Tuğçe Barça
authors.initials: TB
authors.lastname: Şeker
authors.affiliation: Department of Anaesthesiology and Reanimation, İstanbul University Cerrahpaşa Faculty of Medicine, İstanbul, Turkey.
authors.forename: Birsel
authors.initials: B
authors.lastname: Ekici
authors.affiliation: Department of Paediatric Surgery, İstanbul University Cerrahpaşa Faculty of Medicine, İstanbul, Turkey.
authors.forename: Rahsan
authors.initials: R
authors.lastname: Özcan
authors.affiliation: Department of Anaesthesiology and Reanimation, İstanbul University Cerrahpaşa Faculty of Medicine, İstanbul, Turkey.
authors.forename: Fatiş
authors.initials: F
authors.lastname: Altindaş
keywords: Sugammadex; muscular dystrophy; total intravenous anaesthesia