title: Multiple pterygium syndrome: Challenge for anesthesiologist.
abstract: Multiple pterygium syndrome (MPS) is a very rare autosomal recessive disorder characterized by flexion of joint and digit contractures, skin webbing, cleft palate, deformity of the spine, and cervical spine fusion. Difficult airway is associated mainly due to micrognathia, retrognathia, webbing of the neck, and limitation of the mouth opening and neck extension. We are reporting a case of a 5-year-old female diagnosed with MPS and exhibiting a bilateral club foot and congenital vertical talus. The patient was posted for manipulation and above the knee casting under general anesthesia.
authors.affiliation: Department of Anesthesia and Critical Care, All India Institute of Medical Sciences, Jodhpur, Rajasthan, India.
authors.forename: P
authors.initials: P
authors.lastname: Sethi
authors.affiliation: Department of Anesthesia and Critical Care, All India Institute of Medical Sciences, Jodhpur, Rajasthan, India.
authors.forename: P K
authors.initials: PK
authors.lastname: Bhatia
authors.affiliation: Department of Pediatrics, All India Institute of Medical Sciences, Jodhpur, Rajasthan, India.
authors.forename: N
authors.initials: N
authors.lastname: Gupta
authors.affiliation: Department of Pediatrics, All India Institute of Medical Sciences, Jodhpur, Rajasthan, India.
authors.forename: K
authors.initials: K
authors.lastname: Singh
keywords: Anesthesia; challenges; multiple pterygium syndrome