title: Cerebellospinal hemangioblastoma with bilateral pheochromocytoma and hepatic cyst: A rare entity.
abstract: A 45-year-old gentleman presented with headache, dizziness, and unsteadiness of gait. On imaging, he was found to have a cerebellar and a spinal intramedullary hemangioblastoma. To rule out Von Hippel-Lindau (VHL) disease, we did screening of the whole abdomen with ultrasonography followed by contrast-enhanced computed tomography of the abdomen, and surprisingly, the patient was having bilateral adrenal pheochromocytoma and a hepatic cyst. A diagnosis of VHL disease was made on this basis. The patient was operated and he made a very good recovery. We are reporting this interesting case because of its typical findings and its rarity. Disease management and review of literature were also discussed at the end.
authors.affiliation: Department of Neurosurgery, Gauhati Medical College, Guwahati, Assam, India.
authors.forename: Mrinal
authors.initials: M
authors.lastname: Bhuyan
authors.affiliation: Department of Neurosurgery, Gauhati Medical College, Guwahati, Assam, India.
authors.forename: Deep
authors.initials: D
authors.lastname: Dutta
authors.affiliation: Department of Neurosurgery, Gauhati Medical College, Guwahati, Assam, India.
authors.forename: Basanta Kumar
authors.initials: BK
authors.lastname: Baishya
authors.affiliation: Department of Neurosurgery, Gauhati Medical College, Guwahati, Assam, India.
authors.forename: Zakir
authors.initials: Z
authors.lastname: Hussain
keywords: Cerebellospinal; Von Hippel–Lindau disease; hemangioblastoma