title: The Importance of Esophagography in Patients With Recessive Dystrophic Epidermolysis Bullosa.
abstract: OBJECTIVE
  The purpose of this study was to assess esophageal damage in patients with recessive dystrophic epidermolysis bullosa (RDEB) with or without dysphagia.
  
  
  METHODS
  Fourteen patients with either severe generalized or another generalized form of RDEB recruited through a research and support foundation were evaluated for obstructive esophageal lesions by means of barium esophagography.
  
  
  RESULTS
  All patients, even those without dysphagia, had at least one stenosis; five patients had two stenoses. Stenotic lesions occurred most often (74%) in the upper third of the esophagus.
  
  
  CONCLUSIONS
  Esophageal stenosis is a common complication in patients with RDEB, even when they do not have dysphagia. We recommend regular esophagographic examinations of all patients with RDEB.
authors.affiliation: 1 Departamento de Radiología, Dr. Jose E. Gonzalez University Hospital of the Facultad de Medicina of the Universidad Autónoma de Nuevo León, Monterrey, Mexico.
authors.forename: Jesus Dante
authors.initials: JD
authors.lastname: Guerra-Leal
authors.affiliation: 2 Basic Sciences Department, Medical School, Universidad de Monterrey, Av. Ignacio Morones Prieto 4500 Pte., 66238, San Pedro Garza García, Nuevo León, México.
authors.forename: Irene
authors.initials: I
authors.lastname: Meester
authors.affiliation: 1 Departamento de Radiología, Dr. Jose E. Gonzalez University Hospital of the Facultad de Medicina of the Universidad Autónoma de Nuevo León, Monterrey, Mexico.
authors.forename: Juan Ramon
authors.initials: JR
authors.lastname: Cantu-Gonzalez
authors.affiliation: 1 Departamento de Radiología, Dr. Jose E. Gonzalez University Hospital of the Facultad de Medicina of the Universidad Autónoma de Nuevo León, Monterrey, Mexico.
authors.forename: Gerardo
authors.initials: G
authors.lastname: Ornelas-Cortinas
authors.affiliation: 1 Departamento de Radiología, Dr. Jose E. Gonzalez University Hospital of the Facultad de Medicina of the Universidad Autónoma de Nuevo León, Monterrey, Mexico.
authors.forename: Alberto
authors.initials: A
authors.lastname: Montemayor-Martinez
authors.affiliation: 2 Basic Sciences Department, Medical School, Universidad de Monterrey, Av. Ignacio Morones Prieto 4500 Pte., 66238, San Pedro Garza García, Nuevo León, México.
authors.forename: Julio C
authors.initials: JC
authors.lastname: Salas-Alanis
keywords: dystrophic epidermolysis bullosa; esophageal stenosis; esophagography