title: A single-center experience with undifferentiated embryonal sarcoma of the liver.
abstract: Undifferentiated embryonal sarcoma of the liver (UESL) is a rare aggressive mesenchymal pediatric tumor. Previously, reported outcomes have been very poor. Here, we report a single-center experience of five patients with UESL treated with upfront gross total resection and adjuvant chemotherapy. We have a median follow-up of 8 years with a range from 5 to 19 years with 100% event-free survival.
authors.affiliation: Department of Pediatrics, Memorial Sloan Kettering Cancer Center, New York City, New York. mathiasm@mskcc.org.
authors.forename: Melissa D
authors.initials: MD
authors.lastname: Mathias
authors.affiliation: Department of Pediatrics, Memorial Sloan Kettering Cancer Center, New York City, New York.
authors.forename: Srikanth R
authors.initials: SR
authors.lastname: Ambati
authors.affiliation: Department of Pediatrics, Memorial Sloan Kettering Cancer Center, New York City, New York.
authors.forename: Alexander J
authors.initials: AJ
authors.lastname: Chou
authors.affiliation: Department of Pediatrics, Memorial Sloan Kettering Cancer Center, New York City, New York.
authors.forename: Emily K
authors.initials: EK
authors.lastname: Slotkin
authors.affiliation: Department of Pediatrics, Memorial Sloan Kettering Cancer Center, New York City, New York.
authors.forename: Leonard H
authors.initials: LH
authors.lastname: Wexler
authors.affiliation: Department of Pediatrics, Memorial Sloan Kettering Cancer Center, New York City, New York.
authors.forename: Paul A
authors.initials: PA
authors.lastname: Meyers
authors.affiliation: Department of Pediatrics, Memorial Sloan Kettering Cancer Center, New York City, New York.
authors.forename: Heather
authors.initials: H
authors.lastname: Magnan
mesh_terms: D000293:Adolescent; D002648:Child; D002675:Child, Preschool; D005260:Female; D006801:Humans; D008113:Liver Neoplasms / Q000628:therapy*; D008297:Male; D009373:Neoplasms, Germ Cell and Embryonal / Q000628:therapy*; D012509:Sarcoma / Q000628:therapy*
keywords: case series; sarcoma; undifferentiated embryonal sarcoma of the liver