title: A Rare Case of a Recurrent Giant Solitary Fibrous Tumor of the Ciliary Body of the Orbit.
abstract: Solitary fibrous tumors (SFTs) are uncommon spindle-cell tumors of mesenchymal origin initially described in the pleura and subsequently in other extra-pleural sites. These tumors are categorized as tumors of 'intermediate malignancy' under the World Health Organization classification of soft tissue tumors. SFT was virtually non-existent or misdiagnosed until its characteristic features, particularly the strong and diffuse immuno-reactivity to CD 34 were described. Extra-pleural manifestations of SFT, particularly in the head and neck region are rare. Although a number of isolated case reports of orbital SFTs have been described ever since its initial description in 1994, cases of recurrent SFTs have been very few. Recurrences of these tumors following surgery are considered unusual and metastasis exceptional. We describe clinical presentation and the management challenges of recurrent giant orbital SFT in a 15-year old girl along with a brief review of literature.
authors.affiliation: Cancer Institute (WIA), 38, Sardar Patel Rd, Adyar, Chennai, 600036 India.
authors.forename: Arvind
authors.initials: A
authors.lastname: Krishnamurthy
authors.affiliation: Cancer Institute (WIA), 38, Sardar Patel Rd, Adyar, Chennai, 600036 India.
authors.forename: Shirley Sundar
authors.initials: SS
authors.lastname: Singh
authors.affiliation: Cancer Institute (WIA), 38, Sardar Patel Rd, Adyar, Chennai, 600036 India.
authors.forename: Urmila
authors.initials: U
authors.lastname: Majhi
authors.affiliation: Cancer Institute (WIA), 38, Sardar Patel Rd, Adyar, Chennai, 600036 India.
authors.forename: Vijayalakshmi
authors.initials: V
authors.lastname: Ramshankar
authors.affiliation: Cancer Institute (WIA), 38, Sardar Patel Rd, Adyar, Chennai, 600036 India.
authors.forename: Arvind
authors.initials: A
authors.lastname: Krishnamurthy
keywords: Ciliary body tumor; Local recurrence; Orbital tumors; Solitary fibrous tumor