title: [Melkersson Rosenthal syndrome. Report of two pediatric cases].
abstract: Melkersson Rosenthal syndrome is a very infrequent disease of unknown etiology, chronic and progressive course, with neurocutaneous disease that affects the orofacial innervation and mucocutaneous tissues with non-caseating granulomatous infiltration. Clinically, it is characterized by the diagnostic triad: recurrent edema of lips and/or face; recurrent and alternating acute peripheral facial paralysis and scrotal or geographic tongue. The condition generally presents as oligosymptomatic or monosymptomatic form. Two patients are presented with completed triad and oligosymptomatic form. This recent review published by G. Kayabasoglu et al. states that only 30 patients have been described in the international literature in childhood. So we consider this disease in the differential diagnosis in the presence of acute peripheral facial paralysis and/or lips or facial edema.
authors.affiliation: Residencia de Otorrinolaringología Infantil, Hospital General de Niños Pedro de Elizalde, Ciudad Autónoma de Buenos Aires, Argentina.
authors.forename: Lucas
authors.initials: L
authors.lastname: Bordino
authors.affiliation: División de Otorrinolaringología, Hospital General de Niños Pedro de Elizalde, Ciudad Autónoma de Buenos Aires, Argentina.
authors.forename: Mariana L
authors.initials: ML
authors.lastname: Juchli
authors.affiliation: Servicio de Odontología, Hospital General de Niños Pedro de Elizalde, Ciudad Autónoma de Buenos Aires, Argentina.
authors.forename: Marcelo
authors.initials: M
authors.lastname: Fernández
authors.affiliation: División de Otorrinolaringología, Hospital General de Niños Pedro de Elizalde, Ciudad Autónoma de Buenos Aires, Argentina.
authors.forename: María de Los Ángeles
authors.initials: Mde L
authors.lastname: Fitz Maurice
authors.affiliation: Residencia de Otorrinolaringología Infantil, Hospital General de Niños Pedro de Elizalde, Ciudad Autónoma de Buenos Aires, Argentina.
authors.forename: Andrea
authors.initials: A
authors.lastname: Martins
authors.affiliation: División de Otorrinolaringología, Hospital General de Niños Pedro de Elizalde, Ciudad Autónoma de Buenos Aires, Argentina.
authors.forename: Zaida E
authors.initials: ZE
authors.lastname: Ramírez
authors.affiliation: Residencia de Otorrinolaringología Infantil, Hospital General de Niños Pedro de Elizalde, Ciudad Autónoma de Buenos Aires, Argentina.
authors.forename: Roxana
authors.initials: R
authors.lastname: Spini
mesh_terms: D002648:Child; D005260:Female; D006801:Humans; D008297:Male; D008556:Melkersson-Rosenthal Syndrome / Q000175:diagnosis*
keywords: Facial paralysis; Geographic tongue; Melkersson-Rosenthal syndrome; Recurrence