title: Congenital afibrinogenemia: a case report of a spontaneous hepatic hematoma.
abstract: BACKGROUND
  Afibrinogenemia is a rare coagulation disorder. Clinical features of spontaneous bleeding, bleeding after minor trauma, or after surgery have been described as well as thrombo-embolic complications. In this article, we presented the case of a 19-year old female with congenital afibrinogenemia who was admitted with a spontaneous intrahepatic hematoma.
  
  
  CONCLUSIONS
  Supportive treatment including transfusion and fibrinogen administration, associated with repeated packing surgeries and selective embolization, were successfully performed.
authors.affiliation: Surgical Intensive Care Unit Department of Digestive and Metabolic Surgery Department of Radiology, Amiens Picardy University Hospital INSERM U1088, University of Picardy Jules Verne, Amiens, France.
authors.forename: Stephanie
authors.initials: S
authors.lastname: Malaquin
authors.forename: Lionel
authors.initials: L
authors.lastname: Rebibo
authors.forename: Cyril
authors.initials: C
authors.lastname: Chivot
authors.forename: Louise
authors.initials: L
authors.lastname: Badoux
authors.forename: Yazine
authors.initials: Y
authors.lastname: Mahjoub
authors.forename: Herve
authors.initials: H
authors.lastname: Dupont
mesh_terms: D000347:Afibrinogenemia / Q000150:complications* / Q000151:congenital; D005260:Female; D006406:Hematoma / Q000175:diagnosis / Q000209:etiology* / Q000601:surgery; D006801:Humans; D008107:Liver Diseases / Q000175:diagnosis / Q000209:etiology* / Q000601:surgery; D055815:Young Adult