title: Liver and lung transplantation in cystic fibrosis: an adult cystic fibrosis centre's experience.
abstract: Liver disease develops in one-third of patients with cystic fibrosis (CF). It is rare for liver disease to have its onset after 20 years of age. Lung disease, however, is usually more severe in adulthood. A retrospective analysis was performed on nine patients. Three patients required lung transplantation approximately a decade after liver transplant, and another underwent combined liver and lung transplants. Four additional patients with liver transplants are awaiting assessment for lung transplants. One patient is awaiting combined liver and lung transplants. With increased survival in CF, several patients may require more than single organ transplantation.
authors.affiliation: Department of Respiratory and Sleep Medicine, Royal Prince Alfred Hospital, Camperdown, New South Wales, Australia.|Sydney Medical School, University of Sydney, Sydney, New South Wales, Australia.
authors.forename: S
authors.initials: S
authors.lastname: Sivam
authors.affiliation: Department of Respiratory and Sleep Medicine, Royal Prince Alfred Hospital, Camperdown, New South Wales, Australia.|Sydney Medical School, University of Sydney, Sydney, New South Wales, Australia.
authors.forename: Y
authors.initials: Y
authors.lastname: Al-Hindawi
authors.affiliation: Department of Respiratory and Sleep Medicine, Royal Prince Alfred Hospital, Camperdown, New South Wales, Australia.|Sydney Medical School, University of Sydney, Sydney, New South Wales, Australia.
authors.forename: J
authors.initials: J
authors.lastname: Di Michiel
authors.affiliation: Department of Respiratory and Sleep Medicine, Royal Prince Alfred Hospital, Camperdown, New South Wales, Australia.|Sydney Medical School, University of Sydney, Sydney, New South Wales, Australia.
authors.forename: C
authors.initials: C
authors.lastname: Moriarty
authors.affiliation: Lung Transplantation Unit, St Vincent's Hospital, Sydney, New South Wales, Australia.
authors.forename: P
authors.initials: P
authors.lastname: Spratt
authors.affiliation: Lung Transplantation Unit, St Vincent's Hospital, Sydney, New South Wales, Australia.
authors.forename: P
authors.initials: P
authors.lastname: Jansz
authors.affiliation: Lung Transplantation Unit, St Vincent's Hospital, Sydney, New South Wales, Australia.
authors.forename: M
authors.initials: M
authors.lastname: Malouf
authors.affiliation: Lung Transplantation Unit, St Vincent's Hospital, Sydney, New South Wales, Australia.
authors.forename: M
authors.initials: M
authors.lastname: Plit
authors.affiliation: Sydney Medical School, University of Sydney, Sydney, New South Wales, Australia.|Liver Transplant Unit, Royal Prince Alfred Hospital, Camperdown, New South Wales, Australia.
authors.forename: H
authors.initials: H
authors.lastname: Pleass
authors.affiliation: Lung Transplantation Unit, St Vincent's Hospital, Sydney, New South Wales, Australia.
authors.forename: A
authors.initials: A
authors.lastname: Havryk
authors.affiliation: Sydney Medical School, University of Sydney, Sydney, New South Wales, Australia.|AW Morrow Gastroenterology and Liver Centre, Royal Prince Alfred Hospital, Camperdown, New South Wales, Australia.
authors.forename: D
authors.initials: D
authors.lastname: Bowen
authors.affiliation: Sydney Medical School, University of Sydney, Sydney, New South Wales, Australia.|Department of Addiction Medicine, Royal Prince Alfred Hospital, Sydney, New South Wales, Australia.
authors.forename: P
authors.initials: P
authors.lastname: Haber
authors.affiliation: Lung Transplantation Unit, St Vincent's Hospital, Sydney, New South Wales, Australia.
authors.forename: A R
authors.initials: AR
authors.lastname: Glanville
authors.affiliation: Department of Respiratory and Sleep Medicine, Royal Prince Alfred Hospital, Camperdown, New South Wales, Australia.|Sydney Medical School, University of Sydney, Sydney, New South Wales, Australia.
authors.forename: P T P
authors.initials: PT
authors.lastname: Bye
mesh_terms: D000293:Adolescent; D000328:Adult; D001315:Australia; D002648:Child; D003550:Cystic Fibrosis / Q000150:complications* / Q000601:surgery*; D005260:Female; D006801:Humans; D008107:Liver Diseases / Q000601:surgery*; D008111:Liver Function Tests; D016031:Liver Transplantation; D016040:Lung Transplantation; D008297:Male; D012129:Respiratory Function Tests; D012189:Retrospective Studies; D055815:Young Adult
keywords: cystic fibrosis; liver function test; liver transplantation; lung function test; lung transplantation