title: Adult suprapatellar pleiomorphic rhabdomyosarcoma with jejunal metastasis causing intussusception: a case report.
abstract: Jejuno-jejunal intussusception is rarely encountered in adults. Management depends on the viability of the involved bowel. Exploration is favored because in adults generally an underlying 'lead point' is found to be present. Pleimorphic rhabdomyosarcoma (pRMS) arises from striated muscle cells. They are usually diagnosed during childhood and can occur virtually all over the body, controversially in places were few striated cells are found. In adults, these tumors are rare and are mostly encountered in the head-and-neck region. We present the case of a 48-year-old woman with a jejunal metastasis from a suprapatellar pRMS diagnosed 2.5 years earlier resulting in a jejuno-jejunal intussusception.
authors.affiliation: a Dienst Abdominale, Kinder- en Reconstructieve Heelkunde, UZA , Antwerpen , België.
authors.forename: Ben
authors.initials: B
authors.lastname: Gys
authors.affiliation: b Dienst Pathologische Anatomie, UZA , Antwerpen , België.
authors.forename: Dieter
authors.initials: D
authors.lastname: Peeters
authors.affiliation: c Dienst Pathologische Anatomie, UZA en Universiteit Antwerpen , Antwerpen , België.
authors.forename: Ann
authors.initials: A
authors.lastname: Driessen
authors.affiliation: d Dienst Radiologie, UZA , Antwerpen , België.
authors.forename: Annemie
authors.initials: A
authors.lastname: Snoeckx
authors.affiliation: a Dienst Abdominale, Kinder- en Reconstructieve Heelkunde, UZA , Antwerpen , België.
authors.forename: Niels
authors.initials: N
authors.lastname: Komen
mesh_terms: D001706:Biopsy; D001859:Bone Neoplasms / Q000473:pathology*; D005260:Female; D006801:Humans; D007443:Intussusception / Q000175:diagnosis / Q000209:etiology*; D007580:Jejunal Neoplasms / Q000150:complications / Q000175:diagnosis / Q000556:secondary*; D008875:Middle Aged; D012208:Rhabdomyosarcoma / Q000150:complications / Q000175:diagnosis / Q000556:secondary*; D014057:Tomography, X-Ray Computed
keywords: Metastasis; intussusception; sarcoma