title: Hypotonic maculopathy secondary to scleral defect in atypical retinochoroidal coloboma.
abstract: OBJECTIVE
  To describe a patient with unilateral hypotonic maculopathy and optic disc edema after spontaneous bulbar perforation of a full-thickness scleral defect.
  
  
  METHODS
  An 11-year-old girl underwent scleral buckling surgery. Preoperative and postoperative evaluation included optical coherence tomography and high-resolution 3T magnetic resonance imaging.
  
  
  RESULTS
  The scleral defect was covered with Tenon capsule sheaths and a meridional silicone buckle. One year postoperatively, visual acuity and macular and optic disc morphology were completely restored.
  
  
  CONCLUSIONS
  Ocular hypotony related to a defect of the sclera forming the roof of a retinochoroidal coloboma is a rare event. Hypotony was a consequence of a defect at the level of an atypical retinochoroidal coloboma where the scleral wall was found to be absent.
authors.affiliation: Department of Biomedical and Surgical Sciences, Section of Ophthalmology, University of Perugia, S. Maria della Misericordia Hospital, Perugia - Italy.
authors.forename: Tito
authors.initials: T
authors.lastname: Fiore
authors.affiliation: Department of Biomedical and Surgical Sciences, Section of Ophthalmology, University of Perugia, S. Maria della Misericordia Hospital, Perugia - Italy.
authors.forename: Adriana
authors.initials: A
authors.lastname: Pellegrino
authors.affiliation: Department of Biomedical and Surgical Sciences, Section of Ophthalmology, University of Perugia, S. Maria della Misericordia Hospital, Perugia - Italy.
authors.forename: Marco
authors.initials: M
authors.lastname: Lupidi
authors.affiliation: Department of Biomedical and Surgical Sciences, Section of Ophthalmology, University of Perugia, S. Maria della Misericordia Hospital, Perugia - Italy.
authors.forename: Alessio
authors.initials: A
authors.lastname: Cerquaglia
authors.affiliation: Department of Translational Surgery and Medicine, Eye Clinic, University of Florence, Florence - Italy.
authors.forename: Fabrizio
authors.initials: F
authors.lastname: Giansanti
authors.affiliation: Department of Biomedical and Surgical Sciences, Section of Ophthalmology, University of Perugia, S. Maria della Misericordia Hospital, Perugia - Italy.
authors.forename: Carlo
authors.initials: C
authors.lastname: Cagini
mesh_terms: D002648:Child; D002829:Choroid / Q000002:abnormalities* / Q000000981:diagnostic imaging; D003103:Coloboma / Q000150:complications* / Q000000981:diagnostic imaging; D005260:Female; D006801:Humans; D008279:Magnetic Resonance Imaging; D015814:Ocular Hypotension / Q000209:etiology*; D010211:Papilledema / Q000209:etiology*; D012160:Retina / Q000002:abnormalities* / Q000000981:diagnostic imaging; D012164:Retinal Diseases / Q000209:etiology*; D012422:Rupture, Spontaneous; D012591:Scleral Buckling; D015422:Scleral Diseases / Q000150:complications* / Q000000981:diagnostic imaging / Q000601:surgery; D058475:Tenon Capsule / Q000601:surgery; D041623:Tomography, Optical Coherence; D014792:Visual Acuity