title: Operative stabilization of the remaining mobile segment in ankylosed cervical spine in systemic onset - juvenile idiopathic arthritis: A case report.
abstract: We describe a case of a 19-year-old young man with oligoarthritis type of juvenile idiopathic arthritis, who presented with several month duration of lower neck pain and progressive muscular weakness of all four limbs. X-rays of the cervical spine demonstrated spontaneous apophyseal joint fusion from the occipital condyle to C6 and from C7 to Th2 with marked instability between C6 and C7. Surgical intervention began with anterolateral approach to the cervical spine performing decompression, insertion of cage and anterior vertebral plate and screws, followed by posterior approach and fixation. Care was taken to restore sagittal balance. The condition was successfully operatively managed with multisegmental, both column fixation and fusion, resulting in pain cessation and resolution of myelopathy. Postoperatively, minor swallowing difficulties were noted, which ceased after three days. Patient was able to move around in a wheelchair on the sixth postoperative day. Stiff neck collar was advised for three months postoperatively with neck pain slowly decreasing in the course of first postoperative month. On the follow-up visit six months after the surgery patient exhibited no signs of spastic tetraparesis, X-rays of the cervical spine revealed solid bony fusion at single mobile segment C6-C7. He was able to gaze horizontally while sitting in a wheelchair. Signs of myelopathy with stiff neck and single movable segment raised concerns about intubation, but were successfully managed using awake fiber-optic intubation. Avoidance of tracheostomy enabled us to perform an anterolateral approach without increasing the risk of wound infection. Regarding surgical procedure, the same principles are obeyed as in management of fracture in ankylosing spondylitis or Mb. Forestrier.
authors.affiliation: Lovro Suhodolčan, Janez Brecelj, Rok Vengust, Department of Orthopaedic Surgery, University Medical Centre Ljubljana, 1000 Ljubljana, Slovenia.
authors.forename: Lovro
authors.initials: L
authors.lastname: Suhodolčan
authors.affiliation: Lovro Suhodolčan, Janez Brecelj, Rok Vengust, Department of Orthopaedic Surgery, University Medical Centre Ljubljana, 1000 Ljubljana, Slovenia.
authors.forename: Marko
authors.initials: M
authors.lastname: Mihelak
authors.affiliation: Lovro Suhodolčan, Janez Brecelj, Rok Vengust, Department of Orthopaedic Surgery, University Medical Centre Ljubljana, 1000 Ljubljana, Slovenia.
authors.forename: Janez
authors.initials: J
authors.lastname: Brecelj
authors.affiliation: Lovro Suhodolčan, Janez Brecelj, Rok Vengust, Department of Orthopaedic Surgery, University Medical Centre Ljubljana, 1000 Ljubljana, Slovenia.
authors.forename: Rok
authors.initials: R
authors.lastname: Vengust
keywords: Cervical ankylosis; Juvenile idiopathic arthritis; Multilevel both column fixation; Spastic tetraparesis; Unstable cervical segment