title: An illustrative case of primary angiitis of the central nervous system.
abstract: Primary angiitis of the central nervous system is a rare idiopathic vasculitis affecting small- and medium-sized vessels, isolated to the brain, leptomeninges and spinal cord. We report a case of biopsy-proven primary angiitis of the central nervous system, displaying some atypical features. This case highlights several key diagnostic and management issues of the disorder as well as its potential heterogeneity.
authors.affiliation: Institute of Neurological Sciences, Prince of Wales Hospital, Randwick, NSW, Australia.
authors.forename: Elizabeth A
authors.initials: EA
authors.lastname: Shiner
authors.affiliation: Institute of Neurological Sciences, Prince of Wales Hospital, Randwick, NSW, Australia; Prince of Wales Clinical School, UNSW, Kensington, NSW, Australia.
authors.forename: Alessandro S
authors.initials: AS
authors.lastname: Zagami
keywords: Primary angiitis; angiography; central nervous system; cerebral vasculitis; histopathology; magnetic resonance imaging