title: IgG4-Related Disease in Organs Other than the Hepatobiliary-Pancreatic System.
abstract: Immunoglobulin G4-related disease (IgG4-RD) is a new disease entity that was established in this century. It is a systemic and chronic inflammatory disorder. Autoimmune pancreatitis is a representative condition, but there is clearly involvement from other organs, including the kidneys, the retroperitoneal cavity, the lungs, and the thyroid, lacrimal, salivary, pituitary, and prostate glands. To aid in the resolution of the numerous issues related to IgG4-RD, the authors established a registry system of patients in multicenter institutes with IgG4-RD-the SMART registry. Using SMART registry data, they provide an overview of the involvement of organs other than the hepatobiliary-pancreatic system in IgG4-RD and emphasize the importance of consultation and cooperation with other specialists in the diagnosis, treatment, and management of patients with IgG4-RD.
authors.affiliation: Department of Rheumatology, Sapporo Medical University School of Medicine, Sapporo, Japan.
authors.forename: Motohisa
authors.initials: M
authors.lastname: Yamamoto
authors.affiliation: Department of Rheumatology, Sapporo Medical University School of Medicine, Sapporo, Japan.
authors.forename: Hiroki
authors.initials: H
authors.lastname: Takahashi
mesh_terms: D017677:Age Distribution; D001327:Autoimmune Diseases / Q000175:diagnosis / Q000473:pathology*; D005128:Eye Diseases / Q000000981:diagnostic imaging / Q000473:pathology; D005260:Female; D006801:Humans; D007074:Immunoglobulin G / Q000276:immunology*; D007674:Kidney Diseases / Q000000981:diagnostic imaging / Q000473:pathology; D008279:Magnetic Resonance Imaging; D008297:Male; D010902:Pituitary Gland / Q000000981:diagnostic imaging / Q000473:pathology; D011467:Prostate / Q000000981:diagnostic imaging / Q000473:pathology; D012140:Respiratory Tract Diseases / Q000000981:diagnostic imaging / Q000473:pathology; D012187:Retroperitoneal Space / Q000000981:diagnostic imaging / Q000473:pathology; D012469:Salivary Glands / Q000000981:diagnostic imaging / Q000473:pathology; D017678:Sex Distribution; D013961:Thyroid Gland / Q000000981:diagnostic imaging / Q000473:pathology; D014057:Tomography, X-Ray Computed
chemical_list: D007074:Immunoglobulin G