title: ANESTHESIA FOR CHARCOT-MARIE-TOOTH DISEASE: CASE REPORT.
abstract: Charcot-Marie-Tooth disease comprises a group of disorders characterized by progressive muscle weakness and wasting. Reviewing the anaesthetic literature produced conflicting reports about the best anaesthetic options for patients with CMTD; as they are at increased risk of prolonged response to muscle relaxants, malignant hyperthermia and risks of regional anaesthesia. We present a case of the successful use of total intravenous anaesthesia with dexmedetomidine and propofol combined with caudal block using bupivacaine mixed with dexmedetomidine without any complications, for a 17 year old male patient with Charcot Marie-Tooth disease who underwent a lower limb orthopedic surgery.
authors.forename: Khalid R
authors.initials: KR
authors.lastname: Alzaben
authors.forename: Omar Q
authors.initials: OQ
authors.lastname: Samarah
authors.forename: Salameh S
authors.initials: SS
authors.lastname: Obeidat
authors.forename: Oday
authors.initials: O
authors.lastname: Halhouli
authors.forename: Murad
authors.initials: M
authors.lastname: Al Kharabsheh
mesh_terms: D000293:Adolescent; D000758:Anesthesia / Q000379:methods*; D000771:Anesthesia, Intravenous; D002607:Charcot-Marie-Tooth Disease / Q000503:physiopathology*; D006801:Humans; D008297:Male