title: Oral Lesions in Pycnodysostosis Syndrome: Eleven Years of Follow-Up.
abstract: Pycnodysostosis is a rare genetic disease that is characterized by osteosclerosis, short stature, and bone fragility. There are not cases of gnathic bones lesions reported on the international literature. This study aims to describe a clinical case of a 10-year-old girl with pycnodysostosis syndrome and an uncommon association with 4 distinct lesions (dentigerous cyst, central giant cell lesions, and 2 fibro-osseous lesions).
authors.affiliation: *Federal University of Rio Grande do Sul, Porto Alegre, Rio Grande do Sul †Metropolitan Union of Education and Culture, Lauro de Freitas, Brazil.
authors.forename: Viviane Palmeira
authors.initials: VP
authors.lastname: da Silva
authors.forename: Fernanda
authors.initials: F
authors.lastname: Visioli
authors.forename: Bruna Jalfim
authors.initials: BJ
authors.lastname: Maraschin
authors.forename: Juliana Andrade
authors.initials: JA
authors.lastname: Cardoso
authors.forename: Gleicy Gabriela V S C
authors.initials: GG
authors.lastname: Falcão
authors.forename: Márcio Campos
authors.initials: MC
authors.lastname: de Oliveira
authors.forename: Jener Gonçalves
authors.initials: JG
authors.lastname: de Farias
mesh_terms: D000359:Aftercare; D002648:Child; D005260:Female; D006801:Humans; D008334:Mandible / Q000473:pathology*; D008437:Maxilla / Q000473:pathology*; D058631:Pycnodysostosis / Q000175:diagnosis / Q000473:pathology* / Q000628:therapy