title: Spinal Cord Infarction in Hemoglobin SC Disease as an Amusement Park Accident.
abstract: Spinal cord infarction (SCI) is extremely rare in children, and only 2 other reports have described the occurrence of SCI in patients with hemoglobin SC disease (HbSC). Amusement park accidents are serious injuries. Patients with preexisting conditions, such as hypertension, cardiac disease, and recent back or neck injuries, may be at an increased risk. We report the case of a 12-year-old girl with HbSC with a past history of only 2 admissions for pain crises, who presented to the emergency department with symptoms of SCI after riding a roller coaster. Fibrocartilaginous embolism (FCE) is an increasingly recognized cause of SCI after events that put strain on the axial skeleton, such as many amusement park rides. Although radiologic criteria for FCE have been proposed, FCE remains a diagnosis of exclusion. To the best of our knowledge, this is the first documented case of SCI in a patient with HbSC and the first case of FCE after an amusement park accident. This case report highlights that HbSC may confound the differential diagnosis of SCI and aims to document an association with FCE in pediatric patients.
authors.affiliation: School of Medicine, University of Louisville, Louisville, Kentucky; and.
authors.forename: Ryan
authors.initials: R
authors.lastname: Eid
authors.affiliation: Divisions of Hematology/Oncology, Department of Pediatrics, and.
authors.forename: Ashok
authors.initials: A
authors.lastname: Raj
authors.affiliation: Pediatric Neurology, Department of Neurology, University of Louisville School of Medicine, Louisville, Kentucky.
authors.forename: Darren
authors.initials: D
authors.lastname: Farber
authors.affiliation: Pediatric Neurology, Department of Neurology, University of Louisville School of Medicine, Louisville, Kentucky.
authors.forename: Vinay
authors.initials: V
authors.lastname: Puri
authors.affiliation: Divisions of Hematology/Oncology, Department of Pediatrics, and sjbert01@louisville.edu.
authors.forename: Salvatore
authors.initials: S
authors.lastname: Bertolone
mesh_terms: D000059:Accidents; D002574:Cervical Vertebrae; D002648:Child; D003937:Diagnosis, Differential; D004617:Embolism / Q000175:diagnosis / Q000209:etiology*; D005260:Female; D006450:Hemoglobin SC Disease / Q000150:complications*; D006801:Humans; D007238:Infarction / Q000175:diagnosis / Q000209:etiology*; D011998:Recreation; D013116:Spinal Cord / Q000098:blood supply*; D020760:Spinal Cord Ischemia / Q000175:diagnosis / Q000209:etiology*