title: Dandy-Walker malformation and neurocutaneous melanosis in a three-month-old infant.
abstract: Dandy-Walker Malformation (DWM) is a rare congenital malformation of the brain. It is characterized by cystic enlargement of the fourth ventricle which is communicating with an enlarged posterior fossa, cerebellar dysgenesis, high tentorial insertion and hydrocephalus. Neurocutaneous Melanosis (NCM) is a congenital neurocutaneous syndrome characterized by large or multiple melanocytic nevi and benign or malignant melanocytic tumors of the leptomeninges. We report three months old boy who presented with projectile vomiting associated with a noticeable increase in head size. Several congenital nevi were seen all over his body with evident signs of hydrocephalus. The association of DWM and NCM is a rare complex, and to our knowledge, this is the eleventh case to be reported in the literature. In this article, we discuss the proposed pathogenesis, classification and management of the condition.
authors: (1) Ahfad University for Women , Sudan.
authors: Mohamed Osman
authors: MO
authors: Swar
authors: (2) Mohamed Alamin Hamid Hospital for Children, Omdurman , Sudan.
authors: Shaza Mohamed
authors: SM
authors: Mahgoub
authors: (1) Ahfad University for Women , Sudan.
authors: Rehab Omer
authors: RO
authors: Yassin
authors: (1) Ahfad University for Women , Sudan.
authors: Atika Mohamed
authors: AM
authors: Osman
keywords: Dandy-Walker malformation; Neurocutaneous melanosis