title: Living Donor Liver Transplantation Using a Liver Graft With Congenital Intrahepatic Portosystemic Shunt.
abstract: Despite of recent development of imaging modalities, congenital intrahepatic portosystemic shunt (IPSS) is rarely diagnosed. Therefore, living donor liver transplantation using a liver graft with IPSS has not been previously published.
  
  
  METHODS
  We report a 28-year-old male patient with end-stage liver disease secondary to Wilson disease. His 26-year-old brother was a potential living donor, who had an IPSS of 25 mm in diameter at segment 6 as shown by computed tomography. Liver function tests were normal, and blood ammonia concentration was in the upper limit of normal.
  
  
  RESULTS
  Living donor liver transplantation was uneventfully performed. After surgery, a recipient liver function tests showed a quick recovery, and serum ammonia levels were consistently normal. Although thrombosis inside the IPSS was confirmed by computed tomography on postoperative day 21, this thrombosis disappeared at 3 months posttransplant with anticoagulants. Currently (12 months posttransplant), the patient has fully recovered, and the IPSS is still the same size.
  
  
  CONCLUSIONS
  Based on our experience, liver allografts with IPSS can be accepted as potential liver allografts.
authors: Department of Transplantation Surgery, Nagoya University Hospital, Nagoya, Japan.
authors: Hideya
authors: H
authors: Kamei
authors: Department of Transplantation Surgery, Nagoya University Hospital, Nagoya, Japan.
authors: Hisashi
authors: H
authors: Imai
authors: Department of Transplantation Surgery, Nagoya University Hospital, Nagoya, Japan.
authors: Yasuharu
authors: Y
authors: Onishi
authors: Department of Gastroenterological Surgery, Nagoya University Graduate School of Medicine, Nagoya, Japan.
authors: Hiroyuki
authors: H
authors: Sugimoto
authors: Department of Radiology, Nagoya University Graduate School of Medicine, Showa, Nagoya, Japan.
authors: Kojiro
authors: K
authors: Suzuki
authors: Department of Transplantation Surgery, Nagoya University Hospital, Nagoya, Japan.
authors: Yasuhiro
authors: Y
authors: Ogura