title: Pachydermodactyly - a report of two cases.
abstract: Pachydermodactyly (PDD) is a rare and benign form of digital soft tissues fibromatosis, which affects the skin of the fingers. The disorder is characterized by asymptomatic, symmetric, progressive soft tissue swelling of the proximal interphalangeal (PIP) joints of the fingers. The etiology of disease remains unknown. It is usually acquired, even though there are some publications that document family cases. It affects mainly adolescent men. We report two boys with the bilateral swelling of the of the PIP joints of the fingers and skin and subcutaneous tissue thickening. Based on clinical manifestations, radiological study and histopathological examination, pachydermodactyly was diagnosed. PDD is a rare and benign disorder, although it is important to consider other diseases, especially rheumatic conditions, in the differential diagnosis in order to avoid unnecessary additional tests and treatments.
authors: Department of Older Children with subunits of Neurology, Rheumatology and Rehabilitation, St. Louis Regional Specialised Children's Hospital, Krakow, Poland.
authors: Zbigniew
authors: Z
authors: Żuber
authors: Department of Pathological Anatomy, Jagiellonian University Medical College, Krakow, Poland.
authors: Grzegorz
authors: G
authors: Dyduch
authors: Department of Dermatology, Jagiellonian University Medical College, Krakow, Poland.
authors: Andrzej
authors: A
authors: Jaworek
authors: Department of Older Children with subunits of Neurology, Rheumatology and Rehabilitation, St. Louis Regional Specialised Children's Hospital, Krakow, Poland.
authors: Dorota
authors: D
authors: Turowska-Heydel
authors: Department of Older Children with subunits of Neurology, Rheumatology and Rehabilitation, St. Louis Regional Specialised Children's Hospital, Krakow, Poland.
authors: Małgorzata
authors: M
authors: Sobczyk
authors: Department of Older Children with subunits of Neurology, Rheumatology and Rehabilitation, St. Louis Regional Specialised Children's Hospital, Krakow, Poland.
authors: Marta
authors: M
authors: Banach-Górnicka
authors: Department of Older Children with subunits of Neurology, Rheumatology and Rehabilitation, St. Louis Regional Specialised Children's Hospital, Krakow, Poland.
authors: Katarzyna
authors: K
authors: Rusnak
authors: Department of Children Surgery, Jagiellonian University Medical College, Krakow, Poland.
authors: Wojciech
authors: W
authors: Górecki
keywords: hands involvement; pachydermodactyly; proximal interphalangeal joints