title: Polymorphic Ventricular Tachycardia/Ventricular Fibrillation and Sudden Cardiac Death in the Normal Heart.
abstract: Primary electrical diseases manifest with polymorphic ventricular tachycardia (PMVT) and ventricular fibrillation (VF) and along with idiopathic VF contribute to about 10% of sudden cardiac deaths (SCDs) overall. These disorders include long QT syndrome, Brugada syndrome, catecholaminergic polymorphic ventricular tachycardia, short QT syndrome, and early repolarization syndrome. This article reviews the clinical electrophysiological management of PMVT/VF in a structurally normal heart affected with these disorders.
authors: Cardio Vascular Services, South Consulting Suites, Peel Health Campus, 110 Lakes Road, Mandurah, Western Australia 6210, Australia. Electronic address: drashahep@gmail.com.
authors: Ashok J
authors: AJ
authors: Shah
authors: Department of Electrophysiology and Cardiac Pacing, Hôpital Cardiologique du Haut Lévêque, Avenue de Magellan, Pessac Cedex 33604, France.
authors: Meleze
authors: M
authors: Hocini
authors: Department of Electrophysiology and Cardiac Pacing, Hôpital Cardiologique du Haut Lévêque, Avenue de Magellan, Pessac Cedex 33604, France.
authors: Arnaud
authors: A
authors: Denis
authors: Department of Electrophysiology and Cardiac Pacing, Hôpital Cardiologique du Haut Lévêque, Avenue de Magellan, Pessac Cedex 33604, France.
authors: Nicolas
authors: N
authors: Derval
authors: Department of Electrophysiology and Cardiac Pacing, Hôpital Cardiologique du Haut Lévêque, Avenue de Magellan, Pessac Cedex 33604, France.
authors: Frederic
authors: F
authors: Sacher
authors: Department of Electrophysiology and Cardiac Pacing, Hôpital Cardiologique du Haut Lévêque, Avenue de Magellan, Pessac Cedex 33604, France.
authors: Pierre
authors: P
authors: Jais
authors: Department of Electrophysiology and Cardiac Pacing, Hôpital Cardiologique du Haut Lévêque, Avenue de Magellan, Pessac Cedex 33604, France. Electronic address: michel.haissaguerre@chu-bordeaux.fr.
authors: Michel
authors: M
authors: Haissaguerre
mesh_terms: D000293:Adolescent; D017115:Catheter Ablation; D016757:Death, Sudden, Cardiac; D005260:Female; D006801:Humans; D008297:Male; D008875:Middle Aged; D017180:Tachycardia, Ventricular; D014693:Ventricular Fibrillation
keywords: Ablation; Catheter mapping; Electrical storm; Normal heart; Polymorphic ventricular tachycardia; Primary electrical disease; Sudden cardiac death; Ventricular fibrillation