title: Severe liver dysfunction in an infant with cystic fibrosis masquerading as metabolic liver disease.
abstract: We present a rare presentation of cystic fibrosis with neonatal cholestasis. Histological features of mucoviscidosis were present in liver involving the biliary tract, intestinal mucosa, pancreas, and lung. Besides, there was a rare association with autosomal dominant type of polycystic renal disease.
authors: Department of Pediatric Gastroenterology, Postgraduate Institute of Medical Education and Research, Chandigarh, India.
authors: K P
authors: KP
authors: Srikanth
authors: Advanced Pediatric Centre, Postgraduate Institute of Medical Education and Research, Chandigarh, India.
authors: Inusha
authors: I
authors: Panigrahi
authors: Department of Pediatric Gastroenterology, Postgraduate Institute of Medical Education and Research, Chandigarh, India.
authors: Babu Ram
authors: BR
authors: Thapa
authors: Department of Histopathology, Postgraduate Institute of Medical Education and Research, Chandigarh, India.
authors: Kim
authors: K
authors: Vaiphei
mesh_terms: D003550:Cystic Fibrosis / Q000150:complications* / Q000175:diagnosis* / Q000473:pathology; D006801:Humans; D007223:Infant; D007413:Intestinal Mucosa / Q000473:pathology; D008099:Liver / Q000473:pathology; D008107:Liver Diseases / Q000150:complications* / Q000175:diagnosis* / Q000473:pathology; D008168:Lung / Q000000981:diagnostic imaging / Q000473:pathology; D008297:Male; D010179:Pancreas / Q000473:pathology; D007690:Polycystic Kidney Diseases / Q000150:complications / Q000175:diagnosis / Q000473:pathology; D013902:Radiography, Thoracic