title: Recurrent multifocal cutaneous Kaposiform hemangioendothelioma: A rare vascular tumor of infancy and childhood.
abstract: Kaposiform hemangioendothelioma (KHE) is a locally aggressive vascular tumor of childhood although cases occurring in adulthood are also described. The features overlap with juvenile capillary hemangioma and Kaposi sarcoma. We report a rare case of recurrent, multifocal (nose and chin) cutaneous KHE initially occurring in a 3-year-old female child, uncomplicated by Kasabach-Merritt syndrome. Recurrences occurred over the next 6 years and resulted in complete distortion of the nose, requiring plastic repair.
authors: Department of Pathology, Andhra Medical College, King George Hospital, Visakhapatnam, Andhra Pradesh, India.
authors: Bhagyalakshmi
authors: B
authors: Atla
authors: Department of Plastic Surgery, Andhra Medical College, King George Hospital, Visakhapatnam, Andhra Pradesh, India.
authors: P V
authors: PV
authors: Sudhakar
authors: Department of Pathology, St. Luke's Hospital, Milwaukee, WI 53215, USA.
authors: Nagarjun
authors: N
authors: Rao
authors: Department of Pathology, Andhra Medical College, King George Hospital, Visakhapatnam, Andhra Pradesh, India.
authors: Uma
authors: U
authors: Prasad
mesh_terms: D014408:Biomarkers, Tumor / Q000032:analysis; D002675:Child, Preschool; D005260:Female; D006390:Hemangioendothelioma / Q000175:diagnosis* / Q000473:pathology*; D006651:Histocytochemistry; D006801:Humans; D007150:Immunohistochemistry; D059885:Kasabach-Merritt Syndrome / Q000150:complications / Q000175:diagnosis* / Q000473:pathology*; D008853:Microscopy; D009062:Mouth Neoplasms / Q000175:diagnosis* / Q000473:pathology*; D009669:Nose Neoplasms / Q000175:diagnosis* / Q000473:pathology*; D019408:Platelet Endothelial Cell Adhesion Molecule-1 / Q000032:analysis; D012008:Recurrence; D012514:Sarcoma, Kaposi / Q000175:diagnosis* / Q000473:pathology*
chemical_list: D014408:Biomarkers, Tumor; D019408:Platelet Endothelial Cell Adhesion Molecule-1