title: Single-Stage Total Arch Replacement Including Resection of Kommerell Diverticulum in a Patient With Loeys-Dietz Syndrome.
abstract: Loeys-Dietz syndrome (LDS) is an autosomal dominant genetic connective tissue disorder associated with aortic aneurysmal disease. Kommerell diverticulum (KD) is a rare aortic diverticulum, for which the indication for surgery and the surgical techniques remain subjects of debate. We describe our experience with a successful total aortic arch replacement including KD resection through a median sternotomy for a pediatric patient with LDS.
authors: Division of Cardiac Surgery, The Johns Hopkins Hospital, Baltimore, MD, USA.
authors: Chin Siang
authors: CS
authors: Ong
authors: Division of Cardiac Surgery, The Johns Hopkins Hospital, Baltimore, MD, USA, visiting student from The Jikei University School of Medicine, Tokyo, Japan.
authors: Yuhei
authors: Y
authors: Kasai
authors: Division of Cardiac Surgery, The Johns Hopkins Hospital, Baltimore, MD, USA, visiting student from The Jikei University School of Medicine, Tokyo, Japan.
authors: Souta
authors: S
authors: Fukushima
authors: Division of Cardiac Surgery, The Johns Hopkins Hospital, Baltimore, MD, USA nhibino1@jhmi.edu.
authors: Narutoshi
authors: N
authors: Hibino
authors: Division of Cardiac Surgery, The Johns Hopkins Hospital, Baltimore, MD, USA.
authors: Trent
authors: T
authors: Magruder
authors: Division of Cardiac Surgery, The Johns Hopkins Hospital, Baltimore, MD, USA.
authors: Alejandro
authors: A
authors: Suarez-Pierre
authors: Division of Cardiac Surgery, The Johns Hopkins Hospital, Baltimore, MD, USA.
authors: Duke
authors: D
authors: Cameron
authors: Division of Cardiac Surgery, The Johns Hopkins Hospital, Baltimore, MD, USA.
authors: Luca
authors: L
authors: Vricella
mesh_terms: D001013:Aorta, Thoracic / Q000002:abnormalities / Q000000981:diagnostic imaging / Q000601:surgery*; D001018:Aortic Diseases / Q000151:congenital / Q000175:diagnosis / Q000601:surgery*; D002648:Child; D004240:Diverticulum / Q000151:congenital / Q000175:diagnosis / Q000601:surgery*; D005260:Female; D006801:Humans; D021621:Imaging, Three-Dimensional; D055947:Loeys-Dietz Syndrome / Q000175:diagnosis*; D008279:Magnetic Resonance Imaging; D056346:Sternotomy / Q000379:methods; D014057:Tomography, X-Ray Computed; D014656:Vascular Surgical Procedures / Q000379:methods*
keywords: Kommerell diverticulum; Loeys-Dietz syndrome; aberrant right subclavian artery; congenital heart disease