title: Oral rehabilitation of patients with Chediak-Higashi syndrome using zygoma and root form implant-supported fixed prostheses: A report of two patients.
abstract: Chediak-Higashi syndrome (CH-S) is a rare genetic immunodeficiency disorder. Fewer than 500 individuals with CH-S have been reported worldwide in the past 20 years. The dental management of patients in whom CH-S has been diagnosed has been rarely reported and only in the form of a case report. All reports addressed the severe periodontal disease found in those patients, and most studies concluded that periodontal treatment had an unfavorable prognosis. As a result, complete edentulism at an early age because of severe periodontal disease is expected. The purpose of this report was to present 2 patients with CH-S seeking oral rehabilitation after early tooth loss and severe bone resorption as a manifestation of severe periodontal disease. The treatment used bilateral zygoma implants and an all-on-4 concept. The complications encountered and management with a 5-year post-surgery follow-up are also presented.
authors: Assistant Professor, Department of General Dental Practice, Faculty of Dentistry, Kuwait University, Kuwait City, Kuwait. Electronic address: Fawaz.zoubi@hsc.edu.kw.
authors: Fawaz
authors: F
authors: Alzoubi
authors: Professor, Department of Oral and Maxillofacial Surgery, Arthur A. Dugoni School of Dentistry, University of the Pacific, San Francisco, Calif.
authors: Edmond
authors: E
authors: Bedrossian
authors: Professor, Department of Dental Practice, Arthur A. Dugoni School of Dentistry, University of the Pacific, San Francisco, Calif.
authors: Allen
authors: A
authors: Wong
mesh_terms: D000293:Adolescent; D000328:Adult; D002609:Chediak-Higashi Syndrome / Q000601:surgery*; D019094:Dental Prosthesis, Implant-Supported; D005260:Female; D006801:Humans; D007575:Jaw, Edentulous / Q000601:surgery*; D008297:Male; D017060:Patient Satisfaction; D015050:Zygoma / Q000601:surgery*