title: Absent Pulmonary Valve Syndrome With Tricuspid Atresia, Ventricular Septal Defect, and Aneurysmal Dilated Pulmonary Artery: A Case Report of Successful Fontan Completion.
abstract: Of the associated cardiac defects with absent pulmonary valve, the combination of tricuspid atresia, ventricular septal defect, and aneurysmal dilatation of the pulmonary arteries is very rare. We report the case of a low-birth-weight girl (2,282 g) with this anomaly, which was prenatally diagnosed. Fontan completion was successfully achieved at 16 months of age, following staged palliative procedures including banding of the main pulmonary trunk and plication of the aneurysmal dilated central pulmonary artery.
authors.affiliation: 1 Department of Cardiovascular Surgery, Hyogo Prefectural Amagasaki General Medical Center, Amagasaki, Hyogo, Japan.
authors.forename: Ayano
authors.initials: A
authors.lastname: Futuki
authors.affiliation: 1 Department of Cardiovascular Surgery, Hyogo Prefectural Amagasaki General Medical Center, Amagasaki, Hyogo, Japan.
authors.forename: Keiichi
authors.initials: K
authors.lastname: Fujiwara
authors.affiliation: 1 Department of Cardiovascular Surgery, Hyogo Prefectural Amagasaki General Medical Center, Amagasaki, Hyogo, Japan.
authors.forename: Kosuke
authors.initials: K
authors.lastname: Yoshizawa
authors.affiliation: 2 Department of Pediatric Cardiology, Hyogo Prefectural Amagasaki General Medical Center, Amagasaki, Hyogo, Japan.
authors.forename: Hisanori
authors.initials: H
authors.lastname: Sakazaki
mesh_terms: D005260:Female; D018729:Fontan Procedure; D006345:Heart Septal Defects, Ventricular / Q000000981:diagnostic imaging* / Q000601:surgery; D006801:Humans; D007223:Infant; D007231:Infant, Newborn; D011651:Pulmonary Artery / Q000002:abnormalities / Q000000981:diagnostic imaging / Q000601:surgery; D011664:Pulmonary Valve / Q000002:abnormalities / Q000000981:diagnostic imaging / Q000601:surgery; D016896:Treatment Outcome; D018785:Tricuspid Atresia / Q000000981:diagnostic imaging* / Q000601:surgery; D014261:Tricuspid Valve / Q000002:abnormalities / Q000000981:diagnostic imaging / Q000601:surgery
keywords: Fontan procedure; absent pulmonary valve; tricuspid atresia; ventricular septal defect