title: [Diagnosis and Treatment of Erdheim-Chester Disease -Review].
abstract: Erdheim-Chester Disease (ECD) is a rare form of non Langerhans' cell histiocytosis. The etiology of ECD is unknown yet. The disease is characterized by the infiltration of lipid-laden histiocytes with foamy to bones and various organs. The heterogeneous manifestations of ECD vary among different individuals. This results in a presentation that may vary from an indolent focal disease to a life threatening organ failure. This review focuses on the etiology, clinical presentation, diagnostic criteria and treatment of Erdheim-Chester disease (ECD).
authors.affiliation: Department of Hematology, Beijing Friendship Hospital Affiliated to Capital Medical University, Beijing 100050, China.
authors.forename: Jing-Shi
authors.initials: JS
authors.lastname: Wang
authors.affiliation: Department of Hematology, Beijing Friendship Hospital Affiliated to Capital Medical University, Beijing 100050, China.E-mail: zhaowww263@yahoo.com.
authors.forename: Zhao
authors.initials: Z
authors.lastname: Wang
mesh_terms: D031249:Erdheim-Chester Disease; D006801:Humans