title: Hirayama Disease with Periscapular Involvement: A Rare Association.
abstract: Hirayama disease (HD) is a rare disease commonly seen in India and Japan typically presenting in adolescent age group with male predominance and asymmetrical distal pure motor, lower-motor neuron-type weakness. We report a patient of HD who had significant involvement of proximal periscapular muscles along with typical distal involvement. The patient also had scapular winging, which is rare in HD. He was treated conservatively with physiotherapy and hard cervical collar and is presently under follow-up during the static phase of disease.
authors.affiliation: Department of Neurology, King George's Medical University, Lucknow, India.
authors.forename: Vikram V
authors.initials: VV
authors.lastname: Holla
authors.affiliation: Department of Neurology, King George's Medical University, Lucknow, India.
authors.forename: Sanjeev
authors.initials: S
authors.lastname: Kumar
authors.affiliation: Department of Neurology, King George's Medical University, Lucknow, India.
authors.forename: Rakesh
authors.initials: R
authors.lastname: Shukla
keywords: Anterior horn cell disorder; Hirayama disease; MRI