title: Unilateral Glaucoma Associated with Conjunctival Angioma and Choroidal Thickening without Facial Angioma.
abstract: We report a case of a suspected Sturge-Weber syndrome variant diagnosed at the age of 58 with the help of enhanced depth imaging spectral-domain ocular coherence tomography (EDI-SDOCT). A 58-year-old female with unilateral glaucoma was suspected to have choroidal vascular lesion, conjunctival angioma, and no facial port-wine stain who presented to the clinic with bleb dysesthesia many years after trabeculectomy. EDI-SDOCT was performed and revealed markedly increased choroidal thickness in the affected eye. EDI-SDOCT may be helpful in diagnosing Sturge-Weber variants without facial involvement and may aid in the investigation of the pathogenesis of this disease.
authors.affiliation: Department of Ophthalmology and Visual Sciences, University of Maryland School of Medicine, Baltimore, MD, USA.
authors.forename: Osamah J
authors.initials: OJ
authors.lastname: Saeedi
authors.affiliation: Wilmer Eye Institute, Johns Hopkins University, Baltimore, MD, USA.
authors.forename: Luke Y
authors.initials: LY
authors.lastname: Chang
authors.affiliation: Wilmer Eye Institute, Johns Hopkins University, Baltimore, MD, USA.
authors.forename: Karun S
authors.initials: KS
authors.lastname: Arora
authors.affiliation: Wilmer Eye Institute, Johns Hopkins University, Baltimore, MD, USA.
authors.forename: Henry D
authors.initials: HD
authors.lastname: Jampel
authors.affiliation: Wilmer Eye Institute, Johns Hopkins University, Baltimore, MD, USA.
authors.forename: Harry A
authors.initials: HA
authors.lastname: Quigley
mesh_terms: D002829:Choroid / Q000473:pathology*; D003230:Conjunctival Neoplasms / Q000473:pathology*; D005260:Female; D005901:Glaucoma / Q000175:diagnosis* / Q000601:surgery; D006391:Hemangioma / Q000473:pathology*; D006801:Humans; D008875:Middle Aged; D012590:Sclera / Q000098:blood supply; D013341:Sturge-Weber Syndrome / Q000175:diagnosis*; D041623:Tomography, Optical Coherence; D014130:Trabeculectomy; D014690:Venous Pressure
keywords: Choroidal Thickness; Episcleral Venous Pressure; Ocular Coherence Tomography; Sturge–Weber Syndrome