title: General anesthesia in patients with syndrome of Poland.
abstract: The increased use of surgery as a treatment or as an alternative for improvement means that we have a larger number of patients in the operating theatre, including those who suffer from rare diseases. Poland Syndrome is a rare congenital disease associated with muscle development. These patients may have a broad spectrum of abnormalities, which include thoracic anomalies, which can alter the ventilatory management at the level of the airway; the possible onset of malignant hyperthermia. This leads the anaesthetist to take certain preventive measures. We report the case of a patient with Poland syndrome operated for the placement of a breast prosthesis. We avoid halogenated agents, and use a Total Intravenous Anaesthesia with propofol. The appearance of muscle spasms as a result of the use of propofol, forced us into a second anaesthesia to perform total intravenous anaesthesia with Midazolam.
authors.affiliation: Servicio de Anestesiología y Reanimación, Hospital de SAS Jerez de la Frontera, Jerez de la Frontera, Cádiz, España. Electronic address: juliadiazcrespo@gmail.com.
authors.forename: J
authors.initials: J
authors.lastname: Díaz-Crespo
authors.affiliation: Servicio de Anestesiología y Reanimación, Hospital de SAS Jerez de la Frontera, Jerez de la Frontera, Cádiz, España.
authors.forename: Y
authors.initials: Y
authors.lastname: Vázquez-Mambrilla
authors.affiliation: Servicio de Anestesiología y Reanimación, Hospital de SAS Jerez de la Frontera, Jerez de la Frontera, Cádiz, España.
authors.forename: F
authors.initials: F
authors.lastname: García-Herrera
mesh_terms: D000328:Adult; D000771:Anesthesia, Intravenous / Q000379:methods*; D018685:Anesthetics, Inhalation; D018686:Anesthetics, Intravenous / Q000009:adverse effects*; D001940:Breast / Q000002:abnormalities; D019928:Breast Implantation; D000075203:Contraindications, Drug; D004198:Disease Susceptibility; D057915:Drug Substitution; D005260:Female; D006801:Humans; D007431:Intraoperative Complications / Q000139:chemically induced; D008305:Malignant Hyperthermia / Q000517:prevention & control; D008874:Midazolam; D011045:Poland Syndrome / Q000503:physiopathology; D015742:Propofol / Q000009:adverse effects*; D013035:Spasm / Q000139:chemically induced
chemical_list: D018685:Anesthetics, Inhalation; D018686:Anesthetics, Intravenous; D008874:Midazolam; D015742:Propofol
keywords: Anaesthesia; Anestesia; Anestesia total intravenosa con midazolam; Intravenous anaesthesia with midazolam; Poland syndrome; Síndrome de Poland