title: Pulmonary haemodynamics in Fontan physiology after lobectomy in a patient with a single ventricle associated with pulmonary sequestration.
abstract: A 2-year-old girl with a functionally univentricular heart associated with a pulmonary sequestration underwent right lower lobectomy after which increased lung volume with low mean pulmonary artery pressure and pulmonary vascular resistance was documented. A cardiac catheterisation performed after a subsequent total cavopulmonary connection demonstrated favourable Fontan haemodynamics. Lobectomy may have induced compensatory lung growth, contributing to the maintenance of haemodynamics favourable for the long-term success of the Fontan procedure.
authors: 1Department of Pediatric Cardiology,Aichi Children's Health and Medical Center,Aichi,Japan.
authors: Sayaka
authors: S
authors: Mii
authors: 1Department of Pediatric Cardiology,Aichi Children's Health and Medical Center,Aichi,Japan.
authors: Kazushi
authors: K
authors: Yasuda
authors: 2Department of Cardiac Surgery,Aichi Children's Health and Medical Center,Aichi,Japan.
authors: Hiroomi
authors: H
authors: Murayama
mesh_terms: D000015:Abnormalities, Multiple; D000792:Angiography; D001998:Bronchopulmonary Sequestration / Q000175:diagnosis / Q000503:physiopathology / Q000601:surgery*; D006328:Cardiac Catheterization; D002675:Child, Preschool; D005260:Female; D018729:Fontan Procedure / Q000379:methods*; D006352:Heart Ventricles / Q000002:abnormalities* / Q000000981:diagnostic imaging; D006801:Humans; D011013:Pneumonectomy; D011184:Postoperative Period; D011651:Pulmonary Artery / Q000000981:diagnostic imaging / Q000503:physiopathology*; D011652:Pulmonary Circulation / Q000502:physiology*; D014057:Tomography, X-Ray Computed
keywords: Compensatory lung growth; pulmonary arterial growth; pulmonary vascular bed; pulmonary vascular resistance; total cavopulmonary connection