title: Focal Nodulary Hyperplasia of the Liver Due to Congenital Portosystemic Shunt: A Rare Condition Mimicking Hepatocellulary Carcinoma.
abstract: Congenital portosystemic shunts are rare vascular malformations that lead to several complications including liver tumors, pulmonary hypertension, and metabolic encephalopathy. We describe a rare case of a 17-year-old girl with an extrahepatic portosystemic shunt presenting recurrent syncope episodes and a liver mass mimicking hepatocellulary carcinoma.
authors: Departments of *Pediatric Hematology and Oncology †Pediatric Cardiology §Pathology, Ankara Pediatric Hematology and Oncology Training and Research Hospital ‡Department of Radiology, Diskapi Yildirim Beyazit Training and Research Hospital, 06110 Ankara, Turkey.
authors: Arzu
authors: A
authors: Yazal Erdem
authors: Suna
authors: S
authors: Emir
authors: Haci A
authors: HA
authors: Demir
authors: Derya
authors: D
authors: Özyörük
authors: İlker
authors: İ
authors: Çetin
authors: Aynur
authors: A
authors: Turan
authors: Esra
authors: E
authors: Karakuş
mesh_terms: D000293:Adolescent; D006528:Carcinoma, Hepatocellular / Q000175:diagnosis; D003937:Diagnosis, Differential; D005260:Female; D020518:Focal Nodular Hyperplasia / Q000175:diagnosis / Q000209:etiology*; D006501:Hepatic Encephalopathy / Q000209:etiology; D006801:Humans; D022124:Hyperammonemia / Q000209:etiology; D017588:Hyperandrogenism / Q000209:etiology / Q000503:physiopathology; D006976:Hypertension, Pulmonary / Q000209:etiology / Q000503:physiopathology; D008113:Liver Neoplasms / Q000175:diagnosis; D011169:Portal Vein / Q000002:abnormalities* / Q000000981:diagnostic imaging; D013575:Syncope / Q000209:etiology; D016157:Vascular Fistula / Q000151:congenital* / Q000175:diagnosis / Q000000981:diagnostic imaging; D054079:Vascular Malformations; D014682:Vena Cava, Inferior / Q000002:abnormalities* / Q000000981:diagnostic imaging