title: A Rare Presentation of Isolated Congenital Splenic Hemangioma With Kasabach-Merritt Syndrome.
abstract: Splenic hemangiomas (SHs) are the most common benign neoplasms of the spleen. However, they are rare in the newborn period. We present an extremely rare case of congenital SH complicated by Kasabach-Merritt syndrome.
  
  
  
  A 2.93 kg male infant was delivered at term with a prenatal diagnosis of a left infrarenal mass diagnosed by ultrasound at 35 weeks of gestation. Magnetic resonance imaging demonstrated a well-defined splenic mass with multiple flow voids and scattered areas of high intensity suggestive of hemorrhage. He developed anemia, thrombocytopenia, and coagulopathy which required transfusion with packed red cells, platelets, cryoprecipitate, and fresh frozen plasma. Excision biopsy of the spleen led to resolution of anemia, thrombocytopenia, and coagulopathy. The diagnosis of SH was confirmed by histopathology. At 2 months outpatient follow-up, the patient was growing well without any evidence of tumor recurrence.
  
  
  
  Congenital SH is a rare entity that can be fatal if the potential complication of Kasabach-Merritt syndrome is not anticipated, evaluated, and promptly treated. Our patient had a favorable outcome with early surgical excision of the SH.
authors: Department of Pediatrics, Division of Neonatology, University of Miami, Holtz Children's Hospital, Miami, FL.
authors: Fredrick
authors: F
authors: Dapaah-Siakwan
authors: Carleene
authors: C
authors: Bryan
authors: Lashawndra S
authors: LS
authors: Walker
authors: Teresa
authors: T
authors: Del Moral
mesh_terms: D000740:Anemia / Q000209:etiology; D016913:Blood Component Transfusion; D003937:Diagnosis, Differential; D004211:Disseminated Intravascular Coagulation / Q000209:etiology / Q000628:therapy; D042241:Early Diagnosis; D006391:Hemangioma / Q000150:complications / Q000151:congenital* / Q000000981:diagnostic imaging / Q000601:surgery; D006801:Humans; D007231:Infant, Newborn; D059885:Kasabach-Merritt Syndrome / Q000175:diagnosis / Q000209:etiology*; D008279:Magnetic Resonance Imaging; D008297:Male; D018805:Sepsis / Q000175:diagnosis; D013156:Splenectomy; D013160:Splenic Neoplasms / Q000150:complications / Q000151:congenital* / Q000000981:diagnostic imaging / Q000601:surgery