Surgical repair of a truncus arteriosus with unilateral absence of the right proximal pulmonary artery.
The unilateral absence of a proximal pulmonary artery (UAPPA) is rare and is most frequently accompanied by cardiovascular anomalies such as tetralogy of Fallot or septal defects. We report a patient with truncus arteriosus with UAPPA in which we performed a two-stage surgical repair. During the first palliative operation, a right modified Blalock-Taussig shunt was constructed to develop the hypoplastic right pulmonary artery. At 10 months, the patient underwent patch closure of a ventricular septal defect with integration of both pulmonary arteries, and reconstruction of the right ventricular outflow tract using a conduit. Four years postoperatively, he continues to do well.
Department of Cardiovascular Surgery, Tokyo Women's Medical University, Tokyo, Japan. frankfuruta0915@yahoo.co.jp.
Akihisa
A
Furuta
Department of Cardiovascular Surgery, Tokyo Women's Medical University, Tokyo, Japan.
Mitsugi
M
Nagashima
Department of Cardiovascular Surgery, Tokyo Women's Medical University, Tokyo, Japan.
Takeshi
T
Hiramatsu
Department of Cardiovascular Surgery, Tokyo Women's Medical University, Tokyo, Japan.
Goki
G
Matsumura
Department of Cardiovascular Surgery, Tokyo Women's Medical University, Tokyo, Japan.
Kenji
K
Yamazaki
D000015:Abnormalities, Multiple; D000792:Angiography; D006348:Cardiac Surgical Procedures / Q000379:methods*; D006352:Heart Ventricles / Q000601:surgery*; D006801:Humans; D007231:Infant, Newborn; D008297:Male; D011651:Pulmonary Artery / Q000002:abnormalities* / Q000601:surgery; D014339:Truncus Arteriosus, Persistent / Q000175:diagnosis / Q000601:surgery*; D054079:Vascular Malformations / Q000175:diagnosis*