Diffuse Elevated Abdominal Activity on 99mTc-Labeled Red Blood Cell Imaging in a Pediatric Patient With Klippel Trenaunay Syndrome.
Klippel Trenaunay syndrome commonly manifests as lower limb hypertrophy where vascular malformation occurs. However, up to 20% of patients with Klippel Trenaunay syndrome can have gastrointestinal involvement. An 18-year-old man with known Klippel Trenaunay syndrome in the left lower extremity underwent Tc-labeled red blood cell imaging to determine the site of gastrointestinal bleeding. The images did not reveal the site of active bleeding. However, diffuse non-moving activity in the left abdomen and pelvis was noted, which corresponded to hypertrophied colon and related blood vessels, consistent with intestinal involvement of Klippel Trenaunay syndrome.
From the Department of Radiology, Children's Hospital of Philadelphia, University of Pennsylvania Perelman School of Medicine, Philadelphia, PA.
Summer L
SL
Kaplan
Hongming
H
Zhuang
D000005:Abdomen / Q000000981:diagnostic imaging; D000293:Adolescent; D006801:Humans; D007715:Klippel-Trenaunay-Weber Syndrome / Q000000981:diagnostic imaging*; D008297:Male; D011875:Radionuclide Angiography; D019275:Radiopharmaceuticals; D013667:Technetium
D019275:Radiopharmaceuticals; D013667:Technetium