A Rare Ocular Manifestation of Adult Onset Still's Disease: Purtscher's-like Retinopathy.
Adult-onset Still's disease (AOSD) is a rare multisystemic immune-mediated disease of unknown etiology with quotidian spiking fever, evanescent rash, arthralgia, and multiple organ involvement. The few AOSD cases that have been reported developed Purtscher's-like retinopathy associated with thrombotic microangiopathy (TMA). Here, we report Purtscher's-like retinopathy without TMA in a patient with AOSD. A 29-year-old-man who presented for evaluation of blurred vision was diagnosed with AOSD based on Yamaguchi criteria. He had Purtscher's-like retinopathy in his right eye. Lesions improved after steroid treatment. Although almost all reported AOSD cases with Purtscher's-like retinopathy are associated with TMA, in this case such a complication was not encountered.
a Department of Ophthalmology , Gulhane Military Medical Academy Haydarpasa Training Hospital , Uskudar , Istanbul , Turkey.
Cihan
http://orcid.org/0000-0003-2180-0077
C
Buyukavsar
b Department of Infectious Diseases and Clinical Microbiology , Gulhane Military Medical Academy Haydarpasa Training Hospital , Uskudar , Istanbul , Turkey.
Ergenekon
E
Karagoz
a Department of Ophthalmology , Gulhane Military Medical Academy Haydarpasa Training Hospital , Uskudar , Istanbul , Turkey.
Murat
M
Sonmez
a Department of Ophthalmology , Gulhane Military Medical Academy Haydarpasa Training Hospital , Uskudar , Istanbul , Turkey.
Taner
T
Kar
a Department of Ophthalmology , Gulhane Military Medical Academy Haydarpasa Training Hospital , Uskudar , Istanbul , Turkey.
Abdullah
A
Kaya
a Department of Ophthalmology , Gulhane Military Medical Academy Haydarpasa Training Hospital , Uskudar , Istanbul , Turkey.
Eyup
E
Düzgun
a Department of Ophthalmology , Gulhane Military Medical Academy Haydarpasa Training Hospital , Uskudar , Istanbul , Turkey.
Yildiray
Y
Yildirim
D000328:Adult; D004396:Coloring Agents / Q000008:administration & dosage; D004359:Drug Therapy, Combination; D005451:Fluorescein Angiography; D005938:Glucocorticoids / Q000627:therapeutic use; D006801:Humans; D007166:Immunosuppressive Agents / Q000627:therapeutic use; D007208:Indocyanine Green / Q000008:administration & dosage; D008297:Male; D011239:Prednisolone / Q000627:therapeutic use; D011282:Pregnenediones / Q000627:therapeutic use; D012164:Retinal Diseases / Q000175:diagnosis* / Q000188:drug therapy / Q000503:physiopathology; D016706:Still's Disease, Adult-Onset / Q000175:diagnosis* / Q000188:drug therapy / Q000503:physiopathology; D041623:Tomography, Optical Coherence
D004396:Coloring Agents; D005938:Glucocorticoids; D007166:Immunosuppressive Agents; D011282:Pregnenediones; D011239:Prednisolone; D007208:Indocyanine Green; C021988:deflazacort
Adult-onset Still’s disease; Purtscher’s-like retinopathy; Yamaguchi; corticosteroids; microangiopathy