Segmental lesions along blaschko´s lines in an elderly man.
Darier disease (DD) is an autosomal dominant genodermatosis characterized by multiple keratotic and crusted papules over seborrheic areas, along with a variable involvement of oral mucosa, palmoplantar region, and nails. Segmental subtypes (type 1 and 2) are uncommon clinically limited forms of DD that usually present at middle age with few cutaneous lesions following Blaschko´s lines. We report a case of extensive multi segmental DD type 1 that developed in an elderly man, an unusual clinical onset of DD that dermatologists should bear in mind.
Department of Dermatology, Hospital 12 de Octubre, Madrid, Spain. Fatimatousro@gmail.com.
Fátima
F
Tous Romero
Sara
S
Burillo Martinez
Carlos
C
Raya-Morales
Vanessa
V
Gargallo-Moneva
Lidia
L
Maroñas-Jiménez
D000005:Abdomen; D007644:Darier Disease / Q000175:diagnosis / Q000188:drug therapy / Q000473:pathology*; D006801:Humans; D007641:Keratolytic Agents / Q000627:therapeutic use; D007868:Leg Dermatoses / Q000175:diagnosis / Q000188:drug therapy / Q000473:pathology*; D008297:Male; D008875:Middle Aged; D012867:Skin / Q000473:pathology*; D014212:Tretinoin / Q000627:therapeutic use
D007641:Keratolytic Agents; D014212:Tretinoin