A case of Mac Tel 2 with an unusual sub macular vitelliform lesion.
METHODS
Observational case report describing the clinical, FFA, OCT and mfERG findings in an elderly female patient with atypical features of macular telangiectasia (Mac Tel 2) RESULTS: A 71-year-old lady was detected to have characteristic features of Mac Tel 2 in the left eye (LE) and a yellowish sub macular vitelliform like lesion in the right eye (RE). FFA showed ill defined hyper fluorescence in the RE and telangiectasia and parafoveal leakage typical of Mac Tel 2 in the LE. On OCT RE had hyper reflective clump of echoes subfoveally with an intact RPE and LE had foveal thinning with hypo reflective intraretinal cavities. mfERG responses were normal in the RE and reduced in the LE. During the course of 3 years LE showed natural progression while RE remained unchanged.


CONCLUSIONS
Structural and functional evaluation of an unusual sub macular vitelliform lesion seen in association with Mac Tel 2 and its course over a period of 3 years is described. The differentiating features of this lesion from adult onset foveomacular vitelliform dystrophy (AFMD) are discussed.
Department of Ophthalmology, PSG Institute of Medical Sciences and Research, Coimbatore, Tamilnadu, India.
T
T
Lekha
Retina Services, The Eye Foundation, Coimbatore, Tamilnadu, India.
Nikit
N
Sarwate
Retina Services, The Eye Foundation, Coimbatore, Tamilnadu, India.
Renuka
R
Sarwate
Mac Tel 2; mfERG; optical coherence tomography; vitelliform lesion