title: Dental treatment of a patient with Opitz G/BBB syndrome.
abstract: Opitz G/BBB syndrome is a genetic condition characterized by several abnormalities along the midline of the body, such as hypertelorism, craniofacial deformities, and dysphagia. This study reports the clinical features of Optiz syndrome and its importance in the knowledge of patients who are developmentally challenged as a whole, in order to establish adequate dental treatment for a certain clinical case. A 19-year-old patient visited the Paulista University for a dental treatment. The extraoral examination revealed ocular hypertelorism (wide-spaced eyes), oblique eyelids, epicanthus, low-set cart, and intellectual disability. During the intraoral examination, large caries lesions were observed surrounding the braces of the fixed orthodontic appliance and poor oral hygiene. Preventive and restorative treatments were carried out. It was concluded that the knowledge of patients with special needs as a whole is mandatory for an adequate dental treatment. This is a case report that highlights the importance of dentist and interdisciplinary care attendance for all patient systems, the examination and analyses should not be restricted to the oral cavity.
authors.affiliation: Chairman, Professor, Integrated Clinic Discipline, Coordinator of Center for Studies and Special Service for Patients, Professor, Postgraduate Dentistry Courses, UNIP, São Paulo, SP, Brazil.
authors.forename: Élcio Magdalena
authors.initials: ÉM
authors.lastname: Giovani
authors.affiliation: Associate Professor, UNIP, São Paulo, SP, Brazil.
authors.forename: Kelly Cristine Tarquinio
authors.initials: KC
authors.lastname: Marinho
authors.affiliation: Associate Professor, Integrated Clinic and Center for Studies and Special Service for Patients, UNIP, São Paulo, SP, Brazil.
authors.forename: Ruth
authors.initials: R
authors.lastname: Andia-Merlin
mesh_terms: D017742:Dental Care for Chronically Ill; D004947:Esophagus / Q000002:abnormalities*; D005260:Female; D006801:Humans; D006972:Hypertelorism / Q000150:complications*; D007021:Hypospadias / Q000150:complications*; D055815:Young Adult
keywords: Opitz G/BBB syndrome; dental treatment; pathology