title: Pulmonary Hypertension in a Patient With Congenital Heart Defects and Heterotaxy Syndrome.
abstract: BACKGROUND
  Heterotaxy syndrome, also called isomerism, is a condition in which abdominal and thoracic organs are located in abnormal body positions. Pulmonary hypertension (PHTN) is an uncommon clinical feature of heterotaxy syndrome.
  
  
  METHODS
  We describe the case of a 26-year-old male who developed PHTN as a rare manifestation of heterotaxy syndrome. To our knowledge, PHTN has never been reported as a prominent clinical feature in a patient with heterotaxy syndome and congenital cardiac abnormalities.
  
  
  CONCLUSIONS
  It is important for the clinician to be aware of potentially serious consequences of PHTN in the setting of heterotaxy syndrome.
authors.affiliation: Department of Internal Medicine, Advocate Christ Medical Center, Oak Lawn, IL.
authors.forename: Tariq
authors.initials: T
authors.lastname: Yousuf
authors.affiliation: Rosalind Franklin University of Medicine and Science, Chicago, IL.
authors.forename: Jason
authors.initials: J
authors.lastname: Kramer
authors.affiliation: Rosalind Franklin University of Medicine and Science, Chicago, IL.
authors.forename: Brody
authors.initials: B
authors.lastname: Jones
authors.affiliation: Department of Internal Medicine, Advocate Christ Medical Center, Oak Lawn, IL.
authors.forename: Hesam
authors.initials: H
authors.lastname: Keshmiri
authors.affiliation: Department of Cardiology, Advocate Christ Medical Center, Oak Lawn, IL.
authors.forename: Muhyaldeen
authors.initials: M
authors.lastname: Dia
keywords: Heterotaxy syndrome; hypertension–pulmonary; isomerism