Osteomyelitis of Maxilla in Infantile Osteopetrosis: A Case Report with Review of Literature.
Osteopetrosis is a rare genetic disorder that causes generalized sclerosis of bone due to a defect in bone resorption and remodeling. It is usually manifesting in two basic forms: An autosomal dominant benign form (osteopetrosis tarda) and an autosomal recessive malignant form (osteopetrosis congenita). A third form, the intermediate recessive type, has also been reported. Dental abnormality may be attributed to pathological changes in bone remodeling. Osteomyelitis is well documented as a complication of osteopetrosis and is severe and difficult to treat. This is a case of 8-year-old boy with osteopetrosis presenting with the complaint of swelling of left side of face.
Professor and Head, Department of Oral Medicine and Radiology, Government Dental College, Thiruvananthapuram, Kerala, India.
Anita
A
Balan
Lecturer, Department of Oral Medicine and Radiology, Government Dental College, Thiruvananthapuram, Kerala, India.
K L
KL
Girija
Postgraduate Student, Department of Oral Medicine and Radiology, Government Dental College, Thiruvananthapuram, Kerala, India.
P
P
Ranimol
Osteomyelitis; Osteopetrosis.
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