Hemisacrectomy with preservation of the contralateral sacral nerve roots and sacroiliac joint for pelvic neurofibrosarcoma in a 7-year-old child: case report with 2-year follow-up.
Neurofibrosarcoma is rare in the pediatric age group. A malignant tumor of the sacrum presents significant challenges, especially if the goals are to resect with wide and clean surgical margins and to achieve acceptable functional outcomes. The authors report a case of this rare tumor affecting the sacrum and sacral nerve roots of a 7-year-old girl and review the role of total hemisacrectomy sparing the contralateral sacral nerve roots and lumbopelvic reconstruction in the treatment of this disease. This patient is, to the best of the authors' knowledge, the youngest to be treated in this manner.
Neuro-Spine Program, Division of Pediatric Neurosurgery.
Ali H
AH
Palejwala
Neuro-Spine Program, Division of Pediatric Neurosurgery.
Jared S
JS
Fridley
Neuro-Spine Program, Division of Pediatric Neurosurgery.
Krystal
K
Garcia
Division of Pediatric Surgery.
Sanjeev A
SA
Vasudevan
Division of Pediatric Plastic Surgery, Texas Children's Hospital.
David
D
Khechoyan
Division of Pediatric Hematology/Oncology, Texas Children's Cancer Center.
Surya
S
Rednam
Division of Pediatric Urology, Texas Children's Hospital, Houston, Texas; and.
Chester J
CJ
Koh
Neuro-Spine Program, Division of Pediatric Neurosurgery.|Section of Pediatric Neurosurgery, Riley Hospital for Children, Indiana University School of Medicine Department of Neurosurgery, Indianapolis, Indiana.
Andrew
A
Jea
D002648:Child; D005260:Female; D005500:Follow-Up Studies; D006801:Humans; D018319:Neurofibrosarcoma / Q000000981:diagnostic imaging / Q000601:surgery*; D010384:Pelvic Bones / Q000000981:diagnostic imaging / Q000601:surgery*; D019651:Plastic Surgery Procedures / Q000379:methods*; D012446:Sacroiliac Joint / Q000000981:diagnostic imaging / Q000601:surgery*; D012447:Sacrum / Q000000981:diagnostic imaging / Q000601:surgery*; D013126:Spinal Nerve Roots / Q000000981:diagnostic imaging / Q000601:surgery*
MPNST = malignant peripheral nerve sheath tumor; UTI = urinary tract infection; hemisacrectomy; neurofibrosarcoma; oncology; pediatric spine; sacral tumor; sacrectomy