Severe malnutrition causing superior mesenteric artery syndrome in an adolescent with Triple A syndrome.
Triple A syndrome, formerly known as Allgrove syndrome (AS), is characterized by achalasia, alacrima and adrenal insufficiency. Here we report an adolescent male with adrenal insufficiency who developed severe malnutrition secondary to a delayed diagnosis of achalasia. The severe malnutrition in our patient led to superior mesenteric artery (SMA) obstruction syndrome. Severe malnutrition to the point of SMA syndrome has not been previously described in the literature in Triple A syndrome.
Christy
C
Foster
Abha
A
Choudhary
D000293:Adolescent; D000309:Adrenal Insufficiency / Q000150:complications* / Q000473:pathology / Q000503:physiopathology; D002648:Child; D004931:Esophageal Achalasia / Q000503:physiopathology*; D006801:Humans; D008297:Male; D044342:Malnutrition / Q000150:complications* / Q000473:pathology; D011379:Prognosis; D013478:Superior Mesenteric Artery Syndrome / Q000209:etiology* / Q000473:pathology / Q000628:therapy