Progressive idiopathic tractional corectopia with iris thinning.
A 2-month-old boy presented with an irregular left pupil. Over the course of 3 months, progressive pupil ovalization, corectopia, and ballooning of the thinned superior iris tissue caused obstruction of the visual axis. Because of concern for deprivational amblyopia, a sectoral pupilloplasty and sphincterotomies were performed, restoring pupil shape and clearing the visual axis. On postoperative examinations, the pupil remained round, the visual axis clear, and visual acuity of the left eye improved. Findings and clinical course suggested the diagnosis of idiopathic tractional corectopia, a rare congenital disorder of unknown cause that may lead to isolated unilateral progressive corectopia and visual axis obstruction. Patients should receive regular follow-up examinations.
Charité - University of Medicine Berlin, Department of Ophthalmology, Berlin, Germany; Berlin Institute of Health (BIH), Kapelle-Ufer 2, 10117 Berlin, Germany. Electronic address: tobias.brockmann@charite.de.
Tobias
T
Brockmann
Charité - University of Medicine Berlin, Department of Ophthalmology, Berlin, Germany.
Mirjam
M
Rossel
Charité - University of Medicine Berlin, Department of Ophthalmology, Berlin, Germany.
Daniel J
DJ
Salchow
D005124:Eye Abnormalities / Q000175:diagnosis* / Q000601:surgery; D006801:Humans; D007223:Infant; D007498:Iris / Q000002:abnormalities*; D008297:Male; D013508:Ophthalmologic Surgical Procedures; D011681:Pupil Disorders / Q000175:diagnosis* / Q000601:surgery