title: Atypical Arteritis in Internal Carotid Arteries: A Novel Concept of Isolated Internal Carotid Arteritis.
abstract: We presented a 38-year-old woman suffering from acute cerebral infarction due to arteritis limited to bilateral internal carotid arteries without a condition of giant cell arteritis or granulomatosis with polyangitis. Our case is unprecedented and characterized by a young woman with wall enhancement in the internal carotid arteries on contrast-enhanced magnetic resonance imaging (MRI), therapeutic effects of steroids, and positive status for human leucocyte antigen-B39, -B51 and -DR4. These disease characteristics were not in accordance with existing diagnostic criteria of vasculitis, such as Takayasu's arteritis, giant cell arteritis, granulomatosis with polyangiitis, and Behcet's disease. We suggested consideration of a novel "isolated internal carotid arteritis" disease concept.
authors.affiliation: Division of Neurology, Department of Brain and Neurosciences, Tottori University Faculty of Medicine, Yonago 683-8504, Japan.
authors.forename: Kazuki
authors.initials: K
authors.lastname: Fukuma
authors.affiliation: Division of Neurology, Department of Brain and Neurosciences, Tottori University Faculty of Medicine, Yonago 683-8504, Japan.
authors.forename: Hisanori
authors.initials: H
authors.lastname: Kowa
authors.affiliation: †Department of Neurology, Tottori Prefectural Central Hospital, Tottori 680-0901, Japan.
authors.forename: Hiroyuki
authors.initials: H
authors.lastname: Nakayasu
authors.affiliation: ‡Department of Neurology, National Hospital Organization Matsue Medical Center, Matsue 690-8556, Japan.
authors.forename: Kenji
authors.initials: K
authors.lastname: Nakashima
keywords: arteritis; carotid artery; internal; magnetic resonance imaging; vasculitis