title: Bronchoscopic concerns in Proteus syndrome: a case report.
abstract: Proteus syndrome (PS) is a rare congenital hamartomatous disorder with multisystem involvement. PS shows highly clinical variability due to overgrowth of the affected areas, and several features can make anesthetic management challenging. Little is known about the airway problem associated with anesthesia in PS patients. An 11-year-old girl with PS was scheduled for ear surgery under general anesthesia. She had features complicating intubation including facial asymmetry and disproportion, abnormal teeth, limitation of neck movement due to torticollis, and thoracolumbar scoliosis. This study reports on a case of deformed airway of a PS patient under fiberoptic bronchoscopy.
authors.affiliation: Department of Anesthesia and Pain Medicine, Pusan National University Hospital, Busan, Korea.; Department of Anesthesia and Pain Medicine, Pusan National University Hospital, Busan, Korea.
authors.forename: Jung-Min
authors.initials: JM
authors.lastname: Hong
authors.affiliation: Department of Anesthesia and Pain Medicine, Pusan National University Hospital, Busan, Korea.; Department of Anesthesia and Pain Medicine, Pusan National University Hospital, Busan, Korea.
authors.forename: Hyeon Jeong
authors.initials: HJ
authors.lastname: Lee
authors.affiliation: Department of Anesthesia and Pain Medicine, Pusan National University Hospital, Busan, Korea.; Department of Anesthesia and Pain Medicine, Pusan National University Hospital, Busan, Korea.
authors.forename: Eun Soo
authors.initials: ES
authors.lastname: Kim
authors.affiliation: Department of Anesthesia and Pain Medicine, Pusan National University Hospital, Busan, Korea.; Department of Anesthesia and Pain Medicine, Pusan National University Hospital, Busan, Korea.
authors.forename: Hae-Kyu
authors.initials: HK
authors.lastname: Kim
authors.affiliation: Department of Anesthesia and Pain Medicine, Pusan National University Hospital, Busan, Korea.; Department of Anesthesia and Pain Medicine, Pusan National University Hospital, Busan, Korea.
authors.forename: Soeun
authors.initials: S
authors.lastname: Jeon
authors.affiliation: Department of Anesthesia and Pain Medicine, Pusan National University Hospital, Busan, Korea.; Department of Anesthesia and Pain Medicine, Pusan National University Hospital, Busan, Korea.
authors.forename: Hyae-Jin
authors.initials: HJ
authors.lastname: Kim
keywords: Difficult intubation; Hamartomatous disorder; Proteus syndrome