title: Dermato-neuro syndrome in a case of scleromyxedema.
abstract: Scleromyxedema is an uncommon connective tissue disease characterized by mucin deposits, fibrosis, and proliferation of fibroblasts in the dermis. Although it shares similar sclerodermoid features, it is a different clinical entity than scleroderma. A monoclonal gammopathy is almost always present; however, progression to multiple myeloma is rare. It may have many systemic manifestations, of which the most notable being the dermato-neuro syndrome because of its rarity and potential fatal outcome. We present a case of a 50-year-old woman with scleromyxedema in whom the dermato-neuro syndrome developed.
authors.affiliation: Department of Internal Medicine, Dokuz Eylül University Faculty of Medicine, İzmir, Turkey.
authors.forename: Yusuf
authors.initials: Y
authors.lastname: Savran
authors.affiliation: Department of Dermatology, Dokuz Eylül University Faculty of Medicine, İzmir, Turkey.
authors.forename: Sevgi
authors.initials: S
authors.lastname: Akarsu
keywords: Scleromyxedema; connective tissue; dermato-neuro syndrome