title: Pleomorphic Hyalinizing Angiectatic Tumor Arising in the Hand: A Case Report.
abstract: Background:Background: Pleomorphic hyalinizing angiectatic tumors (PHATs) are extremely rare, non-metastasizing tumors of uncertain origin that are typically seen in the lower extremities. To date, it is estimated that less than 100 cases have been reported worldwide since first described in 1996.Methods:The case of a 35-year-old male with a several-year history of a dorsal hand mass is presented. Although the patient was initially asymptomatic, in the months prior to presentation, the patient complained of pain with power grasp and direct pressure over the mass. The patient underwent uncomplicated surgical excision, during which the mass was noted to be adherent to the underlying extensor tendons.Results:Immunopathology confirmed the mass to be PHAT. We believe this is the first documented case of this rare tumor occurring in the hand.Conclusions:History and epidemiology of PHAT are reviewed. Then, in the context of the presented case, pre-operative evaluation, surgical management, pathologic findings and post-operative follow-up are all discussed.
authors.affiliation: The Philadelphia Hand Center, Philadelphia PA, USA.
authors.forename: Patrick M
authors.initials: PM
authors.lastname: Kane
authors.affiliation: The Philadelphia Hand Center, Philadelphia PA, USA.
authors.forename: Michael P
authors.initials: MP
authors.lastname: Gaspar
authors.affiliation: The Philadelphia Hand Center, Philadelphia PA, USA.
authors.forename: Benjamin B
authors.initials: BB
authors.lastname: Whiting
authors.affiliation: The Philadelphia Hand Center, Philadelphia PA, USA.
authors.forename: Randall W
authors.initials: RW
authors.lastname: Culp
mesh_terms: D000328:Adult; D006225:Hand / Q000000981:diagnostic imaging / Q000473:pathology / Q000601:surgery; D006801:Humans; D008297:Male; D012983:Soft Tissue Neoplasms / Q000000981:diagnostic imaging / Q000473:pathology / Q000601:surgery
keywords: hand; mass; pleomorphic hyalinizing angiectatic tumor