title: Congenitally unguarded tricuspid valve orifice with right ventricular apical isolation in an adult.
abstract: Congenitally unguarded tricuspid valve (TV) orifice, a variant of TV dysplasia, is a rare malformation with protean manifestations. This report describes a symptomatic adult male with gross right heart failure and atrial fibrillation, who was found to have an unguarded TV orifice with isolation of the trabecular apical cavity of the right ventricle (RV) and muscular ridges separating outflow tract (forme-fruste of the double-chambered RV). The right ventricular outflow tract remained patent.
authors.affiliation: Department of Cardiology, Fortis Hospital, Shalimar Bagh, New Delhi 88, India. Electronic address: a51hauzkhas@gmail.com.
authors.forename: Jagdish C
authors.initials: JC
authors.lastname: Mohan
authors.affiliation: Department of Cardiology, Fortis Hospital, Shalimar Bagh, New Delhi 88, India.
authors.forename: Madhu
authors.initials: M
authors.lastname: Shukla
authors.affiliation: Department of Cardiology, Fortis Hospital, Shalimar Bagh, New Delhi 88, India.
authors.forename: Vishwas
authors.initials: V
authors.lastname: Mohan
authors.affiliation: Department of Cardiology, Fortis Hospital, Shalimar Bagh, New Delhi 88, India.
authors.forename: Arvind
authors.initials: A
authors.lastname: Sethi
mesh_terms: D000328:Adult; D001281:Atrial Fibrillation / Q000209:etiology; D004452:Echocardiography; D004562:Electrocardiography; D006330:Heart Defects, Congenital / Q000150:complications / Q000175:diagnosis / Q000000981:diagnostic imaging*; D006333:Heart Failure / Q000209:etiology; D006352:Heart Ventricles / Q000000981:diagnostic imaging*; D006801:Humans; D008297:Male; D014261:Tricuspid Valve / Q000002:abnormalities*
keywords: Congenitally unguarded tricuspid orifice; Right heart failure; Right ventricular apical isolation