title: Parachute mitral valve and Pacman deformity of the ventricular septum in a middle-aged male.
abstract: Parachute mitral valve and Pacman heart (incomplete muscular ventricular septal defect) are rare congenital deformities usually reported in infants and children. Very few adult patients with these anomalies are reported but the association of the two has not been described. This report describes a 56-year-old male with exertional dyspnea who was detected to have moderately severe mitral regurgitation and mitral stenosis. Typical parachute deformity of the mitral valve with a reduced opening and common attachment of all the chordae to a single posteromedial papillary muscle was evident. The chordae were elongated, lax, and redundant, which is atypical for this anomaly. Incidentally, detected aneurysm of the basal muscular interventricular septum (Pacman deformity or incomplete triangular septal defect) was also present.
authors.affiliation: Director, Department of Cardiac Sciences, Fortis Hospital, Shalimar Bagh, Delhi 110088, India. Electronic address: a51hauzkhas@gmail.com.
authors.forename: Jagdish C
authors.initials: JC
authors.lastname: Mohan
authors.affiliation: Clinical Associates, Fortis Hospital, Shalimar Bagh, Delhi 110088, India.
authors.forename: Madhu
authors.initials: M
authors.lastname: Shukla
authors.affiliation: Clinical Associates, Fortis Hospital, Shalimar Bagh, Delhi 110088, India.
authors.forename: Vishwas
authors.initials: V
authors.lastname: Mohan
authors.affiliation: Consultant, India.
authors.forename: Arvind
authors.initials: A
authors.lastname: Sethi
mesh_terms: D004417:Dyspnea / Q000209:etiology; D006345:Heart Septal Defects, Ventricular / Q000150:complications / Q000000981:diagnostic imaging*; D006801:Humans; D008297:Male; D008875:Middle Aged; D008943:Mitral Valve / Q000002:abnormalities* / Q000000981:diagnostic imaging; D008944:Mitral Valve Insufficiency / Q000209:etiology; D054088:Ventricular Septum / Q000000981:diagnostic imaging
keywords: Mitral regurgitation; Pacman heart; Parachute mitral valve