title: [Spontaneous Infection of an Atrophic Ureter with an Ectopic Ureteral Opening after Living-Donor Renal Transplantation in a Patient with Kabuki Syndrome].
abstract: A 24-year-old woman with a high fever presented at our hospital. She had been diagnosed with Kabuki syndrome at the age of 4 years because she had the typical facial features of the condition ; she had undergone living donor renal transplantation 12 years prior. She was prescribed a course of antibiotics to treat pyelonephritis of the transplanted kidney and the high fever disappeared, but the fever developed again 3 days after the discharge. Abdominal computed tomography revealed a tubular structure of recent onset running from the left dorsal side to the lower part of the bladder. This structure was filled with pus, which we drained. We also performed laparoscopic ureterectomy of the left ureter to achieve a complete cure. No complication was observed after the surgery and the graft renal function did not deteriorate further.
authors.affiliation: The Department of Urology, Shizuoka General Hospital.
authors.forename: Naoki
authors.initials: N
authors.lastname: Kohei
authors.affiliation: The Department of Urology, Shizuoka General Hospital.
authors.forename: Hideaki
authors.initials: H
authors.lastname: Takada
authors.affiliation: The Department of Urology, Shizuoka General Hospital.
authors.forename: Kosuke
authors.initials: K
authors.lastname: Hishiki
authors.affiliation: The Department of Urology, Shizuoka General Hospital.
authors.forename: Yoshiharu
authors.initials: Y
authors.lastname: Nakashima
authors.affiliation: The Department of Urology, Shizuoka General Hospital.
authors.forename: Koji
authors.initials: K
authors.lastname: Yoshimura
authors.affiliation: The Department of Urology, Shizuoka General Hospital.
authors.forename: Yasunori
authors.initials: Y
authors.lastname: Nishio
authors.affiliation: The Department of Nephrology, Shizuoka General Hospital.
authors.forename: Kenta
authors.initials: K
authors.lastname: Ito
authors.affiliation: The Department of Nephrology, Shizuoka General Hospital.
authors.forename: Ken
authors.initials: K
authors.lastname: Matsuo
authors.affiliation: The Department of Nephrology, Shizuoka General Hospital.
authors.forename: Noriko
authors.initials: N
authors.lastname: Mori
mesh_terms: D000015:Abnormalities, Multiple; D000900:Anti-Bacterial Agents / Q000627:therapeutic use; D004927:Escherichia coli Infections / Q000188:drug therapy; D005145:Face / Q000002:abnormalities*; D005260:Female; D006402:Hematologic Diseases / Q000150:complications*; D006801:Humans; D016030:Kidney Transplantation; D019520:Living Donors; D011704:Pyelonephritis / Q000188:drug therapy* / Q000382:microbiology; D014513:Ureter; D015837:Vestibular Diseases / Q000150:complications*; D055815:Young Adult
chemical_list: D000900:Anti-Bacterial Agents
keywords: Ectopic ureteral opening; Kabuki syndrome; Ureteral stump