title: Recurrent Cholangitis in a Patient with Autosomal Dominant Polycystic Kidney Disease (ADPKD) and Caroli's Disease.
abstract: We herein present a rare case of an autosomal dominant polycystic kidney disease (ADPKD) patient with Caroli's disease, a congenital embryonic biliary tree ductal plate abnormality often associated with autosomal recessive polycystic kidney disease. A 76-year-old woman with ADPKD on hemodialysis was admitted to our hospital with recurrent cholangitis and hepatobiliary stones. Caroli's disease was diagnosed according to typical imaging findings of cystic intrahepatic bile duct dilatation and the central dot sign. Hepatobiliary system abnormalities such as Caroli's disease should be considered in febrile ADPKD patients, even in the absence of typical clinical signs or symptoms.
authors.affiliation: Nephrology Center, Toranomon Hospital, Japan.
authors.forename: Eiko
authors.initials: E
authors.lastname: Hasegawa
authors.forename: Naoki
authors.initials: N
authors.lastname: Sawa
authors.forename: Junichi
authors.initials: J
authors.lastname: Hoshino
authors.forename: Tatsuya
authors.initials: T
authors.lastname: Suwabe
authors.forename: Noriko
authors.initials: N
authors.lastname: Hayami
authors.forename: Masayuki
authors.initials: M
authors.lastname: Yamanouchi
authors.forename: Akinari
authors.initials: A
authors.lastname: Sekine
authors.forename: Rikako
authors.initials: R
authors.lastname: Hiramatsu
authors.forename: Aya
authors.initials: A
authors.lastname: Imafuku
authors.forename: Masahiro
authors.initials: M
authors.lastname: Kawada
authors.forename: Yoshifumi
authors.initials: Y
authors.lastname: Ubara
authors.forename: Tsunao
authors.initials: T
authors.lastname: Imamura
authors.forename: Kenmei
authors.initials: K
authors.lastname: Takaichi
mesh_terms: D000368:Aged; D016767:Caroli Disease / Q000150:complications* / Q000000981:diagnostic imaging / Q000628:therapy; D002761:Cholangitis / Q000175:diagnosis / Q000209:etiology* / Q000628:therapy; D005260:Female; D006801:Humans; D016891:Polycystic Kidney, Autosomal Dominant / Q000150:complications* / Q000175:diagnosis / Q000628:therapy; D012008:Recurrence; D006435:Renal Dialysis