title: Pancreatic Neuroendocrine Tumor in the Setting of Dorsal Agenesis of the Pancreas.
abstract: Dorsal agenesis of the pancreas (DAP) is an uncommon embryological abnormality where there is absence of the distal pancreas. DAP is mostly asymptomatic, but common presenting symptoms include diabetes mellitus, abdominal pain, pancreatitis, enlarged pancreatic head, and, in a few cases, polysplenia. MRCP and ERCP are the gold standard imaging techniques to demonstrate the absence of the dorsal pancreatic duct. The literature on the association of pancreatic neoplasia and DAP is limited. We present the case of a pancreatic neuroendocrine tumor in a patient with dorsal agenesis of the pancreas, with a review of the related literature.
authors.affiliation: Boston University School of Medicine, 72 East Concord St., Boston, MA 02118, USA.
authors.forename: Samih
authors.identifier: 0000-0001-9557-0302
authors.initials: S
authors.lastname: Nassif
authors.affiliation: Department of Pathology and Laboratory Medicine, Boston University School of Medicine, 72 East Concord St., Boston, MA 02118, USA.
authors.forename: Cecilia
authors.identifier: 0000-0002-6793-1892
authors.initials: C
authors.lastname: Ponchiardi
authors.affiliation: Boston University School of Medicine, Moakley Building, 3rd Floor, 830 Harrison Avenue, Boston, MA 02118, USA.
authors.forename: Teviah
authors.identifier: 0000-0002-8560-3606
authors.initials: T
authors.lastname: Sachs