title: [Distal pancreatectomy as surgical option in Pancreas divisum associated with Rubinstein-Taybi syndrome].
abstract: BACKGROUND
  The Rubinstein-Taybi syndrome and pancreas divisum are uncommon diseases in children. The Rubinstein-Taybi syndrome diagnosis is only clinical, and mental retardation and dysmorphic features mainly characterize it. The PD relates to idiopathic pancreatitis in 7.5% of patients suffering from this disorder. It has not been found any cases reported where these diseases are associated and the management of patients with pancreatitis associated with PD is still a challenge.
  
  
  METHODS
  A patient diagnosed with Rubinstein-Taybi syndrome has recurrent abdominal pain of six months and elevated pancreatic enzymes, he underwent a magnetic resonance imaging where pancreas divisum is suspected. Endoscopic drainage was foiled so he underwent intraoperative retrograde pancreatography where aberrant pancreas is confirmed and a distal pancreactectomy and yeyunopancreatic anastomosis is the chosen option.
  
  
  CONCLUSIONS
  The pancreatectomy with pancreato-jejunal anastomosis is an excellent therapeutic option surgical is proposed for a patient with difficulty endoscopic approach and chronic pancreatitis.
authors: Hospital Nacional Docente Madre Niño San Bartolomé. Lima, Perú.
authors: H
authors: H
authors: Delgado Bartra
authors: Hospital Nacional Docente Madre Niño San Bartolomé. Lima, Perú.
authors: F M
authors: FM
authors: Lapouble Ramírez
authors: Universidad de Caldas. Caldas, Colombia.
authors: J
authors: J
authors: Bonilla Pabón
authors: Universidad Peruana de Ciencias Aplicadas. Lima, Perú.
authors: S T
authors: ST
authors: Vega Centeno
keywords: Cholangiography; Chronic pancreatitis; Pancreatectomy; Rubinstein-Taybi Syndrome