title: Erdheim-Chester Disease Presenting as a Solid Renal Mass.
abstract: Erdheim-Chester disease is a rare, systemic histiocytic disorder, usually presenting due to bone manifestations. The most commonly seen urologic manifestation is retroperitoneal fibrosis, leading to ureteral obstruction. We describe a patient with a solid right renal mass, initially concerning for renal cell carcinoma, in addition to diffuse retroperitoneal fibrosis and a chronically obstructed left kidney. The renal mass and retroperitoneal fibrosis are thought to be caused by Erdheim-Chester disease based on imaging findings and biopsy results.
authors: Department of Urology, University of Virginia Health System, Charlottesville, VA. Electronic address: mbc7cr@virginia.edu.
authors: Matthew B
authors: MB
authors: Clements
authors: Department of Urology, University of Virginia Health System, Charlottesville, VA.
authors: Jacques
authors: J
authors: Farhi
authors: Department of Urology, University of Virginia Health System, Charlottesville, VA.
authors: Noah S
authors: NS
authors: Schenkman
mesh_terms: D031249:Erdheim-Chester Disease / Q000150:complications / Q000000981:diagnostic imaging*; D005260:Female; D006801:Humans; D007674:Kidney Diseases / Q000000981:diagnostic imaging* / Q000209:etiology*; D008875:Middle Aged; D014057:Tomography, X-Ray Computed