An Autopsy Case of Aortic Intimal Sarcoma Initially Diagnosed as Polyarteritis Nodosa.
A 61-year-old man had hypertension with stenosis in the left renal artery. When his fever, abdominal pain, and renal dysfunction progressed, he was admitted to our hospital. He was diagnosed with polyarthritis nodosa. His renal function rapidly deteriorated despite immunosuppressive therapy. His digestive tract perforated twice, and he subsequently died. An autopsy revealed that aortic intimal sarcoma caused stenosis in multiple arteries. Both polyarteritis nodosa and aortic intimal sarcoma are very rare diseases and the diagnoses are very difficult. It is very important to consider these entities when making a differential diagnosis of vasculitis.
Department of Respiratory Medicine and Rheumatology, Institute of Biomedical Sciences, Tokushima University Graduate School, Japan.
Yuko
Y
Toyoda
Ryohiko
R
Ozaki
Jun
J
Kishi
Masaki
M
Hanibuchi
Katsuhiro
K
Kinoshita
Toshifumi
T
Tezuka
Hisatsugu
H
Goto
Hiroyuki
H
Ono
Kojiro
K
Nagai
Yoshimi
Y
Bando
Toshio
T
Doi
Yasuhiko
Y
Nishioka
D015746:Abdominal Pain / Q000209:etiology; D001011:Aorta / Q000473:pathology; D001344:Autopsy; D003937:Diagnosis, Differential; D017809:Fatal Outcome; D005334:Fever / Q000209:etiology; D006801:Humans; D008297:Male; D008875:Middle Aged; D010488:Polyarteritis Nodosa / Q000175:diagnosis; D012078:Renal Artery Obstruction / Q000150:complications / Q000175:diagnosis* / Q000473:pathology; D012509:Sarcoma / Q000150:complications / Q000175:diagnosis* / Q000473:pathology; D019043:Vascular Neoplasms / Q000150:complications / Q000175:diagnosis* / Q000473:pathology