[Ectopic craniopharyngioma and Gardner's syndrome: Case report and literature review].
BACKGROUND
Craniopharyngioma accounts for around 3% of all primary tumours of the central nervous system. It is usually located in the suprasellar region, although it may also have an ectopic location.


METHODS
The case is presented on 29 year-old male who underwent surgery for a jaw osteoma when he was 19 years old and was subsequently diagnosed with Gardner's syndrome. He was admitted in our Hospital with right facial paresis and diplopia of one day onset. The examination showed mild right VII and VI cranial nerves paresis. Magnetic resonance imaging of the brain demonstrated a rounded solid and cystic lesion with well-defined contours of about 2cm in diameter filling the fourth ventricle. The patient underwent a posterior fossa craniotomy using a telovelar approach with complete removal of the tumour implanted at roof level of the fourth ventricle. The final histology of the tumour was reported as adamantinomatous craniopharyngioma.


CONCLUSIONS
Craniopharyngioma may appear in another location other than the suprasellar region. Its atypical location may be related to Gardner syndrome by still unknown pathogenic mechanisms.
Servicio de Neurocirugía, Hospital Virgen de la Salud, Toledo, España. Electronic address: alvsalju1@gmail.com.
Juan Antonio
JA
Álvarez Salgado
Servicio de Neurocirugía, Hospital Virgen de la Salud, Toledo, España.
Francisco
F
González-Llanos Fernández de Mesa
Servicio de Neurocirugía, Hospital Virgen de la Salud, Toledo, España.
Jorge Javier
JJ
Villaseñor Ledezma
Servicio de Neurocirugía, Hospital Virgen de la Salud, Toledo, España.
Maria de Los Angeles
ML
Cañizares Méndez
Servicio de Neurocirugía, Hospital Universitario 12 de Octubre, Madrid, España.
Igor
I
Paredes Sansinenea
Servicio de Neurocirugía, Hospital Virgen de la Salud, Toledo, España.
Angel
A
Rodríguez de Lope-Llorca
Servicio de Anatomía Patológica, Hospital Virgen de la Salud, Toledo, España.
Manuela
M
Mollejo Villanueva
D000328:Adult; D002551:Cerebral Ventricle Neoplasms / Q000150:complications / Q000000981:diagnostic imaging / Q000235:genetics* / Q000601:surgery; D003397:Craniopharyngioma / Q000150:complications / Q000000981:diagnostic imaging / Q000235:genetics* / Q000601:surgery; D003399:Craniotomy; D004172:Diplopia / Q000209:etiology; D005158:Facial Paralysis / Q000209:etiology; D020546:Fourth Ventricle; D005736:Gardner Syndrome / Q000175:diagnosis*; D006801:Humans; D008279:Magnetic Resonance Imaging; D008297:Male; D008339:Mandibular Neoplasms / Q000235:genetics; D059906:Neuroimaging; D010016:Osteoma / Q000235:genetics
Craneofaringioma de cuarto ventrículo; Craneofaringioma ectópico; Ectopic craniopharyngioma; Familial adenomatous polyposis; Fourth ventricle craniopharyngioma; Gardner's syndrome; Poliposis adenomatosa familiar; Síndrome de Gardner