Extramammary Paget Disease of the Vulva - Case Report.
Extramammary Paget disease (EPD) is a rare malign neoplasm that may affect the vulva and has manifestations common to benign diseases such as itching, pain and eczema. This leads to delay in diagnosis and consequent worse prognosis. The definitive diagnosis is obtained by biopsy of the vulva, which shows Paget cells. The treatment of choice is wide excision with margins, which leads to sequelae, functional and aesthetic. Recurrence is common. This article reports the case of a 48-year-old female patient with history of vulvar itching for the past 2 years, who had been submitted to various treatments for benign pathologies. The patient was biopsied and was diagnosed with extensive EPD, being submitted to vulvectomy. This article aims to draw attention to the need for biopsy of pruritic vulvar lesions that do not respond to usual treatment.
Department of Gynecology and Obstetrics, Residency Program of the Hospital Universitário Professor Polydoro Ernani de São Thiago, Florianópolis, SC, Brazil.
Bianca Ruschel
BR
Hillmann
Department of Pathology, Residency Program of the Hospital Universitário Professor Polydoro Ernani de São Thiago, Florianópolis, SC, Brazil.
Amanda Amaro
AA
Pereira
Department of Gynecology and Obstetrics, Health Sciences Center, Universidade Federal de Santa Catarina, Florianópolis, SC, Brazil.
Luiz Fernando
LF
Sommacal
D005260:Female; D006801:Humans; D008875:Middle Aged; D010145:Paget Disease, Extramammary / Q000473:pathology / Q000601:surgery; D014846:Vulvar Neoplasms / Q000473:pathology / Q000601:surgery