Spontaneous omental bleeding in a 20-year old patient with hemophilia A. A rare cause for emergency laparotomy.
Spontaneous intraabdominal hemorrhage is a very rare event even in patients with bleeding disorders like hemophilia. Nevertheless this rare case must be considered in patients with coagulopathies presenting with abdominal pain. Prompt radiologic imaging and surgical consultation are of highest priority. Here we report on a 20-year-old patient with moderate hemophilia A, who underwent emergency laparotomy for a spontaneous idiopathic bleeding of the omentum majus. There are few cases in the literature on this sort of event in patients with hemophilia, who mostly suffer from spontaneous joint bleedings. These patients require an intensive, interdisciplinary perioperative care, involving haematologists, surgeons, radiologists and anesthesists. Finally we discuss, whether an optimized, individually adapted treatment with coagulation factors might possibly have prevented this bleeding event in this patient.
Dr. Volker Aumann, Dept. of Pediatrics, University Hospital, Leipziger Str. 44, 39120 Magdeburg, Germany, Tel. +49/(0)391/672-41 90, Fax -42 52, Email: Volker.Aumann@med.ovgu.de.
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V
Aumann
C
C
Chiapponi
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F
Meyer
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C
Wybranski
C J
CJ
Bruns
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O
Jannasch
D003937:Diagnosis, Differential; D004632:Emergency Medical Services / Q000379:methods; D006467:Hemophilia A / Q000150:complications* / Q000175:diagnosis / Q000601:surgery*; D006470:Hemorrhage / Q000175:diagnosis / Q000209:etiology* / Q000601:surgery*; D006801:Humans; D007813:Laparotomy / Q000379:methods*; D008297:Male; D009852:Omentum / Q000601:surgery*; D010532:Peritoneal Diseases / Q000175:diagnosis / Q000209:etiology / Q000601:surgery*; D016896:Treatment Outcome; D055815:Young Adult
Hemophilia A; intraabdominal bleeding; laparotomy