Desmoplastic fibroma of the mandible in young children-a case series.
Desmoplastic fibromas are rare, benign, but aggressive lesions, affecting predominantly young people, with an affinity for the mandible. Four patients with desmoplastic fibromas of the mandible, seen between 1995 and 2015 with long-term follow-up, were identified. Three were treated by wide mandibular resection and immediate reconstruction with rib grafts, and one was treated with chemotherapy. In the three resected cases, there has been no recurrence and all rib grafts were successfully incorporated. The case treated by chemotherapy has persistence of the tumour, but it is not progressing. Desmoplastic fibromas in young children respond well to wide mandibular resection and immediate reconstruction with rib grafts. Chemotherapy may halt progression.
Oral and Maxillofacial Surgery, University of California San Francisco, San Francisco, CA, USA.
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Khatib
Oral and Maxillofacial Surgery, University of California San Francisco, San Francisco, CA, USA. Electronic address: tony.pogrel@ucsf.edu.
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Pogrel
D001706:Biopsy; D002648:Child; D003937:Diagnosis, Differential; D005260:Female; D018220:Fibroma, Desmoplastic / Q000000981:diagnostic imaging* / Q000601:surgery*; D006801:Humans; D007223:Infant; D008297:Male; D008339:Mandibular Neoplasms / Q000000981:diagnostic imaging* / Q000601:surgery*; D019651:Plastic Surgery Procedures
benign tumour of jaws; desmoplastic fibroma; jaw tumours in children