title: The Abernethy malformation-myriad imaging manifestations of a single entity.
abstract: Abernethy malformation, also known as congenital extrahepatic portosystemic shunts (CEPS) is a rare clinical entity and manifests with different clinical symptoms. CEPS are abnormalities of vascular development where there is shunting of portal blood into the systemic venous system. Multidetector computed tomography (MDCT) is a fast and effective modality for evaluation of CEPS. CT displays all the information desired by the surgeon as well as the clinician including the anatomy of the splenic and superior mesenteric veins, size and site of the shunt, presence or absence of the portal vein radicles, and helps to plan the therapy and even the follow-up of these patients. Contrast-enhanced magnetic resonance imaging (MRI) has also emerged as a promising tool for the evaluation of liver lesions associated with the malformation. The Radiologist should be aware of the various imaging appearances of this entity including its complications. In this article, we describe the imaging appearances of CEPS, their complications, and their imaging appearances on CT and MRI. We have also described various associated anomalies.
authors.affiliation: Department of Radiodiagnosis, Sir Gangaram Hospital, New Delhi, India.
authors.forename: Samarjit S
authors.initials: SS
authors.lastname: Ghuman
authors.affiliation: Department of Radiodiagnosis, Sir Gangaram Hospital, New Delhi, India.
authors.forename: Saumya
authors.initials: S
authors.lastname: Gupta
authors.affiliation: Department of Radiodiagnosis, Sir Gangaram Hospital, New Delhi, India.
authors.forename: T B S
authors.initials: TB
authors.lastname: Buxi
authors.affiliation: Department of Radiodiagnosis, Sir Gangaram Hospital, New Delhi, India.
authors.forename: Kishan S
authors.initials: KS
authors.lastname: Rawat
authors.affiliation: Department of Radiodiagnosis, Sir Gangaram Hospital, New Delhi, India.
authors.forename: Anurag
authors.initials: A
authors.lastname: Yadav
authors.affiliation: Department of Surgical Gastroenterology, Sir Gangaram Hospital, New Delhi, India.
authors.forename: Naimish
authors.initials: N
authors.lastname: Mehta
authors.affiliation: Department of Radiodiagnosis, Sir Gangaram Hospital, New Delhi, India.
authors.forename: Seema
authors.initials: S
authors.lastname: Sud
keywords: Abernethy malformation; congenital extrahepatic portosystemic shunts; portosystemic shunts