title: Entire syringomyelia associated with Chiari II malformation and severe scoliosis and hydrocephalus.
abstract: BACKGROUND
  The syrinx can occur in any region of the spinal cord and is common in cervical and/or thoracic region, and distributing along spinal cord is unusual, especially association with Chiari II malformation and scoliosis.
  
  
  OBJECTIVE
  To report a first case of entire syringomyelia associated with Chiari II malformation and severe scoliosis and hydrocephalus.
  
  
  METHODS
  The patient began to experience symptoms of bilateral hand weakness in adulthood. In this patient, MR imaging of the brain and spine showed syrinx along entire spine and hydrocephalus, cerebellar tonsillar herniation, and expansion of the fourth ventricle and posterior cranial fossa. The patient underwent operative treatment to prevent the progression of her neurological deficit. At 12 months' follow-up, the patient's neurological deficit remains stable with the scoliosis left untreated.
  
  
  CONCLUSIONS
  Foramen magnum decompression, duraplasty and syrinx-shunting are effective methods even to CM II and entire syrinx.
authors.forename: Jie
authors.initials: J
authors.lastname: Liang
authors.forename: Weifei
authors.initials: W
authors.lastname: Wu
authors.forename: Neng
authors.initials: N
authors.lastname: Ru
authors.forename: Jianfeng
authors.initials: J
authors.lastname: Chen
mesh_terms: D000328:Adult; D001139:Arnold-Chiari Malformation / Q000150:complications* / Q000000981:diagnostic imaging; D019299:Decompression, Surgical / Q000379:methods*; D018450:Disease Progression; D006801:Humans; D006849:Hydrocephalus / Q000150:complications* / Q000000981:diagnostic imaging; D008279:Magnetic Resonance Imaging; D008297:Male; D012600:Scoliosis / Q000150:complications* / Q000000981:diagnostic imaging; D013123:Spinal Fusion / Q000379:methods*; D013595:Syringomyelia / Q000150:complications* / Q000000981:diagnostic imaging; D016896:Treatment Outcome
keywords: Chiari II malformation; Entire syringomyelia; hydrocephalus; severe scoliosis