title: Steroid Responsive Mononeuritis Multiplex in the Cronkhite-Canada Syndrome.
abstract: The Cronkhite-Canada syndrome (CCS) is a rare disorder of unknown origin characterized by generalized gastrointestinal polyposis, alopecia, hyperpigmentation, and onychodystrophy. We report a case of CCS with concomitant presentation of mononeuritis multiplex. The electrophysiological findings and steroid responsiveness suggests presence of an autoimmune mechanism.
authors.affiliation: Department of Neurology, National Neuroscience Institute, Singapore General Hospital, Singapore; Due-NUS Medical School, Singapore.
authors.forename: Y L
authors.initials: YL
authors.lastname: Lo
authors.affiliation: Department of Anatomical Pathology, Singapore General Hospital , Singapore.
authors.forename: K H
authors.initials: KH
authors.lastname: Lim
authors.affiliation: Department of Anatomical Pathology, Singapore General Hospital , Singapore.
authors.forename: X M
authors.initials: XM
authors.lastname: Cheng
authors.affiliation: Department of Gastroenterology and Hepatology, Singapore General Hospital , Singapore.
authors.forename: S
authors.initials: S
authors.lastname: Mesenas
keywords: Cronkhite–Canada syndrome; autoimmune; mononeuritis multiplex; neuropathy; steroids