title: [A Case of an Abdominal Desmoplastic Small Round Cell Tumor with Metastasis in the Medulla Oblongata].
abstract: A desmoplastic small round cell tumor(DSRCT)is a very rare malignant tumor that mainly occurs in the intra-abdominal cavity in young adults.This neoplasm has an extremely poor prognosis, with a clinical course characterized by rapid progression and metastasis.We present a 31-year-old man who presented with chief complaints of dysphagia, ataxic gait, and hoarseness.He first underwent surgical resection of a tumor in the medulla oblongata; however, the lesion was suspected to be a metastatic neoplasm.Following a thorough medical examination, the patient was diagnosed with retroperitoneal DSRCT with multiple metastatic lesions.He received multidisciplinary treatment including debulking surgery for the primary lesion; radiotherapy for metastatic lesions in the brain, abdomen, and cervical lymph nodes; hepatic artery embolization for liver metastasis; and systemic chemotherapy.The patient died of progressive disease 17 months after the initial diagnosis.
authors.affiliation: Dept. of Surgery, Southern Tohoku General Hospital.
authors.forename: Ayaka
authors.initials: A
authors.lastname: Azami
authors.forename: Yoshinao
authors.initials: Y
authors.lastname: Takano
authors.forename: Michitaka
authors.initials: M
authors.lastname: Honda
authors.forename: Yukitoshi
authors.initials: Y
authors.lastname: Todate
authors.forename: Takeshi
authors.initials: T
authors.lastname: Tada
authors.forename: Mitsuru
authors.initials: M
authors.lastname: Waragai
authors.forename: Daizo
authors.initials: D
authors.lastname: Fukushima
authors.forename: Nobuyasu
authors.initials: N
authors.lastname: Suzuki
authors.forename: Atai
authors.initials: A
authors.lastname: Sato
authors.forename: Tsuyoshi
authors.initials: T
authors.lastname: Abe
authors.forename: Yasushi
authors.initials: Y
authors.lastname: Teranishi
authors.forename: Hideo
authors.initials: H
authors.lastname: Sakuma
mesh_terms: D000008:Abdominal Neoplasms / Q000000981:diagnostic imaging / Q000473:pathology / Q000628:therapy*; D000328:Adult; D001932:Brain Neoplasms / Q000556:secondary* / Q000601:surgery; D003131:Combined Modality Therapy; D058405:Desmoplastic Small Round Cell Tumor / Q000000981:diagnostic imaging / Q000628:therapy*; D017809:Fatal Outcome; D006801:Humans; D008279:Magnetic Resonance Imaging; D008297:Male; D008526:Medulla Oblongata / Q000601:surgery*; D064847:Multimodal Imaging; D014057:Tomography, X-Ray Computed