title: Radical resection and improvised surgical reconstruction for a rare malignant triton tumour of intercostal nerve in a patient with neurofibromatosis type 1.
abstract: A man aged 28 years, with neurofibromatosis type 1, presented with abdominal pain and visible right lower chest swelling. He had cutaneous neurofibromas and several café-au-lait spots. CT scan of the chest and abdomen revealed a giant mass most likely originating from the right 7th intercostal nerve, extending downwards into the abdomen causing massive hepatic compression. A Trucut biopsy showed malignant peripheral nerve sheath tumour. Radical surgical resection with wide margins was performed. The chest wall and diaphragm were reconstructed with improvised surgical technique with excellent results. Final histopathology report revealed a triton tumour of the intercostal nerve.
authors.affiliation: Department of Chest Surgery, King Fahad Specialist Hospital, Dammam, Saudi Arabia.
authors.forename: Ikram Ulhaq
authors.initials: IU
authors.lastname: Chaudhry
authors.affiliation: Division of Thoracic Surgery, King Fahad Specialist Hospital, Dammam, Saudi Arabia.
authors.forename: Ahsan Iqbal
authors.initials: AI
authors.lastname: Cheema
authors.affiliation: Department of Thoracic Surgery, King Fahad Specialist Hospital, Dammam, Saudi Arabia.
authors.forename: Hadi
authors.initials: H
authors.lastname: Mutari
authors.affiliation: Department of Pathology and Laboratory Medicine, King Fahad Specialist Hospital, Dammam, Saudi Arabia.
authors.forename: Samir S
authors.initials: SS
authors.lastname: Amr
mesh_terms: D000328:Adult; D001706:Biopsy; D006801:Humans; D007367:Intercostal Nerves; D008297:Male; D018317:Nerve Sheath Neoplasms / Q000150:complications / Q000175:diagnosis / Q000601:surgery*; D009456:Neurofibromatosis 1 / Q000150:complications* / Q000175:diagnosis; D019616:Thoracic Surgical Procedures / Q000379:methods*; D014057:Tomography, X-Ray Computed