title: Emergency Difficult Airway Management in a Patient with Severe Epidermolysis Bullosa.
abstract: Epidermolysis bullosa (EB) is a rare disease characterised by vesiculobullous lesions with minimal trauma to the skin and mucous membranes. Bleeding, scar tissue, contractures, oedema and lesions that can spread throughout the body can cause a difficult airway and vascular access in patients with EB. Therefore, anaesthetic management in patients with EB is a major problem even for experienced anaesthesiologists. Herein, we report a case of difficult airway management in a patient diagnosed with severe EB who presented for emergency tracheostomy because of respiratory failure under general anaesthesia.
authors.affiliation: Department of Anaesthesiology and Reanimation, İnönü University School of Medicine, Malatya, Turkey.
authors.forename: Ahmet Selim
authors.initials: AS
authors.lastname: Özkan
authors.affiliation: Department of Anaesthesiology and Reanimation, İnönü University School of Medicine, Malatya, Turkey.
authors.forename: Gülay Erdoğan
authors.initials: GE
authors.lastname: Kayhan
authors.affiliation: Department of Anaesthesiology and Reanimation, İnönü University School of Medicine, Malatya, Turkey.
authors.forename: Sedat
authors.initials: S
authors.lastname: Akbaş
authors.affiliation: Department of Anaesthesiology and Reanimation, İnönü University School of Medicine, Malatya, Turkey.
authors.forename: Osman
authors.initials: O
authors.lastname: Kaçmaz
authors.affiliation: Department of Anaesthesiology and Reanimation, İnönü University School of Medicine, Malatya, Turkey.
authors.forename: Mahmut
authors.initials: M
authors.lastname: Durmuş
keywords: Epidermolysis bullosa; difficult airway; nasal fiberoptic intubation