title: Two Rare Vascular Rings With Ductal Origin of the Left Pulmonary Artery: A Previously Unrecognized Syndrome?
abstract: We report two neonates with distal ductal origin of the left pulmonary artery who also had rare vascular rings comprised of a left aortic arch and right arterial duct with a midline/rightward descending aorta. To the best of our knowledge, this association has not previously been described, although other abnormalities of the left pulmonary artery in the setting of vascular rings have been reported. We review the embryology, utility of imaging, and clinical course.
authors.affiliation: 1 Division of Pediatric Cardiology, UT Southwestern Medical Center, Dallas, TX, USA.
authors.forename: Poonam P
authors.initials: PP
authors.lastname: Thankavel
authors.affiliation: 2 Department of Cardiovascular and Thoracic Surgery, UT Southwestern Medical Center, Dallas, TX, USA.
authors.forename: Kristine J
authors.initials: KJ
authors.lastname: Guleserian
authors.affiliation: 3 Institute of Genetic Medicine, Newcastle University, Newcastle, United Kingdom.
authors.forename: Robert H
authors.initials: RH
authors.lastname: Anderson
mesh_terms: D017809:Fatal Outcome; D005260:Female; D006801:Humans; D007231:Infant, Newborn; D007234:Infant, Premature; D008297:Male; D011651:Pulmonary Artery / Q000002:abnormalities* / Q000000981:diagnostic imaging; D013577:Syndrome; D054079:Vascular Malformations / Q000000981:diagnostic imaging* / Q000601:surgery; D000073872:Vascular Ring / Q000000981:diagnostic imaging* / Q000601:surgery
keywords: congenital heart disease; patent arterial duct; pulmonary artery abnormalities; vascular ring