title: Pediatric living donor liver transplantation for congenital hepatic fibrosis using a mother's graft with von Meyenburg complex: A case report.
abstract: This is the first report of living donor liver transplantation (LDLT) for congenital hepatic fibrosis (CHF) using a mother's graft with von Meyenburg complex. A 6-year-old girl with CHF, who suffered from recurrent gastrointestinal bleeding, was referred to our hospital for liver transplantation. Her 38-year-old mother was investigated as a living donor and multiple biliary hamartoma were seen on her computed tomography and magnetic resonance imaging scan. The mother's liver function tests were normal and she did not have any organ abnormality, including polycystic kidney disease. LDLT using the left lateral segment (LLS) graft from the donor was performed. The donor LLS graft weighed 250 g; the graft recipient weight ratio was 1.19%. The operation and post-operative course of the donor were uneventful and she was discharged on post-operative day (POD) 8. The graft liver function was good, and the recipient was discharged on POD 31. LDLT using a graft with von Meyenburg complex is safe and useful. Long-term follow-up is needed with respect to graft liver function and screening malignant tumors.
authors.affiliation: Naoya Yamada, Yukihiro Sanada, Takumi Katano, Masahisa Tashiro, Yuta Hirata, Noriki Okada, Yoshiyuki Ihara, Taizen Urahashi, Koichi Mizuta, Department of Transplant Surgery, Jichi Medical University, Shimotsuke-shi, Tochigi 329-0498, Japan.
authors.forename: Naoya
authors.initials: N
authors.lastname: Yamada
authors.affiliation: Naoya Yamada, Yukihiro Sanada, Takumi Katano, Masahisa Tashiro, Yuta Hirata, Noriki Okada, Yoshiyuki Ihara, Taizen Urahashi, Koichi Mizuta, Department of Transplant Surgery, Jichi Medical University, Shimotsuke-shi, Tochigi 329-0498, Japan.
authors.forename: Yukihiro
authors.initials: Y
authors.lastname: Sanada
authors.affiliation: Naoya Yamada, Yukihiro Sanada, Takumi Katano, Masahisa Tashiro, Yuta Hirata, Noriki Okada, Yoshiyuki Ihara, Taizen Urahashi, Koichi Mizuta, Department of Transplant Surgery, Jichi Medical University, Shimotsuke-shi, Tochigi 329-0498, Japan.
authors.forename: Takumi
authors.initials: T
authors.lastname: Katano
authors.affiliation: Naoya Yamada, Yukihiro Sanada, Takumi Katano, Masahisa Tashiro, Yuta Hirata, Noriki Okada, Yoshiyuki Ihara, Taizen Urahashi, Koichi Mizuta, Department of Transplant Surgery, Jichi Medical University, Shimotsuke-shi, Tochigi 329-0498, Japan.
authors.forename: Masahisa
authors.initials: M
authors.lastname: Tashiro
authors.affiliation: Naoya Yamada, Yukihiro Sanada, Takumi Katano, Masahisa Tashiro, Yuta Hirata, Noriki Okada, Yoshiyuki Ihara, Taizen Urahashi, Koichi Mizuta, Department of Transplant Surgery, Jichi Medical University, Shimotsuke-shi, Tochigi 329-0498, Japan.
authors.forename: Yuta
authors.initials: Y
authors.lastname: Hirata
authors.affiliation: Naoya Yamada, Yukihiro Sanada, Takumi Katano, Masahisa Tashiro, Yuta Hirata, Noriki Okada, Yoshiyuki Ihara, Taizen Urahashi, Koichi Mizuta, Department of Transplant Surgery, Jichi Medical University, Shimotsuke-shi, Tochigi 329-0498, Japan.
authors.forename: Noriki
authors.initials: N
authors.lastname: Okada
authors.affiliation: Naoya Yamada, Yukihiro Sanada, Takumi Katano, Masahisa Tashiro, Yuta Hirata, Noriki Okada, Yoshiyuki Ihara, Taizen Urahashi, Koichi Mizuta, Department of Transplant Surgery, Jichi Medical University, Shimotsuke-shi, Tochigi 329-0498, Japan.
authors.forename: Yoshiyuki
authors.initials: Y
authors.lastname: Ihara
authors.affiliation: Naoya Yamada, Yukihiro Sanada, Takumi Katano, Masahisa Tashiro, Yuta Hirata, Noriki Okada, Yoshiyuki Ihara, Taizen Urahashi, Koichi Mizuta, Department of Transplant Surgery, Jichi Medical University, Shimotsuke-shi, Tochigi 329-0498, Japan.
authors.forename: Atsushi
authors.initials: A
authors.lastname: Miki
authors.affiliation: Naoya Yamada, Yukihiro Sanada, Takumi Katano, Masahisa Tashiro, Yuta Hirata, Noriki Okada, Yoshiyuki Ihara, Taizen Urahashi, Koichi Mizuta, Department of Transplant Surgery, Jichi Medical University, Shimotsuke-shi, Tochigi 329-0498, Japan.
authors.forename: Hideki
authors.initials: H
authors.lastname: Sasanuma
authors.affiliation: Naoya Yamada, Yukihiro Sanada, Takumi Katano, Masahisa Tashiro, Yuta Hirata, Noriki Okada, Yoshiyuki Ihara, Taizen Urahashi, Koichi Mizuta, Department of Transplant Surgery, Jichi Medical University, Shimotsuke-shi, Tochigi 329-0498, Japan.
authors.forename: Taizen
authors.initials: T
authors.lastname: Urahashi
authors.affiliation: Naoya Yamada, Yukihiro Sanada, Takumi Katano, Masahisa Tashiro, Yuta Hirata, Noriki Okada, Yoshiyuki Ihara, Taizen Urahashi, Koichi Mizuta, Department of Transplant Surgery, Jichi Medical University, Shimotsuke-shi, Tochigi 329-0498, Japan.
authors.forename: Yasunaru
authors.initials: Y
authors.lastname: Sakuma
authors.affiliation: Naoya Yamada, Yukihiro Sanada, Takumi Katano, Masahisa Tashiro, Yuta Hirata, Noriki Okada, Yoshiyuki Ihara, Taizen Urahashi, Koichi Mizuta, Department of Transplant Surgery, Jichi Medical University, Shimotsuke-shi, Tochigi 329-0498, Japan.
authors.forename: Koichi
authors.initials: K
authors.lastname: Mizuta
mesh_terms: D001649:Bile Duct Diseases / Q000150:complications / Q000175:diagnosis*; D001706:Biopsy; D002648:Child; D046148:Donor Selection; D005260:Female; D030342:Genetic Diseases, Inborn / Q000175:diagnosis / Q000601:surgery*; D006085:Graft Survival; D006222:Hamartoma / Q000150:complications / Q000175:diagnosis*; D006801:Humans; D008103:Liver Cirrhosis / Q000175:diagnosis / Q000601:surgery*; D008111:Liver Function Tests; D016031:Liver Transplantation / Q000379:methods*; D019520:Living Donors; D008279:Magnetic Resonance Imaging; D009035:Mothers; D011237:Predictive Value of Tests; D012307:Risk Factors; D013997:Time Factors; D014057:Tomography, X-Ray Computed; D016896:Treatment Outcome
keywords: Congenital hepatic fibrosis; Living donor liver transplantation; Pediatric liver transplantation; Von Meyenburg complex