title: Adenoid cystic carcinoma of the lacrimal sac: case report.
abstract: Lacrimal sac tumors are rare with a clinical presentation that typically includes obstruction of the lacrimal drainage system and epiphora as the most frequent symptom. Cribriform adenoid cystic carcinoma (ACC) is the most common malignant epithelial tumor of the lacrimal gland and minor salivary glands; however, its occurrence in the lacrimal drainage apparatus is extremely rare. Given the rarity of ACC, definitive diagnosis is almost invariably late conferring a poor prognosis. Herein we report the case of a 41-year-old woman with primary ACC of the lacrimal sac and describe the ophthalmological examination, diagnosis, and multidisciplinary treatment of this rare type of tumor.
authors.affiliation: Department of Ophthalmology, Costa del Sol Hospital, Marbella, Malaga, Spain.
authors.forename: Antonio
authors.initials: A
authors.lastname: Ramos
authors.affiliation: Department of Ophthalmology, Costa del Sol Hospital, Marbella, Malaga, Spain.
authors.forename: Carmen Del
authors.initials: CD
authors.lastname: Pozo
authors.affiliation: Department of Ophthalmology, Costa del Sol Hospital, Marbella, Malaga, Spain.
authors.forename: Ana
authors.initials: A
authors.lastname: Chinchurreta
authors.affiliation: Department of Ophthalmology, Costa del Sol Hospital, Marbella, Malaga, Spain.
authors.forename: Fernando
authors.initials: F
authors.lastname: García
authors.affiliation: Department of Ophthalmology, Costa del Sol Hospital, Marbella, Malaga, Spain.
authors.forename: Mercedes
authors.initials: M
authors.lastname: Lorenzo
authors.affiliation: Department of Ophthalmology, Costa del Sol Hospital, Marbella, Malaga, Spain.
authors.forename: Saturnino
authors.initials: S
authors.lastname: Gismero
mesh_terms: D000328:Adult; D003528:Carcinoma, Adenoid Cystic / Q000473:pathology* / Q000628:therapy; D005134:Eye Neoplasms / Q000473:pathology* / Q000628:therapy; D005260:Female; D006801:Humans; D007766:Lacrimal Apparatus Diseases / Q000473:pathology* / Q000628:therapy; D008279:Magnetic Resonance Imaging / Q000379:methods; D009301:Nasolacrimal Duct / Q000473:pathology*