title: Sturge-Weber syndrome type 3 manifesting as 'Status migrainosus'.
abstract: Sturge-Weber syndrome (SWS) is a rare neurocutaneous syndrome characterised by facial naevus and leptomeningeal angiomatosis resulting in neurological and ophthalmological complications. In its rare variant, SWS type 3, the clinical hallmark of facial naevus is absent which poses a diagnostic challenge. Here, we present an interesting case of SWS type 3 where a child presented twice with prolonged severe unilateral headache mimicking migraine status followed on both occasions with focal seizures. He developed a dense right-sided homonymous hemianopia, and an urgent brain MRI scan was performed which pointed towards the diagnosis of SWS type 3.
authors.affiliation: Department of Paediatrics, University Hospitals of Leicester NHS Trust, Leicester, UK.
authors.forename: Philip Richard
authors.initials: PR
authors.lastname: Jordan
authors.affiliation: Department of Paediatric Neurology, University Hospital of Leicester NHS Trust, Leicester, UK.
authors.forename: Mehtab
authors.initials: M
authors.lastname: Iqbal
authors.affiliation: Department of Paediatrics, Nottingham University Hospitals Trust, Nottingham, UK.
authors.forename: Manish
authors.initials: M
authors.lastname: Prasad
mesh_terms: D001921:Brain / Q000000981:diagnostic imaging*; D002648:Child; D003937:Diagnosis, Differential; D006801:Humans; D008279:Magnetic Resonance Imaging / Q000379:methods*; D008297:Male; D008881:Migraine Disorders / Q000000981:diagnostic imaging* / Q000209:etiology; D013341:Sturge-Weber Syndrome / Q000150:complications / Q000175:diagnosis*