title: Multifocal Kaposiform Hemangioendothelioma Causing Massive Fetal Chylous Ascites.
abstract: Kaposiform hemangioendothelioma (KHE) is a locally aggressive vascular tumor that usually occurs in soft tissues of the extremity and rarely in the retroperitoneum. We report a unique case of isolated massive fetal ascites attributed to KHE, involving the retroperitoneum and multiple visceral organs, along with the Kasabach-Merritt phenomenon. We suspect that retroperitoneal KHE might have caused massive fetal ascites because of its high potential to invade the lymphatic vessels aggressively in the retroperitoneal space, which possibly permits intestinal lymph leakage into the peritoneal cavities.
authors.affiliation: a Department of Pathology , College of Medicine, Inje University Busan Paik Hospital , Busan , Republic of Korea.
authors.forename: Hyo Jung
authors.initials: HJ
authors.lastname: An
authors.affiliation: b Department of Obstetrics and Gynecology , College of Medicine, Inje University Busan Paik Hospital , Busan , Republic of Korea.
authors.forename: Eun Jung
authors.initials: EJ
authors.lastname: Jung
authors.affiliation: a Department of Pathology , College of Medicine, Inje University Busan Paik Hospital , Busan , Republic of Korea.
authors.forename: Mi Seon
authors.initials: MS
authors.lastname: Kang
authors.affiliation: a Department of Pathology , College of Medicine, Inje University Busan Paik Hospital , Busan , Republic of Korea.
authors.forename: Hwa Jin
authors.initials: HJ
authors.lastname: Cho
authors.affiliation: c Department of Pathology , College of Medicine, Inje University, Haeundae Paik Hospital , Busan , Republic of Korea.
authors.forename: Kyung Han
authors.initials: KH
authors.lastname: Nam
authors.affiliation: b Department of Obstetrics and Gynecology , College of Medicine, Inje University Busan Paik Hospital , Busan , Republic of Korea.|d Paik Institute for Clinical Research, College of Medicine, Busan Paik Hospital , Busan , Republic of Korea.
authors.forename: Jung Mi
authors.initials: JM
authors.lastname: Byun
authors.affiliation: b Department of Obstetrics and Gynecology , College of Medicine, Inje University Busan Paik Hospital , Busan , Republic of Korea.|d Paik Institute for Clinical Research, College of Medicine, Busan Paik Hospital , Busan , Republic of Korea.
authors.forename: Dae Hoon
authors.initials: DH
authors.lastname: Jeong
authors.affiliation: b Department of Obstetrics and Gynecology , College of Medicine, Inje University Busan Paik Hospital , Busan , Republic of Korea.|d Paik Institute for Clinical Research, College of Medicine, Busan Paik Hospital , Busan , Republic of Korea.
authors.forename: Young Nam
authors.initials: YN
authors.lastname: Kim
mesh_terms: D000328:Adult; D002915:Chylous Ascites / Q000175:diagnosis / Q000209:etiology / Q000473:pathology*; D017809:Fatal Outcome; D005260:Female; D005315:Fetal Diseases / Q000175:diagnosis / Q000473:pathology; D005333:Fetus / Q000473:pathology; D006390:Hemangioendothelioma / Q000150:complications / Q000175:diagnosis / Q000473:pathology*; D006801:Humans; D059885:Kasabach-Merritt Syndrome / Q000150:complications / Q000175:diagnosis / Q000473:pathology*; D011247:Pregnancy; D012514:Sarcoma, Kaposi / Q000150:complications / Q000175:diagnosis / Q000473:pathology*
keywords: Fetal ascites; chylous ascites; kaposiform hemangioendothelioma