title: Raised intracranial pressure as a result of pansynostosis in a child with Albright's hereditary osteodystrophy.
abstract: METHODS
  The authors describe the case of an 8-year-old boy with pansynostosis in the context of Albright's hereditary osteodystrophy (AHO). This condition had lead to raised intracranial pressure (ICP). The elevated ICP was a consequence of the rigid skull impeding brain growth. Therefore, a decompressive cranioplasty was performed successfully, leaving further space for the growing brain. Affection of the central nervous system has been documented in AHO. However, affection of the skull bones has rarely been described in literature.
  
  
  CONCLUSIONS
  We suggest that craniosynostosis may develop in patients with AHO and other types of pseudohypoparathyroidism (PHP). Furthermore, we suggest regular head circumference-for-age and ophthalmic examination for children with AHO or other types of PHP.
authors.affiliation: Department of Neurosurgery, Aalborg University Hospital, Hobrovej 18-22, 9000, Aalborg, Denmark. Mamoi@outlook.com.
authors.forename: Sepehr
authors.initials: S
authors.lastname: Mamoei
authors.affiliation: Department of Neurosurgery, Aalborg University Hospital, Hobrovej 18-22, 9000, Aalborg, Denmark.
authors.forename: Søren
authors.initials: S
authors.lastname: Cortnum
mesh_terms: D002648:Child; D003398:Craniosynostoses / Q000150:complications / Q000000981:diagnostic imaging* / Q000601:surgery; D006801:Humans; D019586:Intracranial Hypertension / Q000000981:diagnostic imaging* / Q000209:etiology / Q000601:surgery; D007427:Intracranial Pressure / Q000502:physiology; D008297:Male; D011547:Pseudohypoparathyroidism / Q000150:complications / Q000000981:diagnostic imaging* / Q000601:surgery
keywords: Cranioplasty; Genetics; Intracranial pressure; Pediatric; Synostosis