title: Dental and Anaesthetic Challenges in a Patient with Dystrophic Epidermolysis Bullosa.
abstract: Epidermolysis bullosa is a group of rare genetic disorders characterised by skin and mucous membrane fragility and systemic manifestations of variable severity. We report a case of dystrophic epidermolysis bullosa in an 18-year-old male patient who presented to the Department of Oral Health at Sultan Qaboos University Hospital, Muscat, Oman, in 2015 with recurrent dental pain and infections. Due to the poor dental status of the patient and anticipated operative difficulties due tomicrostomiaand limited mouth opening, the patient underwent full dental clearance under general anaesthesia. This article discusses the dental and anaesthetic challenges encountered during the management of this patient and provides a brief literature review.
authors.affiliation: Department of Anaesthesia & ICU, Sultan Qaboos University Hospital, Muscat, Oman.
authors.forename: Ali
authors.initials: A
authors.lastname: Al-Abadi
authors.affiliation: Oral & Maxillofacial Surgery Residency Program, Oman Medical Specialty Board, Muscat, Oman.
authors.forename: Salah A
authors.initials: SA
authors.lastname: Al-Azri
authors.affiliation: Department of Oral Health, Sultan Qaboos University Hospital, Muscat, Oman.
authors.forename: Abdulaziz
authors.initials: A
authors.lastname: Bakathir
authors.affiliation: Oral & Maxillofacial Surgery Residency Program, Oman Medical Specialty Board, Muscat, Oman.
authors.forename: Yusra
authors.initials: Y
authors.lastname: Al-Riyami
keywords: Case Report; Dentistry; Disease Management; Dystrophic Epidermolysis Bullosa; General Anesthesia; Oman