title: Blastic Plasmocytoid Dendritic Cell Neoplasm With Skin and Myeloid Location.
abstract: Blastic plasmocytoid dendritic cell neoplasm is one of the aggressive hematopoietic malignancy with predilection for the skin. It is a tumor derived from the plasmocytoid dendritic precursor cells. Skin is its most common location; however, it may also affect bone marrow, lymph nodes, or spleen. The condition is rarely diagnosed in children; so far only 36 cases have been reported. The diagnosis usually takes time and there are no uniform treatment guidelines. This paper presents a case of a 6-year-old boy with blastic plasmocytoid dendritic cell neoplasm (skin and myeloid location). He has been treated according to the acute lymphoblastic leukemia treatment protocol.
authors.affiliation: Department of Pediatric Oncology, Haematology and Chemotherapy, Upper Silesia Children's Care Health Centre, Medical University of Silesia, Katowice, Poland.
authors.forename: Agnieszka
authors.initials: A
authors.lastname: Mizia-Malarz
authors.forename: Grażyna
authors.initials: G
authors.lastname: Sobol-Milejska
mesh_terms: D001752:Blast Crisis; D019046:Bone Marrow Neoplasms / Q000473:pathology*; D002648:Child; D003713:Dendritic Cells / Q000473:pathology; D003937:Diagnosis, Differential; D019337:Hematologic Neoplasms / Q000473:pathology*; D006801:Humans; D008297:Male; D009361:Neoplasm Invasiveness; D010954:Plasmacytoma / Q000473:pathology; D054198:Precursor Cell Lymphoblastic Leukemia-Lymphoma / Q000188:drug therapy; D012074:Remission Induction; D012878:Skin Neoplasms / Q000473:pathology*