title: A Rare Case of an Adult with Untreated Bladder Exstrophy Presenting with Signet-Ring Cell Adenocarcinoma of Urinary Bladder.
abstract: Untreated bladder exstrophy in an adult is rare, as the defect is obvious and primary reconstruction is usually done in infancy. There are less than 90 reported cases of primary adenocarcinoma in an untreated bladder exstrophy in literature and only two such case reports from India. Of these, only one case was of signet-ring cell type of mucinous adenocarcinoma. Here we report the second case of signet-ring cell adenocarcinoma in a 63 year old male with untreated bladder exstrophy (oldest patient in literature), to highlight the extreme rarity, yet distinct possibility and challenges faced in surgical management of such cases.
authors.affiliation: Resident, Department of Urology, LTMGH and LTMMC , Sion, Mumbai, Maharashtra, India .
authors.forename: Abhishek J
authors.initials: AJ
authors.lastname: Savalia
authors.affiliation: Associate Professor, Department of Urology, LTMGH and LTMMC , Sion, Mumbai, Maharashtra, India .
authors.forename: Vikash
authors.initials: V
authors.lastname: Kumar
authors.affiliation: Resident, Department of Urology, LTMGH and LTMMC , Sion, Mumbai, Maharashtra, India .
authors.forename: Gaurav
authors.initials: G
authors.lastname: Kasat
authors.affiliation: Professor and HOD, Department of Urology, LTMGH and LTMMC , Sion, Mumbai, Maharashtra, India .
authors.forename: Ajit
authors.initials: A
authors.lastname: Sawant
keywords: Aged; Mucinous adenocarcinoma; Rectus abdominus