title: Anesthetic Management of a Child With Jeune Syndrome for Tracheotomy: A Case Report.
abstract: Jeune syndrome is a rare autosomal-recessive skeletal disorder. Anesthetic management of these patients is often difficult because of thoracic and lung hypoplasia. A 5-month-old boy with Jeune syndrome was scheduled to undergo a tracheotomy. Despite 5-minute preoxygenation with continuous positive airway pressure, the patient's oxygen saturation rapidly dropped during the induction of anesthesia. The continuous positive airway pressure should have been titrated to effective tidal volume during preoxygenation to recruit the patient's functional residual capacity and to prevent desaturation. During tracheotomy, volume-controlled ventilation with a high respiratory rate and sufficient inspiratory time effectively improved the patient's respiratory status.
authors.affiliation: From the *Department of Anesthesiology, Faculty of Medicine, University of Yamanashi, Yamanashi, Japan; †Surgical Center, University of Yamanashi Hospital, University of Yamanashi, Yamanashi, Japan; and ‡Department of Anesthesia, Shizuoka Children's Hospital, Shizuoka, Japan.
authors.forename: Masakazu
authors.initials: M
authors.lastname: Kotoda
authors.forename: Tadahiko
authors.initials: T
authors.lastname: Ishiyama
authors.forename: Katsumi
authors.initials: K
authors.lastname: Okuyama
authors.forename: Takashi
authors.initials: T
authors.lastname: Matsukawa
mesh_terms: D000768:Anesthesia, General / Q000379:methods*; D045422:Continuous Positive Airway Pressure / Q000379:methods; D004613:Ellis-Van Creveld Syndrome / Q000000981:diagnostic imaging / Q000628:therapy*; D006801:Humans; D007223:Infant; D008297:Male; D010102:Oxygen Inhalation Therapy / Q000379:methods*; D013902:Radiography, Thoracic; D014140:Tracheotomy / Q000379:methods*