title: Crouzon syndrome with multiple supernumerary teeth.
abstract: Crouzon syndrome (CS) is an autosomal dominant disorder characterized by craniofacial deformities caused by the early closure of cranial sutures. It is diagnosed by the presence of a flat sphenoid bone, protrusion of eyeballs (exophthalmos), and midfacial hypoplasia. Although hypodontia is usually present in cases with CS, supernumerary teeth are rarely seen. A 16-year-old male patient with CS was referred to our clinic. He had a high forehead, beaked nose, hypertelorism, palpebral ptosis, and asymmetrical orbits. Bilateral multiple supernumerary teeth were observed in his upper and lower jaws. Early diagnosis of CS is helpful in dental and craniofacial treatment. Because of multiple facial and oral problems, this patient required a multidisciplinary treatment approach.
authors.affiliation: Department of Orthodontics, School of Dentistry, Istanbul Medipol University, Istanbul, Turkey.
authors.forename: G S
authors.initials: GS
authors.lastname: Torun
authors.affiliation: Department of Oral and Maxillofacial Radiology, School of Dentistry, Istanbul Medipol University, Istanbul, Turkey.
authors.forename: A
authors.initials: A
authors.lastname: Akbulut
mesh_terms: D000293:Adolescent; D003393:Cranial Sutures; D003394:Craniofacial Dysostosis / Q000175:diagnosis* / Q000235:genetics; D003398:Craniosynostoses / Q000235:genetics; D006801:Humans; D008297:Male; D013100:Sphenoid Bone; D014096:Tooth, Supernumerary / Q000000981:diagnostic imaging* / Q000209:etiology