title: Surgical Considerations in Total Anomalous Pulmonary Venous Connection.
abstract: Total anomalous pulmonary venous connection (TAPVC) is predominantly a neonatal congenital cardiac diagnosis in which the pulmonary veins fail to return to the left atrium. The presence or absence of obstruction defines the clinical presentation, and in the setting of obstructed pulmonary veins, this diagnosis represents a true surgical emergency. Improvements in perioperative care and refinement of surgical techniques continue to allow for improved survival and decreased morbidity. A description of the surgical anatomy and key concepts in the perioperative and surgical management of TAPVC are presented in this review.
authors.affiliation: 1 West Virginia University School of Medicine, Morgantown, WV, USA.
authors.forename: Fawwaz R
authors.initials: FR
authors.lastname: Shaw
authors.affiliation: 2 Seattle Children's Hospital, Seattle, WA, USA.
authors.forename: Jonathan M
authors.initials: JM
authors.lastname: Chen
mesh_terms: D006330:Heart Defects, Congenital / Q000175:diagnosis / Q000601:surgery; D006801:Humans; D007231:Infant, Newborn; D019990:Perioperative Care / Q000379:methods; D011667:Pulmonary Veins / Q000002:abnormalities* / Q000601:surgery; D011668:Pulmonary Veno-Occlusive Disease / Q000209:etiology / Q000601:surgery; D012587:Scimitar Syndrome / Q000175:diagnosis / Q000601:surgery*; D054079:Vascular Malformations / Q000175:diagnosis / Q000601:surgery*
keywords: cardiac surgery; cardiopulmonary bypass surgery; circulatory arrest pediatric; congenital heart disease; heart