title: Isolated Left Subclavian Artery, Complete Atrioventricular Block, and Tricuspid Atresia in a Neonate.
abstract: Isolated left subclavian artery is one of the rarer aortic arch anomalies. It has been associated with other congenital heart diseases, typically tetralogy of Fallot, double-outlet right ventricle, and atrial and ventricular septal defects. Its significant clinical implications include a left-to-right shunt from the vertebrobasilar system, which causes pulmonary overcirculation and subclavian steal. We present an unusual case of a premature infant who was diagnosed prenatally with congenital complete atrioventricular block and tricuspid atresia and was found to have an isolated left subclavian artery postnatally. The patient underwent implantation of a permanent single-chamber epicardial pacing system. To our knowledge, this combination of lesions has not been reported-and in our case, it influenced our surgical planning.
authors.forename: Kanupriya
authors.initials: K
authors.lastname: Chaturvedi
authors.forename: Deepa
authors.initials: D
authors.lastname: Prasad
authors.forename: Ravi
authors.initials: R
authors.lastname: Ashwath
authors.forename: James P
authors.initials: JP
authors.lastname: Strainic
authors.forename: Christopher S
authors.initials: CS
authors.lastname: Snyder
mesh_terms: D000015:Abnormalities, Multiple; D054537:Atrioventricular Block / Q000151:congenital* / Q000175:diagnosis / Q000601:surgery; D002304:Cardiac Pacing, Artificial; D000072226:Computed Tomography Angiography; D018618:Echocardiography, Doppler, Color; D004867:Equipment Design; D005260:Female; D018729:Fontan Procedure; D005865:Gestational Age; D006327:Heart Block / Q000151:congenital* / Q000175:diagnosis / Q000601:surgery; D006801:Humans; D007231:Infant, Newborn; D007234:Infant, Premature; D010138:Pacemaker, Artificial; D011651:Pulmonary Artery / Q000002:abnormalities / Q000000981:diagnostic imaging; D012092:Replantation; D013348:Subclavian Artery / Q000002:abnormalities* / Q000000981:diagnostic imaging / Q000601:surgery; D016896:Treatment Outcome; D018785:Tricuspid Atresia / Q000150:complications* / Q000000981:diagnostic imaging / Q000601:surgery; D054079:Vascular Malformations / Q000150:complications* / Q000000981:diagnostic imaging / Q000601:surgery
keywords: Abnormalities, multiple/diagnosis/surgery; aortic arch syndromes/complications; atrioventricular block/complications/diagnosis/etiology; ductus arteriosus/complications; heart defects, congenital/complications/surgery; infant, newborn; prenatal diagnosis; subclavian artery/abnormalities; subclavian steal syndrome/diagnosis/etiology/pathology; tricuspid atresia/diagnosis