title: Morbihan disease complicated by dermatosis neglecta: An unique presentation.
abstract: Morbihan disease, also referred to as solid facial edema, or rosacea lymphedema, is a rare disorder that involves chronic erythema and solid edema of the cheeks, eyelids, forehead and glabella and may arise as a complication of acne vulgaris or rosacea. Of note, it may be the only initial presenting symptom of these associated diseases. Few cases have been described in the literature, as its first description by Robert Degos in 1957. The condition is characterized by its chronicity, a typical clinical appearance and the lack of specific histopathologic or laboratory findings. The condition may wax and wane but typically does not resolve without treatment. Many cases of this condition tend to be recalcitrant to therapy, with topical and oral antibiotics regimens commonly used for rosacea generally being ineffective. The disease may easily go undiagnosed, as it mimics other more common skin conditions. We present a case of originally undiagnosed Morbihan disease mistaken for an atypical allergic rash, resistant to treatment, and complicated by dermatosis neglecta.
authors.affiliation: Department of Dermatology and Cutaneous Surgery, Miller School of Medicine,University of Miami, Miami, Florida.
authors.forename: Ariel E
authors.identifier: http://orcid.org/0000-0002-8802-1003
authors.initials: AE
authors.lastname: Eber
authors.affiliation: Department of Dermatology and Cutaneous Surgery, Miller School of Medicine,University of Miami, Miami, Florida.
authors.forename: Stephanie
authors.initials: S
authors.lastname: Mlacker
authors.affiliation: Department of Dermatology and Cutaneous Surgery, Miller School of Medicine,University of Miami, Miami, Florida.
authors.forename: Sebastian
authors.initials: S
authors.lastname: Verne
authors.affiliation: Department of Dermatology and Cutaneous Surgery, Miller School of Medicine,University of Miami, Miami, Florida.
authors.forename: Robert
authors.initials: R
authors.lastname: Griffith
authors.affiliation: Department of Dermatology and Cutaneous Surgery, Miller School of Medicine,University of Miami, Miami, Florida.
authors.forename: Jennifer
authors.initials: J
authors.lastname: Ledon
authors.affiliation: Department of Dermatology and Cutaneous Surgery, Miller School of Medicine,University of Miami, Miami, Florida.
authors.forename: Marina
authors.initials: M
authors.lastname: Perper
authors.affiliation: Department of Dermatology and Cutaneous Surgery, Miller School of Medicine,University of Miami, Miami, Florida.
authors.forename: Keyvan
authors.initials: K
authors.lastname: Nouri
authors.affiliation: Dermatopathology Division, Department of Pathology, Sylvester Comprehensive Cancer Center, Miami, Florida.
authors.forename: Jeong Hee
authors.initials: JH
authors.lastname: Cho-Vega
mesh_terms: D004487:Edema / Q000150:complications / Q000473:pathology; D004890:Erythema / Q000150:complications / Q000473:pathology; D005148:Facial Dermatoses / Q000150:complications / Q000473:pathology; D005260:Female; D006801:Humans; D008875:Middle Aged; D012393:Rosacea / Q000150:complications / Q000473:pathology
keywords: Morbihan; acne; acne vulgaris; dermatosis neglecta; rosacea