title: [Solitary and congenital juvenile xanthogranuloma: case report].
abstract: Juvenile xanthogranuloma is a bening pathology and it represents the most common form of non-Langerhans cell histiocytosis. It is characterized by the presence of papules or firm nodules of a pinkish or yellow-brownish nature, which mainly compromise the skin and, exceptionally, other organs. It is a self-limited entity having a spontaneous regression during the first five years of life. We report the case of a one-month-old patient who presented a congenital tumor in the abdomen, whose histopathology showed the presence of multinucleated giant Touton cells, which are typical of this pathology. We emphasize the rare occurrence of this type of lesion and the importance of the multiple differential diagnosis to be taken into account due to the age of the patient and the characteristics of the lesion.
authors.affiliation: Servicio de Dermatología, Hospital Nacional de Pediatría "Prof. Dr. Juan P. Garrahan", Ciudad Autónoma de Buenos Aires, Argentina. letilazarte@gmail.com.
authors.forename: Leticia
authors.initials: L
authors.lastname: Lazarte
authors.affiliation: Servicio de Dermatología, Hospital Nacional de Pediatría "Prof. Dr. Juan P. Garrahan", Ciudad Autónoma de Buenos Aires, Argentina.
authors.forename: Paola C
authors.initials: PC
authors.lastname: Stefano
authors.affiliation: Servicio de Dermatología, Hospital Nacional de Pediatría "Prof. Dr. Juan P. Garrahan", Ciudad Autónoma de Buenos Aires, Argentina.
authors.forename: Marcela
authors.initials: M
authors.lastname: Bocian
authors.affiliation: Servicio de Dermatología, Hospital Nacional de Pediatría "Prof. Dr. Juan P. Garrahan", Ciudad Autónoma de Buenos Aires, Argentina.
authors.forename: Verónica
authors.initials: V
authors.lastname: Solernou
authors.affiliation: Servicio de Dermatología, Hospital Nacional de Pediatría "Prof. Dr. Juan P. Garrahan", Ciudad Autónoma de Buenos Aires, Argentina.
authors.forename: Adrián Martín
authors.initials: AM
authors.lastname: Pierini
authors.affiliation: Servicio de Dermatología, Hospital Nacional de Pediatría "Prof. Dr. Juan P. Garrahan", Ciudad Autónoma de Buenos Aires, Argentina.
authors.forename: Andrea Bettina
authors.initials: AB
authors.lastname: Cervini
mesh_terms: D005260:Female; D006801:Humans; D007223:Infant; D014972:Xanthogranuloma, Juvenile / Q000151:congenital* / Q000175:diagnosis
keywords: abdominal wall; histiocytosis; juvenile xanthogranuloma; non-Langerhans cell