title: Pulmonary Alveolar Proteinosis in Association with Secondary Hemophagocytic Lymphohistiocytosis.
abstract: Pulmonary alveolar proteinosis (PAP) is a rare diffuse lung disease in the pediatric population. There are currently few cases documenting hemophagocytic lymphohistiocytosis as a cause for secondary PAP. We describe an ex-preterm child with secondary hemophagocytic lymphohistiocytosis, complicated by PAP and hypoxemic respiratory failure.
authors.affiliation: Division of Pediatric Respiratory and Sleep Medicine, The Children's Hospital at Montefiore, Albert Einstein College of Medicine, Bronx, NY. Electronic address: JENLIN@montefiore.org.
authors.forename: Jenny
authors.initials: J
authors.lastname: Lin
authors.affiliation: Division of Pediatric Respiratory and Sleep Medicine, The Children's Hospital at Montefiore, Albert Einstein College of Medicine, Bronx, NY.
authors.forename: Aliva
authors.initials: A
authors.lastname: De
authors.affiliation: Division of Pediatric Hematology/Oncology, The Children's Hospital at Montefiore, Albert Einstein College of Medicine, Bronx, NY.
authors.forename: Lisa
authors.initials: L
authors.lastname: Figueiredo
authors.affiliation: Division of Pediatric Hospitalist Medicine, The Children's Hospital at Montefiore, Albert Einstein College of Medicine, Bronx, NY.
authors.forename: Rochelle
authors.initials: R
authors.lastname: Maxwell
authors.affiliation: Division of Pediatric Hospitalist Medicine, The Children's Hospital at Montefiore, Albert Einstein College of Medicine, Bronx, NY.
authors.forename: Emily
authors.initials: E
authors.lastname: Wasserman
authors.affiliation: Division of Pediatric Respiratory and Sleep Medicine, The Children's Hospital at Montefiore, Albert Einstein College of Medicine, Bronx, NY.
authors.forename: Kelly
authors.initials: K
authors.lastname: Adams
authors.affiliation: Division of Pediatric Critical Care Medicine, The Children's Hospital at Montefiore, Albert Einstein College of Medicine, Bronx, NY.
authors.forename: Jacqueline
authors.initials: J
authors.lastname: Weingarten
authors.affiliation: Division of Pediatric Cardiothoracic Surgery, The Children's Hospital at Montefiore, Albert Einstein College of Medicine, Bronx, NY.
authors.forename: Giles
authors.initials: G
authors.lastname: Peek
authors.affiliation: Division of Pediatric Critical Care Medicine, The Children's Hospital at Montefiore, Albert Einstein College of Medicine, Bronx, NY.
authors.forename: Michael
authors.initials: M
authors.lastname: Miksa
mesh_terms: D000015:Abnormalities, Multiple / Q000175:diagnosis / Q000628:therapy; D001707:Biopsy, Needle; D003131:Combined Modality Therapy; D005260:Female; D005500:Follow-Up Studies; D006801:Humans; D007150:Immunohistochemistry; D007223:Infant; D051359:Lymphohistiocytosis, Hemophagocytic / Q000150:complications / Q000175:diagnosis* / Q000628:therapy*; D011649:Pulmonary Alveolar Proteinosis / Q000150:complications / Q000175:diagnosis* / Q000628:therapy*; D013902:Radiography, Thoracic / Q000379:methods; D035583:Rare Diseases; D012121:Respiration, Artificial; D012131:Respiratory Insufficiency / Q000175:diagnosis / Q000209:etiology / Q000628:therapy; D018570:Risk Assessment; D012720:Severity of Illness Index; D014057:Tomography, X-Ray Computed / Q000379:methods; D014139:Tracheostomy / Q000379:methods; D016896:Treatment Outcome