title: Hirayama Disease: A Rare Disease with Unusual Features.
abstract: Hirayama disease, also known as monomelic amyotrophy (MMA), is a rare cervical myelopathy that manifests itself as a self-limited, asymmetrical, slowly progressive atrophic weakness of the forearms and hands predominantly in young males. The forward displacement of the posterior dura of the lower cervical dural canal during neck flexion has been postulated to lead to lower cervical cord atrophy with asymmetric flattening. We report a case of Hirayama disease in a 25-year-old Indian man presenting with gradually progressive asymmetrical weakness and wasting of both hands and forearms along with unusual features of autonomic dysfunction and upper motor neuron lesion.
authors.affiliation: Department of Medicine, Maulana Azad Medical College and Associated Hospitals, New Delhi 110002, India.
authors.forename: S
authors.identifier: 0000-0001-9116-7233
authors.initials: S
authors.lastname: Anuradha
authors.affiliation: Department of Medicine, Maulana Azad Medical College and Associated Hospitals, New Delhi 110002, India.
authors.forename: Vanlalmalsawmdawngliana
authors.initials: V
authors.lastname: Fanai