title: Wide QRS in a 2-month infant associated with recurrent ventricular tachycardia: A case of Brugada-like syndrome.
abstract: We report the case of a 2-month old infant who experienced recurrent sustained ventricular tachycardia (VT) in a structurally normal heart. Resting electrocardiogram (ECG) showed wide QRS with a complete right bundle branch bloc (RBBB) morphology. There was no family history of syncope or sudden death, but the ECGs of the father and the brother showed incomplete RBBB with negative T waves on V1 lead. This case seems to fit well with the newly defined entity of Brugada-like syndrome with a highly suspected genetic underlying disposition.
authors.affiliation: Cardiology B department, Fattouma Bourguiba University Hospital and University of Monastir, avenue du 1er Juin, 5000 Monastir, Tunisia. Electronic address: jomaa_w@hotmail.fr.
authors.forename: W
authors.initials: W
authors.lastname: Jomaa
authors.affiliation: Cardiology B department, Fattouma Bourguiba University Hospital and University of Monastir, avenue du 1er Juin, 5000 Monastir, Tunisia.
authors.forename: W
authors.initials: W
authors.lastname: Selmi
authors.affiliation: Cardiology B department, Fattouma Bourguiba University Hospital and University of Monastir, avenue du 1er Juin, 5000 Monastir, Tunisia.
authors.forename: S
authors.initials: S
authors.lastname: Hamdi
authors.affiliation: Cardiology B department, Fattouma Bourguiba University Hospital and University of Monastir, avenue du 1er Juin, 5000 Monastir, Tunisia.
authors.forename: M A
authors.initials: MA
authors.lastname: Azaiez
authors.affiliation: Cardiology B department, Fattouma Bourguiba University Hospital and University of Monastir, avenue du 1er Juin, 5000 Monastir, Tunisia.
authors.forename: A
authors.initials: A
authors.lastname: El Hraiech
authors.affiliation: Cardiology B department, Fattouma Bourguiba University Hospital and University of Monastir, avenue du 1er Juin, 5000 Monastir, Tunisia.
authors.forename: K
authors.initials: K
authors.lastname: Ben Hamda
authors.affiliation: Cardiology B department, Fattouma Bourguiba University Hospital and University of Monastir, avenue du 1er Juin, 5000 Monastir, Tunisia.
authors.forename: F
authors.initials: F
authors.lastname: Maatouk
mesh_terms: D053840:Brugada Syndrome / Q000175:diagnosis* / Q000235:genetics; D002037:Bundle-Branch Block / Q000175:diagnosis / Q000235:genetics; D004252:DNA Mutational Analysis; D003937:Diagnosis, Differential; D004562:Electrocardiography; D006801:Humans; D007223:Infant; D008297:Male; D012008:Recurrence; D015222:Sodium Channels / Q000235:genetics; D017180:Tachycardia, Ventricular / Q000175:diagnosis* / Q000235:genetics
chemical_list: D015222:Sodium Channels
keywords: Brugada syndrome; Infant; Nourrisson; Syndrome de Brugada; Tachycardie ventriculaire; Ventricular tachycardia