title: A case of proteinase 3 anti-neutrophil cytoplasmic antibody (PR3-ANCA) positive/IgG4-related lung disease.
abstract: IgG4-related lung disease (IgG4-RLD) is a rare and chronic progressive autoimmune disease. We report a case of IgG4-related inflammatory pseudo-tumor of the lung that was seropositive for proteinase 3 anti-neutrophil cytoplasmic antibody (PR3-ANCA). A 61-year-old male had a mass lesion in the right lower lung field in chest X-ray. Transbronchial lung biopsy resulted in a pathological diagnosis of IgG4-RLD. The condition was improved by hormonal therapy.
authors.affiliation: Department of Respiratory Medicine, Yonago Medical Centre, Tottori, Japan.
authors.forename: Hirokazu
authors.initials: H
authors.lastname: Touge
authors.affiliation: Department of Respiratory Medicine, Yonago Medical Centre, Tottori, Japan.
authors.forename: Katsuyuki
authors.initials: K
authors.lastname: Tomita
authors.affiliation: Division of Medical Oncology and Molecular Respirology, Tottori University Faculty of Medicine, Tottori, Japan.
authors.forename: Akira
authors.initials: A
authors.lastname: Yamasaki
authors.affiliation: Division of Medical Oncology and Molecular Respirology, Tottori University Faculty of Medicine, Tottori, Japan.
authors.forename: Eiji
authors.initials: E
authors.lastname: Shimizu
keywords: IgG4; Lung; PR3-ANCA